scholarly journals Congenital Complete Atrioventricular Heart Block in a Pregnant Woman with Sjögren Syndrome: Prenatal Care Follow-Up and the Challenge of Intrauterine Treatment

Author(s):  
Milene Carvalho Carrilho ◽  
Nathalie Jeanne Bravo-Valenzuela ◽  
Edward Araujo Júnior

AbstractThe present report describes a case of complete atrioventricular block (CAVB) diagnosed at 25 weeks of gestation in a pregnant woman with Sjögren's syndrome and positive anti-Ro/SSA antibodies. Fluorinated steroids (dexamethasone and betamethasone) and terbuline were used to increase the fetal heart rate, but the fetal heart block was not reversible, and the administration of drugs was discontinued due to maternal collateral effects. Follow-up fetal echocardiograms were performed, and the fetus evolved with pericardial effusion, presence of fibroelastosis in the right ventricle, and ventricular dysfunction. Interruption of pregnancy by cesarean section was indicated at 34 weeks of gestation, and a cardiac pacemaker was implanted in the male newborn immediately after birth. Therapy for fetuses with CAVB is controversial mainly regarding the use or not of corticosteroids; however, monitoring of the atrioventricular interval by fetal echocardiography should be performed in fetuses from pregnant women with positive autoantibodies anti-Ro/SSA and/or anti-La/SSB to prevent the progression to CAVB.

2019 ◽  
Vol 12 (4) ◽  
pp. e228642
Author(s):  
Rayan Hejazi ◽  
Marwan Balubaid ◽  
Jameel Alata ◽  
Rahaf Waggass

Tetralogy of Fallot (TOF) is the most common form of cyanotic congenital heart disease beyond the age of 3 months. Complete heart block (CHB) is rare but a serious sequalae post-repair of TOF. We present a case of an 18-month-old child who developed late CHB after around 1 year of the corrective surgery of the congenital anomaly. On the regular follow-up visit, the patient assessment was unremarkable. However, there was bradycardia, 55 beats/min. The ECG showed complete atrioventricular dissociation. Echocardiogram was done and demonstrated severe tricuspid regurgitation (TR). The patient required a permanent pacemaker and he is currently well. We are presenting this case as a late unexpected CHB, with a possibility of progressive right-side dilatation as a contributing factor to CHB due to severe TR.


2005 ◽  
Vol 25 (12) ◽  
pp. 1129-1132 ◽  
Author(s):  
A. Sciarrone ◽  
B. Masturzo ◽  
G. Botta ◽  
S. Bastonero ◽  
M. Campogrande ◽  
...  

Author(s):  
A.V. Makogon , I.V. Andrushina , D.A. Chernova

Objectives. The case of the right ventriclar aneurysm is presented. Pregnancy was terminated due to medical conditions. Autopsy was performed. Materials and Results. On carrying out the fetal ultrasound, a fingerlike protrusion with a wide neck, measuring 4  4 mm, was found in the right ventricular apex. There was pericardial effusion. The aneurysm wall was represented by the ectopic thymus tissue. Conclusions. Aneurysm and diverticulum of the fetal heart are dangerous disorders. The rate of fetal complications during pregnancy is high. The diagnosis of aneurysm/diverticulum may be made in the prenatal period. The prognosis of the survivors significantly differs between patients. Infants with no change in size of aneurysm/diverticulum had a normal development and no adverse events during follow-up. It is important to remember about different aetiology of fetal anomalies.


2020 ◽  
Vol 68 (12) ◽  
pp. 1499-1502
Author(s):  
Chihiro Miyagi ◽  
Yoshie Ochiai ◽  
Yusuke Ando ◽  
Manabu Hisahara ◽  
Hironori Baba ◽  
...  

AbstractAn 8-year-old boy had undergone permanent epicardial pacemaker implantation with a Y-shaped bipolar ventricular lead on day 6 after birth for treatment of congenital complete atrioventricular block. He was found to have pulmonary stenosis and mitral stenosis by follow-up echocardiography. Further studies including computed tomography and cardiac catheterization revealed that the pacemaker lead had completely encircled the cardiac silhouette and was in a state of “cardiac strangulation”. We removed the previous pacing leads and generator and implanted a new epicardial dual-chamber pacing system in the right atrium and right ventricle. Additionally, an expanded polytetrafluoroethylene sheet was placed between the new leads and the heart to prevent recurrence of cardiac strangulation.


2022 ◽  
Vol 16 (1) ◽  
Author(s):  
Isabela Wolf-Grotto ◽  
Lucas M. Nogueira ◽  
Basilio Milani ◽  
Erica C. Marchiori

Abstract Background Osteoma is a benign tumor of the bones, which can be classified as central or peripheral. The occurrence in the jawbones is uncommon, but when it occurs, there is a greater prevalence of the mandible. The etiology is still unknown, and the hypothesis of its development is debated. Case presentation A 35-year-old Caucasian man presenting a tumor lesion in the right jawbone that had been growing for 8 years sought medical service complaining of speaking impairment. According to the patient, the tumor appeared shortly after a minor trauma caused by tooth extraction. The diagnosis of the lesion was made through clinical, radiographic, and histological methods, and the surgical treatment was successful and satisfactory for the patient as well as the surgical team, despite a short follow-up. Conclusion Etiopathogenesis of osteoma is not determined in the majority of cases. In the present report, it was possible to hypothesize the association between a minor trauma and the development of the tumor, reinforcing the reactive theory of tumor development. The uncommon location of the osteoma, as well the possibility of identifying the possible cause of the lesion, makes this case particularly interesting.


Author(s):  
A.V. Makogon , I.V. Andrushina

Objective: сurrently antenatal premature closure (restriction) foramen ovale (RFO) is under recognised. The case of the RFO is analysed. Materials. Pregnant woman E was undergone diagnostic ultrasound at 33 weeks of gestation and monitoring up to delivery (39 weeks). The newborn has been followed up 3 months. Fetal heart was examined in general order and in the bicaval view. ПРЕНАТАЛЬНАЯ ДИАГНОСТИКА Рестриктивное овальное окно 231 как причина увеличения правых отделов сердца 2018 Т 17 № 3; 225-231 Results. Fetal examination revealed cardiomegaly, predominance of the right heart, aneurysm of the interatrial septum, high blood velocity through the foramen ovale channel (67.18 sm/s). The diameter of the aortic isthmus (AI) was 3.4 mm (Z-score — 2.06). We concluded that it was ROO. The conclusion of the echocardiography was coarctation of the aorta (CoA). The diameter of the AI reached 4.6 mm (Z-score — 1.01) up to 39 weeks of gestation. The newborn’s echocardiography is normal. Conclusion. Fetal heart ultrasound examination is important for obstetric management in the third trimester of gestation and follow up the newborn. It is necessary to include the PFO into differential diagnosis of the fetal heart right-sided dominance as the most probable cause and to follow up this fetus to delivery. Normally two-phase blood flow in AI is possible at the end of pregnancy.


2020 ◽  
Vol 44 (6) ◽  
pp. 436-441
Author(s):  
Wei Lu ◽  
Gang-gang Qi ◽  
Xiao-jun Li ◽  
Fu-ming He ◽  
Bo Hong

Background: Plasma cell granuloma (PCG) is a rare benign pseudotumorous proliferation of unclear etiology that is mainly situated in the lungs. Gingival PCG is an even more peculiar lesion that usually occurs in middle-aged or elderly individuals and clinically manifests as a solitary entity. Case report: A 15-year-old male with no underlying medical conditions presented with multiple gingival masses in the right maxilla, which were initially thought to be epulis. The lesions were resected completely and the excisional biopsies sent for histological examination. Immunohistochemical (IHC) stain revealed dense polyclonal plasma cell infiltration with positive expression of both kappa and lambda light chains, confirming a diagnosis of gingival PCG. Subsequently, the affected gingiva healed uneventfully, with no sign of recurrence over 2 years of follow-up. Conclusions: The present report depicts an extremely unusual case of gingival PCG occurring in a juvenile with multiple lesions, which is worth attention in clinical pediatric dentistry. Excisional-biopsy and histological investigations are imperative for a confirmative diagnosis and to exclude potential aggressive conditions. Complete resection of lesions seems to be a valid treatment, while long-term clinical follow-up is still needed.


1999 ◽  
Vol 18 (3) ◽  
pp. 33-42 ◽  
Author(s):  
Lisa Reneé Klassen

Complete congenital heart block (CCHB) is a rare disease of the newborn that carries significant morbidity and mortality. It generally occurs as a result of the presence of maternal autoantibodies that are transferred to the fetus and affect the fetal heart, or it may be associated with a congenital structural abnormality of the heart.Infants with CCHB are at risk for diminished cardiac output and the subsequent development of congestive heart failure. Many infants require the placement of a cardiac pacemaker.It is essential that the nurse caring for these infants have a good understanding of the disease process and be familiar with the unique problems that these infants and their families may encounter.


2021 ◽  
pp. 112067212110547
Author(s):  
Zoi Tsani ◽  
Antonios Ntafos ◽  
Victoria Toumanidou ◽  
Anna Dastiridou ◽  
Ioanna Ploumi ◽  
...  

Purpose To report acute visual acuity loss in a pregnant woman with nephrotic syndrome. Case Report A 34-year-old pregnant woman was referred to our service for acute, bilateral visual impairment, associated with bilateral below knee edema (BKE). Best-corrected visual acuity (BCVA) was hand motion in the right eye and 20/200 in the left eye. Dilated fundus exam disclosed multiple pigment epithelium detachments involving the macula in both eyes. After consultation with a nephrologist a diagnosis of nephrotic syndrome was made. Unfortunately, a week later she lost the fetus. At follow-up evaluation, 20 days after the miscarriage, BCVA improved to 20/25 in both eyes with near normal restoration of the retinal anatomy. Conclusion In nephrotic syndrome, sequestration of interstitial fluids, which leads to classic generalized edema, could be the origin of interstitial accumulation of fluids in the retinal and subretinal layers. Increased awareness by the gynaecologists and prompt treatment may prevent fetus miscarriage.


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