scholarly journals Splenogonadal fusion: a case report and review of the literature

BMC Urology ◽  
2021 ◽  
Vol 21 (1) ◽  
Author(s):  
Guangjie Chen ◽  
Xiaohao Wang ◽  
Yijun Zhao ◽  
Linfeng Zhu ◽  
Daxing Tang
Keyword(s):  
Congenital Anomaly ◽  
Abdominal Cavity ◽  
Young Patients ◽  
Single Stage ◽  
Two Stage ◽  
Splenogonadal Fusion ◽  
Rare Congenital Anomaly ◽  
Left And Right ◽  
The Right ◽  
Stage 1

Abstract Background Splenogondal fusion (SGF) is a rare congenital anomaly characterized by abnormal association between the splenic tissue and the gonads or mesonephric remnants. SGF that requires separate two-stage laparoscopic staged Fowler-Stephen orchiopexy on both the left and right sides is extremely rare. SGF could be misdiagnosed as testicular malignancy and leads to unnecessary orchiectomy. Case presentation This is a case of an 8-month old male infant presented with bilateral cryptorchidism, B-mode ultrasound visualized the left and right testes in the lower abdominal cavity and the upper margin of the left testicle as a hypoechoic mass extending to the spleen, indicating an undescended right testis and possible SGF on the left side. Single-site laparoscopic examination confirmed the diagnosis of SGF on the left side and an undescended right testis. As both testes were high and the right spermatic vessel was poorly developed and short, a routine single stage orchiopexy would be difficult and risky, therefore, separate two-stage laparoscopic staged Fowler-Stephen orchiopexies for both sides were implemented. Stage 1 of the staged Fowler-Stephen orchiopexy for the right side was performed first without treating the left side, Stage 2 for the right side, separation of the left testis from the spleen as well as Stage 1 for the left side were performed 7 months later, and Stage 2 for the left side was performed 7 months after that. Follow-up ultrasound 1 year after the surgery revealed no obvious abnormalities in the shapes of the testes or their blood supply. This treatment strategy prevented unnecessary orchiectomy. Conclusions We reported a rare case of SGF that needed separate two-stage laparoscopic staged Fowler-Stephen orchiopexies for both sides, and a review of the recent literature. SGF is a rare congenital anomaly often diagnosed incidentally during exploration/surgery for scrotal swelling/mass, cryptorchidism or inguinal hernia in young patients. Surgeons, especially pediatric surgeons should be aware of this rare condition to avoid unnecessary, life-altering radical orchiectomy. When routine single stage orchiopexy is not feasible or risky for either side, separate two-stage laparoscopic staged Fowler-Stephen orchiopexies could be performed on both the left and right sides to avoid unnecessary orchiectomy.

Splenogonadal Fusion: A Rare Congenital Anomaly in Children

BJUI ◽  
2012 ◽  
Author(s):  
Osman Zeki Karakus ◽  
Mustafa Ozcetin ◽  
Fikret Erdemir
Keyword(s):  
Congenital Anomaly ◽  
Splenogonadal Fusion ◽  
Rare Congenital Anomaly

scholarly journals Partial anomalous pulmonary venous connection detected during right pneumonectomy

2019 ◽  
Vol 30 (3) ◽  
pp. 497-498
Author(s):  
Bülent Mustafa Yenigün ◽  
Gökhan Kocaman ◽  
Ayşegül Gürsoy Çoruh ◽  
Rıfat Murat Akal
Keyword(s):  
Lung Cancer ◽  
Congenital Anomaly ◽  
Case Report ◽  
Surgical Treatment ◽  
Septal Defect ◽  
Lung Resection ◽  
Rare Congenital Anomaly ◽  
The Right ◽  
Anomalous Pulmonary Venous Connection ◽  
Lung Resections

Abstract Partial anomalous pulmonary venous connection (PAPVC) is a rare congenital anomaly. Generally, it is seen on the right side and is associated with an atrial septal defect. Herein, we present a case of a 50-year-old male patient with a supracardiac type PAPVC detected during pneumonectomy for a right hilar mass. This is the second case report in the literature presenting surgical treatment of both lung cancer and PAPVC using pneumonectomy. Thoracic surgeons should be aware of this anomaly when they are planning to perform a major lung resection. If PAPVC and lung cancer are in the same lobe, anatomical lung resections including pneumonectomy can be safely performed.

scholarly journals Swing-back and trap-door technique repair for interrupted aortic arch with right-sided descending aorta

2019 ◽  
Vol 29 (5) ◽  
pp. 818-819
Author(s):  
Shuichi Shiraishi ◽  
Ai Sugimoto ◽  
Masanori Tsuchida
Keyword(s):  
Congenital Anomaly ◽  
Aortic Arch ◽  
Surgical Repair ◽  
Interrupted Aortic Arch ◽  
Thoracic Cavity ◽  
Descending Aorta ◽  
Rare Congenital Anomaly ◽  
Trap Door ◽  
Oesophageal Obstruction ◽  
The Right

Abstract A right-sided descending aorta with a left aortic arch is a rare congenital anomaly in which the aortic arch crosses the midline from the left side of the trachea coursing to the descending aorta in the right thoracic cavity. The surgical repair of an interrupted aortic arch with a right-sided descending aorta carries great risks of bronchial and oesophageal obstruction. Herein, we describe a case of successful surgical repair of an interrupted aortic arch with a right-sided descending aorta using the swing-back and trap-door techniques.

On the Performance of a Two-Stage Vibration Isolation System Which has Geometrically Nonlinear Stiffness

2014 ◽  
Vol 136 (6) ◽  
Author(s):  
Zeqi Lu ◽  
Tiejun Yang ◽  
Michael J. Brennan ◽  
Xinhui Li ◽  
Zhigang Liu
Keyword(s):  
Resonance Frequency ◽  
Vibration Isolation ◽  
Low Frequency ◽  
Single Stage ◽  
Nonlinear Stiffness ◽  
Two Stage ◽  
Isolation System ◽  
Beneficial Effects ◽  
Isolation Systems ◽  
The Right

Linear single-stage vibration isolation systems have a limitation on their performance, which can be overcome passively by using linear two-stage isolations systems. It has been demonstrated by several researchers that linear single-stage isolation systems can be improved upon by using nonlinear stiffness elements, especially for low-frequency vibrations. In this paper, an investigation is conducted into whether the same improvements can be made to a linear two-stage isolation system using the same methodology for both force and base excitation. The benefits of incorporating geometric stiffness nonlinearity in both upper and lower stages are studied. It is found that there are beneficial effects of using nonlinearity in the stiffness in both stages for both types of excitation. Further, it is found that this nonlinearity causes the transmissibility at the lower resonance frequency to bend to the right, but the transmissibility at the higher resonance frequency is not affected in the same way. Generally, it is found that a nonlinear two-stage system has superior isolation performance compared to that of a linear two-stage isolator.

scholarly journals Urethral Duplication with Two Hypospadic Meati—An Unusual Variant

2016 ◽  
Vol 04 (01) ◽  
pp. 037-040 ◽  
Author(s):  
Joseph Davidson ◽  
Naomi Wright ◽  
Massimo Garriboli
Keyword(s):  
Congenital Anomaly ◽  
Male Infant ◽  
Single Stage ◽  
Type Ii ◽  
Urethral Duplication ◽  
Unique Case ◽  
Rare Congenital Anomaly ◽  
Unusual Variant ◽  
Proximal Urethra

AbstractDuplication of the urethra is a rare congenital anomaly, with approximately 300 cases reported in the literature. We report a unique case of this condition in a male infant. This case differs from the classical Effman type II-A2 duplication because of the presence of two hypospadic urethral meati, as opposed to a ventral or dorsal accessory meatus with a normally positioned distal urethra. The patient underwent a single-stage repair consisting of a proximal urethra-urethral anastomosis and distal urethral tubularization at 21 months of age with excellent results in terms of both function and cosmesis.

scholarly journals The Ruptured Pericardial Cyst to the Right Atrium: A Case Report

2020 ◽  
Author(s):  
Freidoun SABZI ◽  
Reza FARAJI
Keyword(s):  
Congenital Anomaly ◽  
Case Report ◽  
Chest Pain ◽  
Right Atrium ◽  
Imaging Modality ◽  
Physical Exam ◽  
Right Atrial ◽  
Rare Congenital Anomaly ◽  
Pericardial Cysts ◽  
The Right

The pericardial cysts (PC) are rare congenital anomaly. They are usually asymptomatic or incidentally found during surgery or by an imaging modality. We report a 35-yr-old man referred to Imam Ali Hospital, Kermanshah, western Iran in 2017, with palpitation, chest pain and dyspnea and physical exam revealed sign and symptoms of right atrial compression and tamponade.

scholarly journals Solitary coronary artery: An unusual cause of atypical chest pain

2019 ◽  
Vol 16 (1) ◽  
pp. 55-56
Author(s):  
Laxman Dubey ◽  
Ridhi Adhikari ◽  
Suresh Deep
Keyword(s):  
Computed Tomography ◽  
Congenital Anomaly ◽  
Chest Pain ◽  
Coronary Artery ◽  
Coronary Angiography ◽  
Coronary Sinus ◽  
Sinus Of Valsalva ◽  
Atypical Chest Pain ◽  
Rare Congenital Anomaly ◽  
The Right

Coronary arteries arising from single coronary sinus is a rare congenital anomaly. We report a 30-year-old male who presented with atypical chest pain and computed tomography coronary angiography revealed a solitary coronary artery originating from a single ostium in the right sinus of Valsalva. 

scholarly journals Prosthetic management 56 years after rotationplasty due to proximal femoral focal deficiency (PFFD)

2007 ◽  
Vol 31 (3) ◽  
pp. 313-320 ◽  
Author(s):  
N. Roux ◽  
S. Pieters
Keyword(s):  
Congenital Anomaly ◽  
Reconstructive Procedure ◽  
Rare Congenital Anomaly ◽  
Level Of Functioning ◽  
Prosthetic Fitting ◽  
Proximal Femoral Focal Deficiency ◽  
The Right ◽  
Made In

Proximal femoral focal deficiency (PFFD) is a rare congenital anomaly of the femur. Rotationplasty has been described as a reconstructive procedure in the management of PFFD. A 68-year-old woman with PFFD of the right leg and rotationplasty at the age of 12 years had prosthetic fitting problems after a fall. The authors describe the analysis of the prosthetic fitting problems and the considerations made in prosthetic management. Following a fall, 56 years after rotationplasty, this woman has a good prosthetic fitting and a satisfying level of functioning.

scholarly journals Proboscis Lateralis with Rhinosinusitis

2017 ◽  
Vol 32 (1) ◽  
pp. 41-43
Author(s):  
Laurence Michael N. Vera Cruz ◽  
Gil M. Vicente
Keyword(s):  
Congenital Anomaly ◽  
Obstructive Sleep Apnea ◽  
Sleep Apnea ◽  
Paranasal Sinuses ◽  
Multidisciplinary Approach ◽  
Sinus Surgery ◽  
Rare Congenital Anomaly ◽  
Obstructive Sleep ◽  
The Right ◽  
Proboscis Lateralis

Objective: This report aims to describe unique manifestations of proboscis lateralis and highlight the importance of a multidisciplinary approach to address the problems that arise from this rare congenital anomaly. Methods: Study Design:            Case Report Setting:                       Tertiary Government Hospital Patient:                      One Results: A 13 year-old girl diagnosed with proboscis lateralis presented with a trunk-like appendage projecting from the surface of the right supramedial canthal area. She also had clear nasal discharge, nasal congestion, mouth-breathing, and snoring since birth. Paranasal Sinus (PNS) CT scan with 3D reconstruction showed agenesis of the right paranasal sinuses, and expansile aeration of the left paranasal sinuses. Due to her condition, the drainage system of the paranasal sinuses was obstructed, causing chronic rhinosinusitis (CRS). This hindered plans for reconstructive surgery despite medical management, hence the patient underwent Endoscopic Sinus Surgery (ESS). Conclusion: Proboscis lateralis is a rare congenital anomaly that results in aesthetic problems as well as airway concerns, such as rhinosinusitis and obstructive sleep apnea syndrome (OSAS). Management entails a multidisciplinary approach to address functional and aesthetic problems of the patient. Keywords: proboscis lateralis, chronic rhinosinusitis, obstructive sleep apnea, endoscopic sinus surgery, multidisciplinary approach, plastic surgery, reconstructive surgery

Coexistence of transvers testicular ectopia and incarcerated inguinal hernia: A rare case report

2020 ◽  
Author(s):  
Ahmet Hikmet Şahin
Keyword(s):  
Congenital Anomaly ◽  
Inguinal Hernia ◽  
Rare Case ◽  
Incarcerated Inguinal Hernia ◽  
Rare Congenital Anomaly ◽  
Transverse Testicular Ectopia ◽  
Rare Case Report ◽  
The Mean ◽  
The Right ◽  
Testicular Ectopia

Transverse testicular ectopia is a rare congenital anomaly in which both testes are located in the same hemiscrotum or inguinal region. The mean age at presentation was reported as 4 years. It is more common on the right side. We here report a case with incarcerated inguinal hernia and transverse testicular ectopia. The most important points in the diagnosis of transverse testicular ectopia are to be aware of this infrequent malformation and performing genitourinary examination of male newborns.

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