scholarly journals Surgical Management of Cervico-facial Cystic Lymphangioma in Children

2021 ◽  
Vol 3 (3) ◽  
pp. 96-99
Author(s):  
O. Oulghoul ◽  
F. Hadid ◽  
O. Benhoummad ◽  
Y. Rochdi ◽  
A. Raji

Introduction: Cystic lymphangioma or cystic hygroma is a congenital malformation of the lymphatic system that manifests as a soft, benign, and painless mass. It originates from remnants of embryonic lymphatic tissue that retains the potential for proliferation. Material and methods: Our retrospective study involved 16 cases of cystic lymphangioma managed between 2017 and 2020. Results: This study included 9 girls and 7 boys with a mean age of 4.2 years. Cystic lymphangioma was visible in 7 cases at birth and in 6 cases before the age of 2 years, and beyond 2 years in 3 cases. The tumor was cervical in 11 cases, including one case of parotid extension, and 02 cases of sub maxillary extension, jugal in one and one case of parotid localization, and one case of lingual localization. Surgical indication was based on clinical examination and imaging in all cases. Excision was considered complete in 12 cases and incomplete in four cases. In three cases, excision was difficult due to adhesion to the internal jugular vein and the carotid bifurcation, base of the tongue in one case and facial nerve in one case. Early complications were, hematoma [one case], lymphorrhea [one case], jugal recurrence [one case] nine months after surgical excision. Conclusion: Cervico-facial cystic lymphangioma is a particular pathology whose management is challenging, complex and multidisciplinary.

Author(s):  
Ehsan Hedayat ◽  
Mohammad Hossein Nabian

Background: Cystic hygroma (cystic lymphangioma) is a malformation of the lymphatic system. It is rare in adults and trauma may be the cause in some cases. Surgical and non-surgical treatment methods have been described in the management of cystic hygroma. Case Report: A 38-year-old woman, known case of systemic lupus erythematosus (SLE), presented a huge cystic formation in the posterior aspect of her thigh following trauma. We treated the patient using a combination of three treatment methods including surgical excision, intra-cavity bleomycin injection, and post-operative use of compression pants. Conclusion: Huge post-traumatic cystic hygroma in adults is rare. By the combination of the above three therapeutic regimens, there was no cystic lesion recurrence after eight months.


Author(s):  
Rosalia S. Coutada ◽  
Joao P. Silva ◽  
Domingos C. Ribeiro ◽  
Paula M. Pinheiro

Lymphangioma is a rare congenital malformation of the lymphatic system that occur in 1 per 6000 live births. The most common site of lymphangioma is the neck (also named cystic hygroma), accounting for 75% of the cases, and it is strongly related to aneuploidies. Axillary location is very rare and appears not to be associated with chromosomal abnormalities. Tumor growth, fetal anemia secondary to intralesional bleeding, hydrops fetalis and shoulder dystocia are possible obstetric complications of this condition. The prognosis is generally good in the absence of abnormal karyotype, fetal hydrops or extension of the lymphangioma to adjacent tissues. Surgical excision or sclerotherapy are the main treatment choices. The authors present a case of a right fetal axillary lymphangioma and review the literature.


2019 ◽  
Vol 12 (8) ◽  
pp. e230326
Author(s):  
Christopher Payne ◽  
Michael J Gigliotti ◽  
Alejandro Castellvi ◽  
Alexander Yu

Lymphangioma, or cystic hygroma, involving the epidural space and spinal soft tissue, is a rare benign lesion consisting of an abnormal collection of lymphatic tissue isolated from the normal lymphatic system. This case report is the most extensive case of cystic hygroma involving the spine reported in the literature. A 23-year-old man with a history of cystic hygromas of the neck and thorax presented with bilateral upper and lower extremity weakness that progressively worsened over 3 months. A left hemilaminectomy from C4 to T5 with endoscopic exploration and cyst drainage was performed. At last follow-up, the patient was ambulating and returned to work. Aggressive decompression of mass lesions resulting in myelopathy, such as the spinal cystic hygromas, resulted in improved motor function as well as overall function status.


2017 ◽  
Vol 25 (5) ◽  
pp. 395-397
Author(s):  
Talha Dogruyol ◽  
Halil Tozum ◽  
Tahir Sevval Eren

Cystic hygroma is a benign tumor of lymphatic tissue. It usually develops before the second year of life and is rarely seen in adults. A 26-year-old woman was referred to our clinic with a swelling in the left supraclavicular region, which had appeared 5 months earlier and grown rapidly. Ultrasonography, computed tomography, and magnetic resonance imaging showed a 7-cm cystic lesion in the neighborhood of the carotid artery and jugular vein medially and the supraclavicular region inferiorly The lesion was dissected completely from the surrounding tissue. The patient had no complications and was discharged on postoperative day one.


Author(s):  
Vargas-Hernandez Victor Manuel

Lymphangiomas are congenital, hamartomatous and uncommon malformations of the lymphatic system that affect the skin and subcutaneous tissues. The most frequently used classification divides these lesions into 2 main groups according to the depth and size of these abnormal lymphatic vessels; arise from kidnappings of lymphatic tissue that should normally communicate with the lymphatic system. Most appear to be developmental lesions that occur relatively early in life, rarely occur in adulthood. The histological features that favor diagnosis are the presence of lymphoid aggregates in the stroma; They appear on any part of the skin and mucous membranes and surgical management with complete surgical excision.


2017 ◽  
Vol 9 (2) ◽  
pp. 167-169
Author(s):  
Babar Irfan ◽  
Maha Tahir ◽  
Omar Irfan ◽  
Hamza Abdur Rahim Khan ◽  
Saulat H Fatimi

Lymphangiomas are congenital malformations of lymphatic tissue. This benign condition is generally found in the neck region and is discovered by 2 years of age. Here we report the case of a 12 year old child who presented with a cervical and mediastinal cystic hygroma that had progressed to such a space occupying nature as to cause the shifting of the trachea. The entire mass was successfully resected with a lower neck incision. Our case suggests the necessity of considering cystic lymphangioma in the differential diagnosis of lateral neck masses and use of adequate imaging to substantiate the preoperative diagnosis.Cardiovasc. j. 2017; 9(2): 167-169


2021 ◽  
Vol 5 (2) ◽  
pp. 254-260
Author(s):  
Vaulinne Basyir ◽  
Try Genta Utama

Background : Hygroma coli is a malformation of the lymphatic system in the form of a membrane cyst filled with fluid, limited by the epithelium that is located in the anterolateral or occipito-cervical region. The prenatal diagnosis of cystic hygroma coli by ultrasound is based on an apparently bilateral, mostly symmetrical, and sometimes unilateral cystic structure located in the occipitocervical region. Large hygroma coli can cause pressure on the respiratory tract and digestion, so it requires management as soon as possible.The main treatment modality is surgical excision to remove the cystic lesion. The prognosis of a hygroma coli cyst depends on its size and the action taken because it is rare for cases to experience spontaneous regression.Destination : Reported a case of hygroma colliMethods : Case ReportCase Report : Case 24 years old women with preterm G1P0A0L0 26-27 weeks + Hygroma colli + IUFD + Suspected COVID-19. On ultrasound examination, it was found that BPD =4,71; AC = 15,91; FL = 2,89; EFW = 330 gr; FHR = (-); Cyst = 5,06 x 3,26. The presence of head presentation, IUFD, hygroma colli was found. The patient was planned for labor induction and the progress of labor was followed. Patient provided inform consent that baby was death during pregnancy and need to be labored. The baby was born, weight 300 gr, body length 14 cm and A/S 0/0. Postmortem physical examination revealed findings of hygroma colli infants such membrane cyst filled with fluid that located in the occipito-cervical region. Conclusion: Hygroma colli is a malformation of the lymphatic system and the prognosis or complications depends on the size of cyst. Careful prenatal examination is required in diagnosis and termination of pregnancyKeywords: Hygroma Colli, prenatal diagnosis


Author(s):  
Swanit Hemant Deshpande ◽  
Vishal Narkhede ◽  
Sunny Agarwal ◽  
Satish Balkrishna Dharap

Lymphangiomas are congenital malformations of the lymphatic system. Multiple intra-abdominal cystic lymphangiomas are rare in adults. Author present a case of a 39-year-old male, presenting with recurrent episodes of haemorrhagic ascites. Laparoscopic biopsy and imaging investigations revealed multiple intra-abdominal cystic lymphangiomas involving the spleen, the liver and the retro-peritoneum. Surgical excision including splenectomy, excision of retroperitoneal and mesenteric lesions was done. The patient has been asymptomatic for 2 years on follow-up.


2014 ◽  
Vol 46 (1-2) ◽  
pp. 12-15
Author(s):  
Amar Kumar Saha ◽  
Shaikh Sayidul Haque ◽  
KM Saiful Islam

Cystic hygroma is a congenital malformation of the lymphatic system. Surgical excision is the treatment of choice, but injection of a sclerosing agent into the cyst is an alternative procedure. The aim of this study was to review the efficacy of intralesional bleomycin injection in cystic hygroma. This study was carried out in a private clinic in Khulna over a period of 2 years on 7 patients. Bleomycin at a dosage of 0.4-0.6 mg/kg was injected into the cyst and repeated injection was given at an interval of 4-8 weeks. Clinical outcomes were reviewed and analyzed. Seven patients, 4 males and 3 females, aged between one month and 4 years were treated with intralesional bleomycin injections. Complete clinical resolution was obtained in 6 cases (86%). Mass reduction was noted in 1 (14%) patient. Adverse reactions including mild fever, local swelling, redness and pain at the site of injection occurred in 3 cases (43%). These reactions persisted for only a few days. Transient systemic side effect like vomiting noted in one patient. So intralesional bleomycin injection is a safe and effective alternative to the surgical treatment of cystic hygroma. DOI: http://dx.doi.org/10.3329/bmjk.v46i1-2.18233 Bang Med J (Khulna) 2013; 46 : 12-15


2021 ◽  
Vol 14 (1) ◽  
pp. e232385
Author(s):  
Jessica Farnan ◽  
Ellen Morrison ◽  
Derek Barrry Hennessey

Proximal-type epithelioid sarcoma is an ultra-rare, high-grade soft tissue malignancy usually presenting as a deep-seated painless mass in the proximal extremities. Most patients are diagnosed as young adults, between 20 and 40 years of age. Perineal and genital masses do occur but are extremely rare and represent a challenging tumour to diagnose and treat. Early radical excision is recommended due to its aggressive behaviour and poor prognosis. Median overall survival from initial diagnosis is 30 months. We present the case of a 22-year-old man with a left groin proximal-type epithelioid sarcoma who is sadly deceased 12 months after initial presentation despite early surgical excision, completion of both first-line and palliative chemotherapy, and palliative radiotherapy.


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