scholarly journals Neonatal Sacrococcygeal Teratoma: Our Experience with 10 Cases

2013 ◽  
Vol 2 (1) ◽  
pp. 4 ◽  
Author(s):  
Shalini Sinha ◽  
Yogesh Kumar Sarin ◽  
Vidyanand P Deshpande

Aim: To analyse the outcome of neonatal sacrococcygeal teratomas (SCT) in our setup.Materials and Methods: Hospital records of 10 neonates, who were operated for SCT during 14 years time period, were retrieved and analysed. Letters were sent to 6 parents/ caretakers of children who were lost to follow up; none of them responded.Results: Seven girls and 3 boys with a mean age of 9 days (range 1- 30 days) underwent excision of SCT in the neonatal period. Antenatal pickup rates were poor (2/10). Two patients presented with tumor rupture. Though all had an obvious mass at birth, only half of them presented on day 1 of life. The remaining 5 patients came late at a mean age of 11 days. Half of the SCTs were 10 cm or larger in size. One patient was misdiagnosed as meningomyelocoele. All underwent complete excision with coccygectomy by posterior approach in prone position. There were only 2 patients who could be classified as Altman Type II, the rest were all Altman Type I. Histopathology (HPE) revealed mature cystic teratoma (n=8), grade 1 immature teratoma (n=1) and grade 3 immature teratoma (n=1). There was no mortality; and complications were seen in 3/10 patients (1 neurogenic bladder, 1 major wound infection with ventriculitis and 1 minor wound infection). The mean follow up was 25 months (range 1 month to 6 years) in 4 patients with no recurrence.Conclusions: Neonatal SCTs are usually benign with a good outcome after complete surgical excision with a low complication rate. Although long term follow up has been advocated, the follow up was poor in this series.

Author(s):  
Budiman Ritonga ◽  
Kadek Deddy Ariyanta ◽  
I. Made Darmajaya

Mature sacrococcygeal teratoma (SCT) are uncommon neoplasm comprised of mixed elements derived from three germ layers. They attract attention because of their gross appearance and bizarre histology. Tumor of the sacrococcygeal region, referred to as sacrococcygeal teratomas (SCTs) in most reports, generally present in two distinct fashions: neonates with large predominately external lesions, which are detected in utero or at birth and are rarely malignant; and older infants and children who present with primarily hidden pelvic tumors with a much higher rate of malignancy. Sacrococcygeal teratomas are the most common extragonadal tumor in neonates, accounting for up to 70% of all teratomas in childhood. A 3 to 4:1 female to male ratio is generally reported. Surgical resection remains the mainstay of therapy and recurrence is rare following complete excision. A 14 years old girl was presented to us by her parents with a mass at the buttock since birth. She was delivered at home by traditional midwife after a term, unsupervised pregnancy to a 35 years old woman. Both pregnancy and delivery were uneventful. Direct rectal examination revealed a mass has displaced the recto-sigmoid anteriorly. The CT scan revealed a heterogenous mass with a solid, cystic, and multiple classification density at the anterior of coccygeus bone, and push the coccygeus to the posterior. The mass infiltrated the subcutis, and attached to the posterior aspect of rectum. A 14 years old girl presented by mature SCT since newborn comprising ectoderm, mesoderm, and endoderm tissue. She had a complete surgical excision (including coccygectomy) with primary wound closure. A complete surgical excision remains the mainstay of therapy of mature SCT.


2021 ◽  
pp. 1-3
Author(s):  
Sanjib Kumar Jena ◽  
Prajwaleet Gour ◽  
Kamalkant Khidtta ◽  
Debraj Saha

OBJECTIVE: 1.To demonstrate the clinical presentation, radiological features, management and histopathological features of sacrococcygeal tumors in neonates. Material And Methods: Between 1st March 2020 and 1st December 2020, 5 cases(4 male, 1 female) of sacrococcygeal teratomas(SCT) were diagnosed in Government Medical College Nagpur using ultrasonography(USG) and Computed tomography(CT) scans. In each case, tumor size, its content, mass effect, and classication according to the Altman's criteria were determined and compared with other features. Then the patients underwent surgery and samples were sent for histopathological correlation. Results: Among the 5 patients, 3 were of Type I type and 2 were of type II type. In histopathological reports, 4 were of mature type and 1 was of immature type. Conclusion: USG and CT scans are effective in diagnosing and localizing the extent and involvement of SCT. SCT appear to be entirely benign during the neonatal period. Complete surgical excision remains the mainstay of treatment.


2019 ◽  
Vol 12 (6) ◽  
pp. e229486 ◽  
Author(s):  
Sherif Monib ◽  
Mohamed Ibrahim

Male genital tract angiomyofibroblastoma (AMF) is a rare benign tumour, with a total of 34 cases reported in literature. We are presenting a case of AMF of the glans penis in a 68-year-old man who presented with a progressively increasing in size large lesion located on the tip of his penis. Following routine investigations, the lesion was surgically excised with no adjuvant treatment, the patient was followed-up for 5 years with no evidence of local, nodal or distant recurrence. As AMF of the glans penis is extremely rare, there is not enough literature to support management guide lines, but it appears that AMF responds very well to complete surgical excision; occasional cases of recurrence have been previously reported, so a long-term follow-up is advised.


2020 ◽  
Vol 56 (4) ◽  
pp. 309
Author(s):  
Dita Paramita Oktaviani ◽  
Sakti Hoetama ◽  
Soetojo Soetojo

Parameatal urethral cyst is a scarce congenital condition that was first reported in two males in 1956, until now in reported literature only found less than 50 cases, in both adults and children. Our patient, case of parameatal urethral cyst in a 5 years old boy is reported. Complete excision with total removal of the epithelium of the cyst is required management for the treatment and prevention of cyst reocurrance. A 5 years old male with a cystic lesion around urethral meatus since birth. At least 5 month the parents complain distorted urinary flow and poor appearance, and no other urinary symptom, no history of trauma. On physical examination, cystic mass with spherical shape which was about 0.5 cm in diameter was found around external meatus. There was no inflammatory sign. And there was normal blood laboratory (blood counts and blood chemistry) and urine laboratory (urine analysis and urine culture). The patient undergo completely excision of the cyst under general anaesthesia, and remove all of the lining epithelium. Good appearance results were obtained after 2 months follow up, without meatal strictures and urine stream problems, and no postoperative complications or recurrence. Pathological : Squamous epithelial, granulation tissue with chronic inflamation. Parameatal urethral cyst is a very rare benign condition that is asymptomatic in most of the cases. It may be present since birth or appear later and is prevalent in young males. Its etiology remains unclear and treatment is by complete surgical excision to avoid complications and recurrence. Good cosmetic results were obtained in this case without any recurrence at two months follow-up.


2010 ◽  
Vol 25 (9) ◽  
pp. 2976-2981 ◽  
Author(s):  
E. Puricelli ◽  
A. Bettinelli ◽  
N. Borsa ◽  
F. Sironi ◽  
C. Mattiello ◽  
...  

2009 ◽  
Vol 9 (3) ◽  
pp. 454-458 ◽  
Author(s):  
O. Friberg ◽  
L.-G. Dahlin ◽  
J. Kallman ◽  
E. Kihlstrom ◽  
B. Soderquist ◽  
...  

FACE ◽  
2021 ◽  
pp. 273250162110536
Author(s):  
Joshua Harrison ◽  
Samantha Marley ◽  
Shawhin Shahriari ◽  
Christian Bowers ◽  
Anil Shetty

We report a rare case of an extramedullary plasmacytoma (EMP) in the frontal sinus with an indolent clinical presentation. Although a history of trauma was absent, the initial diagnosis was a mucocele, based on the radiological findings. Upon surgical excision, the patient was found to have an EMP. EMP, a form of solitary plasmacytoma, has a significantly high rate of conversion to multiple myeloma. This mandates long-term follow-up, even after successful radiotherapy and/or resection. While radiation therapy is generally considered a first line treatment for EMP, surgical intervention may provide optimal treatment in complicated cases. This case presentation highlights the prognosis of patients diagnosed with EMP.


Author(s):  
Rajiv Kumar Jain ◽  
Chultim D. Bhutia ◽  
Deepak Kumar Gupta ◽  
Ashvanee Kumar Chaudhary ◽  
Gagan Rangari ◽  
...  

<p class="abstract">Pleomorphic adenoma are common benign salivary gland tumours, which are found in majority in major salivary glands such as parotids and submandibular glands. However, Pleomorphic adenoma to originate from dorsum of the nose is a rare entity. In rare cases, it can be found in unusual sites such as upper aero digestive tracts, palate and lacrimal glands. Complete surgical resection is the treatment of choice. Though, the evolution to malignancy and recurrence is not usually encountered, still a long-term follow-up is recommended. Here, we report a 53 year old female , complained of swelling in the left side of dorsum of nose for 10 years with a feeling of heaviness over the left side of face and difficulty in vision on the side of swelling due to the enlarged size of the swelling which gave a feeling of vision disruption , also had a prior history of  incision and drainage 4 years ,done elsewhere. On clinical examination, nodular mass was palpated on left side dorsum of nose which was freely mobile, and Skin over the swelling had blackish pigmentation. Anterior rhinoscopy revealed no abnormalities. Complete surgical excision via a lateral rhinotomy incision was performed. Cytological and histological evaluation revealed the presence of pleomorphic adenoma. We observed a decent cosmetic outcome with no evidence of recurrence.</p>


2021 ◽  
Vol 14 (9) ◽  
pp. e242242
Author(s):  
Zhi Yon Charles Toh ◽  
Thomas Cooper ◽  
Maryam Jessri ◽  
Frank S-C Chang

Granular cell tumour (GCT) is a rare soft tissue lesion which many consider to have malignant potential of yet unknown aetiopathogenesis. Oral GCT lesions may occur in an area of leucoplakia and are predominantly present on the tongue. This case study highlights an uncommon presentation of this condition located on the buccal mucosa and illustrates the need for meticulous evaluation of suspicious lesions. Due to the malignant risk associated with GCT lesions, it is important to make the correct diagnosis and ensure complete surgical excision for these cases. Ongoing long-term follow-up is also indicated to monitor for recurrence or malignancy.


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