scholarly journals Leiomyosarcoma of vascular origin: a rare presentation

2019 ◽  
Vol 6 (10) ◽  
pp. 3841
Author(s):  
Sreeramulu P. N. ◽  
Nipun A. C. ◽  
Anup . ◽  
Vikranth N. Suresh
Keyword(s):  
Soft Tissue ◽  
Smooth Muscles ◽  
Vena Cava ◽  
Soft Tissue Neoplasm ◽  
Rare Presentation ◽  
Rare Type ◽  
Adjacent Structures ◽  
Vascular Origin ◽  
The Right ◽  
Malignant Soft Tissue

Malignant soft tissue neoplasm exhibiting smooth muscle differentiation is called leiomyosarcoma (LMS). LMS arising from the smooth muscles of tunica media of the major blood vessels like inferior vena cava (IVC) is a rare type of neoplasm, accounting for less than 0.5% of adult soft tissue sarcoma, affecting <1/1,00,000 of all adult malignancies. The prognosis of this tumor is poor, as patients often present with intra or extra-luminal growth often with invasion of adjacent structures. Only 400 cases of IVC LMS have been reported. Here we report a case of 40 year old female with large asymptomatic mass per abdomen of 3 months duration occupying the central and right part of abdomen. Investigations revealed a large retroperitoneal mass of 20.4*22.8*22.5 cms arising from the right kidney, likely Renal cell carcinoma. On exploration a huge tumor of size 25*25*20 cms was seen arising from retroperitoneum on right side, right kidney its vessels and ureter could not be seen separately. IVC could not be delineated. Histopathology report revealed it to be LMS of vascular origin. We report one such case because although incidence of such cases is low but should be considered in the differential diagnosis of mass per abdomen which grows unusually fast.

scholarly journals Emphysematous pyelonephritis with air bubble in the inferior vena cava

2020 ◽  
Vol 26 (1) ◽  
Author(s):  
Tiffany A. Perkins ◽  
Alberic Rogman ◽  
Murali K. Ankem
Keyword(s):  
Septic Shock ◽  
Inferior Vena Cava ◽  
Inferior Vena ◽  
Vena Cava ◽  
Rare Presentation ◽  
Emphysematous Pyelonephritis ◽  
Case Presentation ◽  
Air Bubble ◽  
First Case ◽  
The Right

Abstract Background Emphysematous pyelonephritis (EPN) with gas in the inferior vena cava (IVC) is a rare presentation and to our knowledge, this is the first case report in the urologic literature. Case presentation A 35-Year-old obese diabetic Hispanic female presented to the emergency room with a clinical picture of septic shock. Prompt computerized tomography scan revealed EPN with gas throughout the right renal parenchyma and extending to the right renal vein, IVC, and pulmonary artery. She died before surgical intervention Conclusion This case demonstrates that patients presenting with severe EPN have a high mortality risk and providers should acknowledge that septic shock, endogenous air emboli, or a combination of both could result in cardiovascular collapse and sudden death.

scholarly journals Confirmation of ovarian follicles in an enantiornithine (Aves) from the Jehol biota using soft tissue analyses

2020 ◽  
Vol 3 (1) ◽  
Author(s):  
Alida M. Bailleul ◽  
Jingmai O’Connor ◽  
Zhiheng Li ◽  
Qian Wu ◽  
Tao Zhao ◽  
...  
Keyword(s):  
High Resolution ◽  
Soft Tissue ◽  
Smooth Muscles ◽  
Ovarian Follicles ◽  
Tissue Preservation ◽  
Jehol Biota ◽  
Avian Evolution ◽  
The Right ◽  
Original Interpretation ◽  
Contractile Structure

AbstractThe remains of ovarian follicles reported in nine specimens of basal birds represents one of the most remarkable examples of soft-tissue preservation in the Early Cretaceous Jehol Biota. This discovery was immediately contested and the structures alternatively interpreted as ingested seeds. Fragments of the purported follicles preserved in an enantiornithine (STM10-12) were extracted and subjected to multiple high-resolution analyses. The structures in STM10-12 possess the histological and histochemical characteristics of smooth muscles fibers intertwined together with collagen fibers, resembling the contractile structure in the perifollicular membrane (PFM) of living birds. Fossilized blood vessels, very abundant in extant PFMs, are also preserved. Energy Dispersive Spectroscopy shows the preserved tissues primarily underwent alumino-silicification, with minor mineralization via iron oxides. No evidence of plant tissue was found. These results confirm the original interpretation as follicles within the left ovary, supporting the interpretation that the right ovary was functionally lost early in avian evolution.

scholarly journals P169 Uterine leiomyoma extension into right side cardiac

2020 ◽  
Vol 21 (Supplement_1) ◽  
Author(s):  
K Diniz Ferrer ◽  
CARLOS Silveira ◽  
ADRIAN Reis ◽  
PAULA Abreu E Lima ◽  
ROBERT Diniz ◽  
...  
Keyword(s):  
Inferior Vena Cava ◽  
Right Atrium ◽  
Uterine Leiomyoma ◽  
Inferior Vena ◽  
Tumor Resection ◽  
Vena Cava ◽  
Cardiac Imaging Techniques ◽  
First Case ◽  
Adjacent Structures ◽  
The Right

Abstract Funding Acknowledgements governmental grants Uterine leiomyoma is a commom disease in women, however, intravenous leiomyomatosis of uterine origin extending via inferior vena cava into the right side of the heart,known as intracardiac leiomyomatosis is a rare condition (3%). In 1907, Durk reported the first case of intracardiac extension. The patient was a Woman, 35 years old, admitted to our emergency department for an intracardiac mass. She had shortness of breath,fatigue and chest pain. The transthoracic two dimensional echocardiography showed an echogenic oval mass mobile in right atrium and projected through right ventricle in diastole. This mass was observed to extend from inferior vena cava to the right atrium. The echotransesophageal three dimensional showed a large mobile mass that extended from inferior vena cava to the right atrium. A Computer tomographic (CT) scan showed a hypodense multilobulated mass in the pelvis, which had invaded the inferior vena cava and right atrium. The patient underwent a two stages surgery. In first stage (transatrial tumor resection). The operation was performed normal temperature with establisment of cardiopulmonary bypass (CPB). Subsequently, the pathological report was confirmed uterin smooth muscle origin. The second stage surgery ( total histerectomy) was done four weeks later for removing lobulated mass uterin with dimensions 20x15x7.5cm with confirmed histopathological of leiomyoma. Because of it is nonspecific clinical presentation and rarity, an intracardiac Leiomyomatosis continues to be a misdiagnosed as either thrombus or myxoma. The cardiac imaging techniques like a transthoracic echocardiography 2d and transesophageal echocardiography 3d have been used to define the presence, extension of tumor as appearance of the mass and involvement of adjacent structures. Abstract P169 Figure. Echotransesophageal 3D (bicaval view)

scholarly journals Primary Extraskeletal Myxoid Chondrosarcoma: A Case Report

2021 ◽  
Author(s):  
Renuka Bangalore Nagaraj ◽  
Arshiya Sultana
Keyword(s):  
Case Report ◽  
Soft Tissue ◽  
Histopathological Examination ◽  
Matrix Material ◽  
Needle Aspiration ◽  
Extraskeletal Myxoid Chondrosarcoma ◽  
Soft Tissue Neoplasm ◽  
Rare Tumour ◽  
Myxoid Chondrosarcoma ◽  
Malignant Soft Tissue

Extraskeletal Myxoid Chondrosarcoma (EMC) is a rare malignant soft tissue sarcoma with uncertain differentiation, most often seen in males. The incidence is 3% of all soft tissue tumours with limited literature available on its cytological features. EMC may arise from lower extremities, upper extremities, retroperitoneum, pelvis, and buttocks. This case report was an effort to understand the role of Fine Needle Aspiration Cytology (FNAC), histopathology and immunochemistry in the diagnosis of EMC. Authors hereby report a case of a 70-year-old male patient with slow-growing soft tissue swelling on the back just behind the right shoulder who was referred for FNAC. Patient complete history and clinical findings were recorded. Radiological images were suggestive of malignant soft tissue neoplasm with no involvement of underlining bone. FNAC reveled tumour cells which appeared monotonous and they were seen in a myxoid stroma background. Subsequently, the excised lesion was sent for histopathological examination and the report revealed the presence of abundant chondromyxoid matrix material within which were found numerous elongated spindly shaped cells. These cells had moderately pleomorphic elongated nuclei with focal solid fibrocollagenous areas along intersecting fascicles of the moderately pleomorphic spindly cell. Few of these cells had multilobulated bizarre nuclei with nuclear inclusions. Immunohistochemical stains showed diffuse positivity for S-100, vimentin, and focally positive for Epithelial Membrane Antigen (EMA). The FNAC, histopathology and immunohistochemical features confirm the diagnosis of EMC on right shoulder. It’s a rare tumour whose diagnosis is made depending on history, clinical location, growth pattern, histopathology, and immunohistochemistry.

CASE REPORT : LIPOSARCOMA OF THE SHOULDER

2021 ◽  
pp. 35-36
Author(s):  
Tannistha Chakraborty ◽  
Vamsi Krishna ◽  
T. Raghupathy
Keyword(s):  
Soft Tissue ◽  
Soft Tissue Tumor ◽  
Benign Neoplasm ◽  
Soft Tissue Tumours ◽  
Long Duration ◽  
Cutaneous Localization ◽  
History Of ◽  
Local Radiation ◽  
The Right ◽  
Malignant Soft Tissue

Lipoma, a benign neoplasm of adipocytes, is the most common mesenchymal soft tissue tumor of adulthood, but rarely present with huge sizes in their cutaneous localization. Liposarcomas are the second most common soft tissue sarcoma following malignant brous histiocytoma. They comprise approximately 16-18% of all malignant soft tissue tumours. It is most common in the trunk followed by lower extremity, upper extremity and head and neck.. While lipomas can be clinically diagnosed , transformation of lipomas into liposarcoma is rare. Here we report the case of a 55 gentleman, who came with a history of swelling over the right shoulder with a probable malignant transformation due to history of long duration of presence of swelling. Management is usually by wide excision. Local radiation and chemotherapy may be necessary for high grade lesions.

Giant mantle cell lymphoma in the soft tissue of the leg: rare presentation

2021 ◽  
pp. 030089162110019
Author(s):  
Büşra Erşan Erdem ◽  
Umay Kiraz ◽  
Çiğdem Vural ◽  
Halil Atmaca ◽  
Ahmet Tuğrul Eruyar
Keyword(s):  
Bone Marrow ◽  
Soft Tissue ◽  
Mantle Cell Lymphoma ◽  
Cell Lymphoma ◽  
Clinical History ◽  
Case Description ◽  
Rare Presentation ◽  
Common Presentation ◽  
Mantle Cell ◽  
The Right

Background: Mantle cell lymphomas are aggressive, mature B-cell neoplasms characteristically showing overexpression of cyclin D1. Although lymphadenopathy is the most common presentation, involvement of extranodal sites including bone marrow, peripheral blood, liver, gastrointestinal system, and Waldeyer ring is also seen frequently. Soft tissue localization is extremely rare. It has blastoid and pleomorphic subtypes associated with aggressive course. Case description: We describe a 74-year-old man who had been diagnosed 3 years previously with “mantle cell lymphoma-blastoid type” and presented 3 months ago with a giant mass in the right lower extremity that enlarged rapidly up to 15 cm in a few months. Conclusion: We present this rare presentation, which was evaluated in favor of hemangioma before biopsy, together with the data in the literature to emphasize the need for differential diagnosis, especially in cases with a clinical history.

Granulosa Cell Tumour – A Rare Presentation at Age Twenty

2020 ◽  
Author(s):  
Munazza Anis
Keyword(s):  
Granulosa Cell ◽  
Tertiary Care ◽  
Granulosa Cell Tumor ◽  
Cell Tumor ◽  
Care Hospital ◽  
Age Group ◽  
Rare Presentation ◽  
Rare Type ◽  
Juvenile Granulosa Cell Tumor ◽  
The Right

Granulosa cell tumor is a rare type of ovarian tumor, which arises from sex cord stroma. Histologically this tumor has two types and is named according to the common age group they affect; adult granulosa cell tumor (AGCT) and juvenile granulosa cell tumor. AGCT constitutes 2-5% of all ovarian cancers. Mostly present in women of age > 40 years. In this case report, we discussed the role of conservative surgery in young adult reported with granulosa cell tumor. An unmarried teenage girl presented at a private tertiary care hospital with abdominal pain and abdominal distention. Radiological examinations suggested a mass originating from the right ovary for which laparotomy was done and a ruptured cyst was found near the right ovary with a mass adherent to surrounding peritoneal viscera. Right ovarian cystectomy along with omental biopsy and left ovarian biopsy was performed. Rare presentation of this tumor will help clinicians to not categorize the type histologically with the age group.

scholarly journals Hematemesis, a Rare Presentation for Downhill Esophageal Varices

2021 ◽  
pp. 359-364
Author(s):  
Jeremy Van ◽  
Shubha Singh
Keyword(s):  
Blood Flow ◽  
Esophageal Varices ◽  
Inferior Vena ◽  
Superior Vena ◽  
Vena Cava ◽  
Disease Process ◽  
Rare Presentation ◽  
Retrograde Blood Flow ◽  
Flow Through ◽  
The Right

Downhill esophageal varices (DEV) are a rare form of esophageal varices associated with superior vena cava obstruction. Obstruction leads to retrograde blood flow through collateral venous channels, including the esophageal venous plexus, to redirect blood flow to the right atrium via the inferior vena cava. This leads to the formation of DEV. It is a rare phenomenon to have gastrointestinal bleeding, especially hematemesis, on a patient’s first presentation with this disease process. We describe such a case here involving a patient with DEV secondary to metastatic renal cell carcinoma presenting with hematemesis.

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