Otologic Symptoms and Findings of the Pseudotumor Cerebri Syndrome: A Preliminary Report

1985 ◽  
Vol 93 (3) ◽  
pp. 398-402 ◽  
Author(s):  
Aristides Sismanis ◽  
Gordon B. Hughes ◽  
Esrafil Abedi ◽  
George H. Williams ◽  
Larry A. Isrow
Keyword(s):  
Hearing Loss ◽  
Intracranial Pressure ◽  
Intracranial Hypertension ◽  
Preliminary Report ◽  
Clinical Manifestations ◽  
Pseudotumor Cerebri ◽  
Benign Intracranial Hypertension ◽  
Pulsatile Tinnitus ◽  
Increased Intracranial Pressure ◽  
Pseudotumor Cerebri Syndrome

Pseudotumor cerebri or benign intracranial hypertension is a syndrome characterized by increased intracranial pressure without focal signs of neurologic dysfunction. The clinical manifestations of this syndrome are usually headache and/or disturbance of vision. Although tinnitus, hearing loss, and vertigo have been described in association with intracranial hypertension, otologic symptomatology as the presenting manifestation of this syndrome has not been previously reported. In this article we report the otologic symptoms and findings of two pseudotumor cerebri patients, one of whom presented with pulsatile tinnitus. The pathogenesis of the otologic symptoms, diagnostic workup, and management of these patients are discussed.

scholarly journals Current Perspectives on Idiopathic Intracranial Hypertension without Papilloedema

Life ◽  
2021 ◽  
Vol 11 (6) ◽  
pp. 472
Author(s):  
Susan P. Mollan ◽  
Yu Jeat Chong ◽  
Olivia Grech ◽  
Alex J. Sinclair ◽  
Benjamin R. Wakerley
Keyword(s):  
Intracranial Pressure ◽  
Intracranial Hypertension ◽  
Lumbar Puncture ◽  
Idiopathic Intracranial Hypertension ◽  
Pseudotumor Cerebri ◽  
Obesity Epidemic ◽  
Refractory Headache ◽  
Pseudotumor Cerebri Syndrome ◽  
Detailed Search ◽  
Degree Of Association

The pseudotumor cerebri syndrome embraces disorders characterised by raised intracranial pressure, where the commonest symptom is headache (90%). Idiopathic intracranial hypertension without papilloedema (IIHWOP) is increasingly recognised as a source of refractory headache symptoms and resultant neurological disability. Although the majority of patients with IIHWOP are phenotypically similar to those with idiopathic intracranial hypertension (IIH), it remains uncertain as to whether IIHWOP is nosologically distinct from IIH. The incidence, prevalence, and the degree of association with the world-wide obesity epidemic is unknown. Establishing a diagnosis of IIHWOP can be challenging, as often lumbar puncture is not routinely part of the work-up for refractory headaches. There are published diagnostic criteria for IIHWOP; however, some report uncertainty regarding a pathologically acceptable cut off for a raised lumbar puncture opening pressure, which is a key criterion. The literature provides little information to help guide clinicians in managing patients with IIHWOP. Further research is therefore needed to better understand the mechanisms that drive the development of chronic daily headaches and a relationship to intracranial pressure; and indeed, whether such patients would benefit from therapies to lower intracranial pressure. The aim of this narrative review was to perform a detailed search of the scientific literature and provide a summary of historic and current opinion regarding IIHWOP.

scholarly journals MRI-findings in idiopathic intracranial hypertension (Pseudotumor cerebri)

2021 ◽  
Author(s):  
Julia Juhász ◽  
Johannes Hensler ◽  
Olav Jansen
Keyword(s):  
Intracranial Pressure ◽  
Intracranial Hypertension ◽  
Idiopathic Intracranial Hypertension ◽  
Case Reports ◽  
Fluid Pressure ◽  
Pseudotumor Cerebri ◽  
Unknown Etiology ◽  
Increased Intracranial Pressure ◽  
Mri Findings ◽  
Detailed Medical History

Background Pseudotumor cerebri, also known as idiopathic intracranial hypertension, is a disorder of increased intracranial pressure of unknown etiology. Main symptom is headache which has a characteristic similar to other headache diseases, therefore the idiopathic intracranial hypertension often remains undetected. The incidence is 1/100 000 with the number of unreported cases being much higher. This article highlights the essential role of MRI in the differential diagnosis. Methods A literature search was carried out on idiopathic intracranial hypertension and Pseudotumor cerebri in English and German. Original and Review articles as well as case reports were taken into account. Since the main focus of the article is MRI diagnostics, some images were selected to illustrate the characteristic MRI morphological features. Results and Conclusion The diagnosis of idiopathic intracranial hypertension is based on an exclusion procedure. Most common syndromes are headache, transient visual obscurations, pulsatile tinnitus and nausea. In the presence of an underlying cause for the increased intracranial pressure one speaks of a secondary intracranial hypertension. The diagnostics include a detailed medical history, neurological and ophthalmic examination, lumbar puncture, and neuroradiological imaging procedures. MRI, in particular, has become increasingly important in recent years, since signs for changes in cerebrospinal fluid pressure are now detectable and well-defined. The therapeutic approaches are symptom-oriented and aim to lower the pressure. With a precise diagnosis and timely start of therapy, idiopathic intracranial hypertension has a good prognosis, especially with regard to the preservation of eyesight. Key Points:  Citation Format

BENIGN INTRACRANIAL HYPERTENSION AND OTITIC HYDROCEPHALUS

PEDIATRICS ◽  
1959 ◽  
Vol 23 (2) ◽  
pp. 257-259
Author(s):  
J. GORDON MILLICHAP
Keyword(s):  
Cerebrospinal Fluid ◽  
Intracranial Hypertension ◽  
Pseudotumor Cerebri ◽  
Common Symptom ◽  
Moderate Degree ◽  
Benign Intracranial Hypertension ◽  
Abducens Palsy ◽  
Increased Intracranial Pressure ◽  
Normal Composition ◽  
Infants And Young Children

BENIGN intracranial hypertension or pseudotumor cerebri, as the condition is termed more frequently, is a syndrome of increased intracranial pressure with a normal ventricular system and cerebrospinal fluid of normal composition. Headache of moderate degree is the most common symptom and vomiting, impairment of vision and diplopia occur less often; papilledema and abducens palsy are the usual neurologic signs. The prognosis is almost invariably good. Although few reports of the syndrome are found in pediatric literature, its occurrence is relatively common during childhood. The review of reports by Davidoff, Foley, and others has disclosed that 84 (37%) of 224 patients were children and of these 75 (90%) were between 5 and 15 years of age. The infrequent occurrence or recognition of the syndrome in infants and young children is noteworthy.

Update in Pediatric Pseudotumor Cerebri Syndrome

2020 ◽  
Vol 40 (03) ◽  
pp. 286-293
Author(s):  
Shannon J. Beres
Keyword(s):  
Surgical Treatment ◽  
Intracranial Hypertension ◽  
Pediatric Population ◽  
Age Groups ◽  
Rare Condition ◽  
Pseudotumor Cerebri ◽  
Significant Morbidity ◽  
Increased Intracranial Pressure ◽  
Pseudotumor Cerebri Syndrome ◽  
Eye Exams

AbstractPseudotumor cerebri syndrome (PTCS) is a rare condition in children presenting with headache and papilledema from increased intracranial pressure that can cause significant morbidity. This can be idiopathic, also known as idiopathic intracranial hypertension or primary intracranial hypertension, or can be secondary to medications and associated medical conditions. Given the threat to vision, early detection and treatment is needed in all age groups. However, identifying papilledema or pseudopapilledema in children presents unique challenges sometimes as a result of differences between prepubertal and postpubertal children, further elucidating the complex pathophysiology. Management requires brain imaging, lumbar puncture, and frequent eye exams with medical and rarely surgical treatment. Visual outcomes in children are favorable if caught early and management can be prolonged over years. Pediatric PTCS is different from adult PTCS in many ways, and this review will focus on the most updated definitions of the disease, theories of pathophysiology, management, and treatment in the pediatric population.

scholarly journals Two Observations of Blindness in Idiopathic Intracranial Hypertension

1995 ◽  
Vol XXVII (1-2) ◽  
pp. 35-37
Author(s):  
A. S. Deev ◽  
A. V. Karpikov ◽  
I. V. Zakharushkina ◽  
L. M. Orlova
Keyword(s):  
Central Nervous System ◽  
Nervous System ◽  
Brain Tumor ◽  
Intracranial Pressure ◽  
Intracranial Hypertension ◽  
Idiopathic Intracranial Hypertension ◽  
Clinical Syndrome ◽  
Benign Intracranial Hypertension ◽  
Increased Intracranial Pressure ◽  
The Central Nervous System

In recent years, more and more attention of domestic neurologists has been attracted by the clinical syndrome with symptoms of increased intracranial pressure without signs of organic damage to the central nervous system - benign intracranial hypertension (DVH). It is often also referred to as idiopathic intracranial hypertension and false brain tumor.

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