Catching Takayasu Early: Diagnosing the “Pulseless” Disease in a Child with Palpable Pulses

Takayasu arteritis is a systemic vasculitis of large vessels that mainly involves the aorta and its branches. It normally presents in the third decade of life and is rarely seen in children. We report a case of childhood Takayasu arteritis, in a 12-year-old girl, who presented with abdominal pain and hypertension. Although all her peripheral pulses were palpable, there was a discrepancy between her upper and lower limbs’ blood pressure. CT angiography revealed stenosis of the abdominal aorta, at the origin of the celiac artery and right renal artery. She was started on steroids and an antihypertensive, after which she attained remission. Five years down the line, the child has sustained remission, with no signs of disease progression. Early diagnosis of Takayasu and initiation of immunosuppression, before the onset of the classic “pulseless” phase, may contribute to improved long-term prognosis.

Absent Bilateral Upper Limb Pulses in Middle Age Male? Takayasu Arteritis

Takayasu arteritis also termed as pulseless disease is a rare and chronic inflammatory arteritis of large vessels. It is manifested mainly in young age group between 10-40 years with a female predominance. Anesthetic management of these patients is challenging in view of fluctuation in blood pressure, intimal fibrosis and stenosis of major blood vessels and multiorgan involvement. Here we present a case of 55 year old male patient with bilateral absent upper limb pulses posted for emergency surgery in view of gall bladder perforation that was successfully managed under general anesthesia. Keywords: Takayasu; Chronic; Inflammatory.

Atypical Presentation of Takayasu's Arteritis—A Case Report

Takayasu's arteritis, known as “pulseless disease,” is a chronic idiopathic inflammatory disease, which has a greater predilection for large vasculature in the body. Initially described in the1800s, this rare condition is more commonly seen in Asian women in 40 years age group. Herein, the authors report the case of a 36-year-old woman whose exertional claudication was the initial manifestation of active Takayasu's arteritis along with involvement of multiple peripheral arteries not involving ostial area of the vessels, instead affecting the proximal area and also presenting with thrombosis of right CIA (common iliac artery), which is an unusual presentation in case of Takayasu's arteritis without aneurysmal involvement.

Stenting in Takayasu’s Arteritis: A Case Report

Takayasu arteritis (TA), also known as idiopathic medial aortopathy or pulseless disease, is a granulomatous large vessel vasculitis that predominantly affects the aorta and its major branches. It may also affect the pulmonary arteries. The exact cause is not well known but the pathology is thought to be similar to giant cell arteritis. There is segmental and patch granulomatous inflammation of the aorta which results in stenosis, thrombosis and aneurysm formation. Half of the patients present with an initial systemic illness whereas the other 50% present with late-phase complications. There is a strong female predominance (F: M ~ 9:1), an increased prevalence in Asian populations, and it tends to affect younger patients (<50 years of age). The typical age of onset is at around 15-30 years of age. Here, it is reported a case of 9 years old girl with Takayasu’s arteritis.

Scleritis and Takayasu’s disease – rare combined presentation

Introduction: Takayasu’s disease (TD) (pulseless disease, aortic arch syndrome) is a rare but potentially life-threatening chronic giant cell vasculitis. The major complications attributed to the disease include Takayasu’s retinopathy, secondary hypertension, aortic regurgitation, and arterial aneurysm. The aim of this study is to describe a patient with Takayasu’s disease and scleritis and to show its association.Case report: We describe a 44-year-old female patient with Takayasu’s disease who presented with bilateral anterior scleritis in the form of painful red eye. Patient did not have any associated autoimmune diseases. Patient was diagnosed to have TD and was treated with immunosuppressant.Conclusion: Scleritis though rare can be a vasculitic feature of TD. This is a first report of Takayasu’s disease with scleritis, which has been documented in Nepal.

Takayasu’s arteritis in pregnancy: a rare case report from BJGMC and Sassoon Hospital Pune, Maharashtra, India

Takayasu’s arteritis is a chronic idiopathic vasculitis affecting aorta and its primary branches, commonly seen in young women of Asian or oriental descent during child bearing age. Incidence is 2.6 cases/million/year. It affects females in the reproductive years accounting for almost 80% of the cases. A 34 year female G2P1L1 with 9 months of amenorrhea with previous LSCS known case of takayasu arteritis, epilepsy with right side hemiparesis with aphasia. She proceeded to have elective LSCS with ventouse delivery under epidural anaesthesia and delivered alive healthy female baby weight 2.4 kg and patient was transferred to intensive care unit for observation for 48 hrs. patients intrapartum post partum period was uneventful and discharged after 1month with cardiology fitness. Pregnancy with takayasu arteritis (pulseless disease) requires a multidisciplinary management from gynaecologist, cardiologist, neurologist for favourable maternal and fetal outcome.

Takayasu Arteritis Involving Multiple Peripheral Arteries of a 37-year-old Female: A Case Report and Brief Overview

Takayasu arteritis, formerly known as “pulseless disease”, is a chronic idiopathic vasculitis which affects the large vessels in the body. First described in the 1800’s, this rare condition is more commonly found in Asian women in their 40’s. Herein, we report the case of a young woman whose exertional angina and claudication were the initial presentation of active Takayasu arteritis. The importance of modern technology of imaging such as CT, MRI and angiography, can often have paramount importance for confirming a diagnosis and the extent of the pathology. Newer modalities of investigation helps in evaluation of vascular involvement and its haemodynamic effects on cardiovascular system. Previously majority of patient had to be diagnosed clinically. Now a days by CT peripheral Angiogram this disease can be diagnosed. Invasive procedure of peripheral Angiogram is troublesome but single IV dye injection can revealed the actual scenario. So it has got important scientific value.Bangladesh Heart Journal 2015; 30(2) : 92-95

A Case Report of Takayasu’s Arteritis

Takayasu’s arteritis, or “pulseless” disease is a rare, idiopathic, chronic granulomatous vasculitis that affects aorta and its major branches. This report describes a 57- year-old man who presented with gradual loss of vision, syncopal attack and arm claudication. His ocular findings suggested bilateral ocular ischemic syndrome. He was later diagnosed as having Takayasu’s disease.DOI: http://dx.doi.org/10.3329/medtoday.v24i2.15013 Medicine Today 2012 Vol.24(2): 79-81

An unusual “pulseless disease”

Simultaneous loss of upper extremity pulses, excluding shock, is present in clinical pictures like aortic dissection (type 1 sec. De Backey), but remarkably in Takayasu’s arteritis, named “pulseless disease”. We describe a case of loss of upper extremities pulses secondary to bilateral simultaneous artery embolization during atrial fibrillation.