scholarly journals Alveolar soft part sarcoma of the retroperitoneum: A case report

2021 ◽  
Vol 15 (10) ◽  
pp. 20-26
Author(s):  
Satyam Satyam ◽  
Alpana Manchanda ◽  
Ramya Kamraj ◽  
Anju Garg ◽  
Kaushik Majumdar
Keyword(s):  
Rare Case ◽  
Soft Tissue Tumor ◽  
Clinical Symptoms ◽  
Soft Part ◽  
Surgical Excision ◽  
Young Female ◽  
High Rate ◽  
Alveolar Soft Part Sarcoma ◽  
Rare Location ◽  
Slow Growing

Alveolar soft part sarcoma is a rare soft tissue tumor with uncertain histogenesis. It is a slow growing tumor with a high rate of metastasis. The tumor is not easily identified as clinical symptoms are not pronounced. The retroperitoneum is a rare location of tumor, with a few cases published in literature. Surgical excision is the mainstay of treatment. Here we describe a rare case of a large retroperitoneal Alveolar soft part sarcoma in a young female with radiological and histopathological findings.

scholarly journals Alveolar soft part sarcoma of extremity

2020 ◽  
Vol 8 (10) ◽  
pp. 3735
Author(s):  
Shilpa Kaushal ◽  
Muninder K. Negi
Keyword(s):  
Vascular Invasion ◽  
Soft Part ◽  
External Beam Radiotherapy ◽  
Distant Metastases ◽  
Surgical Excision ◽  
Alveolar Soft Part Sarcoma ◽  
High Likelihood ◽  
Histopathological Feature ◽  
History Of ◽  
Slow Growing

Alveolar soft-part sarcoma (ASPS) is an extremely rare connective tissue tumor, predominantly seen in adolescents and young adults, with a female preponderance. Alveolar soft-part sarcoma (ASPS) is a slow growing tumor, but with high likelihood of metastasis, leading to high mortality. A classical histopathological feature of an alveolar pattern from the biopsy of the lesion favors the diagnosis. We report a case of 14 years old male patient who presented with a history of single painless swelling over thigh for which surgical excision was done. Histopathology was suggestive of Alveolar soft-part sarcoma (ASPS). There was no evidence of distant metastases. He was treated with external beam radiotherapy in view of vascular invasion.

scholarly journals iCREATE: imaging features of primary and metastatic alveolar soft part sarcoma from the EORTC CREATE study

2020 ◽  
Vol 20 (1) ◽  
Author(s):  
Naami Charlotte Mcaddy ◽  
Hind Saffar ◽  
Saskia Litière ◽  
Pieter Jespers ◽  
Patrick Schöffski ◽  
...  
Keyword(s):  
Pulmonary Metastases ◽  
Soft Part ◽  
Primary Tumour ◽  
High Rate ◽  
Alveolar Soft Part Sarcoma ◽  
Imaging Features ◽  
Antiangiogenic Treatment ◽  
Feeding Vessels ◽  
Slow Growing ◽  
Sites Of Metastases

Abstract Background Alveolar Soft Part Sarcoma (ASPS) is a rare, slow-growing, but highly vascular soft tissue sarcoma, characterised by a high rate of metastases at presentation. Although imaging features of the primary are well described, less detail is available on the imaging pattern of metastatic ASPS. The EORTC 90101 (CREATE) study assessed the efficacy of Crizotinib in patients with metastatic ASPS and presents a unique opportunity to describe the imaging phenotype of primary and metastatic ASPS, based on prospectively collected imaging. Methods A retrospective review of the staging CT scans of 32 patients with ASPS from the CREATE study was undertaken and the imaging features of primary and metastatic disease were assessed. Results Imaging of the primary tumour was available in 7/32 cases (28%). All primary tumours demonstrated marked vascularity with prominent feeding vessels (7/7, 100%). The most frequent sites of metastases included lung (30/32, 94%), nodal (7/32, 22%), bone (5/32, 16%) and muscle/subcutaneous (5/32, 16%). Features of hypervascularity were identified at all sites, more appreciable in the lungs, with feeding vessels frequently demonstrated in pulmonary metastases (21/32, 66%). Conclusion Analysis of imaging from the CREATE cohort of patients with metastatic ASPS demonstrates that metastases from ASPS are predominantly hypervascular and demonstrate feeding vessels comparable to primary ASPS, suggesting potential sensitivity of this rare sarcoma for antivascular/antiangiogenic treatment approaches.

scholarly journals A rare clinical case: schwannoma of tongue

2019 ◽  
Vol 5 (3) ◽  
pp. 789
Author(s):  
Chandra Veer Singh ◽  
Sheetal Radia ◽  
Saalim Sheikh ◽  
Vijay Haribhakti
Keyword(s):  
Head And Neck ◽  
Rare Case ◽  
Neck Region ◽  
Surgical Excision ◽  
Imaging Studies ◽  
Head And Neck Tumours ◽  
Head And Neck Region ◽  
Complete Surgical Excision ◽  
Slow Growing ◽  
Rule Out

<p class="abstract">Schwannoma are slow growing tumours, which can arise from any peripheral nerve. 10% of schwannomas that occur in the head and neck region mostly originate from the vagus or sympathetic nervous system. Extracranial schwannomas in the head and neck region are rare neoplasm. Intraoral schwannoma are only 1% of the all head and neck tumours. Diagnosis is established by imaging studies such as magnetic resonance imaging or computed tomography, while FNAC is used to rule out other conditions. We report a rare case of lingual schwannomas generally present as a painless lump schwannoma of the tongue in a 27-year-old male complaining of asymptomatic swelling over a posterolateral surface of the tongue, treated by complete surgical excision. The diagnosis was established on the basis of clinical, histopathological, and immunohistochemical examination. We report a rare case of schwannoma over the posterolateral surface of tongue. Prognosis is good for the patient when this condition is correctly diagnosed as the condition rarely recurs after complete resection.</p>

scholarly journals Gingival Lipoma: A Rare Case Report

2017 ◽  
Vol 1 (1) ◽  
pp. 37-39
Author(s):  
Sweta Shrestha ◽  
Shaili Pradhan ◽  
Ranjita Shrestha Gorkhali
Keyword(s):  
Rare Case ◽  
Surgical Excision ◽  
Soft Tissue Tumors ◽  
Rare Case Report ◽  
Postsurgical Complication ◽  
Benign Tumours ◽  
One Year ◽  
Slow Growing ◽  
Oral Soft Tissue

Lipomas are benign tumours of mesenchymal origin (mature adipocytes) that are comparatively uncommon in the oral cavity corresponding to less than 4.4% of all benign oral soft tissue tumors. Clinically, they present as slow growing, soft, asymptomatic masses. Histopathologically, they appear as thinly encapsulated lesion composed of mature adipocytes with inconspicuous vascularity. The pathogenetic mechanisms of oral lipomas are still unclear. They are usually treated by surgical excision and bear excellent prognosis. Here we report a case of intraoral lipoma in 54 year old male patient in the left lower lingual alveolar mucosal region that was treated by surgical excision using electrocautery without any postsurgical complication. One-year follow-up showed no evidence of recurrence.

scholarly journals Peripheral Ameloblastoma of Upper Gingiva in a Patient with Port-Wine Stain

2020 ◽  
Vol 2020 ◽  
pp. 1-5
Author(s):  
Natheer H. Al-Rawi ◽  
Sahar Othman ◽  
Ab Rani Samsudin
Keyword(s):  
Rare Case ◽  
Soft Tissue Tumor ◽  
Present Report ◽  
Pyogenic Granuloma ◽  
Port Wine Stain ◽  
Port Wine ◽  
Histological Features ◽  
Odontogenic Origin ◽  
Histological Characteristics ◽  
Slow Growing

The peripheral ameloblastoma (PA), also known as extraosseous ameloblastoma, is a rare soft tissue tumor of odontogenic origin, accounting for 1–5% of all ameloblastoma. In some cases, saucerization of underlying bone is the only radiological evidence of this lesion, and PA has identical histological characteristics of intraosseous ameloblastoma. However, it is slow growing, less aggressive, and less invasive in nature. The present report describes a rare case of PA in the maxillary labial gingiva of a 37-year-old man with port-wine vascular malformation. PA was clinically diagnosed as a pyogenic granuloma, and following the surgical treatment of the lesion, its histological features were of ameloblastoma. This case illustrates the importance of including peripheral ameloblastoma in the differential diagnosis of painless exophytic gingival swelling.

Alveolar Soft Part Sarcoma Presenting as a Uterine Polyp

2019 ◽  
Vol 152 (Supplement_1) ◽  
pp. S37-S37
Author(s):  
Mariangela Gomez ◽  
Kerry Whiting
Keyword(s):  
Soft Tissue Tumor ◽  
Soft Part ◽  
Female Genital Tract ◽  
Alveolar Soft Part Sarcoma ◽  
Complete Excision ◽  
Molecular Features ◽  
Malignant Soft Tissue Tumor ◽  
Pathological Evaluation ◽  
Malignant Soft Tissue ◽  
Female Genital

Abstract Background Alveolar soft part sarcoma (ASPS) is a rare malignant soft tissue tumor, mainly localized in the extremities, occurring principally in adolescents and young adults. ASPS is uncommon in the female genital tract. Case report We here report a case of ASPS in a 20-year-old nullipara, presenting with vaginal bleeding and profound anemia requiring blood transfusions. Ultrasonographic examination revealed a polyp in the lower uterine segment. Surgical resection of the polyp was performed, and pathological evaluation showed the typical histological, immunohistochemical, and molecular features consistent with ASPS. At the time of this report, the patient was scheduled for total hysterectomy with promising results. Conclusion Given the infrequency of ASPS, pathological evaluation is or utmost importance in order to establish an accurate diagnosis. When presenting as a primary tumor, complete excision is fundamental in the treatment.

Alveolar Soft Part Sarcoma of Uterine Corpus in a Young Female

2020 ◽  
Vol Publish Ahead of Print ◽  
Author(s):  
Vikarn Vishwajeet ◽  
Poonam Elhence ◽  
Pratibha Singh ◽  
Navdeep K. Ghuman
Keyword(s):  
Soft Part ◽  
Young Female ◽  
Alveolar Soft Part Sarcoma ◽  
Uterine Corpus

Small cell neuroendocrine carcinoma of the nasal cavity and paranasal sinuses: a rare case

2012 ◽  
Vol 126 (12) ◽  
pp. 1284-1286 ◽  
Author(s):  
I P Tang ◽  
S Singh ◽  
G Krishnan ◽  
L M Looi
Keyword(s):  
Nasal Cavity ◽  
Neuroendocrine Carcinoma ◽  
Paranasal Sinuses ◽  
Rare Case ◽  
Surgical Excision ◽  
Small Cell ◽  
High Rate ◽  
Intracranial Extension ◽  
Small Cell Neuroendocrine Carcinoma ◽  
Rare Tumour

AbstractObjective:We report a rare case of small cell neuroendocrine carcinoma of the nasal cavity and paranasal sinuses with intracranial extension, and discuss the management of this rare tumour.Results:Small cell neuroendocrine carcinoma involving the nasal cavity and paranasal sinuses with intracranial extension may be treated successfully with surgery alone, without development of local recurrence.Conclusion:Small cell neuroendocrine carcinoma is a locally aggressive tumour with a high rate of recurrence. Early and aggressive surgical excision with or without radiotherapy or chemotherapy can improve a patient's outcome and prognosis. Regular follow up is needed to detect any local or distant recurrence.

Alveolar Soft Part Sarcoma of the Head and Neck Region

1998 ◽  
Vol 107 (9) ◽  
pp. 810-814 ◽  
Author(s):  
Brian C. Hunter ◽  
Alfio Ferlito ◽  
Kenneth O. Devaney ◽  
Alessandra Rinaldo
Keyword(s):  
Head And Neck ◽  
Soft Part ◽  
Neck Region ◽  
Surgical Excision ◽  
Alveolar Soft Part Sarcoma ◽  
Malignant Neoplasms ◽  
Head And Neck Region ◽  
Neck Area ◽  
Over Time ◽  
Sizable Number

Alveolar soft part sarcoma is a soft tissue malignancy most often found in the extremities of young adults; when these tumors arise in the head and neck area, they usually appear in the orbit or the tongue. Their initial behavior is relatively indolent, but over time a sizable number of these tumors recur locally and metastasize; as such, they are best regarded as fully malignant neoplasms. The derivation of these tumors remains uncertain: while some have suggested that these are tumors of muscle origin and others have postulated a neuroendocrine origin, the evidence accumulated to date is conflicting, and so these neoplasms continue to be regarded as tumors of uncertain origin. Surgical excision is the mainstay of therapy.

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