In Reply: Late-Onset Hearing Loss

PEDIATRICS ◽  
1989 ◽  
Vol 83 (5) ◽  
pp. 808-808
Author(s):  
KAREN D. HENDRICKS-MUNOZ ◽  
JOSEPH P. WALTON
Keyword(s):  
Hearing Loss ◽  
High Risk ◽  
Sensorineural Hearing Loss ◽  
Late Onset ◽  
Sensorineural Hearing ◽  
Fetal Circulation ◽  
Persistent Fetal Circulation ◽  
Audiologic Testing

We concur with Nield et al who point out that progressive sensorineural hearing loss is not limited to infants with persistent fetal circulation. It was not the intent of the study to imply that delayed hearing loss was limited to infants with persistent fetal circulation. Our center routinely refers for serial audiologic testing all infants who meet the high-risk registry criteria for deafness (ASHA 1984;26:17-21). Unfortunately, many of the infants in the study did not meet criteria established by the registry and, therefore, were not referred for evaluation.

Hearing and Neurodevelopmental Outcome in Survivors of Persistent Pulmonary Hypertension of the Newborn

PEDIATRICS ◽  
1992 ◽  
Vol 90 (3) ◽  
pp. 392-396 ◽  
Author(s):  
Mary-Joan Marron ◽  
Maria A. Crisafi ◽  
John M. Driscoll ◽  
Jen-Tien Wung ◽  
Yvonne T. Driscoll ◽  
...  
Keyword(s):  
Pulmonary Hypertension ◽  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Neurodevelopmental Outcome ◽  
Supplemental Oxygen ◽  
Sensorineural Hearing ◽  
Persistent Pulmonary Hypertension ◽  
Arterial Oxygen ◽  
Abnormal Chest ◽  
Audiologic Testing

Thirty-four infants who had a diagnosis of severe persistent pulmonary hypertension of the newborn at birth (alveolar-arterial oxygen difference > 600) were treated without paralysis or hyperventilation to induce alkalosis. All survived. Twenty-seven of these 34 eligible infants (79%) underwent neurologic, intelligence, and audiologic testing between 10 months and 6 years of age. Children who were younger than 1 year of age at the initial hearing test were retested after they reached 2 years of age. The average IQ was within the normal range (mean = 96.23). None had sensorineural hearing loss. Severe neurologic abnormalities were seen in 4 children, 3 of whom had been severely asphyxiated at birth (determined by biochemical criteria). Mild neurologic abnormalities were observed in 5 children. Two infants had bronchopulmonary dysplasia because they required supplemental oxygen for 29 and 66 days, respectively, and had abnormal chest roentgenograms; 1 patient takes intermittent doses of albuterol (Ventolin) and neither currently requires supplemental oxygen. This study of 27 infants with severe persistent pulmonary hypertension of the newborn suggests that conservative management without induced alkalosis or respiratory paralysis is accompanied by no sensorineural hearing loss and a good neurologic outcome.

scholarly journals Early-Onset Sensorineural Hearing Loss and Late-Onset Neurologic Complaints Caused by a Mitochondrial Mutation at Position 7472

1998 ◽  
Vol 124 (8) ◽  
pp. 886 ◽  
Author(s):  
Robbert J. H. Ensink ◽  
Kristien Verhoeven ◽  
Henri A. M. Marres ◽  
Patrick L. M. Huygen ◽  
Georges W. Padberg ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Early Onset ◽  
Late Onset ◽  
Sensorineural Hearing ◽  
Mitochondrial Mutation

Ocular albinism with infertility and late‐onset sensorineural hearing loss

2018 ◽  
Vol 176 (7) ◽  
pp. 1587-1593 ◽  
Author(s):  
Bjørn K. Fabian‐Jessing ◽  
Else Marie Vestergaard ◽  
Astrid S. Plomp ◽  
Arthur A. Bergen ◽  
Wouter A. Dreschler ◽  
...  
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Late Onset ◽  
Sensorineural Hearing ◽  
Ocular Albinism

scholarly journals Oto acoustic emissions in early detection of sensorineural hearing loss in high-risk neonates

2021 ◽  
Vol 7 (11) ◽  
pp. 1794
Author(s):  
J. Ramanjaneyulu ◽  
S. Rajesh Kumar ◽  
V. Krishna Chaitanya ◽  
A. Kusumanjali
Keyword(s):  
Hearing Loss ◽  
High Risk ◽  
Early Detection ◽  
Sensorineural Hearing Loss ◽  
Brain Stem ◽  
Sensitivity And Specificity ◽  
Acoustic Emissions ◽  
Otoacoustic Emission ◽  
Auditory Neuropathy ◽  
Sensorineural Hearing

<p><strong>Background: </strong>Early identification of congenital hearing loss and early intervention ameliorated many adverse consequences. This study was performed to observe effectiveness of otoacoustic emission in screening of hearing loss in high-risk babies.</p><p><strong>Methods: </strong>Prospective study on 45 high-risk newborns delivered during period of 2013-2014. Selective newborn hearing performed with oto acoustic emissions (OAE) and auditory brain stem responses (ABR), in high-risk infants aged below 7 days, 15 days, after 45 days and after 90 days.</p><p><strong>Results: </strong>Study population comprised of 45 high-risk newborns. In 1<sup>st</sup> level screening, 28 (62%) babies showed recordable OAE, 17 (38%) babies failed. In 2<sup>nd</sup> level screening 31 (81%) passed and 7 (19%) failed and death occurred in 7 infants. In 3<sup>rd</sup> level screening both OAE and brain stem evoked response audiometry (BERA), was performed in 38 cases and positivity was reported in 37 cases. 4<sup>th</sup> level screening was similar to 3<sup>rd</sup> level screening where 3 babies failed ABR test. In our study incidence of sensorineural hearing loss found to be 78.91% (3/38×1000) per 1000 high-risk babies. Auditory neuropathy was observed in 2 (4.4%) patients. Sensitivity and specificity of OAE was 100% and 33.3% respectively. In high-risk low birth weight neonates’ sensitivity and specificity was 66.7% and 50.0%.</p><p><strong>Conclusions: </strong>In high-risk babies, appropriate time for screening with OAE is around 60 days of age. OAE are useful diagnostic tool in evaluation of high-risk neonates for early detection of sensorineural hearing loss.</p>

Late-Onset Sensorineural Hearing Loss in Coffin-Lowry Syndrome

ORL ◽  
1998 ◽  
Vol 60 (4) ◽  
pp. 224-226 ◽  
Author(s):  
Frank Rosanowski ◽  
Ulrich Hoppe ◽  
Ute Pröschel ◽  
Ulrich Eysholdt
Keyword(s):  
Hearing Loss ◽  
Sensorineural Hearing Loss ◽  
Late Onset ◽  
Sensorineural Hearing

Framingham Risk Score as a Prognostic Predictor of Sudden Sensorineural Hearing Loss: A Preliminary Study

2017 ◽  
Vol 126 (5) ◽  
pp. 382-387 ◽  
Author(s):  
Young-Soo Chang ◽  
Ji Eun Choi ◽  
Jungmin Ahn ◽  
Nam-Gyu Ryu ◽  
Il Joon Moon ◽  
...  
Keyword(s):  
Hearing Loss ◽  
High Risk ◽  
Sensorineural Hearing Loss ◽  
Risk Score ◽  
Framingham Risk Score ◽  
Risk Group ◽  
Sudden Sensorineural Hearing Loss ◽  
Sensorineural Hearing ◽  
Risk Scores ◽  
Framingham Risk

Objectives/Hypothesis: Predicting the prognosis of idiopathic sudden sensorineural hearing loss (ISSHL) remains challenging. This investigation aimed to apply Framingham Risk Scores (FRS) to assess the combination of prognostic factors following ISSHL and investigate the predictive role of FRS in patients with multiple comorbidities including hypertension, diabetes, and hyperlipidemia. Study design: Retrospective study. Methods: Twenty-one patients presenting with unilateral idiopathic sudden sensorineural hearing loss and multiple comorbidities were surveyed. Framingham Risk Score was calculated, and patients were assigned into high-risk (FRS ≥20%) and low-risk (FRS <20%) groups. Mean pure tone audiometry (PTA) threshold of both groups and hearing outcomes following established criteria were investigated. All patients were treated with the same protocol of oral methylprednisolone. Results: Overall successful recovery rate (complete + marked recovery) was 23.81%. The mean PTA threshold of the low-risk group showed significant improvement (mean PTA ± standard error, SE: pretreatment, 73.23 ± 11.80; posttreatment, 54.89 ± 10.25, P = .002), while the high-risk group did not show significant improvement in mean PTA threshold (mean PTA ± SE: pretreatment, 71.94 ± 11.77; posttreatment, 68.89 ± 12.81, P = .73). Conclusion: Framingham Risk Scores may be useful in predicting outcomes for ISSHL patients with multiple comorbidities.

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