Aggressive Cranial Vault Decompression for Cranial Hyperostosis: Technical Case Report of Two Cases

2005 ◽  
Vol 57 (suppl_1) ◽  
pp. E212-E212 ◽  
Author(s):  
J. Mocco ◽  
Ricardo J. Komotar ◽  
Brad E. Zacharia ◽  
Neil A. Feldstein ◽  
Jeffrey N. Bruce
Keyword(s):  
Intracranial Pressure ◽  
Signs And Symptoms ◽  
Operative Management ◽  
Cranial Vault ◽  
Increased Intracranial Pressure ◽  
The Past ◽  
Cranial Nerve Dysfunction ◽  
Surgical Options ◽  
Nerve Dysfunction ◽  
Clinically Significant

Abstract OBJECTIVE AND IMPORTANCE: Camurati-Engelmann's disease, also known as progressive diaphysial dysplasia, is a disorder of the bone metabolism. Neurological manifestations of progressive diaphysial dysplasia include cranial nerve dysfunction, generalized weakness, cerebellar herniation, and increased intracranial pressure. In the past, surgical intervention has been of limited and temporary benefit. We present two patients with cranial hyperostosis secondary to Camurati-Engelmann's disease who were treated successfully with a single surgery involving a combination of multiple craniotomies for cranial vault decompression. CLINICAL PRESENTATION: Two patients presented with signs and symptoms of increased intracranial pressure secondary to Camurati-Engelmann's syndrome. Radiological workup revealed marked cranial hyperostosis. INTERVENTION: The patients underwent aggressive cranial vault decompression. Multiple craniotomies were performed, and the inner table was then drilled down until the bone was 1 cm thick. CONCLUSION: Effective surgical options are needed for clinically significant cranial hyperostosis. In an effort to further define operative management in these patients, we describe a single, aggressive surgical procedure that may be used for successful cranial decompression.

scholarly journals Pediatric Idiopathic Intracranial Hypertension Post-measles Vaccine: A Case Report

2021 ◽  
Author(s):  
Ahmed Arafa Helaly ◽  
Ahmed Ezzat ◽  
Mohammed Gamal Abdellatif
Keyword(s):  
Intracranial Pressure ◽  
Intracranial Hypertension ◽  
Idiopathic Intracranial Hypertension ◽  
Signs And Symptoms ◽  
Normal Brain ◽  
Measles Vaccine ◽  
Increased Intracranial Pressure ◽  
Csf Pressure ◽  
General Signs ◽  
Sixth Nerve

Idiopathic intracranial hypertension is characterized by an increase in intracranial pressure with no significant structural cause. The diagnostic criteria include general signs and symptoms of generalized increased intracranial pressure or papilledema, increased Cerebrospinal Fluid (CSF) pressure (>250 mm H2 O), and normal brain imaging. It usually occurs in adults but rarely can be seen in children. We report a 7-year-old child with a manifestation of increased intracranial tension after the measles vaccine, associated with bilateral sixth nerve palsy and bilateral facial palsy with lower motor neuron features. Normal magnetic resonance imaging and CSF results were normal, except for an increase in CSF pressure. The symptoms began to be resolved after lumbar puncture with the complete resolution of symptoms after one and half months. We add also acetazolamide at the proper dose to reduce intracranial pressure from the first day of diagnosis.

scholarly journals Central neurocytomas of uncommon locations: report of two cases

2006 ◽  
Vol 64 (4) ◽  
pp. 1015-1018 ◽  
Author(s):  
Francinaldo Lobato Gomes ◽  
Luciano Ricardo França ◽  
Samuel Tau Zymberg ◽  
Sérgio Cavalheiro
Keyword(s):  
Differential Diagnosis ◽  
Intracranial Pressure ◽  
Obstructive Hydrocephalus ◽  
Signs And Symptoms ◽  
Pineal Region ◽  
Additional Treatment ◽  
Third Ventriculostomy ◽  
Increased Intracranial Pressure ◽  
The Brain ◽  
Uncommon Location

We report two patients with central neurocytomas at an uncommon location in the brain. The first, a 58-year-old man presenting with signs and symptoms of increased intracranial pressure, had a tumor located at the pineal region. The second, a 21-year-old woman with tumor in the aqueductal region had worsening migraine-like headaches and diplopia. Both patients had obstructive hydrocephalus treated by neuroendoscopic third ventriculostomy and biopsy of the tumors. No additional treatment was done. We conclude that neurocytomas should be considered in the differential diagnosis of tumors located in the pineal and aqueductal regions.

Infantile Water Intoxication After a Swimming Lesson

PEDIATRICS ◽  
1982 ◽  
Vol 70 (4) ◽  
pp. 599-600 ◽  
Author(s):  
Gerald N. Goldberg ◽  
Elmer S. Lightner ◽  
Wayne Morgan ◽  
Sid Kemberling
Keyword(s):  
Intracranial Pressure ◽  
Signs And Symptoms ◽  
Water Intoxication ◽  
Increased Intracranial Pressure ◽  
Accidental Ingestion ◽  
Near Drowning ◽  
Early Infant

This report emphasizes a danger inherent in early infant swimming programs, ie, the need to observe the infant closely for ingestion of excessive amounts of water. A physician faced with a history compatible with near-drowning or possible aspiration of water must consider the diagnosis of acute water intoxication. Accidental ingestion of water can produce hyponatremia with resulting signs and symptoms of acute water intoxication, ie, lethargy, vomiting, seizures, and increased intracranial pressure.

scholarly journals Mechanisms of visual loss in papilledema

2007 ◽  
Vol 23 (5) ◽  
pp. E5 ◽  
Author(s):  
Clemens M. Schirmer ◽  
Thomas R. Hedges
Keyword(s):  
Intracranial Pressure ◽  
Visual Loss ◽  
Treatment Options ◽  
Signs And Symptoms ◽  
Illustrative Case ◽  
Potential Treatment ◽  
Increased Intracranial Pressure ◽  
Intracranial Mass Lesion ◽  
Optic Discs

✓ The term “papilledema” indicates swelling of the optic discs secondary to increased intracranial pressure. Papilledema can be caused by an intracranial mass lesion or by other factors. Visual symptoms frequently accompany papilledema, which can lead to permanent visual loss if left untreated. Starting with an illustrative case, the authors review the pathophysiology of the visual signs and symptoms of papilledema. They also briefly review potential treatment options, focusing on the role of the neurosurgeon in the treatment of patients with papilledema.

Insidious Onset of Familial Craniosynostosis

1993 ◽  
Vol 30 (4) ◽  
pp. 401-405 ◽  
Author(s):  
Steven R. Cohen ◽  
Robert C. Dauser ◽  
Jerome L. Gorski
Keyword(s):  
Optic Nerve ◽  
Intracranial Pressure ◽  
Ct Scan ◽  
Late Onset ◽  
Cranial Vault ◽  
Optic Nerve Sheath ◽  
Increased Intracranial Pressure ◽  
Nerve Sheath ◽  
Insidious Onset

A mother, son, and daughter are presented, in whom serial photographs document an insidious and late onset of exorbitism and midfacial retrusion consistent with a diagnosis of familial nonsyndromic craniosynostosis. Papilledema was found in the 4.5-year-old daughter because of increased intracranial pressure secondary to a reduction in cranial vault size, whereas optic nerve sheath swelling on CT scan was found in the son.

Systemic Weber-Christian disease presenting as an intracranial mass lesion

1980 ◽  
Vol 52 (1) ◽  
pp. 134-137 ◽  
Author(s):  
John R. Mangiardi ◽  
Z. Harry Rappaport ◽  
Joseph Ransohoff
Keyword(s):  
Intracranial Pressure ◽  
Signs And Symptoms ◽  
Mass Lesion ◽  
Increased Intracranial Pressure ◽  
Content Type ◽  
Intracranial Mass ◽  
Intracranial Mass Lesion ◽  
Fine Print

✓ A case is reported in which systemic Weber-Christian disease presented as a dural mass causing the signs and symptoms of increased intracranial pressure. The literature and possible pathogenesis of this entity are discussed.

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