scholarly journals A Case of Bilateral Profound Hearing loss Caused by Idiopathic Labyrinthitis that Showed a Clinical Course Similar to that of Delayed Endolymphatic Hydrops

2019 ◽  
Vol 78 (2) ◽  
pp. 61-68
Author(s):  
Keita Tsukada ◽  
Hideaki Moteki ◽  
Rika Yasukawa ◽  
Shin-ichi Usami
Keyword(s):  
Hearing Loss ◽  
Clinical Course ◽  
Endolymphatic Hydrops ◽  
Profound Hearing Loss ◽  
Delayed Endolymphatic Hydrops

Delayed Endolymphatic Hydrops

1978 ◽  
Vol 87 (6) ◽  
pp. 743-748 ◽  
Author(s):  
Harold F. Schuknecht
Keyword(s):  
Hearing Loss ◽  
Endolymphatic Hydrops ◽  
Meniere’S Disease ◽  
Ménière’S Disease ◽  
Disease Entity ◽  
Profound Hearing Loss ◽  
Episodic Vertigo ◽  
Delayed Endolymphatic Hydrops ◽  
Ménière's Disease ◽  
Fluctuating Hearing Loss

Delayed endolymphatic hydrops is a disease entity that can be differentiated from Meniere's disease. Typically it occurs in patients who have sustained a profound hearing loss in one ear, usually from infection or trauma, and then after a prolonged period of time develop either episodic vertigo from the same ear (ipsilateral delayed endolymphatic hydrops) or fluctuating hearing loss, also sometimes with episodic vertigo, in the opposite ear (contralateral delayed endolymphatic hydrops). The ipsilateral form of the disease may be treated by labyrinthectomy but no satisfactory therapy is available for the contralateral form of the disease.

Delayed Endolymphatic Hydrops: A Case Study

2008 ◽  
Vol 19 (03) ◽  
pp. 204-209 ◽  
Author(s):  
Rachel Lazaro ◽  
Larry Lundy ◽  
David Zapala
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Endolymphatic Hydrops ◽  
Sensorineural Hearing ◽  
Ménière’S Disease ◽  
Episodic Vertigo ◽  
Delayed Endolymphatic Hydrops ◽  
Patient’S History ◽  
Estudio De Caso

Delayed endolymphatic hydrops (DEH) is an unusual variation of Ménière's disease characterized by episodic vertigo that develops some time after the onset of a profound, typically unilateral sensorineural hearing loss. This case study describes a 48-year-old male who presented with complaints of episodic vertigo and disequilibrium 15 years following the onset of unilateral sensorineural hearing loss. The patient's history, audiologic findings, and vestibular evaluation led to the diagnosis of DEH. The case highlights the diagnostic and treatment challenges associated with this condition and focuses attention on principles that guide the audiologist in collecting evidence that aids in solving these challenges. El hidrops endolinfático retardado (DEH) es una variante inusual de la Enfermedad de Ménière, caracterizada por vértigo episódico que se desarrolla en el tiempo luego del inicio de una hipoacusia sensorineural unilateral típica. Este estudio de caso describe una varón de 48 años que presentó quejas de vértigo episódico y desequilibrio, 15 años después del inicio de una hipoacusia sensorineural unilateral. La historia del paciente, los hallazgos audiológicos y la evaluación vestibular llevaron al diagnóstico de DEH. El caso destaca los retos diagnósticos y terapéuticos asociados con esta condición y concentra su atención en los principios que guían al audiólogo en la recolección de evidencia que ayude a resolver estos retos.

scholarly journals Endolymphatic Hydrops in Patients With Intralabyrinthine Schwannomas

2021 ◽  
Vol 7 ◽  
Author(s):  
Yibo Zhang ◽  
Feitian Li ◽  
Chunfu Dai ◽  
Wuqing Wang
Keyword(s):  
Hearing Loss ◽  
Temporal Bone ◽  
Tumor Recurrence ◽  
Endolymphatic Hydrops ◽  
Profound Hearing Loss ◽  
Postoperative Mri ◽  
Clinical Presentations ◽  
Intratympanic Injection ◽  
Lost To Follow Up

Purpose: The presence of endolymphatic hydrops (EH) in patients with intralabyrinthine schwannomas (ILSs) is poorly understood. This study aims to determine whether there is a correlation between endolymphatic hydrops and clinical presentations of ILS.Methods: Data from nine patients with ILSs were retrospectively reviewed between 2007 and 2020. Temporal bone MRI with intratympanic or intravenous injection of gadolinium was applied to detect ILSs and EH.Results: 3D real inversion recovery (IR) sequence MRI of the temporal bone confirmed ipsilateral EH in four patients (4/6). All four patients with EH on MRI presented with vertigo similar to Meniere's disease. Among these patients with EH, one patient with EH in the cochlea showed moderate sensorineural hearing loss, while three patients with EH in both the vestibule and cochlea showed profound hearing loss. MRI demonstrated a transmacular tumor (TMA) in one patient, intravestibular (IV) in four patients, and vestibulocochlear (VC) in four patients. Two IV cases showed moderated hearing loss, while the TMA and VC cases showed profound hearing loss. Transotic resection of the tumor was applied in five patients; translabyrinthine resection was applied in one patient; two patients were under observation; and one patient was given intratympanic injection of gentamicin (ITG). During follow-up, all of the treated patients reported relief of vertigo, and postoperative MRI was performed in two patients, which showed no tumor recurrence. The two patients under observation showed no deterioration of hearing loss or vertigo. One patient was lost to follow-up.Conclusion: EH concurrent with ILSs has been underestimated previously. With the extensive application of temporal bone MRI paradigms, such as 3D-real IR sequence MRI, more cases of potential EH in patients with ILS will be identified. The severity of hearing loss may be associated with the location of the tumor and the degree of EH.

A Case of Syphilitic Labyrinthitis with a Clinical Course Similar to Delayed Endolymphatic Hydrops.

1998 ◽  
Vol 57 (5) ◽  
pp. 475-479
Author(s):  
Tadashi Kitahara ◽  
Junko Murata ◽  
Hidehiro Obata ◽  
Shin-ichi Okumura
Keyword(s):  
Clinical Course ◽  
Endolymphatic Hydrops ◽  
Delayed Endolymphatic Hydrops

scholarly journals Hearing Impairment in Angolan Children with Acute Bacterial Meningitis With and Without Otitis Media and Otorrhea

2021 ◽  
Author(s):  
Laura Lempinen ◽  
Anu Laulajainen-Hongisto ◽  
Antti A. Aarnisalo ◽  
Luis Bernardino ◽  
Heikki Peltola ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Bacterial Meningitis ◽  
Hearing Impairment ◽  
Otitis Media ◽  
Clinical Course ◽  
Acute Bacterial Meningitis ◽  
Profound Hearing Loss ◽  
Significant Difference ◽  
Ear Infections ◽  
Hearing Loss In Childhood

Abstract Background: Bacterial meningitis (BM) is a common cause of hearing loss in childhood. Our aim was to investigate bacterial etiology, hearing impairment, and outcome in childhood BM with vs. without otitis media (OM) in the resource-poor settings of Angola. Methods: Hearing was tested through brainstem-evoked response audiometry (ABR) in 391 (76%) of 512 children with confirmed BM. The bacteria identified from the ear discharge were compared to those from CSF and the relevance of findings was examined in terms of hearing among children with or without OM on day 1 and 7 of hospitalization, and at follow-ups of 1, 3 and 6 month(s).Results: No correlation was found in bacteriology between the ear discharge and CSF, and the most common ear pathogens more likely reflected chronic than acute middle ear infections. On day 7 in hospital, hearing impairment (>40 dB) was common, regardless of whether concomitant OM or not (in 27% vs. 30%, respectively), whereas on day 7, profound hearing loss (>80 dB) was diagnosed slightly more in children without OM 16% vs. 10% accordingly. Any hearing deficit on day 7 was associated with a higher risk of complicated or fatal clinical course (OR 2.76, CI95% 1.43-5.29, P = .002).Conclusion: No significant difference prevailed in hearing thresholds between children with or without OM in hospital on day 7 or at later follow-ups. Any hearing impairment on day 7 associated with a higher risk for complicated clinical course or death. Trial registration: ISRCTN62824827. Registered 22 June 2005, http://www.isrctn.com/ ISRCTN62824827.

scholarly journals Long-term efficacy of triple semicircular canal plugging in the treatment of patients with ipsilateral delayed endolymphatic hydrops

2021 ◽  
Vol 11 (1) ◽  
Author(s):  
Daogong Zhang ◽  
Yafeng Lv ◽  
Xiaofei Li ◽  
Yawei Li ◽  
Yongdong Song ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Semicircular Canal ◽  
Endolymphatic Hydrops ◽  
Complete Control ◽  
Term Efficacy ◽  
Delayed Endolymphatic Hydrops ◽  
Intratympanic Gentamicin ◽  
Substantial Control

AbstractThis study aims to explore the long-term efficacy of triple semicircular canal plugging (TSCP) in the treatment of intractable ipsilateral delayed endolymphatic hydrops (DEH), so as to provide an alternative therapy for this disease. Forty-eight patients diagnosed with ipsilateral DEH referred to vertigo clinic of our hospital between Dec. 2010 and Dec. 2017, were included in this study for retrospective analysis. All patients were followed up for 2 years. Vertigo control and auditory functions were measured and analyzed. Pure tone audiometry, caloric test, and vestibular evoked myogenic potential (VEMP) were performed in two-year follow-up. Forty-five patients who accepted intratympanic gentamicin (26.7 mg/mL) twice given one week apart were selected as a control group. The total control rate of vertigo in TSCP group was 97.9% (47/48) in the two-year follow-up, with complete control rate of 83.3% (40/48) and substantial control rate of 14.6% (7/48). The rate of hearing loss was 22.9% (11/48). The total control rate of vertigo in intratympanic gentamicin group was 80.0% (36/45), with complete control rate of 57.8% (26/45) and substantial control rate of 22.2% (10/45), and the rate of hearing loss was 20.0% (9/45). The vertigo control rate of TSCP was significantly higher than that of intratympanic gentamicin (χ2 = 6.01, p < 0.05). There was no significant difference of hearing loss rate between two groups. (χ2 = 0.12, p > 0.05). TSCP, which can reduce vertiginous symptoms in patients with intractable ipsilateral DEH, represents an effective therapy for this disorder.

What Do We Want Them To Be When They Grow Up?

2010 ◽  
Vol 20 (1) ◽  
pp. 27-31
Author(s):  
Lyn Robertson
Keyword(s):  
Hearing Loss ◽  
Social Development ◽  
Young Women ◽  
Hearing Aids ◽  
Test Scores ◽  
Spoken Language ◽  
Language Therapy ◽  
Profound Hearing Loss ◽  
Children With Hearing Loss ◽  
Learning To Listen

Abstract Learning to listen and speak are well-established preludes for reading, writing, and succeeding in mainstream educational settings. Intangibles beyond the ubiquitous test scores that typically serve as markers for progress in children with hearing loss are embedded in descriptions of the educational and social development of four young women. All were diagnosed with severe-to-profound or profound hearing loss as toddlers, and all were fitted with hearing aids and given listening and spoken language therapy. Compiling stories across the life span provides insights into what we can be doing in the lives of young children with hearing loss.

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