Rinoplasti pada kelainan hidung kongenital

2015 ◽  
Vol 45 (1) ◽  
pp. 53
Author(s):  
Trimartani Trimartani ◽  
Novra Widayanti

Latar belakang: Nasal bifida dan supernumerary nostril merupakan kelainan hidung  kongenital yang sangat jarang.  Nasal bifida disebut juga hidung ganda atau celah hidung, mempunyai manifestasi sangatberagam mulai dari lekukan minimal pada puncak hidung hingga celah maksila. Supernumerary  nostrilmerupakan bagian dari kelainan duplikasi hidung. Tujuan: Sebagai ilustrasi kepada ahli THT-KL mengenaikasus kelainan hidung kongenital yang jarang ditemukan. Kasus: Dilaporkan tiga kasus anak dengankelainan hidung kongenital selama bulan Agustus-Desember 2012. Satu kasus dengan  nasal bifida, satukasus dengan nasal bifida disertai atresia koana, dan satu kasus dengan triple nostril. Penatalaksanaan:Pada kasus nasal bifida dilakukan rekonstruksi hidung menggunakan  tandur dermis dan pada kasustriple nostril dilakukan fistulektomi dan rekonstruksi alae. Kesimpulan: Nasal bifida dan triple nostrilmerupakan kelainan hidung kongenital yang jarang ditemukan. Kelainan ini membutuhkan rekonstruksiyang optimal. Indikasi waktu dari operasi pada kasus kelainan hidung kongenital ini berdasarkan ukuranhidung menyerupai ukuran dewasa dan perkembangan sosial anak. Kata kunci: kelainan hidung kongenital, nasal bifida, supernumerary nostril, duplikasi hidungABSTRACT Background: Bifid nose  and supernumerary nostril are  rare nasal congenital anomalies. The appearance of bifid nose, also called double nose or cleft nose, varies from a simple groove at thenasal apex to a maxillary cleft.  Supernumerary nostril is a kind of nasal duplication. Purpose: Thiscase report is to forewarn general practitioners and ENT specialist about these rare nasal congenitalanomaly cases. Case: Reported three cases with congenital nasal anomaly, one case with bifid nose, onecase with bifid nose and choanal atresia, and one case with triple nostril. Management: The cases withbifid nose underwent nasal reconstruction using dermal graft and the case with triple nostril underwentfistulectomy and alae reconstruction. Conclusion: Bifid nose and triple nostril are rare nasal congenitalanomaly that need optimal reconstruction. Indication for the time of the operation for cases of congenitalnasal deformities is based on the size approaching the adult size and on the child’s social development. Keywords: congenital nasal anomaly, bifid nose, supernumerary nostril, nasal duplication

PEDIATRICS ◽  
1959 ◽  
Vol 23 (1) ◽  
pp. 150-150
Author(s):  
JOSEF WARKANY

This book was written, according to the foreword, primarily for students and general practitioners. It is designed as a quick reference to aid in discussions with parents and to facilitate an understanding of the anatomic anomalies discussed, of the resulting functional disturbances and their treatment. The authors are plastic surgeons and the subject matter is chosen essentially from their point of view. They deal with a variety of congenital anomalies but also with disorders resulting from postnatal injuries. Such etiologically heterogeneous subjects as deformities of the skull and brain, facial clefts, hemangiomas, fractures and dislocations of the facial bones and dental caries are discussed.


1998 ◽  
Vol 12 (2) ◽  
pp. 81-86 ◽  
Author(s):  
Jacqueline E. Jones ◽  
Eytan Young ◽  
Linda Heier

Although the most common form of nasal obstruction in neonates is soft tissue edema, congenital bony nasal deformities are being recognized as an important cause of newborn airway obstruction. In addition to the well described choanal atresia, CT imaging of the newborn in respiratory distress reveals two other forms of bony nasal cavity deformities: nasal pyriform aperture stenosis and nasal cavity stenosis. All of the three types of bony nasal cavity deformities have characteristic anatomical features, are associated with distinctive congenital anomalies, and are postulated to have differing embryological causes. Five patients with congenital bony nasal cavity deformities are presented. These cases illustrate the clinical and radiological presentation of varied types of congenital nasal cavity obstruction as well as the criteria used to guide clinical management.


2009 ◽  
Vol 135 (6) ◽  
pp. 543 ◽  
Author(s):  
T. Andrew Burrow ◽  
Howard M. Saal ◽  
Alessandro de Alarcon ◽  
Lisa J. Martin ◽  
Robin T. Cotton ◽  
...  

1988 ◽  
Vol 97 (5) ◽  
pp. 448-453 ◽  
Author(s):  
John U. Coniglio ◽  
James V. Manzione ◽  
Arthur S. Hengerer

The CHARGE association is a collection of multisystem congenital anomalies including choanal atresia. A review of the literature failed to identify any specific findings that suggested the need to alter the management of choanal atresia in these patients. Our review of 24 patients with choanal atresia managed between 1974 and 1986 identified nine patients with the CHARGE criteria. These nine patients demonstrated a higher prevalence of surgical failures than the patients without the CHARGE association. The reasons are discussed, and computed tomographic scans demonstrate the anatomic findings of a more contracted nasopharynx and narrowed posterior choanal region. Thus, successful repairs require a more radical resection of the posterior nasal septum and lateral bony walls that can be achieved only with a transpalatal approach. The preoperative airways of CHARGE association patients are also at increased risk of obstruction and may require intubation or tracheotomy during the early life of the patient.


2018 ◽  
Vol 21 (04) ◽  
pp. 816-819
Author(s):  
Adil Ayub ◽  
Ayesha Ayub ◽  
Ayub-ur- Rehman

Choanal atresia (CA) is a rare, congenital malformation resulting as a failure incommunication between the posterior nasal cavity and the nasopharynx. The clinical course isoften asymptomatic in unilateral CA leading to higher rates of misdiagnosis, in comparison tobilateral CA, which manifests itself as a surgical emergency at birth. Most cases present asisolated malformations, but it may also be associated with other congenital anomalies in 20-50%of cases. Currently, the most important diagnostic tool for CA is computerized tomography (CT)and confirmatory diagnosis is usually achieved with the help of nasoendoscopic examination.Although, different surgical approaches have been used in the past, transnasal endoscopicrepair is currently preferred over others. Herein, we describe our experience of three cases andshare our simple stentless endoscopic technique, to facilitate physicians working in low facilityunits for a timely diagnosis and prompt treatment.


PEDIATRICS ◽  
1969 ◽  
Vol 43 (3) ◽  
pp. 468-469
Author(s):  
G. van Leeuwen

In our paper, "Screening for Hidden Congenital Anomalies" (Pediatrics, 41:147, 1968), the point of course was that we do just that, not that we develop arguments over the best method to diagnose choanal atresia. It was also not intended that we torture our little friends by "ramming foreign bodies down their nostrils" (Pediatrics, 42:873, 1968) and public apology is herewith rendered to all infants so molested. There are two objections to Dr. Abel's rarely quoted reference.


1979 ◽  
Vol 93 (12) ◽  
pp. 1223-1228 ◽  
Author(s):  
Israel Brama ◽  
Dan Engelhard

SummaryFOUR cases of bilateral congenital choanal atresia are presented. Three of them (75 per cent) were shown by Electric Response Audiometry (ERA) tests to have, in addition, congenital nerve deafness; and two had other congenital anomalies. Thus, congenital nerve deafness should be considered as a possible congenital anomaly associated with choanal atresia. Early diagnosis and treatment of congenital choanal atresia can prevent death from asphyxia during the neonatal period, but after surgical correction of the atresia the possible existence of additional anomalies has to be determined and treated.By the use of electric response audiometry we are able to detect sensorineural hearing loss during the neonatal period and can plan the rehabilitation of deaf infants.


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