scholarly journals Cochlea implantation in patients with superficial hemosiderosis

Author(s):  
E. Artukarslan ◽  
F. Matin ◽  
F. Donnerstag ◽  
L. Gärtner ◽  
T. Lenarz ◽  
...  

Abstract Introduction Superficial hemosiderosis is a sub-form of hemosiderosis in which the deposits of hemosiderin in the central nervous system damage the nerve cells. This form of siderosis is caused by chronic cerebral hemorrhages, especially subarachnoid hemorrhages. The diversity of symptoms depends on the respective damage to the brain, but in most of the cases it shows up as incipient unilateral or bilateral hearing loss, ataxia and signs of pyramidal tracts. We are investigating the question of whether cochlear implantation is a treatment option for patients with superficial hemosiderosis and which strategy of diagnostic procedure has to be ruled out preoperatively. Materials and methods In a tertiary hospital between 2009 and 2018, we examined (N = 5) patients with radiologically confirmed central hemosiderosis who suffered from profound hearing loss to deafness were treated with a cochlear implant (CI). We compared pre- and postoperative speech comprehension (Freiburg speech intelligibility test for monosyllables and HSM sentence test). Results Speech understanding improved on average by 20% (monosyllabic test in the Freiburg speech intelligibility test) and by 40% in noise (HSM sentence test) compared to preoperative speech understanding with optimized hearing aids. Discussion The results show that patients with superficial siderosis benefit from CI with better speech understanding. The results are below the average for all postlingual deaf CI patients. Superficial siderosis causes neural damages, which explains the reduced speech understanding based on central hearing loss. It is important to correctly weigh the patient's expectations preoperatively and to include neurologists within the therapy procedure.

2021 ◽  
pp. 014556132110640
Author(s):  
Hantai Kim ◽  
Jungho Ha ◽  
Eun Sol Gil ◽  
Jeong Hun Jang ◽  
Hun Yi Park ◽  
...  

Objectives When there is a difference in hearing on both ears, where to perform the first cochlear implantation (CI) becomes an important issue. The purpose of the study was to evaluate which ear should be chosen for the first implantation in sequential bilateral CI with a long inter-implant period. Methods The study population consisted of 34 severe-to-profound sensorineural hearing loss pediatrics with the inter-implant period of ≥3 years between the first CI (CI-1) and the second CI (CI-2) before the age of 19 (mean of inter-implant period: 7.1-year). The patients were classified into Group A (CI-1 was performed on the ear with better hearing), Group B (CI-1 on the ear with worse hearing), or Group C (symmetrical hearing in both ears). Speech intelligibility test results were compared between the groups. Results The monosyllabic word scores of CI-1 were excellent in Groups A (91.7±7.9%) and B (92.5±3.6%) but slightly lower in Group C (85.7±14.9%) before the second implantation ( P = .487). At 3 years after the second implantation, all groups demonstrated excellent scores in the bilateral CI condition (95.9±3.0% in Group A; 99.1±.8% in Group B; 97.5±2.9% in Group C, P = .600). However, when the patients were tested in using CI-2 only in Groups A and B after using bilateral CI for 3 years, the scores were inconsistent in Group A (79.6±23.9%; range: 22.2-94.4%), while those were higher and more constant in Group B (92.9±4.8%; 86.8-100.0%). Conclusions The first CI is strongly recommended to perform on a worse hearing ear if they had different hearing levels between ears. Even with the first CI on a worse hearing ear, its performance never deteriorates. In addition, if they receive the second CI several years later, it will be likely that the second one functions better.


1966 ◽  
Vol 9 (2) ◽  
pp. 253-258 ◽  
Author(s):  
James Jerger ◽  
Carolyn Malmquist ◽  
Charles Speaks

A sentence intelligibility test and three monosyllabic word intelligibility tests, recorded through three hearing aids, were presented to 36 subjects with diverse types of hearing loss. Although hearing aids were rank ordered meaningfully on the sentence intelligibility test-in inverse proportion to the harmonic distortion-performance differences were not systematically reflected in the monosyllabic word test results.


Informatics ◽  
2021 ◽  
Vol 18 (3) ◽  
pp. 68-82
Author(s):  
M. I. Porhun ◽  
M. I. Vashkevich

A method for the simulation of reduced frequency resolution of the ear in patients with sensorineural hearing loss is proposed. The method is based upon the ability to adjust it according to the audiogram of a concrete person by frame-by-frame signal processing in the frequency domain. Simulation of the effect of the reduced frequency resolution of the ear is achieved by processing the components of amplitude spectrum of the original sound signal by the "smearing" function. The "smearing" function is formed from the amplitude-frequency characteristics of the auditory filters, which bandwidth is determined by the audiogram of the deaf person. The proposed method is implemented in the MATLAB. An experimental study of the effect of the reduced frequency resolution of the ear using the speech intelligibility test was conducted. The experiment involved 15 people who listened the records processed by the proposed method with various settings and noise conditions. Experimental data have shown that reduced frequency resolution of the ear leads to the deterioration in speech intelligibility, especially in the presence of background noise. Based on the answers of the participants of the experiment, the confusion tables of sounds were compiled, reflecting the fact of indistinguishability of sounds similar in frequency, that confirms the correctness of the proposed method.


1990 ◽  
Vol 88 (S1) ◽  
pp. S175-S175
Author(s):  
Michael Nilsson ◽  
Jean Sullivan ◽  
Sigfrid D. Soli

2011 ◽  
Vol 31 (35) ◽  
pp. 12638-12643 ◽  
Author(s):  
J. E. Peelle ◽  
V. Troiani ◽  
M. Grossman ◽  
A. Wingfield

2017 ◽  
Vol 28 (01) ◽  
pp. 058-067 ◽  
Author(s):  
Samuel R. Atcherson ◽  
Lisa Lucks Mendel ◽  
Wesley J. Baltimore ◽  
Chhayakanta Patro ◽  
Sungmin Lee ◽  
...  

AbstractIt is generally well known that speech perception is often improved with integrated audiovisual input whether in quiet or in noise. In many health-care environments, however, conventional surgical masks block visual access to the mouth and obscure other potential facial cues. In addition, these environments can be noisy. Although these masks may not alter the acoustic properties, the presence of noise in addition to the lack of visual input can have a deleterious effect on speech understanding. A transparent (“see-through”) surgical mask may help to overcome this issue.To compare the effect of noise and various visual input conditions on speech understanding for listeners with normal hearing (NH) and hearing impairment using different surgical masks.Participants were assigned to one of three groups based on hearing sensitivity in this quasi-experimental, cross-sectional study.A total of 31 adults participated in this study: one talker, ten listeners with NH, ten listeners with moderate sensorineural hearing loss, and ten listeners with severe-to-profound hearing loss.Selected lists from the Connected Speech Test were digitally recorded with and without surgical masks and then presented to the listeners at 65 dB HL in five conditions against a background of four-talker babble (+10 dB SNR): without a mask (auditory only), without a mask (auditory and visual), with a transparent mask (auditory only), with a transparent mask (auditory and visual), and with a paper mask (auditory only).A significant difference was found in the spectral analyses of the speech stimuli with and without the masks; however, no more than ∼2 dB root mean square. Listeners with NH performed consistently well across all conditions. Both groups of listeners with hearing impairment benefitted from visual input from the transparent mask. The magnitude of improvement in speech perception in noise was greatest for the severe-to-profound group.Findings confirm improved speech perception performance in noise for listeners with hearing impairment when visual input is provided using a transparent surgical mask. Most importantly, the use of the transparent mask did not negatively affect speech perception performance in noise.


2021 ◽  
Vol 20 (4) ◽  
pp. 8-14
Author(s):  
M. Yu. Boboshko ◽  
◽  
E. V. Zhilinskaya ◽  
◽  

Deterioration in speech intelligibility, the most common complaint of people with hearing loss, leads to social isolation and dramatically reduces the quality of life. The correction of peripheral hearing loss by hearing aid fitting does not always solve this problem in patients with chronic sensorineural hearing loss (SNHL). That is why in the process of audiological examination of patients with complaints of hearing loss, it is necessary to include methods of speech audiometry, which make it possible to comprehensively assess the functioning of the auditory system. The aim of the study: assessment of speech intelligibility in patients of different ages with SNHL. 94 people from 20 to 74 years of age were examined: 54 patients with SNHL (14 young and 40 elderly) and 40 people with normal hearing thresholds (20 young and 20 elderly). Besides the standard audiological examination, speech audiometry testing was conducted: evaluation of monosyllabic words intelligibility in quiet, binaural rapidly alternating speech test, dichotic digits test, Russian matrix sentence test (RuMatrix). Results: Speech intelligibility in elderly patients with SNHL was shown to be significantly worse than in young patients with a similar degree of hearing loss. The RuMatrix test in noise was proved to be the most sensitive test for comprehensive evaluation of the hearing system functioning.


Revista CEFAC ◽  
2010 ◽  
Vol 12 (4) ◽  
pp. 662-670 ◽  
Author(s):  
Tatiane Maria Pelitero ◽  
Alessandra Kerli da Silva Manfredi ◽  
Andrea Pires Corrêa Schneck

OBJETIVO: comparar o desempenho na Avaliação Simplificada do Processamento Auditivo (ASPA) e no Pediatric Speech Intelligibility Test (PSI), de crianças com alteração de Aprendizagem da Leitura e Escrita e sem este tipo de alteração. MÉTODOS: participaram da pesquisa 28 crianças na faixa etária de 8 a 12 anos, do sexo masculino e feminino. Os participantes foram submetidos ao Teste de Desempenho Escolar (TDE) para a categorização dos grupos de estudo e controle, e, para avaliação das habilidades auditivas foram aplicados a ASPA e o Teste PSI. RESULTADOS: não foi observada associação estatisticamente significante entre o desempenho nos testes de Processamento Auditivo (PA) e o grupo com dificuldades de aprendizagem, apesar de ter sido verificada maior frequência de alterações no grupo de estudo em relação ao grupo controle, em todos os testes. Na ASPA, o teste em que se observou maior número de alterações foi o Teste de Memória Sequencial Verbal, contudo, o Teste de Memória Sequencial Não-verbal foi o que mostrou maior diferença entre os grupos. CONCLUSÃO: Não foram encontradas diferenças estatisticamente significantes no desempenho na Avaliação Simplificada do Processamento Auditivo (ASPA) e no Pediatric Speech Intelligibility Test (PSI), das crianças com alteração de Aprendizagem da Leitura e Escrita e sem alteração.


2005 ◽  
Vol 114 (7) ◽  
pp. 533-538 ◽  
Author(s):  
Chris Halpin ◽  
Grace Owen ◽  
Gustavo A. Gutiérrez-Espeleta ◽  
Katherine Sims ◽  
Heidi L. Rehm

Objectives: Norrie disease is an X-linked recessive disorder in which patients are born blind and develop sensory hearing loss in adolescence. The hearing loss associated with Norrie disease has been shown in a genetically altered knockout mouse to involve dysfunction of the stria vascularis; most other structures are preserved until the later stages of the disease. The objective of this study was to characterize the audiologic phenotype of Norrie disease for comparison with the pathophysiologic mechanism. Methods: The design combined two series of clinical audiologic evaluations, with special attention to speech intelligibility. Results: The audiologic results for 12 affected individuals and 10 carriers show that patients with Norrie disease retain high speech intelligibility scores even when the threshold loss is severe. Conclusions: The cochlear mechanism — failure of the stria vascularis — accounts for some of the higher values in the wide distribution of speech scores in cases with similar pure tone audiograms.


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