scholarly journals Determination of Sensitivity and Specificity of High Resolution CT Scan in Evaluation of Cardiac and Extra-Cardiac Anomalies among Bangladeshi Children

2021 ◽  
Vol 2 (6) ◽  
pp. 51-55
Author(s):  
M. Shirin ◽  
R. Mondal ◽  
H. Zubery
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Cardiovascular Diseases ◽  
Congenital Heart ◽  
Invasive Procedure ◽  
Coarctation Of Aorta ◽  
Suitable Alternative ◽  
Gold Standard Method ◽  
Pediatric Age Group ◽  
Ct Angiogram

Congenital heart disease (CHD) is one of the important causes of morbidity and mortality in the pediatric age group. Invasive angiography is considered as gold standard method for the diagnosis of pediatric cardiovascular diseases. Multi-detector CT cardiac angiogram by using 64 slice scanner is a useful modality and suitable alternative to previous invasive procedure in evaluation of congenital heart disease. The present study was conducted in the Department of Cardiology of NICVD during the period of September 2019 to August 2020 (One year). We selected 40 patients presenting in the outpatient department of National Institute of Cardiovascular Diseases and Hospital (NICVD) who were diagnosed to have congenital heart disease clinically and radiologically. CT angiogram revealed ASD in 10%, coarctation of aorta in 5%, Pentalogy of Fallot in 2.5%, Tetralogy of Fallot (TOF) in 32.5%, Ventricular septal defect (VSD) in 30.0%, PAH in 2.5%, PS in 5%, RVH with PS in 2.5%, PDA in 5% and Tricuspid atresia with ASD with VSD with PS in 2.5% patients. Conventional catheter angiogram revealed ASD in 5%, VSD in 32.5%, TOF in 30%, PS in 12.5%, Coarctation of aorta in 5% and Pentalogy of Fallots in 5%. The diagnostic performance of MDCT in the diagnosis and evaluation of congenital heart disease was high.

Aortic Saturation Predicted Operability in Acyanotic Congenital Heart Disease with Left-to-Right Shunt

2021 ◽  
Vol 104 (5) ◽  
pp. 740-745
Keyword(s):  
Congenital Heart Disease ◽  
Pulmonary Hypertension ◽  
Heart Disease ◽  
Oxygen Saturation ◽  
Cardiac Catheterization ◽  
Congenital Heart ◽  
Diagnostic Yield ◽  
Invasive Procedure ◽  
Roc Curve Analysis ◽  
Acyanotic Congenital Heart Disease

Background: Cardiac catheterization is the gold standard to determine operability in patients with congenital heart disease (CHD) with left to right shunt and pulmonary hypertension. Objective: To determine if systemic oxygen saturation could be used as a screening tool for acyanotic CHD patients who are operable without having to undergo an invasive procedure. Materials and Methods: All cardiac catheterization data at the King Chulalongkorn Memorial Hospital between 2002 and 2017 were retrospectively reviewed. The inclusion criteria were acyanotic lesion with left-to-right shunt, mean pulmonary artery pressure of 25 mmHg or more, pulmonary overcirculation (Qp:Qs greater than 1), and absence of significant left sided heart disease (LAP or PCWP of less than 15 mmHg). Operability was defined as Rpi of 6 WU.m² or less and Rp:Rs of less than 0.3 in room air. The value of aortic saturation as diagnostic test for operability was analyzed by ROC curve analysis. Results: Two hundred twenty-six patients, with a median age of two years old, (IQR 0.11, 6.00) were divided into pre-tricuspid shunt (ASD, PAPVR, 9.7%), complete atrioventricular (AV) canal defect (13%), and other post-tricuspid lesion (VSD, PDA, 77%). Aortic saturation cut-off values to predict operability with 100% specificity were 98.5% in pre-tricuspid shunt, 100% in post-tricuspid shunt group, and 94.5% in complete AV canal group. Conclusion: In the present study population, aortic saturation may be used to determine operability in acyanotic CHD patients with pulmonary overcirculation. Diagnostic yield is best in patients with complete AV canal defect in whom oxygen saturation of 95% or above identified operability with close to 100% specificity. In other lesions, there appears to be no oxygen saturation that is safe to preclude cardiac catheterization. Keywords: Congenital heart disease, Acyanotic heart disease, Non-cyanotic heart lesions, Pulmonary hypertension, Operability, Aortic saturation

scholarly journals Ectopia Cordis: A Rare Congenital Heart Disease

2019 ◽  
Vol 11 (2) ◽  
pp. 183-186
Author(s):  
Naharuma Aive Hyder Chowdhury ◽  
Mohammad Sharifuzzaman ◽  
Mohammad Abul Kalam Azad ◽  
Tuhin Haque ◽  
Jesmin Hossain
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Congenital Heart ◽  
Single Ventricle ◽  
Venous Drainage ◽  
Great Artery ◽  
Complex Congenital Heart Disease ◽  
Ct Angiogram ◽  
Rare Congenital Abnormality ◽  
Multiple Abnormalities

Three days old female presented with beating heart outside the thoracic cavity. This is a rare congenital abnormality associated multiple abnormalities. Patient came with features of infection. To diagnose routine blood investigation along with echocardiography and CT angiogram of heart,great vessel and abdomen were done. She was diagnosed as functionally single ventricle with hypoplastic branch pulmonary artery with malposed great artery with anomalous pulmonary venous drainage. Thisis lethal variety of ectopic cordis. Our patient had no adequate space in mediastinum to replace heart and she was in septicemia, so managed medically. Patient expired at her 6thday due to sepsis and intracardiac complex congenital heart disease. Cardiovasc. j. 2019; 11(2): 183-186

CARDIOVASCULAR DISEASES AND EVALUATE OUTCOMES IN TREATMENT OF CARDIOVASCULAR DISEASES AT VIETNAM NATIONAL CHILDREN’S HOSPITAL IN 2019

2020 ◽  
Vol 4 (3) ◽  
Author(s):  
Nong Manh
Keyword(s):  
Cardiovascular Disease ◽  
Congenital Heart Disease ◽  
Heart Disease ◽  
Cardiovascular Diseases ◽  
Congenital Heart ◽  
Treatment Results ◽  
Cross Sectional ◽  
Children's Hospital ◽  
Children’S Hospital ◽  
Heart Center

Objectives: To describe characteristics of cardiovascular disease and treatment results at the Children's Heart Center, Vietnam National children’s hospital in 2019. Subjects: Children aged 2 months to 15 years diagnosed with cardiovascular disease at Children's Heart Center, Vietnam National children’s hospital from January 2019 to December 2019. Research methodology: cross-sectional description. Results and conclusions: Congenital heart disease was common in children <5 years old, especially the age <12 months. Complications of the disease are mainly pneumonia, malnutrition. Most treated children get relief of symptoms and leave the hospital early in about 1 week.  

Nonimmune Hydrops Fetalis in the Liveborn: Series of 32 Autopsies

2005 ◽  
Vol 8 (3) ◽  
pp. 369-378 ◽  
Author(s):  
María M. Rodríguez ◽  
Jocelyn H. Bruce ◽  
Xavier F Jiménez ◽  
Rita L. Romaguera ◽  
Eduardo Bancalari ◽  
...  
Keyword(s):  
Congenital Heart Disease ◽  
Heart Disease ◽  
Cardiovascular Diseases ◽  
Congenital Heart ◽  
Chromosomal Abnormalities ◽  
Hydrops Fetalis ◽  
Urogenital Sinus ◽  
Prune Belly Syndrome ◽  
Congenital Infections ◽  
Nonimmune Hydrops

Nonimmune hydrops fetalis (NIHF) or generalized soft tissue edema and cavity effusions may be due to cardiovascular diseases, congenital infections, genitourinary malformations, thoracic masses, placental conditions, chromosomal abnormalities, and idiopathic. We report 32 cases of NIHF from among 429 neonates who underwent autopsies (incidence 7.45%). Sixteen cases (50%) had cardiovascular disease; all were due to low output cardiac failure; 7 had structural congenital heart disease. Three of the children with congenital heart disease also had chromosomal abnormalities: 2 had trisomy 18 and 1 had Noonan syndrome. Among myocardial conditions were five subjects with cardiomyopathies (1 of each of the following types): oncocytic, dilated, endocardial fibroelastosis, cardiac glycogenosis, and carnitine deficiency; 3 had myocarditis, and 1 had cardiac rhabdomyomas. Congenital infections were due to cytomegalovirus in 3 cases, bacteria in 2, and parvovirus in 1. The mechanism of NIHF in these cases might be a combination of decreased myocardial contractility due to myocarditis and fetal anemia. Genitourinary diseases were present in 5 newborns: Two had congenital nephrotic syndrome, 1 had VACTER association, 1 had prune-belly syndrome, and 1 had urogenital sinus malformation. Intrathoracic lesions were found in 2 babies (pulmonary sequestration and diaphragmatic hernia). One twin died of volume overload due to twin transfusion syndrome. Only 2 newborns were classified as idiopathic. Our study shows that cardiovascular diseases that lead to heart failure or impaired venous return are more common in the liveborn (50%), whereas congenital infections are more common in the stillborn with NIHF.

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