B098 20-Years of cochlear implantation at the national research center for audiology and hearing rehabilitation

2011 ◽  
Vol 75 ◽  
pp. 28
Author(s):  
G. Tavartkiladze ◽  
N. Dmitriyev ◽  
V. Fedoseev ◽  
N. Mileshina ◽  
V. Bakhshinyan ◽  
...  
Keyword(s):  
Cochlear Implantation ◽  
Research Center ◽  
Hearing Rehabilitation

Subtotal Petrosectomy with Cochlear Implantation or Osseointegrated Hearing Rehabilitation

2021 ◽  
Vol Publish Ahead of Print ◽  
Author(s):  
Kathy Zhang ◽  
Flora Yan ◽  
Shaun A. Nguyen ◽  
Ted A. Meyer
Keyword(s):  
Cochlear Implantation ◽  
Hearing Rehabilitation ◽  
Subtotal Petrosectomy

scholarly journals Halláscsökkenést okozó etiológiai tényezők cochlearis implantáción átesett gyermekekben

2019 ◽  
Vol 160 (21) ◽  
pp. 822-828
Author(s):  
Nóra Kecskeméti ◽  
Anita Gáborján ◽  
Magdolna Szőnyi ◽  
Marianna Küstel ◽  
Ildikó Baranyi ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Cochlear Implantation ◽  
Speech Development ◽  
Sensorineural Hearing ◽  
Diagnostic Process ◽  
Sufficient Information ◽  
Hearing Rehabilitation ◽  
Junction Protein ◽  
Newborn Hearing

Abstract: Introduction: Congenital sensorineural hearing loss is one of the most common sensory defects affecting 1–3 children per 1000 newborns. There are a lot of causes which result in congenital hearing loss, the most common is the genetic origin, but infection, cochlear malformation or other acquired causes can be reasons as well. Aim: The aim of this study was to establish the etiological factors of congenital profound sensorineural hearing loss in children who underwent cochlear implantation. Results: Our results show that the origin of the hearing loss was discovered in 62.9% of our patients. The most common etiological factor was the c.35delG mutation of the gap junction protein β-2 gene, the allele frequency was 38.7% in our cohort. Infection constituted to 10.1%, and meningitis and cytomegalovirus infection were the second most common cause. 79.9% of our patients received sufficient hearing rehabilitation before the end of the speech development’s period (6 years old), but 11.2% of our cases were still diagnosed late. Conclusions: Based on our data we can state that genetic evaluation is crucial in the diagnostic process of congenital profound sensorineural hearing loss. Sufficient hearing rehabilitation affects the whole life of the child, and by late cochlear implantation the speech development falls behind. We can decrease the ratio of the late implantation with the new protocol of newborn hearing screening, and with sufficient information provided to the colleagues, so the children may be referred to the proper center for rehabilitation without delay. Orv Hetil. 2019; 160(21): 822–828.

scholarly journals Mythbusters! The Truth about Common Misconceptions in Cochlear Implantation

2021 ◽  
Vol 42 (04) ◽  
pp. 352-364
Author(s):  
Erika A. Woodson ◽  
Ksenia Aaron ◽  
Ahn Nguyen-Huynh ◽  
Jonathan Vargo ◽  
Sarah E. Mowry
Keyword(s):  
Quality Of Life ◽  
Cochlear Implantation ◽  
Positive Impact ◽  
Insurance Coverage ◽  
Residual Hearing ◽  
Mri Scan ◽  
Hearing Rehabilitation ◽  
Anesthetic Risk ◽  
Common Misconceptions

AbstractCochlear implantation (CI) is the preferred method of hearing rehabilitation when patients cannot perform well with traditional amplification. Unfortunately, there are still significant misconceptions around this life-changing intervention. The goal of this article is to address some of the most common myths around CI surgery. After reading this article, the learner will be able to explain the utility of CI in patients with residual hearing and recognize that insurance coverage is widespread. The reader will be able to list common risks associated with this well-tolerated procedure including anesthetic risk and the risk of vestibular dysfunction. Additionally, the reader will be able to identify the significant positive impact of CI on patients' quality of life. Finally, the reader will identify that many patients can safely have an MRI scan after implantation, including nearly all contemporary recipients.

Cochlear implantation in superficial siderosis

1996 ◽  
Vol 110 (12) ◽  
pp. 1151-1153 ◽  
Author(s):  
Richard M. Irving ◽  
John M. Graham
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Hearing Loss ◽  
Cochlear Implantation ◽  
Superficial Siderosis ◽  
Nervous System Disorder ◽  
Central Nervous System Disorder ◽  
Hearing Rehabilitation ◽  
System Disorder ◽  
Careful Assessment

AbstractSuperficial siderosis is a rare central nervous system disorder characterized by deafness, ataxia, and pyramidal signs. The hearing loss is believed to be predominantly neural and is usuallly progressive and bilateral. Careful assessment is therefore necessary to determine the best approach to hearing rehabilitation. A case is presented of usperficial siderosis in a young woman who has benegited significantly from cochlear implantation using the Nucleus dvice.

scholarly journals TMPRSS3 Gene Variants With Implications for Auditory Treatment and Counseling

2021 ◽  
Vol 12 ◽  
Author(s):  
In Seok Moon ◽  
Andrew R. Grant ◽  
Varun Sagi ◽  
Heidi L. Rehm ◽  
Konstantina M. Stankovic
Keyword(s):  
Hearing Loss ◽  
Genetic Testing ◽  
Cochlear Implantation ◽  
Clinical Manifestations ◽  
Clinical Information ◽  
Hearing Rehabilitation ◽  
Novel Variants ◽  
Novel Variant ◽  
Number Variation ◽  
Syndromic Hearing Loss

Objective: To identify and report novel variants in the TMPRSS3 gene and their clinical manifestations related to hearing loss as well as intervention outcomes. This information will be helpful for genetic counseling and treatment planning for these patients.Methods: Literature review of previously reported TMPRSS3 variants was conducted. Reported variants and associated clinical information was compiled. Additionally, cohort data from 18 patients, and their families, with a positive result for TMPRSS3-associated hearing loss were analyzed. Genetic testing included sequencing and copy number variation (CNV) analysis of TMPRSS3 and the Laboratory for Molecular Medicine’s OtoGenome-v1, -v2, or -v3 panels. Clinical data regarding patient hearing rehabilitation was interpreted along with their genetic testing results and in the context of previously reported cochlear implant outcomes in individuals with TMPRSS3 variants.Results: There have been 87 previously reported TMPRSS3 variants associated with non-syndromic hearing loss in more than 20 ancestral groups worldwide. Here we report occurrences of known variants as well as one novel variant: deletion of Exons 1–5 and 13 identified from our cohort of 18 patients. The hearing impairment in many of these families was consistent with that of previously reported patients with TMPRSS3 variants (i.e., typical down-sloping audiogram). Four patients from our cohort underwent cochlear implantation.Conclusion: Bi-allelic variants of TMPRSS3 are associated with down-sloping hearing loss regardless of ancestry. The outcome following cochlear implantation in patients with variants of TMPRSS3 is excellent. Therefore, cochlear implantation is strongly recommended for hearing rehabilitation in these patients.

scholarly journals Two Down Syndrome Patients with Bilateral Profound Hearing Loss: Case Report and Literature Review

2018 ◽  
Vol 1 (2) ◽  
pp. 8
Author(s):  
Yu Zheng ◽  
Juan-Mei Yang ◽  
Meng Zhao ◽  
Xiao-Qing Qian ◽  
Fang-Lu Chi
Keyword(s):  
Hearing Loss ◽  
Down Syndrome ◽  
Cochlear Implantation ◽  
Review Literature ◽  
Profound Hearing Loss ◽  
Rehabilitation Process ◽  
Hearing Rehabilitation ◽  
Suitability Assessment ◽  
First Case ◽  
Low Incidence

Hearing loss is not uncommon among patients with Down syndrome (DS). It has been reported in 38–78% of the Down syndrome population. However, profound hearing loss in DS patients is rarely noticed due to its low incidence. In this article, we reported two Down syndrome patients with bilateral profound hearing loss in two cases. The first case involved an eight-year-old DS child experiencing extremely severe defects in terms of language and severe defects in terms of gross motor function, adaptability, and sociability. The second case revolved around another DS child with bilateral cochlear nerve absence. We review literature on the DS patients with hearing loss and conclude that profound sensorineural hearing loss in those patients has not received enough attention so far. We also recommend that cochlear implantation (CI) suitability assessment and timely intervention via cochlear implantation are necessary in DS patients. Besides, benefits from CI would be limited and hearing rehabilitation process could be much slower when compared with children without additional inabilities.

Influence of Cochlear Implantation on Postural Control and Risk of Falls

2019 ◽  
Vol 24 (5) ◽  
pp. 245-252 ◽  
Author(s):  
Julia Louza ◽  
Christopher Rösel ◽  
Robert Gürkov ◽  
Eike Krause ◽  
Friedrich Ihler
Keyword(s):  
Postural Control ◽  
Cochlear Implantation ◽  
Individual Risk ◽  
Body Sway ◽  
Test Protocol ◽  
Hearing Rehabilitation ◽  
Risk Of Falls ◽  
The Mean ◽  
The Individual ◽  
Mean Risk

Background: Cochlear implantation is an important method of hearing rehabilitation. Earlier studies have shown the influence of implantation on the vestibular system. However, until now, the effect of hearing rehabilitation with cochlear implants (CI) on postural control and body stability has not been sufficiently studied. Objective: To analyse the effect of hearing rehabilitation with activated CI and different sound inputs (music, speech text, and white noise) on postural control and risk of falls after implantation. Methods: This was a prospective clinical trial that included 33 adult patients with at least 6 months’ use of a CI (mean time after implantation = 23 months). All patients underwent a standard or geriatric (for patients >60 years) balancing deficit test protocol with a mobile posturography system (VertiGuard®) in different situations (CI deactivated/activated and different sound inputs). As the main outcome measure, the risk of falls (%) after each protocol was calculated by evaluating body sway both forward to backward and side to side (°/s). Results: With the CI deactivated, the mean risk of falls was 45.5%. After activation of the CI, there was a small decrease in the mean risk of falls, but it was statistically significant. With an additional sound input (music or speech text) this decrease was more pronounced: 42.0 and 42.4%, respectively. This effect seems to be more pronounced in older patients. Regarding the individual patients, 72% had an improvement in the risk of falls with an activated CI, and 28% had a slight deterioration. An activated CI accompanied by sound input (music) further improved the individual risk of falls. Conclusions: Compared with prior research, this study found that the risk of falls after implantation decreased over a longer time period. Furthermore, the use of a CI and different sound inputs had a positive effect on postural control. These findings support the need for optimal hearing rehabilitation, especially in elderly patients. Although this effect is relatively small, it is important to consider for further studies that rehabilitation with CI may reduce the risk of falls. While the auditory system supposedly contributes to postural control only to a small degree and the mechanism is still poorly understood, further studies with bigger samples are warranted to clarify these effects.

scholarly journals A Case of Intralabyrinthine Schwannoma Removal and Sequential BonebridgeTM Implantation

2021 ◽  
Vol 64 (12) ◽  
pp. 949-953
Author(s):  
Jeong Hae Park ◽  
Jae Sang Han ◽  
Yeonji Kim ◽  
Shi Nae Park
Keyword(s):  
Hearing Loss ◽  
Cochlear Implantation ◽  
Benign Tumor ◽  
Bone Conduction ◽  
Tumor Removal ◽  
Hearing Rehabilitation ◽  
Bone Conduction Implant ◽  
Intralabyrinthine Schwannoma ◽  
Rare Benign Tumor ◽  
Cochlear Ossification

Intralabyrinthine schwannoma (ILS) is a rare benign tumor that arises within the membranous labyrinthine. Since hearing loss is inevitable after tumor removal in most cases, an appropriate rehabilitation method should be considered. A 41-year-old male, who was diagnosed with ILS underwent tumor removal via translabyrinthine approach, has subsequently experienced right-side deafness as a result. Seventeen months after the tumor removal, a surgery for hearing rehabilitation was performed. Since cochlear implantation was not doable due to cochlear ossification, an active transcutaneous bone conduction implant (BonebridgeTM , MEDEL) was placed at the sinodural angle. To the best of our knowledge, this is the first report describing hearing rehabilitation with BonebridgeTM implantation after ILS removal.

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