scholarly journals Undifferentiated Pleomorphic Sarcoma Originating in the Porta Hepatis: Report of a Rare Case

2019 ◽  
Vol 103 (9-10) ◽  
pp. 477-481
Author(s):  
Sho Okimoto ◽  
Tsuyoshi Kobayashi ◽  
Shintaro Kuroda ◽  
Hirotaka Tashiro ◽  
Hideki Ohdan
Keyword(s):  
Rare Case ◽  
Tumor Resection ◽  
The Body ◽  
Porta Hepatis ◽  
Undifferentiated Pleomorphic Sarcoma ◽  
Pleomorphic Sarcoma ◽  
Immunohistochemical Markers ◽  
Contrast Enhanced ◽  
One Year ◽  
Enhanced Computed Tomography

Undifferentiated pleomorphic sarcoma (UPS) is a soft tissue sarcoma in adults. Although it can occur in any part of the body, its most common site is the extremities, followed by the trunk and retroperitoneum. Here, we describe a rare case of UPS originating in the porta hepatis of an 83-year-old man that was incidentally detected via contrast-enhanced computed tomography. Because malignancy was suspected, we performed a tumor resection with cholecystectomy. Consistent with a diagnosis of UPS, histopathology revealed highly cellular lesions with scattered pleomorphic spindle cell fascicles arranged in a storiform pattern; further, results of tests for all immunohistochemical markers were negative. One year after surgery, the patient is currently doing well without any evidence of tumor recurrence. To our knowledge, this is the first report of UPS originating in the porta hepatis.

Imaging of a Rare Case of Diaphragmatic Tumor

2017 ◽  
Vol 3 (1) ◽  
pp. 25-27
Author(s):  
Ajit Reddy ◽  
Anil K Shukla ◽  
Sowmya Anand ◽  
Nitish Suresh
Keyword(s):  
Rare Case ◽  
Surgical Excision ◽  
Malignant Neoplasms ◽  
Primary Tumors ◽  
Contrast Enhanced ◽  
History Of ◽  
Upper Abdominal ◽  
Diaphragmatic Tumor ◽  
Enhanced Computed Tomography ◽  
Upper Abdomen

ABSTRACT Primary tumors of the diaphragm are quite rare. About 150 cases have been reported in the literature. Fibrosarcomas are the most common malignant neoplasms of the diaphragm; however, only a few (less than 20) cases have been reported to date. We present a case of an extremely rare tumor of the diaphragm. A 65-year-old woman presented with history of vague upper abdominal pain since 2 months and distension for 2 weeks. Ultrasonography features were in favor of a mass arising from left dome of diaphragm with evidence of vascularity on Doppler; lesion was displacing spleen inferiorly. Contrast-enhanced computed tomography scan of the abdomen revealed a mass located in the region of the left dome of diaphragm and deriving blood supply from the branches of abdominal aorta. Surgical excision was planned, keeping in mind the diagnosis of a left diaphragmatic tumor. Laparotomy revealed a left diaphragmatic tumor growing caudally into the upper abdomen. How to cite this article Anand S, Suresh N, Reddy AK, Shukla AK. Imaging of a Rare Case of Diaphragmatic Tumor. J Med Sci 2017;3(1):25-27.

scholarly journals Symptomatic Imperforate Hymen in Early Infancy: A Case Report

2020 ◽  
Vol 58 (226) ◽  
Author(s):  
Geha Raj Dahal ◽  
Subash Phuyal ◽  
Pooja Agrawal
Keyword(s):  
Rare Case ◽  
Abdominal Mass ◽  
Pelvic Mass ◽  
Primary Amenorrhea ◽  
Vaginal Opening ◽  
Imperforate Hymen ◽  
Contrast Enhanced ◽  
Abdominal Examination ◽  
Enhanced Computed Tomography ◽  
Contrast Enhanced Computed Tomography

Imperforate hymen, though a congenital anomaly, usually presents late in puberty as lowerabdominal pain, primary amenorrhea, and cyclical pain. Blood collects in vagina and uterus,proximal to imperforate hymen leading to their distention. Its presentation at infancy is a rare entity.We report such a rare case of symptomatic imperforate hymen in infancy, who presented with acuteretention of urine, chills and rigor. Abdominal examination revealed an intra-abdominal mass in thelower abdomen and pelvis with the absence of vaginal opening on perineal examination. Contrast enhanced computed tomography abdomen showed large abdominopelvic cystic lesion posterior tothe urinary bladder and anterior to the rectum consistent with a highly distended vagina. She wasmanaged by the incision of the imperforate hymen and drainage of the pus. A high index of suspicionis necessary whenever a female infant presents with abdomino-pelvic mass with symptoms of feveror urinary retention.

A Rare Case of Undifferentiated Pleomorphic Sarcoma of the Pancreas and Literature Review

2021 ◽  
Author(s):  
Ze Liang ◽  
Jingzhao Han ◽  
Hongfang Tuo ◽  
Dongdong Xue ◽  
Hanxiang Yu ◽  
...  
Keyword(s):  
Epigastric Pain ◽  
Abdominal Ultrasound ◽  
The Body ◽  
Case Presentation ◽  
Undifferentiated Pleomorphic Sarcoma ◽  
Pleomorphic Sarcoma ◽  
Multinucleated Cells ◽  
Imaging Characteristics ◽  
Hypoechoic Mass ◽  
Pulmonary Lymph Node

Abstract BackgroundPrimary undifferentiated pleomorphic sarcoma (UPS) of the pancreas is an exceedingly rare malignant tumor, with only 15 cases have been reported in the medical literature. At present, clinicians have poor recognition of the tumor, the epidemiology, diagnosis and treatment of this disease have yet not been established. Case presentationIn this report, we depict the clinical and imaging characteristics of a 37-year-old man presenting with a primarily cystic UPS. The patient complained of epigastric pain and distention over 20 days. Abdominal CT and pancreatic magnetic resonance imaging revealed cystic and cystic solid masses in the pancreatic body and tail. An abdominal ultrasound echogram revealed the mass in the body of the pancreas to be cystic with separation echo inside, and the wall was thick, not smooth. Besides, a hypoechoic mass was seen in the tail area of the pancreas with an inhomogeneous echoic pattern, containing small patches of no echo zone in the central. Microscopically, spindle fibroblast-like cells are arranged in a characteristic storiform pattern with pleomorphic and multinucleated cells. Immunohistochemically, tumor cells were positive for CD68 and vimentin. Seven months postoperatively, he was diagnosed with pulmonary lymph node metastasis and died five months later. Combined with this case report, we also reviewed the literature regarding UPS of the pancreas. ConclusionsAs we know, this is the first report on ultrasonography findings of pancreatic UPS. Despite there are no distinctive manifestation of UPS, a solid cystic lesion on ultrasonography or a hypodense area in the lesion on T2-weighted imaging, should be considered for differential diagnosis with pancreatic UPS. We believe this article may add some ideas into the diagnosis and therapy of patients with this tumor.

scholarly journals Retroperitoneal paraganglioma: a chameleon masquerading as an adrenal pheochromocytoma

2019 ◽  
Vol 101 (2) ◽  
pp. e62-e65 ◽  
Author(s):  
K Parmar ◽  
A Chandna ◽  
S Kumar
Keyword(s):  
Vena Cava ◽  
Final Diagnosis ◽  
Contrast Enhanced ◽  
Rare Tumours ◽  
Close Proximity ◽  
Adrenal Pheochromocytoma ◽  
Suprarenal Mass ◽  
One Year ◽  
Enhanced Computed Tomography ◽  
Contrast Enhanced Computed Tomography

Retroperitoneal paragangliomas are rare tumours arising from neural crest cells located near or in the autonomic nervous system; right from the skull bass to the pelvic floor. Often called the great masqueraders, their diagnosis and treatment is often difficult and fraught with danger, considering the close proximity of these tumours to important retroperitoneal organs. A 29-year-old woman presented to the outpatient department with complaints of paroxysms of headache, sweating and palpitations for one year. She was found to have elevated urinary metadrenalines (metanephrines) and a suprarenal mass on contrast-enhanced computed tomography of the abdomen, which demonstrated increased tracer activity on I-131 iodine-123 meta-iodobenzylguanidine scintigraphy. Adrenal pheochromocytoma was diagnosed and she underwent laparoscopic adrenalectomy after stabilisation of her blood pressure. Laparoscopy revealed a large suprarenal mass with dense adhesions to the inferior vena cava that was carefully separated from the vein and surrounding structures. The cut section revealed a heterogeneous mass encasing a normal adrenal gland and histopathology confirmed the same, confirming the final diagnosis of retroperitoneal paraganglioma.

scholarly journals Unusual trichobezor of stomach and intestines as a manifestation of Rapunzel syndrome: a rare case report

2019 ◽  
Vol 6 (12) ◽  
pp. 4569
Author(s):  
Tejinder Pal Singh Sodhi ◽  
Sameer Pundeer ◽  
Maneshwar Singh Utaal ◽  
Kirti Savyasacchi Goyal
Keyword(s):  
Computed Tomography ◽  
Rare Case ◽  
Proximal Jejunum ◽  
Rare Form ◽  
Rapunzel Syndrome ◽  
Contrast Enhanced ◽  
Rare Case Report ◽  
Enhanced Computed Tomography ◽  
Contrast Enhanced Computed Tomography ◽  
Entire Stomach

Rapunzel syndrome is a rare form of trichobezoar with accumulation of large amounts of hair extending from stomach to variable portion of small intestine. An 18 year old girl was brought to surgery opd with complaints of vomiting on and off since 3 months. Contrast enhanced computed tomography abdomen showed a bezoar extending from stomach into the duodenum and proximal jejunum suggestive of Rapunzel syndrome with 3rd and 4th part of duodenum along with duodenojejunal junction. On laparotomy, a trichobezoar occupying the entire stomach measured 100 cm in length and 700 grams in weight. Since the mass formed in Rapunzel syndrome is generally too large to be removed endoscopically or laparoscopically, it requires removal by open gastrostomy. 

scholarly journals Anesthetic Management in Anterior Mediastinal Pheochromocytoma Case

2020 ◽  
Author(s):  
Yücel Özgür
Keyword(s):  
Rare Case ◽  
Mediastinal Mass ◽  
Anesthetic Management ◽  
Tumor Resection ◽  
The Body ◽  
Anterior Mediastinal Mass ◽  
Open Thoracotomy ◽  
Anesthesia Management ◽  
History Of ◽  
Different Parts

Paraganglioma can be found in different parts of the body. In this case report, a rare case of anterior mediastinal paraganlioma was examined. Pheochromocytoma can pose problems in intraoperative anesthesia management. A 17-year-old male patient with an anterior mediastinal mass was first scheduled for thoracoscopic tumor resection, and then proceeded with open thoracotomy. The patient, who was diagnosed with preoperative pheochromocytoma, had a history of dual antihypertensive drug use. The patient, who showed an intraoperative labile course, had episodes of hypertension (270/140 mmHg) and tachycardia (200 bpm). Esmolol and nitroglycerin infusion was applied and intervened. Diagnosis of paraganglioma-related pheochromocytoma can be challenging. Risks can be minimized by making appropriate decisions and interventions before and during the operation.

Undifferentiated Pleomorphic Sarcoma of a Chronic Burn Scar of the Knee With Lymph Node Metastasis

2021 ◽  
pp. 153473462110601
Author(s):  
Jong Yun Choi ◽  
Won Jin Cha ◽  
Jeeyoon Kim ◽  
Ee Room Jung ◽  
Sung No Jung ◽  
...  
Keyword(s):  
Lymph Node ◽  
Lymph Node Metastasis ◽  
Cell Carcinoma ◽  
Rare Case ◽  
Spatial Distance ◽  
Burn Scar ◽  
Undifferentiated Pleomorphic Sarcoma ◽  
Node Metastasis ◽  
Pleomorphic Sarcoma ◽  
Pleomorphic Cells

Malignant transformation of chronic burn scars are usually toward cutaneous lineages, including squamous cell carcinoma, basal cell carcinoma, and malignant melanoma. Sarcomas are less common. Undifferentiated pleomorphic sarcoma(UPS) is a subtype of soft tissue sarcoma with storiform-pleomorphic cells of uncertain origin, and has sparingly been reported to arise from burn scars. The majority are localized lesions probably due to the spatial distance of mesenchymal cells from the epithelium. The authors describe a rare case of UPS of the chronic burn scar of his knee with ipsilateral femoral and external iliac lymph node metastasis.

scholarly journals The rare case of De Garengeot hernia: femoral hernia containing perforated appendicitis

2019 ◽  
Vol 2019 (11) ◽  
Author(s):  
Lei Ying ◽  
Jeong-Moh John Yahng
Keyword(s):  
Femoral Hernia ◽  
Rare Case ◽  
Clinical Symptoms ◽  
Perforated Appendicitis ◽  
Vermiform Appendix ◽  
Hernia Sac ◽  
Contrast Enhanced ◽  
Enhanced Computed Tomography ◽  
Groin Hernias ◽  
De Garengeot Hernia

Abstract Femoral hernias account for ~4% of all groin hernias but are much more common in females, especially those over the age of 70. Risk of incarceration is overall low but can include structures such as bowel, omentum, bladder, ovary and very rarely, the appendix. The subset of femoral hernias containing the vermiform appendix is known as de Garengeot hernias. We describe a rare case of an 87-year-old female patient who presented with an incarcerated right femoral hernia confirmed on contrast-enhanced computed tomography scan of the abdomen and pelvis, with subsequent open hernia reduction revealing a perforated necrotic appendix with pus contained in the hernia sac. Histopathology revealed acute appendicitis with increased stromal fibrosis suggestive of a chronic process. Pre-operative diagnosis of de Garengeot hernias remains challenging due to their non-specific presentation and attenuated clinical symptoms, and most diagnoses are made intraoperatively.

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