scholarly journals Primary cardiac hemangioendothelioma of the right ventricle

Author(s):  
Xiaoyan Chen ◽  
Jianxiu Fang ◽  
Qingmei Yang ◽  
Haifeng Guo

Primary cardiac hemangioendothelioma is a very rare low-grade malignancy. We present a case of a 41-year-old female patient with a huge primary cardiac hemangioendothelioma that arose from the right ventricle was recurred after being removed, and the diagnostic images given by echocardiography.

2012 ◽  
Vol 10 (1-2) ◽  
pp. 0-0
Author(s):  
Edgaras Kulikauskas ◽  
Eligijus Poškus ◽  
Dileta Rutkauskaitė ◽  
Kęstutis Strupas

Edgaras Kulikauskas1, Eligijus Poškus1, Dileta Rutkauskaitė2, Kęstutis Strupas1 1Vilniaus universiteto ligoninės Santariškių klinikų Gastroenterologijos, nefrologijos, urologijos ir abdominalinės chirurgijos klinika, Santariškių g. 2, LT-08661 Vilnius2Vilniaus universiteto Medicinos fakulteto Krūtinės ligų, alergologijos ir radiologijos klinika, Santariškių g. 2, LT-08661 Vilnius El. paštas: [email protected] Pirminiai retroperitoniniai navikai yra reti, pasižymintys didele histologine įvairove. Apie 80 proc. pirminių retroperitoninio tarpo navikų yra piktybiniai, o gerybinės lipomos šioje vietoje aptinkamos labai retai. Augdamos lėtai lipomos gali pasiekti 20 cm dydį ir kelių kilogramų svorį, nesukeldamos ryškesnės simptomatikos. Šių nepiktybinių navikų diagnostika remiasi radiologiniais tyrimais. Atskirti lipomas nuo piktybinių riebalinių navikų, ypač geros diferenciacijos liposarkomomis, kurios retai metastazuoja, tačiau pasižymi dideliu recidyvų dažnumu, gali būti labai sudėtinga. Dėl šių priežasčių riebaliniai retroperitoninio tarpo navikai turi būti vertinami kaip liposarkomos, kol neįrodoma kitaip. Radikalus chirurginis naviko pašalinimas yra pirmiausia pasirenkamas gydymo metodas.Pateikiame klinikinį retroperitoninės lipomos, nustatytos 61 metų amžiaus vyrui, gydymo atvejį. Navikas diagnozuotas remiantis klinika ir kompiuterinės tomografijos tyrimu. Operacijos metu rasta ir pašalinta 40 × 40 × 20 cm dydžio, 6500 g svorio lipoma, diagnozė patvirtinta histologinio tyrimo metu. Devintą parą po operacijos, ligonis išrašytas į namus. Reikšminiai žodžiai: retroperitoninis tarpas, lipoma, chirurgija. Giant retroperitoneal lipoma: case report and literature review Edgaras Kulikauskas1, Eligijus Poškus1, Dileta Rutkauskaitė2, Kęstutis Strupas1 1Clinic of Gastroenterology, Urology and Abdominal Surgery, Vilnius University Hospital “Santariškių klinikos”, Santariškių Str. 2, LT-08661 Vilnius, Lithuania2Vilnius University, Medical Faculty, Clinic of Chest Diseases, Allergology and Radiology, Santariškių Str. 2, LT-08661 Vilnius, Lithuania E-mail: [email protected] Primary retroperitoneal tumours are rare and show a high histological variety. About 80% of retroperitoneal tumours are malignant; benign lipomas in this location are exceptionally rare. These slow-growing tumors can grow up to more than 20 cm and weight a few kilograms. The differential diagnosis of lipomas with liposarcomas may be problematic, especially for tumours with low-grade malignancy, which have a predilection for local recurrence but do not generally metastatize. Fatty tumours of the retroperitoneum should be considered to be potential liposarcomas until proven otherwise, and a radical lesion excision should always be performed, if possible.We report a case of a giant retroperitoneal lipoma in a 61-year-old male. A CT scan of his abdomen showed a large mass of fat density displacing organs to the right side. The patient underwent a radical tumour excision. Laparotomy showed a giant fatty mass measuring 40 x 40 x 20 cm and weighing 6500 g. The pathological examination revealed benign lipoma. The patient was discharged home on postoperative day 9. Key words: retroperitoneal space, lipoma, surgery


2020 ◽  
Vol 8 (10) ◽  
pp. 1263-1267
Author(s):  
Abdulrahman M. Bin Mohi ◽  
◽  
Ahmed A. Alzahrani ◽  
Bashar R. Reda

Chondromais considered a nonmalignant tumor that composed of mature hyaline cartilage and commonly occur in hands and feet. Overall incidents show that females are predominant comparing to males with evenly distributed range of ages. Multiple chondromas have to be differentiated from osteochondroma and chondrosarcoma. This paper reports three different types of lesions in one patient.Osteochondroma or exostosis is the most common benign tumor of the skeleton. It is a developmental osseous anomaly, which arises from exophytic outgrowth on bone surfaces characteristically. Osteochondroma account for about 12% of bone tumors. Here, we have described a 22 years old female patient with left knee joint pain and swelling of the left distal femur with limited movements. The incisional biopsy of the left distal femur identified low-grade chondrosarcoma and chondroma after histopathology. This underwent one-stage surgical excision of the tumor with a posterior approach and tumor resection from the femur. After surgery, an unusual pain appears in the right hip joint during the post-operative period.Machine resonance imaging (MRI), and X-ray of pelvis help to diagnose thewell-differentiated chondrosarcoma and chondroma. This was a case of osteochondroma in the right proximal femur, chondroma like lesion in the left proximal femur and chondrosarcoma in the left distal femur. Ethical consideration: Written informed consent was obtained from the patient for publication of this case report and accompanying images. Conflict of interest: There is no conflict of interest.


2011 ◽  
Vol 4 (4) ◽  
pp. 219
Author(s):  
Chad A. Reade ◽  
Apar Kishor Ganti ◽  
Anne Kessinger

Epithelioid hemangioendothelioma (EHE) is a rare vascular-derived malignancy. Within the thorax, EHE originating in the pleura is less often reported than EHE originating in the lung. Pulmonary EHE has been referred to as a borderline or low-grade malignancy that exhibits an unpredictable course. It often is associated with a long life expectancy and occasional spontaneous remission. Because the natural history of pleural EHE is less well understood, a literature review was conducted to investigate the characteristics of the disease. Twenty-two cases of pleural EHE were identified. The disease occurred more often in men than women, appeared in the right thorax more often than the left, exhibited a virulent course, was usually refractory to systemic therapy, and was often associated with a short survival. These characteristics differ substantially from those of pulmonary EHE and suggest that the clinician should approach pleural EHE anticipating an especially aggressive malignancy which likely will not respond to current therapeutic measures.


The Clinician ◽  
2019 ◽  
Vol 13 (1-2) ◽  
pp. 65-71
Author(s):  
N. S. Chipigina ◽  
N. Yu. Karpova ◽  
M. M. Tulinov ◽  
E. V. Golovko ◽  
L. M. Goloukhova ◽  
...  

Objective: to describe a rare case of infective endocarditis (IE) with isolated localization in the pulmonary valve (PV).Materials and methods. We observed primary IE with isolated localization in the PV in a 27-year-old female patient without risk factors of right-side IE.Results. The disease was caused by Streptococcus gordonii and proceeded acutely with typical signs of right-side IE: fever above 38 °С, chills, clinical picture of bilateral septic embolic abscess pneumonia, as well as secondary anemia, secondary thrombocytopenia, and glomerulonephritis. Echocardiography showed large vegetations in the PV prolapsing in the right ventricle and pulmonary artery.Conclusion. IE with localization in the PV should be suspected in patients with fever and clinical picture of septic embolic pneumonia in absence of other embolic situations.


2007 ◽  
Vol 135 (7-8) ◽  
pp. 468-471 ◽  
Author(s):  
Milan Stojanovic ◽  
Branislav Goldner ◽  
Spasenija Djukic

Introduction Liposarcoma of a bone is a very rare tumor of the fatty marrow, originating from lipoblasts. Its frequency is 1:1000 of all bone tumors. The long bones and the lower extremities are predominantly affected, equally in males and females between 30 and 70 years of age. In the estimation of its biological behavior, histological graduation (G), the surgical localization of the tumor (T) and the presence or absence of metastases (M), are very important. A tumor with low grade differentiation, with transosseal propagation and metastases, has a poor prognosis. Surgical resection-amputation, chemotherapy and radiotherapy are the therapeutic methods of choice. Case outline Twelve years ago, in a 58-year old man, there was a radiologically diagnosed sarcoma in the lower part of the right femur manifested with painful swelling in that region. The high suprapatellar amputation was done. There was a histologically proved liposarcoma of a high grade of malignancy. According to the therapeutic protocol, chemotherapy and radiotherapy were applied. During the period of 12 years, the patient had a relapse on the stump, metastatic dissemination in the soft tissue of small pelvis twice, once in the left scapular region and in the inguinal lymph nodes, six operations and 8-year accumulation of metastatic deposits in the lung. Now, the patient feels relatively well, mobile, and walks 5 kilometres every day. Conclusion Unusual behaviour of the liposarcoma of high grade malignancy with which the patient has been living for 12 years, could be explained by the patient?s strong immunobiological system in the struggle to retain its vitality and mobility.


2017 ◽  
Vol 9 (12) ◽  
pp. E1084-E1087 ◽  
Author(s):  
Jong Hui Suh ◽  
Do Yeon Kim ◽  
Jeong Seob Yoon ◽  
Eun Su Park ◽  
Chan Beom Park

2001 ◽  
Vol 15 (4) ◽  
pp. 267-270 ◽  
Author(s):  
Rie Yasui ◽  
Toru Minatogawa ◽  
Naoyuki Kanoh ◽  
Yasuo Nakata ◽  
Akira Kubota

Nasal hemangiopericytoma-like (HPCL) tumor is a rare vascular tumor and should be differentiated from typical hemangiopericytomas (HPCs). This study reports the case of an HPCL tumor in a 77-year-old man with histological and immunohistochemical features. After preoperative evaluation of the blood supply, the dark-red right intranasal tumor was resected completely via the right maxillary sinus. The final histopathological diagnosis was HPCL tumor based on several stains: vimentin (+), α-SMA (+), etc. Moreover, there were few p53 (+) cells and the Ki-67 and topoisomerase IIα labeling indices were both under 5%. These findings indicated that this tumor was a low-grade malignancy. The immunohistochemical investigations used are useful for making the diagnosis of HPCL tumor and determining the treatment, malignancy, and prognosis. (American Journal of Rhinology 15 267–270, 2001)


Author(s):  
Kenya Kobayashi ◽  
Yasuji Miyakita ◽  
Fumihiko Matsumoto ◽  
Go Omura ◽  
Satoko Matsumura ◽  
...  

AbstractIn traditional craniofacial resection of tumors invading the anterior skull base, the bilateral olfactory apparatus is resected. Recently, transnasal endoscopy has been used for olfactory preservation in resections of unilateral low-grade malignancies. However, for tumors that invade the orbita or for high-grade malignancies, the transnasal endoscopic skull base surgery has been controversial. This video demonstrates the surgical techniques of olfactory preservation during craniofacial resection of a high-grade malignancy invading the hemianterior skull base and orbita.We present the case of a 32-year-old woman with osteosarcoma in the right ethmoid sinus. The tumor invaded the ipsilateral cribriform plate, dura menta, and orbital periosteum; however, the nasal septum and crista galli were intact (Fig. 1A, B). Because the tumor was a high-grade malignancy and the orbita had been invaded, we performed craniofacial resection instead of endoscopic resection (Fig. C2A). We drilled into the right side of the crista galli, midline of the cribriform plate, and perpendicular plate of the ethmoid bone via craniotomy. As a result, we accessed the nasal cavity directly (Fig. 2B). To preserve the nasal septum, we detached the remaining right septal mucosa through the transfacial approach (Fig. 2C). Because of the high risk of cerebrospinal fluid leakage as a result of previous irradiation, we performed vascularized free flap reconstruction of the skull base instead of pericranial flap.Postoperative computed tomography revealed no evidence of tumor (Fig. 1C, D). The patient's sense of smell returned after 1 postoperative day, and she was discharged on the postoperative day 14.The link to the video can be found at: https://youtu.be/XzPABYwzkjs.


2021 ◽  
Author(s):  
Chunsen Li ◽  
Mengqiao Wang ◽  
Hongwei Dang ◽  
Yan Pan ◽  
Yi Liu ◽  
...  

Abstract BackgroundPrimitive myxoid mesenchymal tumor of infancy (PMMTI) is a rare tumor and its molecular mechanism and prognosis remain unclear. We here report a case of PMMTI, and review the reported literature of PMMTI.Case presentationA one-year-old boy found a lump in his right groin. The size of the mass was 1 cm×1 cm. Computed tomography showed a round, slightly dense shadow of 38 mm×32 mm in the right groin. The tumor was removed for pathological examination, and the size of the tumor was 6.0 cm×5.0 cm×3.0 cm. Tumor cells are diffusely distributed, mainly spindle cells. The blood vessels were abundant, many adipocytes can be observed in some areas, and focal lymphocyte infiltration can be seen in a few areas. Immunophenotype was as follows: histone H3 at lysine 27 (H3K27me3), B-cell lymphoma 6 corepressor (BCOR) and Bcl-2 were positive, cluster of differentiation 99 (CD99) showed diffuse reactivity, BCL6 was scattered positive, Ki-67 proliferation index was 20%. Dual-color fluorescence in situ hybridization (FISH) showed red and green signal nuclei caused by the deletion of ETV6 gene rearrangement. The patient underwent extensive surgical resection during the recurrence period and was in good condition 7 months later.ConclusionsPMMTI is at least a low-grade malignancy. BCOR, BCL2, BCL6, and CD99 can be used as special IHC markers, and most PMMTI cases exhibit BCOR ITD change. H3K27me3 may be used as a new IHC marker for PMMTI.


Sign in / Sign up

Export Citation Format

Share Document