scholarly journals Peran pemeriksaan radiologis: barium enema pada penyakit hirschprung

2020 ◽  
Vol 2 (1) ◽  
pp. 83-86
Author(s):  
Rizki Novtarina
Keyword(s):  
Barium Enema ◽  
Anal Verge ◽  
Abdominal Distension ◽  
Transitional Zone ◽  
Parasympathetic Nerves ◽  
Slowing Down ◽  
Area 7 ◽  
Lateral Decubitus ◽  
Hirschprung's Disease ◽  
Proximal Zone

Hirschprung's Disease (HD) is an aganglionic disease segment of the parasympathetic nerves of Meissner and Auerbach. HD occurs in 1 in 5000 live births. Symptoms include late meconium, green vomiting, and abdominal distension. There are two types of HD short segments and long segments. This transitional zone is usually found in the rectosigmoid region or sigmoid colon, colon descendants, rectum, other colon and can occur in the small intestine. A medium according to type, 75 percent type of long segment, and 15% type of short segment. In the diagnosis, radiological imaging of the barium enema is needed with the position of Anteroposterior-Supine, Semi-Erect, Left Lateral Decubitus. There are seven typical images found (1) Transitional zones, (2) aganglionic segments, (3) Thickening of the mucosal portion of the proximal zone of the zone, (4) Slowing down of barium evacuation, (5) Comparison of rectosigmoid caliber less than 1, (6) Spasms aganglionic area, (7) Image of cobblestone mucosa. Immunohistochemical examination by suction biopsy through taking three places, namely two, three, and five centimeters (cm) from the anal verge.

The double contrast barium enema: Improvements to lateral decubitus views including the use of a wedge filter

1978 ◽  
Vol 29 (2) ◽  
pp. 197-199 ◽  
Author(s):  
Gerald de Lacey ◽  
Brian Wignall ◽  
Jane Ambrose ◽  
Kay Baylis ◽  
Colin Bridges
Keyword(s):  
Barium Enema ◽  
Double Contrast ◽  
Double Contrast Barium Enema ◽  
Lateral Decubitus ◽  
Wedge Filter

scholarly journals DIAGNOSTIC ACCURACY OF BARIUM ENEMA FINDINGS IN HIRSCHSPRUNG'S DISEASE

2016 ◽  
Vol 29 (3) ◽  
pp. 155-158 ◽  
Author(s):  
Mehran PEYVASTEH ◽  
Shahnam ASKARPOUR ◽  
Nasrollah OSTADIAN ◽  
Mohammad-Reza MOGHIMI ◽  
Hazhir JAVAHERIZADEH
Keyword(s):  
Barium Enema ◽  
Predictive Value ◽  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Transitional Zone ◽  
Dentate Line ◽  
Contrast Enema ◽  
Cross Sectional ◽  
Specificity And Sensitivity ◽  
Sensitivity Specificity

ABSTRACT Background: Hirschsprung's disease is the most common cause of pediatric intestinal obstruction. Contrast enema is used for evaluation of the patients with its diagnosis. Aim: To evaluate sensitivity, specificity, positive predictive value, and negative predictive value of radiologic findings for diagnosis of Hirschsprung in patients underwent barium enema. Methods: This cross sectional study was carried out in Imam Khomeini Hospital for one year starting from 2012, April. Sixty patients were enrolled. Inclusion criteria were: neonates with failure to pass meconium, abdominal distention, and refractory constipation who failed to respond with medical treatment. Transitional zone, delay in barium evacuation after 24 h, rectosigmoid index (maximum with of the rectum divided by maximum with of the sigmoid; abnormal if <1), and irregularity of mucosa (jejunization) were evaluated in barium enema. Biopsy was obtained at three locations apart above dentate line. PPV, NPV, specificity , and sensitivity was calculated for each finding. Results: Mean age of the cases with Hirschsprung's disease and without was 17.90±18.29 months and 17.8±18.34 months respectively (p=0.983). It was confirmed in 30 (M=20, F=10) of cases. Failure to pass meconium was found in 21(70%) cases. Sensitivity, specificity, PPV, and NPV were 90%, 80%, 81.8% and 88.8% respectively for transitional zone in barium enema. Sensitivity, specificity, PPV, and NPV were 76.7%, 83.3%, 78.1% and 82.1% respectively for rectosigmoid index .Sensitivity, specificity, PPV, and NPV were 46.7%, 100%, 100% and 65.2% respectively for irregular contraction detected in barium enema. Sensitivity, specificity, PPV, and NPV were 23.3%, 100%, 100% and 56.6% respectively for mucosal irregularity in barium enema. Conclusion: The most sensitive finding was transitional zone. The most specific findings were irregular contraction, mucosal irregularity, and followed by cobblestone appearance.

scholarly journals Barium Enema in Hirschsprung’s Disease : Correlation of Clinical Outcome

2018 ◽  
Vol 29 (Number 2) ◽  
pp. 24-28
Author(s):  
K Laila ◽  
T K Chowdhury ◽  
S A Talukder ◽  
T Banu
Keyword(s):  
Sigmoid Colon ◽  
Barium Enema ◽  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Transitional Zone ◽  
Lateral View ◽  
Erect Posture ◽  
Female Ratio ◽  
X Ray ◽  
Medical College

The anticipated level of aganglionosis can influence the surgical planning in Hirschsprung's disease (HD). The aim of this study was to find out the role of barium enema in diagnosis of HD. Barium enema is usually performed in patients referred for investigation for constipation. This prospective study was performed in the department of pediatric surgery Chittagong Medical College & Hospital. During this period a total of 198 patients were clinically diagnosed as HD. All patients were initially evaluated by plain x- ray abdomen in erect posture. Among 198 patients, 43 patients had perforation in plain x- ray and 31 were clinically unstable at presentation. Those 74 patients were excluded from the study. Rest 124 participating patients were divided into three groups: Neonate, Infant and children according to their age. Male to female ratio was 2.44: I. Barium enema X- ray early film, 24 hours delayed film (Antero-posterior and lateral view) were done for every patient. Length of radiological narrow zone (RNZ), radiological Transitional zone (RTZ) and Recto-sigmoid index (RSI) was measured in cm. Photo of X- ray was taken for every patient. RIZ was demonstrated in 74 (60%) patients. RNZ was demonstrated in 94 (75%) studied population. RSI was measured in 65 (52.42%) subjects. Retention of barium more than 24 hours was found in 95 (75%) patients. Redundant sigmoid colon was found in 54 (43.5%) patients. Right-sided sigmoid colon was present in 46(30.6%) patients. Saw-toothed appearance in spastic colon was seen in 38 (30.6%) patients. Mucosal edema and irregularities were present in 25 (20.2%) patients. Rounded transverse colon was seen in 6 children. Barium mixed with stool was found in 32 (25.8%) patients. Mosaic pattern of colon was present in 10 patients. Visualization of RTZ is a reliable sign ofH13. Besides the RIZ BE in HD has various other radiological features.

Short-Segment Hirschsprung's Disease

1988 ◽  
Vol 18 (1) ◽  
pp. 16-19 ◽  
Author(s):  
John T Momoh
Keyword(s):  
Clinical Diagnosis ◽  
Clinical Features ◽  
Barium Enema ◽  
Muscle Biopsy ◽  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Abdominal Distension ◽  
Short Segment ◽  
Rectal Muscle

The clinical features and treatment of 15 children with short-segment Hirscbsprung's disease were reviewed. It accounted for 25% of all Hirschsprung's cases seen 1975–84. The symptomatology, which was generally mild, consisted of slowly progressive abdominal distension with one of three defaecating patterns: persistent or intermittent diarrhoea; 2–3 normal daily motions; and constipated stool passed infrequently. Diagnosis was based mainly on the clinical features and barium enema findings. Eight patients had formal sphincterectomy and 3 had rectal muscle biopsy; follow up to 2½ years in some of the patients with sphincterectomy showed satisfactory results. Factors that would expedite clinical diagnosis are discussed.

Rare association of Beckwith-Wiedemann syndrome with Hirschsprung’s disease in an infant with hypoglycemia

2020 ◽  
Vol 13 (4) ◽  
pp. e235121 ◽  
Author(s):  
Nikhil Shah ◽  
Anuradha Khadilkar ◽  
Vaman Khadilkar ◽  
Sagar Lad
Keyword(s):  
High Glucose ◽  
Hirschsprung's Disease ◽  
Hirschsprung’S Disease ◽  
Rectal Biopsy ◽  
Abdominal Distension ◽  
Intravenous Fluids ◽  
Congenital Hyperinsulinism ◽  
Rare Association ◽  
Hirschprung's Disease ◽  
Hyperinsulinemic Hypoglycaemia

Hypoglycaemic due to congenital hyperinsulinism in Beckwith-Wiedemann syndrome is commonly seen. It is usually transient and is managed by enteral feeds, high glucose-containing intravenous fluids and medications like diazoxide. We describe a case of an infant with genetically proven Beckwith-Wiedemann syndrome with prolonged hyperinsulinemic hypoglycaemia. Despite treatment with high glucose-containing intravenous fluids, diazoxide and octreotide, her hypoglycaemia persisted. In addition to this, she also developed features of intestinal obstruction, which further complicated the management of hypoglycaemia. She underwent a rectal biopsy for this, which was highly suggestive of Hirschprung’s disease. Following surgery, her abdominal distension and feed intolerance were settled and sugar control was improved. We present a rare association of Hirschsprung’s disease with Beckwith-Wiedemann syndrome. To the best of our knowledge, this association has not been previously reported and this added to the difficulty in managing hyperinsulinemic hypoglycaemia in our patient.

Paediatrician’s Suspicion and Radiologist’s Precision in Diagnosing Hirschprung’s Disease in a Child: Case Report

2020 ◽  
Vol 10 (2) ◽  
pp. 38-41
Author(s):  
Shashi Sharma ◽  
Tanu Singh ◽  
Rohit Sharma ◽  
Vinod Bende ◽  
Praveen Gulia ◽  
...  
Keyword(s):  
Case Report ◽  
Early Diagnosis ◽  
Delayed Diagnosis ◽  
Hirschsprung Disease ◽  
Abdominal Distension ◽  
Plain Radiography ◽  
Motor Disorders ◽  
Short Segment ◽  
Pull Through ◽  
Hirschprung's Disease

Hirschprung’s disease (HD) is also called as aganglionic megacolon. The entity falls in the group of congenital motor disorders. The usual presentation is in the form of not passing of meconium, abdominal distension with or without vomiting. We present a 2-years old child who was brought with complaints of constipation and difficulty in passing stool. The child was evaluated radiologically by plain radiography, ultrasonography (USG) and barium enema and was diagnosed as a case of short segment type of Hirschsprung disease. The parents had been counselled and advised for pull-through surgery for the child. It is a dilemma for the paediatrician to confirm the diagnosis of Hirschprung’s disease until a radiologically confirmed diagnosis is made. Many cases are delayed for the treatment because of non-diagnosis or delayed diagnosis. The importance lies in the early diagnosis for further surgical management.

scholarly journals GAMBARAN PASIEN HIRSCHSPRUNG DI RSUP PROF. DR. R. D. KANDOU MANADO PERIODE JANUARI 2010 – SEPTEMBER 2014

e-CliniC ◽  
2015 ◽  
Vol 3 (1) ◽  
Author(s):  
Elfianto D. Corputty ◽  
Harsali F. Lampus ◽  
Alwin Monoarfa
Keyword(s):  
Barium Enema ◽  
Ganglion Cells ◽  
Hirschsprung Disease ◽  
Abdominal Distension ◽  
Distal Intestine ◽  
Radiologic Evaluation ◽  
Functional Intestinal Obstruction ◽  
Duhamel Procedure ◽  
Intrinsic Component ◽  
Disease Present

Abstract: Hirschsprung disease is a developmental disorder of the intrinsic component of the enteric nervous system that is characterized by the absence of ganglion cells in the myenteric and submucosal plexuses of the distal intestine. Because these cells are responsible for normal peristalsis, patients with Hirschsprung disease present with functional intestinal obstruction at the level of aganglionosis. This researched purpose to know the description of Hirschsprung ddisease patient in RSUP Prof. Dr. R. D. Kandou Manado for period January 2010 to September 2014. The research method used was a descriptive retrospective. This study found 45 cases of Hirschsprung Disease. Males are more than females with ratio 1,3:1 with the age group are from 2 day to 45 years old. Most Hirscshprung disease patients came with the main complaints: abdominal distension, difficult to defecate and not defecation from birth, with the concomitant complaints, that is vomiting and abdominal pain. The most supporting examination of Hirscshprung disease is radiologic evaluation, that is plain abdominal x-ray and barium enema, and patologi anatomi evaluation, that is mucosal biopsy and suction biopsy. The most used surgery technique of Hirscsprung disease patients is colostomy and duhamel procedure. The most frequent complication of Hirschsprung disease is sepsis. The most outcome is improved clinical condition.Keywords: Hirschsprung disease, description of patientAbstrak: Penyakit Hirschsprung merupakan kelainan perkembangan komponen intrinsik pada sistem saraf enterik yang ditandai oleh absennya sel-sel ganglion pada pleksus myenterik dan submukosa di intestinal distal. Karena sel-sel ini bertanggung jawab untuk peristaltik normal, pasien-pasien penyakit Hirschprung akan mengalami obstruksi intestinal fungsional pada level aganglion. Tujuan Penelitian ini untuk mengetahui gambaran pasien Hirschsprung di RSUP Prof. Dr. R. D. Kandou Manado periode Januari 2010 sampai September 2014. Metode penelitian ini bersifat deskriptif retrospektif. Pada penelitian ini ditemukan 45 kasus penyakit Hirschsprung. Laki-laki lebih banyak dari perempuan dengan rasio 1,3:1 dengan umur mulai dari 2 hari sampai 45 tahun. Secara umum, pasien Hirschsprung datang dengan keluhan utama yaitu perut kembung, tidak BAB sejak lahir dan sulit BAB, disertai keluhan penyerta yaitu muntah atau nyeri perut. Secara umum pemeriksaan penunjang yang digunakan adalah pemeriksaan radiologi yaitu foto polos abdomen dan barium enema, dan pemeriksaan patologi anatomi yaitu biopsi eksisi dan biopsi hisap. Sebagian besar pasien Hirschsprung dilakukan tindakan bedah kolostomi dan duhamel. Komplikasi pada umumnya adalah sepsis. Hasil akhir penatalaksanaan pada umumnya cukup baikKata kunci: penyakit hirschsprung, gambaran pasien

Analysis and lattice imaging of a transitional event on garnets

1978 ◽  
Vol 36 (1) ◽  
pp. 270-271
Author(s):  
J.Y. Laval
Keyword(s):  
Yttrium Iron Garnet ◽  
Reciprocal Lattice ◽  
Transitional Zone ◽  
Lattice Imaging ◽  
Yttrium Iron ◽  
X Ray ◽  
Ionic Process ◽  
The Matrix ◽  
High Resolution Technique ◽  
Iron Garnet

The exsolution of magnetite from a substituted Yttrium Iron Garnet, containing an iron excess may lead to a transitional event. This event is characterized hy the formation of a transitional zone at the center of which the magnetite nucleates (Fig.1). Since there is a contrast between the matrix and these zones and since selected area diffraction does not show any difference between those zones and the matrix in the reciprocal lattice, it is of interest to analyze the structure of the transitional zones.By using simultaneously different techniques in electron microscopy, (oscillating crystal method microdiffraction and X-ray microanalysis)one may resolve the ionic process corresponding to the transitional event and image this event subsequently by high resolution technique.

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