Relationship of Plasma Acute-Phase Protein to Amino Acid Levels During High-Dose Branched Chain Amino Acid Support in Sepsis

Author(s):  
C. Chiarla ◽  
I. Giovannini ◽  
J. H. Siegel ◽  
M. Castagneto
1984 ◽  
Vol 8 (6) ◽  
pp. 622-627 ◽  
Author(s):  
Roger A. Bonau ◽  
S.D. Ang ◽  
Malayappa Jeevanandam ◽  
John M. Daly

2016 ◽  
Vol 3 ◽  
Author(s):  
Urho M. Kujala ◽  
Markku Peltonen ◽  
Merja K. Laine ◽  
Jaakko Kaprio ◽  
Olli J. Heinonen ◽  
...  

2011 ◽  
Vol 30 (10) ◽  
pp. 1724-1727 ◽  
Author(s):  
Vefik Arica ◽  
Secil Gunher Arica ◽  
Huseyin Dag ◽  
Hatice Onur ◽  
Ömer Obut ◽  
...  

Beta-ketothiolase deficiency is a rare autosomal recessive disorder of isoleucine and ketone body metabolism. This disorder is clinically characterized by ketoacidotic attacks. Ketoacidosis, vomiting, and dehydration, lethargy and coma may be seen during attacks. A 9-month-old girl was admitted to our hospital with acidosis and dehydration. The patient was lethargic. Ketoacidosis was suspected because of acetone odor on her breath. Her blood glucose level was 262 mg/dL and urine ketone was (++++). Branched chain amino acid levels were elevated in her blood sample. Organic acid analysis of urine revealed 2-methylacetoacetyl-CoA thiolase deficiency. This was reported because of rarity of the disease and we should consider it in the differential diagnosis of ketoacidotic episodes.


2015 ◽  
Vol 1 (6) ◽  
Author(s):  
Bénédicte Allam-Ndoul ◽  
Frédéric Guénard ◽  
Véronique Garneau ◽  
Olivier Barbier ◽  
Louis Pérusse ◽  
...  

Sign in / Sign up

Export Citation Format

Share Document