scholarly journals An Unusual Findings of Elevated Urinary Copper Excretion in a Patient with Subacute Sclerosing Panencephalitis (SSPE): A Case Report

2018 ◽  
Vol 3 (2) ◽  
pp. 113-115
Author(s):  
Ariful Islam ◽  
Yamin Shahriar Chowdhury ◽  
Sheikh Azimul Haq ◽  
Narayan Chandra Saha ◽  
Nazmul Haque
Keyword(s):  
Cerebrospinal Fluid ◽  
Case Report ◽  
Physical Examination ◽  
Subacute Sclerosing Panencephalitis ◽  
Drop Attacks ◽  
Urinary Copper ◽  
Scholastic Performance ◽  
History Of ◽  
Eeg Changes ◽  
Urinary Copper Excretion

Subacute sclerosing panencephalitis is a progressive neurological disorder of childhood and early adolescence. It is caused by persistent defective measles virus1.We report a ten years old normally developed female patient who came with a history of drop attacks while walking, declining scholastic performance, progressively increasing myoclonic jerks. She had history of measles at five years of age though she was vaccinated as per EPI schedule. Physical examination and cerebrospinal fluid findings along with EEG changes in addition supported its diagnosis as a case of SSPE. The presence of increased urinary excretion of copper in SSPE is so far not yet reported in any published literature.Journal of National Institute of Neurosciences Bangladesh, 2017;3(2): 113-115

scholarly journals Graham-Little Piccardi Lassueur Syndrome: case report

2012 ◽  
Vol 87 (5) ◽  
pp. 775-777 ◽  
Author(s):  
Raquel Bissacotti Steglich ◽  
Renata Elise Tonoli ◽  
Giselle Martins Pinto ◽  
Fernanda Melo Müller ◽  
Isabelle Maffei Guarenti ◽  
...  
Keyword(s):  
Case Report ◽  
Physical Examination ◽  
Hair Follicles ◽  
Rare Disorder ◽  
Rare Syndrome ◽  
Scarring Alopecia ◽  
History Of

A 33-year-old woman presented with a 3-year history of progressive alopecia of the scalp. Past treatment with hydroxicloroquine did not show improvement. Physical examination revealed multiple areas of alopecia with atrophic aspect of the scalp, and axillary and pubic hypotrichosis. Dermoscopy showed hyperkeratosis and accentuation of follicular ostia. Anatomopathological examination revealed decrease in the number of hair follicles, upper perifollicular infiltrate and areas with fibrosis. The Piccardi-Lassueur-Graham-Little syndrome is a rare disorder, characterized by the triad of multifocal scarring alopecia of the scalp, keratotic follicular eruption and hypotrichosis of axillary and pubic regions. Management is a challenge and many medications tried have controversial results. We report a case of this rare syndrome which improved with corticoids.

scholarly journals Subacute Sclerosing Panencephalitis

2019 ◽  
Vol 37 (4) ◽  
pp. 205-208
Author(s):  
Gobinda Chandra Banik ◽  
Sakib Aman ◽  
Farhana Sultana ◽  
Syed Mohammad Arif
Keyword(s):  
Cerebrospinal Fluid ◽  
Virus Infection ◽  
Antibody Titer ◽  
Measles Virus ◽  
Subacute Sclerosing Panencephalitis ◽  
Abnormal Behavior ◽  
Short History ◽  
Altered Consciousness ◽  
History Of ◽  
Metachromatic Leucodystrophy

  Subacute sclerosing panencephalitis (SSPE) is chronic progressive encephalitis of childhood and young adoloscent due to persistent measles virus infection. This case illustrates a 14 year old girl presented with short history of intellectual decline, abnormal behavior, myoclonus and altered consciousness with suggestive neuroimaging mimicking metachromatic leucodystrophy. Subsequently she was diagnosed to be a case of Subacute sclerosing panencephalitis (SSPE) on the basis of Electroencephalography (EEG) and Cerebrospinal fluid(CSF) measles antibody titer. J Bangladesh Coll Phys Surg 2019; 37(4): 205-208

scholarly journals Extensive nasopharyngeal angiofibroma – case report

1970 ◽  
Vol 15 (2) ◽  
pp. 75-77
Author(s):  
M Alamgir Chowdhury ◽  
Mousumi Malakar ◽  
SM Golam Rabbani ◽  
Naseem Yasmeen ◽  
Shahidul Islam
Keyword(s):  
Case Report ◽  
Physical Examination ◽  
Nasal Cavity ◽  
Neck Region ◽  
Lateral Rhinotomy ◽  
Male Population ◽  
Vascular Neoplasm ◽  
Nasopharyngeal Angiofibroma ◽  
Recurrent Epistaxis ◽  
History Of

Juvenile nasopharyngeal angiofibroma is a benign vascular neoplasm, but it is locally aggressive. This accounts for less than 0.5% of all the neoplasm in the head & neck region in the male population only. Here we report a case of 10-year-old boy with a blackish red smooth polypoidal mass in the nasal cavity, with history of recurrent epistaxis. On physical examination it was suspected as nasopharyngeal angiofibroma. We removed it totally by lateral rhinotomy approach. And the diagnosis was nasopharyngeal angiofibroma on histopathology. Key words: Angiofibroma; Nasopharyngeal. DOI: 10.3329/bjo.v15i2.5061 Bangladesh J Otorhinolaryngol 2009; 15(2): 75-77

scholarly journals Compound Presentation: A Case Report of One of the Rarest Varieties- Vertex, Hand, and Feet Presentation

2021 ◽  
Vol 8 (2) ◽  
Author(s):  
Sium AF ◽  
◽  
Tilahun A ◽  
Mersha A ◽  
Yihun S ◽  
...  
Keyword(s):  
Case Report ◽  
Physical Examination ◽  
Cesarean Delivery ◽  
Conservative Management ◽  
Similar Type ◽  
Cervical Dilation ◽  
Compound A ◽  
Case Summary ◽  
Spontaneous Correction ◽  
History Of

Background: Compound presentation occurs in approximately 1/700 deliveries. Being the rarest type, there is scarce literature about the recommended management for vertex-hand-feet variety of compound presentation. We report a similar type of compound presentation. Case Summary: A 25 years-old primigravida who claimed to be 9 months ammenorric presented with a history of pushing down pain of 12 hours duration with associated history of passage of liquor of 4 hours duration. Up on physical examination she was in active first of labor at cervical dilation of 5 centimeters and the presentation was compound- a vertex-hand-feet variety. Cesarean delivery was done after two hours of conservative management and the outcome was an alive 2300grams male neonates with no perinatal or maternal complication. Conclusion: In the rarest variety of compound presentation, which is a vertex, hand, and feet type, spontaneous correction is unusual if the fetus is alive and interference is usually necessary.

scholarly journals Idiopathic Hypertrophic Pachymeningitis: A Case Report from Bangladesh

2018 ◽  
Vol 3 (2) ◽  
pp. 110-112
Author(s):  
Meera Momtaz Sabeka ◽  
Md Nazrul Islam
Keyword(s):  
Case Report ◽  
Physical Examination ◽  
Optic Atrophy ◽  
Severe Headache ◽  
Imaging Studies ◽  
Hypertrophic Pachymeningitis ◽  
History Of ◽  
Diagnostic Clue ◽  
Work Up ◽  
Rule Out

A 52 years old lady presented with sudden severe headache with the history of similar intense headache twenty years back which ended up with left sided blindness. Her physical examination was unremarkable except optic atrophy of the left eye. Investigation included biochemical work up, imaging studies and CSF study. The MRI of brain with contrast gave the key diagnostic clue with characteristic findings of hypertrophic pachymeningitis. Other investigations helped to rule out possible etiologies and the diagnosis idiopathic hypertrophic pachymeningitis was finally made. The patient has been treated with steroid and enjoyed improvement in her yearlong symptoms.Journal of National Institute of Neurosciences Bangladesh, 2017;3(2): 110-112

Ovarian cancer associated with carcinomatous meningitis: a case report and review of the literature

2007 ◽  
Vol 17 (5) ◽  
pp. 1136-1140 ◽  
Author(s):  
L. Decelle ◽  
L. D'HONDT ◽  
M. Andre ◽  
P. Delree ◽  
B. Calicis ◽  
...  
Keyword(s):  
Ovarian Cancer ◽  
Cerebrospinal Fluid ◽  
Case Report ◽  
Rare Event ◽  
Carcinomatous Meningitis ◽  
Second Line ◽  
Rare Entity ◽  
Review Of The Literature ◽  
History Of ◽  
Line Chemotherapy

We report the case of a 62-year-old patient who developed a carcinomatous meningitis while on second-line chemotherapy for ovarian cancer. Cytologic analyses confirmed that carcinomatous cells of ovarian origin were present in cerebrospinal fluid. Carcinomatous meningitis is a very rare event in the natural history of ovarian carcinoma. We discuss the specificity of our case in the light of the literature. In addition, we present some relevant radiologic and pathologic documents illustrating this rare entity.

Bilateral, spontaneous cerebrospinal fluid rhinorrhoea: endoscopic, uninasal, trans-septal approach for simultaneous closure

2011 ◽  
Vol 125 (11) ◽  
pp. 1185-1188
Author(s):  
M Kurien ◽  
G A Mathew ◽  
S L Abraham ◽  
A Irodi
Keyword(s):  
Cerebrospinal Fluid ◽  
Case Report ◽  
English Language ◽  
Past History ◽  
Cerebrospinal Fluid Leakage ◽  
Endoscopic Repair ◽  
Recent Onset ◽  
Cerebrospinal Fluid Rhinorrhoea ◽  
Fluid Leakage ◽  
History Of

AbstractBackground:Bilateral, spontaneous cerebrospinal fluid rhinorrhoea is extremely rare, with only one previous case report (this patient developed contralateral cerebrospinal fluid leakage four years after successful endoscopic repair). We present the first English-language report of simultaneous, bilateral, spontaneous cerebrospinal fluid rhinorrhoea.Objective:To recommend a simple alternative endoscopic technique for simultaneous closure of bilateral, spontaneous cerebrospinal fluid rhinorrhoea.Case report:A 47-year-old woman presented with recent onset of bilateral, spontaneous cerebrospinal fluid rhinorrhoea, a recent history suggestive of meningitis, and a past history of pneumococcal meningitis. Bony defects on both sides of the cribriform plate were closed endoscopically in the same anaesthetic session, via a uninasal, trans-septal approach, enabling both leakage sites to be sealed simultaneously.Conclusion:In cases of bilateral, spontaneous cerebrospinal fluid rhinorrhoea, uninasal, trans-septal endoscopic repair is a simple and effective technique for simultaneous closure of cerebrospinal fluid leakage.

scholarly journals PeutzJeghers syndrome: A case report and literature review

2014 ◽  
Vol 4 (8) ◽  
pp. 677-679
Author(s):  
A Lakhey ◽  
H Shakya
Keyword(s):  
Case Report ◽  
Literature Review ◽  
Physical Examination ◽  
Rectal Bleeding ◽  
Buccal Mucosa ◽  
Autosomal Dominant ◽  
Hamartomatous Polyps ◽  
Pigmented Lesions ◽  
History Of ◽  
Peutz Jeghers Syndrome

Peutz–Jeghers Syndrome is an autosomal dominant inheritedhamartomatous polyp. We present a case of a 5-year-old young boywith a history of per rectal bleeding and mass protruding out of the anus. Physical examination revealed presence of mucocutaneous pigmented lesions over the tongue, and few hamartomatous polyps protruding out of the rectum suggesting Peutz–Jeghers syndrome. The presence in early infancy of small, well-demarcated and dark-brown to blue-black lentigines on the lips,buccal mucosa and perioral skin, should alert the clinician to Peutz–Jeghers Syndrome.DOI: http://dx.doi.org/10.3126/jpn.v4i8.11597 Journal of Pathology of Nepal; Vol.4,No. 8 (2014) 677-679

scholarly journals Hepatic Liquoric Cyst as a Complication of Ventriculoperitoneal Shunt Insertion: A Case Report

2021 ◽  
Author(s):  
Lívio Pereira de Macêdo ◽  
Arlindo Ugulino Netto ◽  
Kauê Franke ◽  
Pierre Vansant Oliveira Eugenio ◽  
Lucas Ribeiro de Moraes Freitas ◽  
...  
Keyword(s):  
Cerebrospinal Fluid ◽  
Case Report ◽  
Ventriculoperitoneal Shunt ◽  
Individual Case ◽  
Abdominal Imaging ◽  
Case Description ◽  
Shunt Insertion ◽  
Important Complication ◽  
History Of

Abstract Background The ventriculoperitoneal shunt (VPS) procedure is still the most used technique for management of hydrocephalus. This article reports a case of hepatic cerebrospinal fluid (CSF) pseudocyst as a rare, but important, complication of the VPS insertion. Case Description An 18-year-old male presented to the hospital complaining of temporal headache and visual turbidity for approximately 3 months with a history of VPS insertion for treatment of hydrocephalus and revision of the valve in adolescence. The diagnosis was based on abdominal imaging, demonstrating an extra-axial hepatic CSF pseudocyst free from infection. Following the diagnosis, the management of the case consisted in the removal and repositioning of the catheter on the opposite site of the peritoneum. Conclusion The hepatic CSF pseudocyst is an infrequent complication of VPS procedure, but it needs to be considered when performing the first evaluation of the patient. Several techniques are considered efficient for the management of this condition, the choice must be made based on the variables of each individual case.

scholarly journals Fixation Rotator cuff repair of shoulder by Patch augmentation technique. A Case Report

2021 ◽  
Vol 9 (8) ◽  
pp. 1814-1818
Author(s):  
Mohammed Yaseen Azher
Keyword(s):  
Case Report ◽  
Rotator Cuff ◽  
Physical Examination ◽  
Range Of Motion ◽  
Rotator Cuff Repair ◽  
Left Shoulder ◽  
Synthetic Graft ◽  
History Of ◽  
Cuff Repair

Abstract: Rotator cuff repair has excellent outcomes for many patients but continues to be suboptimal for large, retracted tears, and revision procedures. In certain circumstances, augmentation may be explored to aid healing. This is a case study. A 61-yearold man with a 3-month history of left shoulder arthroscopic subacromal decompression with bursectomy, acromioplasty, rotator cuff repair with patch augmentation, strengthening with bio synthetic graft fleece, and ACJ excision. After a physical examination, the left shoulder was found to have active forward elevation of 130 degrees and passive forward elevation of 150 degrees, pain in the periscapular region, rotator cuff strength of 4/5, and distal neurovascular integrity. Finally, the patient is pleased with the results of the operation, and he now has a decent functional range of motion, although he still has weak muscles and severe scapular discomfort

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