scholarly journals Symmetrical Facial Giant Plaque-Type Juvenile Xanthogranuloma: Case Report and Review of the Literature

2021 ◽  
pp. 399-406
Author(s):  
Kaspar Itin ◽  
Peter Häusermann ◽  
Peter Itin ◽  
Nicole Fosse

Juvenile xanthogranuloma (JXG) is the most common type of non-Langerhans cell histiocytosis. JXG is a rare benign tumor, which may be present at birth or develop later. The classical form of JXG is characterized by a red-yellowish benign papule or nodule with predilection sites on the head, neck, and trunk, although lesions can appear on extremities or extracutaneous sites. In most cases there is only one lesion, whereas numerous papules or nodules may occur. Special forms of JXG such as mixed, giant, subcutaneous, eruptive, clustered, and plaque-like have been reported and associations between JXG and systemic diseases have been made. Diagnosis mainly relies on the clinical appearance, and histology usually can confirm the disease. Here we present a very rare case of symmetrical giant facial plaque-type juvenile xanthogranuloma (SGFP-JXG) and compare it with classical JXG, variations of JXG, and discuss the differential diagnosis. A 4-year-old Caucasian female presented with plaque-like lesions composed of yellowish confluent papules on both the cheeks. The histological evaluation revealed a histiocytic lesion with a formation of Touton giant cells and immunohistochemistry results confirmed the diagnosis of the SGFP-JXG. In comparison to classical JXG, the onset of SGFP-JXG sometimes occurs later and the spontaneous resolution period may be prolonged. No associated diseases and no systemic involvements were observed. Histopathology is required to differentiate this form of JXG from other histiocytosis. To the best of our knowledge, only four cases of SGFP-JXG have been reported in the literature so far.

2021 ◽  
pp. 336-340
Author(s):  
Monica Ivanov ◽  
Bianca Stroe ◽  
Valeriu Ardeleanu ◽  
Razvan Hainarosie ◽  
Vlad Constantin ◽  
...  

Congenital epulis is a rare benign tumor of the newborn that could be detected in the prenatal period. Females are more often affected than males and the premaxillary region is usually the predilection site for this oral mass. Excision is the treatment of choice and no recurrences have been reported so far. We present our experience with two cases of congenital epulis, detected in the second trimester of gestation and treated shortly after birth with no further complications. Histopathology should differentiate between congenital epulis and other congenital oral tumors even if its clinical appearance is usually enough to make a tentative diagnosis. A multidisciplinary assessment in the management of this tumor can avoid unwanted complications such as airway obstruction or bleeding.


2021 ◽  
Vol 29 (8) ◽  
pp. 858-861
Author(s):  
Moeinadin Safavi ◽  
Narges Akhlaghi ◽  
Bahar Ashjaei

Lipoblastoma is a rare benign tumor of primitive white fat in children, which usually involves the trunk and extremities. It rarely involves retroperitoneum, head, neck, and mediastinum. Herein, the authors introduce a rare presentation of lipoblastoma as a large intrathoracic mass.


2021 ◽  
Vol 9 (01) ◽  
pp. 525-528
Author(s):  
Z. Sayad ◽  
◽  
B. Dani ◽  
R. Elazzouzi ◽  
S. Benazzou ◽  
...  

We report a rare case of a parotid oncocytoma in a 63-year-old woman. It is a rare benign tumor accounting for less than 1.5% of all salivary gland tumors. It is known as the parotid mitochondrioma because it is made of cells rich in mitochondria with granular cytoplasm. It is a rare entity poorly documented in the literature, and there are no pathognomonicsymptoms or imaging, which makes the diagnosis of this tumor challenging.Surgery is the main treatment, and the diagnosis is confirmed by the histological study of the specimen. Through this observation, and in light of the literature, we will underline the anatomoclinical and radiological peculiarities of this tumor, to induce clinicians to consider this histological type.


2017 ◽  
Vol 25 (6) ◽  
pp. 555-558 ◽  
Author(s):  
Arash H. Lahouti ◽  
Michael Brodherson ◽  
Yaniv Larish ◽  
Pamela D. Unger

Sertoliform cystadenoma is a rare benign tumor of the rete testis with 8 previously reported cases and an additional 14 cases reported in an abstract form. It usually presents with a unilateral scrotal mass, clinically and radiologically indistinguishable from malignant testicular tumors. We report a 39-year-old man who presented with a right testicular mass. The patient underwent radical inguinal orchiectomy. Grossly, no masses were appreciated. After histologic examination with subsequent immunohistochemical staining, a sertoliform cystadenoma of the rete testis was diagnosed.


2021 ◽  
pp. 1-5
Author(s):  
Jan Hemza ◽  
Jan Hemza

Ganglioneuroma is a very rare benign tumor growing from the vegetative, autonomic nervous system. It grows from the central or peripheral part. We describe cervical ganglioneuroma in a 38-year-old man growing in the C7/Th1 foramen area on the right before the fibers enter the ganglion stellatum. It is a non-dumbbell shaped tumor growing between ganglion stellatum and ganglion cervicale. Treatment is resection with total tumor excess. Complete surgical resection is a very effective therapy. The relapse of the tumor is not described in literature studies. Similar type of this case has been described only once in literature and reviewed from anglophone literature, which is selected with the exclusion of neurofibromatosis and with localization in the neck area [1].


CytoJournal ◽  
2014 ◽  
Vol 11 ◽  
pp. 25 ◽  
Author(s):  
Tarek Jazaerly ◽  
Sudeshna Bandyopadhyay ◽  
Nour Almardini ◽  
Mujtaba Husain

Sebaceous lymphadenoma (SLA) is a rare benign tumor of the salivary gland that commonly arises in the parotid gland in adults. It is rarely diagnosed correctly preoperatively. In addition, to the best of our knowledge, SLA has not been described yet in the literature in association with Cowden's syndrome (CS). We present an extremely rare case of parotid SLA that was diagnosed preoperatively by fine needle aspiration in a patient with CS.


2020 ◽  
Vol 2020 ◽  
pp. 1-5
Author(s):  
Maria Enrica Miscia ◽  
Gabriele Lisi ◽  
Giuseppe Lauriti ◽  
Angela Riccio ◽  
Dacia Di Renzo ◽  
...  

Giant mesenteric lipoblastoma is a rare benign tumor arising from the adipocytes. It can mimic malignant tumors, and its diagnosis is difficult before surgery. Imaging studies could lead the diagnosis but not confirm it. Those tumors arising in the abdomen are usually larger and can cause symptoms of compression. Surgical excision is the treatment of choice, and a long-term follow-up is necessary to detect local recurrences. Only a few cases of lipoblastomas arising from the mesentery are reported in literature. We present a case of a rare giant lipoblastoma arising from the mesentery of a 6-year-old girl, with a history of postprandial abdominal pain.


2020 ◽  
Vol 9 (2) ◽  
pp. 14-16
Author(s):  
Summyia Farooq ◽  
Basharat Farooq Rather ◽  
Farhat Abbas

Extraskeletal chondroma (also known as ”Chondroma of soft parts”) is a cutaneous condition, a rare benign tumor of mature cartilage usually occurs in the hands, feet, head and neck. This tumor regularly presents as a small solitary nodule. The histogenesis of the cancer is controversial, but some have suggested a metaplastic origin. Chondroma of the fallopian tube is very rare. There are only three case reports in English literature. The source of this tumor can be subcoelomic mesenchyme of the tubal serosa or mesenchyme of the mesosalpinx. We describe a case of chondroma arising from the serosal surface of the fallopian tube with a review of the literature. A 30-yr-old woman with term pregnancy visited the hospital for cesarean section and tubal ligation. On operating findings, 1 1.5 cm sized nodular mass was noted in the left tubal serosal area. The excised mass showed a multilobulated appearance covered with a thin fibrous membrane. The cut surface was solid, grayish-yellow, and myxoid with a focal gelatinous area. The microscopic finding showed islands and elongated lobules of mature benign cartilage.


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