Alveolar soft part sarcoma presenting in an unusual laryngeal location

Alveolar soft part sarcoma (ASPS) is a rare malignant neoplasm that tends to occur in the deep soft tissues of both adults and children. ASPS has a progressive clinical course that is unfortunately characterised by late metastases and an overall poor prognosis. Although the tumour has been reported in a wide range of anatomic sites, few cases of primary laryngeal ASPS are reported in the literature. Here, we report the case of a 24-year-old man with no significant medical history who presented with progressive mild dysphonia and hoarseness. Imaging studies revealed a well-circumscribed, partially cystic submucosal mass with involvement of the right vocal fold and other local structures, and the patient was referred for surgical excision. Morphological and immunohistochemical examination of the excised lesion revealed ASPS. The findings of this case are compared with those of seven additional cases of primary laryngeal ASPS, which were found following literature review.

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Alveolar soft-part sarcoma of the oral cavity: A review of literature

Rare Tumors ◽

10.1177/2036361318810907 ◽

2018 ◽

Vol 10 ◽

pp. 203636131881090 ◽

Cited By ~ 3

Author(s):

Pankaj Shelke ◽

Gargi Sachin Sarode ◽

Sachin Chakradhar Sarode ◽

Rahul Anand ◽

Ghevaram Prajapati ◽

...

Keyword(s):

Soft Tissues ◽

Medical Literature ◽

Soft Part ◽

Case Reports ◽

Correct Diagnosis ◽

Treatment Strategies ◽

Malignant Neoplasm ◽

Alveolar Soft Part Sarcoma ◽

Prognostic Features ◽

English Medical Literature

An alveolar soft-part sarcoma is a malignant neoplasm primarily affecting the soft tissues of head and neck. The aim of the present review is to systematically present the demographic and clinico-pathological data of articles published in the English medical literature. A comprehensive search of the databases (PubMed, Medline, SCOPUS, Web of Science, and Google Scholar) along with cross references to the published articles on alveolar soft-part sarcoma for eligible studies/case reports published since 1957 till date was done to retrieve the data. A total of 74 cases were identified and analyzed from 42 papers published in the English medical literature. All the clinical, radiographic, and prognostic features were analyzed and presented along with the treatment strategies. Alveolar soft-part sarcoma is a rare and aggressive malignancy of uncertain histologic origin with a propensity for vascular invasion and distant metastasis. This neoplasm requires careful clinical, radiographic, and histopathologic evaluation to reach to the correct diagnosis.

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A RARE CASE OF RECURRENT ADENOID CYSTIC CARCINOMA OF THE BUCCAL MUCOSA

10.36106/ijsr/3714486 ◽

2021 ◽

pp. 1-2

Author(s):

Surya Rao Rao Venkata Mahipathy ◽

Alagar Raja Durairaj ◽

Narayanamurthy Sundaramurthy ◽

Anand Prasath Jayachandiran ◽

Suresh Rajendran

Keyword(s):

Adenoid Cystic Carcinoma ◽

Buccal Mucosa ◽

Malignant Neoplasm ◽

Neck Region ◽

Surgical Excision ◽

Minor Salivary Glands ◽

Head And Neck Region ◽

Adenoid Cystic ◽

The Right ◽

Carcinoma Buccal Mucosa

Adenoid cystic carcinoma is a malignant neoplasm most commonly originating in the minor salivary glands of head and neck region. Among intra oral adenoid cystic carcinoma, buccal mucosa is one of the rarer sites. Here, we report a case of recurrent adenoid cystic carcinoma of the right buccal mucosa in a 33 year old female. As this is an uncommon site for adenoid cystic carcinoma, it should be considered as a differential diagnosis of mass of buccal mucosa. It is imperative that we identify such cases and plan for early surgical excision with adequate margins.

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Alveolar soft part sarcoma of the right calf

Medicine ◽

10.1097/md.0000000000018952 ◽

2020 ◽

Vol 99 (5) ◽

pp. e18952

Author(s):

Bin Wang ◽

Huanhuan Wang ◽

Jinlong Wei ◽

Limei Qu ◽

Lingbin Meng ◽

...

Keyword(s):

Soft Part ◽

Alveolar Soft Part Sarcoma ◽

The Right

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Alveolar Soft Part Sarcoma of the Head and Neck Region

Annals of Otology Rhinology & Laryngology ◽

10.1177/000348949810700914 ◽

1998 ◽

Vol 107 (9) ◽

pp. 810-814 ◽

Cited By ~ 40

Author(s):

Brian C. Hunter ◽

Alfio Ferlito ◽

Kenneth O. Devaney ◽

Alessandra Rinaldo

Keyword(s):

Head And Neck ◽

Soft Part ◽

Neck Region ◽

Surgical Excision ◽

Alveolar Soft Part Sarcoma ◽

Malignant Neoplasms ◽

Head And Neck Region ◽

Neck Area ◽

Over Time ◽

Sizable Number

Alveolar soft part sarcoma is a soft tissue malignancy most often found in the extremities of young adults; when these tumors arise in the head and neck area, they usually appear in the orbit or the tongue. Their initial behavior is relatively indolent, but over time a sizable number of these tumors recur locally and metastasize; as such, they are best regarded as fully malignant neoplasms. The derivation of these tumors remains uncertain: while some have suggested that these are tumors of muscle origin and others have postulated a neuroendocrine origin, the evidence accumulated to date is conflicting, and so these neoplasms continue to be regarded as tumors of uncertain origin. Surgical excision is the mainstay of therapy.

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Giant Fibroepithelial Polyp of Vulva: A Case Report and Review of Literature

PRILOZI ◽

10.2478/prilozi-2018-0051 ◽

2018 ◽

Vol 39 (2-3) ◽

pp. 127-130 ◽

Cited By ~ 2

Author(s):

Meral Rexhepi ◽

Elizabeta Trajkovska ◽

Florin Besimi ◽

Nagip Rufati

Keyword(s):

Histopathological Examination ◽

Treatment Options ◽

Polypoid Lesion ◽

Malignant Neoplasm ◽

Reproductive Period ◽

Lower Genital Tract ◽

Wide Range ◽

Fibroepithelial Polyps ◽

The Right ◽

Rule Out

Abstract Fibroepithelial stromal polyps of vulva are the type of mesenchymal lesion that typically occurs in women of reproductive period. They are common, usually small and hystologically benign. Larger lesions are rare and likely arise from proliferation of mesenchymal cells within the hormonally sensitive subepithelial stromal layer of the lower genital tract. We present a case of 16 year old female with a giant polypoid lesion of the vulva localized on the right labium. The mass measure was 18×12×3 cm. Total surgical resection of the lesion was performed. Histopathological examination reported a fibroepithelial stromal polyp of the vulva. The patient showed no evidence of recurrence four years after the resection. Fibroepithelial polyps of the vulvar region are benign lesions that have a wide range of morphologic appearances and may be misinterpreted as malignant. Total excision is the best treatment options and histopathological examination is strongly recommended to rule out a malignant neoplasm.

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Complete Ossification of the Stylohyoid Chain as Cause of Eagle's Syndrome: A Very Rare Case Report

The Journal of Contemporary Dental Practice ◽

10.5005/jp-journals-10024-1569 ◽

2014 ◽

Vol 15 (4) ◽

pp. 500-505 ◽

Cited By ~ 1

Author(s):

Antônio Sérgio Guimarães ◽

Daniel Humberto Pozza ◽

Idercy Cabral de Castro ◽

Iván Claudio Suazo Galdames ◽

Sandro Palla

Keyword(s):

Case Report ◽

Rare Case ◽

Soft Tissues ◽

Surgical Excision ◽

Styloid Process ◽

Eagle’S Syndrome ◽

Elongated Styloid Process ◽

Rare Case Report ◽

The Right ◽

Stylohyoid Chain

ABSTRACT Aim To report on a patient with Eagle's syndrome with a complete and very large ossification of the stylohyoid complex on the right side that to our best knowledge has never been published previously. Background Eagle's syndrome is characterized by a set of symptoms that are caused by the irritation of the neurovascular and soft-tissues caused by an elongated styloid process or ossification of stylohyoid ligament. Case description Because of the high discomfort and pain degree as well as limitations of mandibular and head mobility and also the thickness of the ossified stylohyoid chain, the patient was treated surgically by removing the hypertrophic segment. Conclusion These symptoms subsided completely after the surgical excision of the anomaly. The elongated styloid process on the left side was symptom free. Clinical significance Eagle's syndrome symptoms are not specific and can mimic those of other disorders, the syndrome must be included in the differential diagnosis of patients with pain in the orofacial, pharyngeal and cervical area. How to cite this article Guimarães AS, Pozza DH, de Castro IC, Galdames ICS, Palla S. Complete Ossification of the Stylohyoid Chain as Cause of Eagle's Syndrome: A Very Rare Case Report. J Contemp Dent Pract 2014;15(4):500-505.

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Alveolar soft part sarcoma of extremity

International Journal of Research in Medical Sciences ◽

10.18203/2320-6012.ijrms20204263 ◽

2020 ◽

Vol 8 (10) ◽

pp. 3735

Author(s):

Shilpa Kaushal ◽

Muninder K. Negi

Keyword(s):

Vascular Invasion ◽

Soft Part ◽

External Beam Radiotherapy ◽

Distant Metastases ◽

Surgical Excision ◽

Alveolar Soft Part Sarcoma ◽

High Likelihood ◽

Histopathological Feature ◽

History Of ◽

Slow Growing

Alveolar soft-part sarcoma (ASPS) is an extremely rare connective tissue tumor, predominantly seen in adolescents and young adults, with a female preponderance. Alveolar soft-part sarcoma (ASPS) is a slow growing tumor, but with high likelihood of metastasis, leading to high mortality. A classical histopathological feature of an alveolar pattern from the biopsy of the lesion favors the diagnosis. We report a case of 14 years old male patient who presented with a history of single painless swelling over thigh for which surgical excision was done. Histopathology was suggestive of Alveolar soft-part sarcoma (ASPS). There was no evidence of distant metastases. He was treated with external beam radiotherapy in view of vascular invasion.

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Blue rubber bleb nevus syndrome: A rare cause of chronic gastro intestinal bleed in children

Indian Journal of Child Health ◽

10.32677/ijch.v8i10.3088 ◽

2021 ◽

Vol 8 (10) ◽

pp. 374-376

Author(s):

Sufla Saxena ◽

Himanshu Batra ◽

Vikas Taneja

Keyword(s):

Soft Tissues ◽

Argon Plasma Coagulation ◽

Argon Plasma ◽

Surgical Excision ◽

Uneventful Recovery ◽

Gi Tract ◽

Plasma Coagulation ◽

Rare Congenital Disorder ◽

Wide Range ◽

Lower Gi Bleeding

Blue rubber bleb nevus syndrome (BRBNS) is a rare congenital disorder presenting with multifocal venous malformations of the skin, soft tissues, and gastrointestinal (GI) tract. Here, we report a case of a 10-year-old girl who presented with recurrent lower GI bleeding and abdominal pain requiring repeated blood transfusion for 2 years. A contrast computed tomography showed multiple cavernous haemangiomas in the liver, oesophagogastroduodenoscopy and colonoscopy showed multiple hemangiomas from esophagus to large bowel. Her molecular pathology confirmed BRBNS. She underwent endoscopic argon plasma coagulation with uneventful recovery. In spite of a wide range of therapeutic options for the management of BRBNS described in the literature, the efficacy of those available therapies, including surgical excision, is not well established.

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Alveolar soft part sarcoma of the tongue

The Journal of Laryngology & Otology ◽

10.1017/s002221510011059x ◽

1989 ◽

Vol 103 (10) ◽

pp. 952-954 ◽

Cited By ~ 20

Author(s):

F. Cetik ◽

C. Ozsahinoglu ◽

F. Kivanc ◽

E. Secinti

Keyword(s):

Soft Part ◽

Neck Region ◽

Unknown Origin ◽

Surgical Excision ◽

The Body ◽

Alveolar Soft Part Sarcoma ◽

Pathological Features ◽

Head And Neck Region ◽

The Past ◽

Clinical And Pathological Features

AbstractIn this report a 13-year-old girl with characteristic clinical and pathological features of alveolar soft part sarcoma of the tongue is presented. Alveolar soft part sarcoma is a rare malignant tumor of unknown origin. Forty eight cases of alveolar soft part sarcoma have so far been reported in the head and neck region. Median survival reported for all sites of the body is 79 months following various modes of therapy. In this case, the treatment was surgical excision of the mass combined with radiotherapy and chemotherapy. The patient has been asymptomatic for the past 12 months.

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