scholarly journals Jaffe-Lichtenstein Syndrome Associated with a Simple Bone Cyst: Unprecedented Rare Case Report

2020 ◽  
Vol 31 (5) ◽  
pp. 557-561
Author(s):  
Poliana Gonçalves Miranda ◽  
João César Guimaraes Henriques ◽  
Luiz Fernando Barbosa de Paulo ◽  
Cizelene do Carmo Faleiros Veloso Guedes ◽  
Fabio Franceschini Mitri ◽  
...  
Keyword(s):  
Fibrous Dysplasia ◽  
Bone Cyst ◽  
Final Diagnosis ◽  
The Body ◽  
Bone Architecture ◽  
World Health ◽  
Ossifying Fibroma ◽  
Simple Bone Cyst ◽  
Single Bone ◽  
The Right

Abstract Lesions denominated fibro-osseous lesions of the jaw constitute a diversified group of disorders, in which the normal bone architecture is replaced by fibroblasts, collagen fibers and immature bone. At present, the World Health Organization recognizes four variants of these lesions, namely: bone-cement dysplasia, fibrous dysplasia, ossifying fibroma and Familial gigantiform cementoma. Fibrous dysplasia may present in the monostotic form, affecting one single bone or an isolated craniofacial region; and in the Polyostotic form, involving two or more bones of the skeleton, and eventual association with syndromic conditions. The patient, C.P.G., 43 years old, sought attendance due to symptomatic increase in the region of the mandibular body on the right side. Imaging exams revealed craniofacial areas with ground-glass aspect, beyond the extensive mandibular radiolucent lesion. During the physical exam, spots of the Café au lait type disposed on the right side of the body were identified, in addition to uncoordinated gait with distinct shortening of the right leg. Additional radiographic exams showed evidence of skeletal dissemination of the disease. The patient denied any sexual precocity, and the final diagnosis was fibrous dysplasia, expressed by means of the Jaffe-Lichtenstein syndrome, in association with a simple bone cyst.

scholarly journals Desmoplastic Fibroma and Cemento Ossifying Fibroma of The Anterior Maxilla: A Rare Case Report

2021 ◽  
Vol 24 (1) ◽  
pp. 21-27
Author(s):  
Victor Pakpahan ◽  
Eky Nasuri ◽  
Vera Julia
Keyword(s):  
Rare Case ◽  
Histopathological Examination ◽  
Neck Region ◽  
The Body ◽  
Ossifying Fibroma ◽  
Desmoplastic Fibroma ◽  
Anterior Maxilla ◽  
Main Complaint ◽  
Rare Case Report ◽  
The Right

Tumors located in the maxillofacial part of the body were classified by WHO in 2017 and among these are intraosseous form of fibromatosis known as Desmoplastic and Cemento-ossifying fibromas. These tumors usually occur in the head and neck region, especially in the mandible and are relatively rare in the maxilla. Meanwhile, this study aims to discribe a rare case of the cemento ossifying fibroma that had been previously diagnosed as desmoplastic fibroma with a mass tumor in the anterior of the maxilla. A 22 years old female reported to the Cipto Mangkusumo Hospital with the main complaint of a lump in the right side of the upper jaw which appeared 2 years prior to the operation. In April 2017, the patient had a biopsy in Tarakan Hospital and the result was a desmoplastic fibroma. Due to the lump enlargement, the patient was admitted to RSCM in July 2019 and had biopsy incision with a diagnosis of cemento ossifying fibroma which was confirmed by the histopathological examination and histology report. The resection of the right part of maxilla was conducted alongside with reconstruction using the free fibular flap. Moreover, cemento ossifying fibroma and desmoplastic fibroma shared similar features, namely, clinical, histological and radiological features which are important in establishing the diagnosis and treatment of patient. Hence, extensive enucleation or resection is required due to the progressive nature of the tumor to prevent the potential for further recurrences.

scholarly journals Giant cell tumor of bone in an eighteenth-century Italian mummy

2021 ◽  
Author(s):  
Luca Ventura ◽  
Enrico Petrella ◽  
Sara Piciucchi ◽  
Elisabetta Cilli ◽  
Donata Luiselli ◽  
...  
Keyword(s):  
Eighteenth Century ◽  
Giant Cell Tumor ◽  
Giant Cell ◽  
Bone Cyst ◽  
Giant Cells ◽  
Cell Tumor ◽  
World Health ◽  
Ossifying Fibroma ◽  
Small Subset ◽  
Left Femur

AbstractGiant cell tumor (GCT) of the bone is a locally aggressive and rarely metastasizing neoplasm. It is composed of neoplastic mononuclear stromal cells with a monotonous appearance admixed with macrophages and osteoclast-like giant cells. In a small subset of cases, GCT is malignant. Terminology previously related to this entity, and which is no longer supported by the World Health Organization, includes osteoclastoma and benign fibrous histiocytoma (BFH). Giant cells occur in numerous other pathologic conditions of the bone, which accounts for the misrepresentation of these non-GCT tumors in the early literature. Non-ossifying fibroma (NOF), aneurysmal bone cyst, and chondroblastoma have been erroneously labeled GCT for this reason. A single description of an ancient GCT was reported by Brothwell and Sandison and subsequently mentioned by Aufderheide and Rodrìguez-Martìn who were astonished that more of these tumors had not been identified in archaeological cases. To the best of our knowledge, no other cases of ancient GCT have been cited in the paleopathology literature. The study of this type of neoplasm in antiquity can be used as a means to better understand its characteristics and behavior and to expand the depth of time of the etiology of these lesions. We report a case of GCT of the left femur observed following the total body CT imaging of a partially mummified adult female, dating to eighteenth century.

scholarly journals Simple Bone Cyst and Fibrous Dysplasia Occurring Simultaneously in Both Mandibles: Case Report

2013 ◽  
Vol 6 (1) ◽  
pp. 34-40
Author(s):  
Hong-Soon Kim ◽  
Chan-Jong Song ◽  
Dong-Ju Seol ◽  
Jae-Wook Lee ◽  
Baek-Soo Lee ◽  
...  
Keyword(s):  
Case Report ◽  
Fibrous Dysplasia ◽  
Bone Cyst ◽  
Simple Bone Cyst

scholarly journals CISTO ÓSSEO SIMPLES - RELATO DE CASO CLÍNICO

2015 ◽  
Vol 5 (3) ◽  
Author(s):  
Anne Lopes Oliveira ◽  
Jandson Michel Santos ◽  
Adriano Assis ◽  
Sílvia Regina de Almeida Reis ◽  
Alena Peixoto Medrado
Keyword(s):  
Bone Cyst ◽  
Excisional Biopsy ◽  
World Health ◽  
Radiographic Examination ◽  
Simple Bone Cyst ◽  
Neoplastic Lesion ◽  
Left Mandible ◽  
History Of ◽  
Health Organization ◽  
Pain Symptoms

The World Health Organization classifies simple bone cyst as a non-neoplastic lesion related to bones, defined as an intraosseous cyst, which features a thin capsule. Its etiology remains unknown, and the most accepted explanation is related to the history of trauma. It is in most cases clinically asymptomatic and the diagnosis is often established through routine radiographic examination. The objective of this study is to report a case of a simple bone cyst in the left mandible region in a young patient underwent imaging  examinations for follow-up orthodontic treatment.The patient attended the Maxillofacial Traumatology Surgery Service showing circumscribed unilocular radiolucent lesion, in the left mandible region.Reported no significant swelling or pain symptoms. Excisional biopsy was performed and histopathological findings showed bone tissue associated with a thin membrane of connective tissue, and absence of epithelial lining. Today, after two years of surgical treatment, there is no evidence of recurrence.

scholarly journals Florid Cemento-Osseous Dysplasia-Associated Simple Bone Cyst Showing Marked Irregular Border and High Apparent Diffusion Coefficient Value

2020 ◽  
Vol 2020 ◽  
pp. 1-7
Author(s):  
Ikuho Kojima ◽  
Takashi Nishioka ◽  
Maya Sakamoto ◽  
Yuko Sai ◽  
Yushi Ezoe ◽  
...  
Keyword(s):  
Bone Cyst ◽  
High Density ◽  
Low Density ◽  
Imaging Findings ◽  
Simple Bone Cyst ◽  
Adc Value ◽  
Osseous Dysplasia ◽  
Apparent Diffusion ◽  
Irregular Border ◽  
The Right

A simple bone cyst (SBC) is an intrabone cavity without epithelial lining, which occasionally occur with fibrous-osseous lesions. The imaging finding of the scalloped border and conserving the lamina dura, periodontal ligament spaces, or follicular spaces are considered radiographically pathognomonic of SBC. SBC has been reported to occur with fibrous-osseous lesions, including cemento-osseous dysplasia (COD). Computed tomography (CT) imaging findings are sparse, and there are no reports of magnetic resonance imaging (MRI) findings, including apparent diffusion coefficient (ADC) value calculated by diffusion-weighted MRI for the florid COD-associated SBC. We report a case of a 39-year-old woman who was referred to our hospital because a panoramic radiograph of her right mandible showed asymptomatic radiolucency in the apical molar area. CT images showed a low-density lesion in the periapical areas of the right mandible, which accompanied a well-defined, high-density lesion, and a mixed low/high-density lesion with an unusual marked irregular border in the left mandible. The MRI showed cyst-like extremely hyperintense signals on fat-suppressed T2-weighted images at the right mandibular low-density and the left mandibular mixed low/high-density areas. ADC map showed high values (over 2.5×10−3 mm2/s) at the cystic areas in the bilateral mandible. We performed incisional biopsies of the bilateral mandibular lesions and resections of the bilateral maxillary lesions. Surgical and histopathological findings established a diagnosis of florid COD in the bilateral mandible and maxilla, simultaneously complicated by multiple SBCs in the bilateral mandible. The ADC value of cystic component is useful for the diagnosis, if the COD-associated SBC exhibits solitary, nonspecific, or rare imaging findings.

scholarly journals Atypical Presentation of Giant Mandibular Aneurysmal Bone Cyst with Cemento-Ossifying Fibroma Mimicking Sarcoma

2019 ◽  
Vol 2019 ◽  
pp. 1-5
Author(s):  
Haneen Al-Maghrabi ◽  
Serge Verne ◽  
Bassam Al-Maghrabi ◽  
Osamah Almutawa ◽  
Jaudah Al-Maghrabi
Keyword(s):  
English Literature ◽  
Bone Cyst ◽  
World Health ◽  
Bone Lesions ◽  
Ossifying Fibroma ◽  
The Past ◽  
The World ◽  
Aneurysmal Bone Cysts ◽  
Bony Lesion ◽  
Health Organization

Aneurysmal bone cysts (ABCs) are an uncommon osteolytic intraosseous bone lesions. ABCs commonly involve metaphysis of long bones and are rarely diagnosed in craniofacial bones. The World Health Organization (WHO) designates ABCs as benign, but locally destructive, rapidly growing masses. ABC can be clinically misdiagnosed as a malignant tumor. In this article, we present a case of a 12-year-old female patient who presented to a maxillofascial outpatient clinic complaining of huge jaw swelling over the past 3 months, which was clinically suggestive of sarcoma. Few reported cases in the English literature describe ABC presented with huge rapidly growing mass causing destructive bony lesion that was clinically mimic sarcoma, which initiates this case report. We also discuss the most important pathologic differential diagnosis of tumors with malignant behavior and review the literature.

Simple Bone Cyst and Ossifying Fibroma in Periapical Region: an Uncommon Case Report

2018 ◽  
Vol 126 (3) ◽  
pp. e59
Author(s):  
Talita Da Silva Nery De Souza ◽  
Agnes Assao ◽  
Antônio Carlos Rossetto ◽  
Denise Tostes Oliveira
Keyword(s):  
Case Report ◽  
Bone Cyst ◽  
Ossifying Fibroma ◽  
Simple Bone Cyst ◽  
Uncommon Case

scholarly journals Aggressive Multilocular Osteoblastoma in the Mandible: A Rare and Difficult Case to Diagnose

2014 ◽  
Vol 25 (5) ◽  
pp. 451-456 ◽  
Author(s):  
Maria Luiza Anjos Pontual ◽  
Andréa Anjos Pontual ◽  
Rafael Grotta Grempel ◽  
Leonardo Rocha Mendes Campos ◽  
Antonio de Lisboa Lopes Costa ◽  
...  
Keyword(s):  
Malignant Tumors ◽  
White Male ◽  
Bone Lesion ◽  
Safety Margin ◽  
Final Diagnosis ◽  
The Body ◽  
Ossifying Fibroma ◽  
Difficult Case ◽  
State University ◽  
Diagnostic Dilemma

Osteoblastoma is a benign neoplasia and is uncommon in the jaws. In some cases, this lesion presents extremely aggressive local characteristics and is termed aggressive osteoblastoma. Because the clinical, radiographic and histopathologic characteristics are similar to those of a variety of benign and malignant tumors, it poses a diagnostic dilemma. This report presents a case of an aggressive osteoblastoma in the mandible and discusses the differential diagnosis of this lesion. A 13-year-old white male sought the Stomatology Clinic at the State University of Paraíba, Campina Grande, PB, Brazil, complaining of asymptomatic swelling on the left side of his face. Cone-beam computerized tomography showed a multilocular, hypodense bone lesion, located in the body of the left mandible and lower third of the ascending ramus. The initial diagnostic hypothesis was juvenile ossifying fibroma or osteosarcoma. After histopathologic examination, the final diagnosis was aggressive osteoblastoma. Surgical resection with a safety margin was performed. There was no evidence of recurrence after a follow-up period of 4 years.

scholarly journals Chondrosarcoma of Cranial Vault: Case Report and Review of Literature

2021 ◽  
Vol 7 (2) ◽  
pp. 119-124
Author(s):  
Keshav Mishra ◽  
◽  
Somnath Sharma ◽  
Devendra K. Purohit ◽  
Arpita Jindal ◽  
...  
Keyword(s):  
Final Diagnosis ◽  
Primary Treatment ◽  
Cranial Vault ◽  
World Health ◽  
Unusual Site ◽  
Who Grade ◽  
Skull Vault ◽  
Well Differentiated ◽  
Health Organization ◽  
The Right

Background and Importance: Chondrosarcoma is a rare malignant cartilage forming tumor, usually arising from long bones and rarely observed in the cranium. In the cranium, it commonly arises from the skull base with the skull vault being a highly unusual site. Case Presentation: We present the case of a 30-year female presenting with complaints of headache for 6 months. The patient was found to have large chondrosarcoma in the right frontoparietal region, which is an extremely rare location. The final diagnosis was based on histological examination, suggestive of well-differentiated chondrosarcoma [the World Health Organization (WHO); grade I]. Conclusion: Cranial vault chondrosarcoma is an uncommon histological diagnosis with surgery as the primary treatment option; however, adjuvant radiotherapy plays a definitive role, especially in aggressive or incomplete removed cases.

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