Hearing Recovery and Vestibular Symptoms in Patients with Sudden Deafness and Profound Hearing Loss

1994 ◽  
Vol 114 (sup514) ◽  
pp. 41-44 ◽  
Author(s):  
Minako Yamamoto ◽  
Jin Kanzaki ◽  
Kaoru Ogawa ◽  
Yasuhiro Inoue ◽  
Shunya Ikeda
Keyword(s):  
Hearing Loss ◽  
Sudden Deafness ◽  
Profound Hearing Loss ◽  
Hearing Recovery ◽  
Vestibular Symptoms

scholarly journals Hearing Recovery in Sudden Deafness with Profound Hearing Loss.

1998 ◽  
Vol 101 (6) ◽  
pp. 836-840 ◽  
Author(s):  
Hajime Sano ◽  
Makito Okamoto ◽  
Masatoshi Hirayama ◽  
Yuichi Ono ◽  
Mitsukuni Nitta
Keyword(s):  
Hearing Loss ◽  
Sudden Deafness ◽  
Profound Hearing Loss ◽  
Hearing Recovery

Post-irradiation sudden deafness

1999 ◽  
Vol 113 (9) ◽  
pp. 815-817 ◽  
Author(s):  
Yi-Ho Young ◽  
Pei-Jen Lou
Keyword(s):  
Hearing Loss ◽  
Late Complication ◽  
Sudden Onset ◽  
Sudden Deafness ◽  
Profound Hearing Loss ◽  
Post Irradiation ◽  
Vascular Insufficiency ◽  
Hearing Recovery ◽  
Radiation Induced Cancer ◽  
Radiation Induced

AbstractAs in radiation-induced cancer, post-irradiation sudden deafness (PISD) is defined as sudden onset deafness in patients post-irradiation. Fifteen nasopharyngeal carcinoma (NPC) patients with PISD were enrolled in this study. The mean interval from the completion of irradiation to the occurrence of PISD was 12 years. Seven had total deafness, seven had profound hearing loss, and one had moderate hearing loss. Nine out of 15 (60 per cent) patients experienced hearing recovery within three months after treatment. In conclusion, PISD is a late complication in NPC patients post-irradiation. The causative mechanism is theorized as vascular insufficiency.

Cochlear Implant Outcomes in Patients with Neurosarcoidosis

2021 ◽  
pp. 1-7
Author(s):  
Dario Ebode ◽  
Fleur Cohen-Aubart ◽  
Stéphanie Trunet ◽  
Evelyne Ferrary ◽  
Ghizlène Lahlou ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Cochlear Implantation ◽  
Case Series ◽  
Corticosteroid Treatment ◽  
Auditory Neuropathy ◽  
Disease Exacerbation ◽  
Profound Hearing Loss ◽  
Hearing Recovery ◽  
Speech Performance

<b><i>Introduction:</i></b> Audiovestibular symptoms are rare in sarcoidosis, but they may also be the first manifestation of the disease. Sudden or progressive bilateral hearing loss is usually associated with vestibular impairment. The mechanism of hearing loss remains unclear, but clinical presentation and magnetic resonance imaging suggest a retrocochlear site for the lesion in most patients. Several cases of hearing recovery after corticosteroid treatment have been reported. In patients with severe or profound hearing loss, the benefit of cochlear implantation is challenging to predict in the case of auditory neuropathy and is rarely described. We present a case series of cochlear implantation in patients with documented neurosarcoidosis. <b><i>Results:</i></b> Seven cases of cochlear implantation in 4 patients with neurosarcoidosis are reported. All of the patients showed a great improvement very quickly in both quiet and noise. Speech performance remained stable over time with a follow-up ranging from 4 to 11 years, even in patients who had disease exacerbation. <b><i>Conclusion:</i></b> Cochlear implantation is possible in deaf patients with neurosarcoidosis. The excellent benefit obtained in our patients suggests a particular type of neuropathy, but endocochlear involvement cannot be entirely ruled out.

Audiological Patterns in Patients with Autoimmune Hearing Loss

2021 ◽  
pp. 1-10
Author(s):  
George Psillas ◽  
Grigorios G. Dimas ◽  
Michalis Daniilidis ◽  
Paris Binos ◽  
Thomas Tegos ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Clinical Symptoms ◽  
Human Leukocyte ◽  
Progressive Hearing Loss ◽  
Leukocyte Antigen ◽  
Statistical Effect ◽  
Hearing Recovery ◽  
Negative Effect ◽  
Vestibular Symptoms ◽  
Autoimmune Hearing Loss

<b><i>Introduction:</i></b> The aim of this study was to illustrate clinical and audiological patterns of hearing impairment in patients with autoimmune hearing loss (AIHL). <b><i>Methods:</i></b> Fifty-three patients with AIHL were retrospectively recruited, and a tapering schema of steroid treatment was administered in all these patients. The diagnosis of AIHL was essentially based on clinical symptoms, such as recurrent, sudden (sensorineural hearing loss [SSHL]), fluctuating, or quickly progressing (&#x3c;12 months) SSHL (uni-/bilateral), in association with the coexistence of autoimmune diseases, high antinuclear antibodies (ANA) and the presence of human leukocyte antigen (HLA) B27, B35, B51, C04, and C07. Logistic regression analysis was applied to correlate the clinical data and laboratory features of AIHL with final outcomes. <b><i>Results:</i></b> The onset of AIHL was mainly progressive (49%), followed by SSHL (39.6%) or fluctuating (11.3%). The pure-tone audiogram showed more commonly a downsloping pattern (42.6% of ears), but also an upsloping, flat, cookie-bite, or inverse cookie-bite shape. Bilateral progressive AIHL was more frequently simultaneous (23 patients) than heterochronous (4 patients). Nineteen patients (35.8%) showed a favorable response to steroid therapy. The presence of recurrent, bilateral SSHL versus recurrent, unilateral SSHL had statistically negative effect on hearing recovery (OR = 0.042, <i>p</i> &#x3c; 0.05). The heterochronous bilateral SSHL may have better prognosis than simultaneous bilateral SSHL (OR = 10.000, <i>p</i> = 0.099). The gender, age, concomitant autoimmune disease, high ANA, HLA alleles, tinnitus, and vestibular symptoms had no statistical effect on a favorable outcome of AIHL. <b><i>Conclusions:</i></b> A bilateral, simultaneous, and progressive hearing loss combined with downsloping audiogram occurred more often in patients with AIHL. Bilateral simultaneous SSHL with recurrences represents the worse prognostic form of AIHL.

Sudden Deafness with Severe Loss of Cochlear Neurons

1977 ◽  
Vol 86 (4) ◽  
pp. 541-547 ◽  
Author(s):  
Tetsuo Ishii ◽  
Minoru Toriyama
Keyword(s):  
Hearing Loss ◽  
Nasopharyngeal Carcinoma ◽  
Organ Of Corti ◽  
Complete Loss ◽  
Cochlear Nerve ◽  
Sudden Deafness ◽  
Profound Hearing Loss ◽  
Cochlear Neurons ◽  
Temporal Bones ◽  
Possible Cause

We report our postmortem findings in the temporal bones of a patient who, at the age of 13, after having had a cold, experienced a sudden and profound hearing loss in her right ear. She died of nasopharyngeal carcinoma at 41. The patient's right temporal bone showed a complete loss of cochlear neurons, but the organ of Corti was well-preserved. These findings indicate a primary degeneration of the cochlear nerve. The authors speculated that the possible cause of this sudden deafness was severe neuronitis of the cochlear nerve.

scholarly journals Oscillucusis and sudden deafness in a migraine patient

2003 ◽  
Vol 61 (3B) ◽  
pp. 848-850 ◽  
Author(s):  
Elcio Juliato Piovesan ◽  
Pedro Andre Kowacs ◽  
Lineu Cesar Werneck ◽  
Charles Siow
Keyword(s):  
Hearing Loss ◽  
Migraine Attack ◽  
Migraine Patient ◽  
Complex Disease ◽  
Sudden Deafness ◽  
Clinical Aspects ◽  
Profound Hearing Loss ◽  
Autonomic Symptoms ◽  
Neurologic Symptoms

Migraine is a complex disease that includes neurologic, gastrointestinal and autonomic symptoms, although headache is most common feature. In a portion of cases headache is preceded by focal neurologic symptoms termed auras. Auditory symptoms only rarely occur as part of an aura. We describe a patient whose 13-year migraine history that included the abnormal perception an oscillation of the intensity of ambient sounds (oscillucusis). During a migraine attack immediately after oscillucusis, the patient developed acute and permanent sudden deafness. Clinical and neurologic examinations revealed only profound hearing loss in her left ear. Audiometric testing confirmed the sensorineural nature of the hearing loss. The clinical aspects and physiopathology of auditory symptoms in this case and in patients with migraine is reviewed.

Clinical Profile of Patients With Unilateral Sudden Sensorineural Hearing Loss: Correlation With Hearing Prognosis

2021 ◽  
pp. 019459982098657
Author(s):  
Adriana Perez Ferreira Neto ◽  
Rafael da Costa Monsanto ◽  
Line Dore Saint Jean ◽  
Lucas Sonzzini Ribeiro de Souza ◽  
Norma de Oliveira Penido
Keyword(s):  
Risk Factors ◽  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Odds Ratio ◽  
Univariate Analysis ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Profound Hearing Loss ◽  
Hearing Recovery ◽  
Independent Risk Factors

Objective To characterize, with a standard systematic protocol, the clinical and audiometric profile of patients with idiopathic sudden sensorineural hearing loss (ISSNHL) and to correlate the findings with hearing recovery prognosis. Study Design Retrospective cohort of patients with ISSNHL. Setting Outpatients of a tertiary referral center followed for 20 years. Methods We collected clinical information, including the presence of tinnitus, vertigo, and comorbidities, as well as initial pure tone averages, degree of hearing loss, audiogram curves, and time between hearing loss onset and treatment. These variables were statistically analyzed for their impact on hearing recovery prognosis. All patients were treated with oral corticosteroids, following a standard treatment protocol. Hearing recovery was defined according to the criteria of the American Academy of Otolaryngology–Head and Neck Surgery Foundation, and hearing outcomes were reported via a standardized method (scattergrams). Results Our final study group comprised 186 patients. Most patients were between 41 and 60 years of age. Univariate analysis revealed that vertigo; presence of severe or profound initial hearing loss; flat, U-shaped, and descending audiogram curves; and initiating treatment ≥15 days were correlated with worse hearing recovery. However, the multivariate logistic model revealed that only the presence of severe or profound hearing loss (odds ratio, 6.634; 95% CI, 2.714-16.216; P < .001) and initiating treatment ≥15 days (odds ratio, 0.250; 95% CI, 0.102-0.610; P = .008) were independent risk factors for worse hearing recovery prognosis. Conclusion This study demonstrated that the presence of severe or profound hearing loss at the first audiogram and initiating treatment after 14 days from ISSNHL onset were independent risk factors associated with a worse hearing recovery prognosis.

scholarly journals Association Between Hearing Characteristics/Prognosis and Vestibular Function in Sudden Sensorineural Hearing Loss With Vertigo

2020 ◽  
Vol 11 ◽  
Author(s):  
Yixu Wang ◽  
Le Wang ◽  
Yuanyuan Jing ◽  
Lisheng Yu ◽  
Fanglei Ye
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Low Frequency ◽  
Vestibular Function ◽  
Vestibular Dysfunction ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Profound Hearing Loss ◽  
Potential Association ◽  
Hearing Recovery

Sudden sensorineural hearing loss (SSNHL) patients with vertigo have a poorer prognosis. However, the factors associated with hearing recovery remain uncertain. This retrospective study was to evaluate the association between hearing characteristics/hearing recovery and the patterns of vestibulocochlear lesions in SSNHL patients with vertigo. Patients were classified into groups according to the patterns of vestibular dysfunction. We not only compared hearing characteristics and prognosis among subgroups but also determined the potential association between vestibular lesion location and hearing recovery. The shapes of the audiogram differed significantly between patients with normal vestibular function and patients with vestibular dysfunction (p = 0.022). Patients whose audiogram indicated profound hearing loss were 3.89 times more likely to have vestibular dysfunction than those whose audiogram shape indicated low-frequency hearing loss (95% CI, 1.02–14.86, p = 0.047). Patients who had saccule dysfunction were 0.11 times as likely to have hearing recovery than those who had normal saccule function (95% CI, 0.11–0.31, p = 0.001). When adjusted for sex and age, patients who had saccule dysfunction were 0.07 times as likely to have hearing recovery than those who had normal saccule function (95% CI, 0.02–0.22, p = 0.001). Abnormal results following cVEMP testing may be a potential predictive factor for poor hearing recovery.

Saccular damage in patients with idiopathic sudden sensorineural hearing loss without vertigo

2008 ◽  
Vol 139 (4) ◽  
pp. 541-545 ◽  
Author(s):  
Seok Min Hong ◽  
Jae Yong Byun ◽  
Chan Hum Park ◽  
Jun Ho Lee ◽  
Moon Suh Park ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
High Frequency ◽  
Hearing Threshold ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Vestibular Evoked Myogenic Potentials ◽  
Profound Hearing Loss ◽  
Hearing Recovery ◽  
A Prospective Study

Objective Saccule could be damaged in patients with idiopathic sudden sensorineural hearing loss (ISSHL) with vertigo and with high-frequency sensorineural hearing loss. Thus, the saccule might be deteriorated subclinically in ISSHL cases without vertigo. Therefore, we investigated saccular damage in ISSHL patients without vertigo through vestibular evoked myogenic potentials (VEMP). Study Design A prospective study. Subjects and Methods Fifty-two patients with ISSHL without vertigo were enrolled in the study. We identified VEMP in patients with ISSHL and analyzed the association of VEMP with initial hearing threshold, each threshold according to frequency, the type of audiogram, and hearing recovery. Results For cases with absent VEMP, we found significant differences between patients with 90 dB or more hearing loss and those with a hearing loss less than 55 dB with frequencies over 1000 Hz. Patients with profound hearing loss presented significantly high abnormal and absent VEMP than patients with audiograms of other types. Conclusion These findings suggest that the subclinical deterioration of the saccular neuroepithelium is associated with patients with ISSHL having profound hearing loss at the high frequency.

What Do We Want Them To Be When They Grow Up?

2010 ◽  
Vol 20 (1) ◽  
pp. 27-31
Author(s):  
Lyn Robertson
Keyword(s):  
Hearing Loss ◽  
Social Development ◽  
Young Women ◽  
Hearing Aids ◽  
Test Scores ◽  
Spoken Language ◽  
Language Therapy ◽  
Profound Hearing Loss ◽  
Children With Hearing Loss ◽  
Learning To Listen

Abstract Learning to listen and speak are well-established preludes for reading, writing, and succeeding in mainstream educational settings. Intangibles beyond the ubiquitous test scores that typically serve as markers for progress in children with hearing loss are embedded in descriptions of the educational and social development of four young women. All were diagnosed with severe-to-profound or profound hearing loss as toddlers, and all were fitted with hearing aids and given listening and spoken language therapy. Compiling stories across the life span provides insights into what we can be doing in the lives of young children with hearing loss.

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