Cochlear implantation of a deaf blind patient with mitochondrial cytopathy

1999 ◽  
Vol 113 (4) ◽  
pp. 353-354 ◽  
Author(s):  
Helen E. Cullington
Keyword(s):  
Quality Of Life ◽  
Mitochondrial Dna ◽  
Case Report ◽  
Cochlear Implant ◽  
Cochlear Implantation ◽  
The Body ◽  
Genetic Defects ◽  
Mitochondrial Cytopathy ◽  
Sensorineural Hearing Impairment

AbstractGenetic defects of the mitochondrial DNA often cause sensorineural hearing impairment, accompaniment by disorders of organs within the body. This case report describes cochlear implantation of a 33-year-old deaf blind female with mitochondrial cytopathy. The outcome was very successful, and vastly improved quality of life for this patient. Many cases of mitochondrial cytopathy cause progressive deafness; it is, therefore, likely that other patients with this unusual disorder will present for cochlear implant assessment.

scholarly journals A Cochlearis Implantáltak Funkcionális Indexe (CIFI) magyarországi bevezetésével szerzett kezdeti tapasztalatok

2019 ◽  
Vol 160 (33) ◽  
pp. 1296-1303
Author(s):  
Gréta Bodzai ◽  
Márton Kovács ◽  
János Uzsaly ◽  
Kinga Harmat ◽  
Adrienn Németh ◽  
...  
Keyword(s):  
Quality Of Life ◽  
Cochlear Implant ◽  
Cochlear Implantation ◽  
Social State ◽  
Remarkable Improvement ◽  
Quality Of Life Questionnaires ◽  
Function Index

Abstract: Introduction: The success of cochlear implantation can be evaluated with audiological measurements and quality of life questionnaires. Aim: Our aim was to translate and introduce the Cochlear Implant Function Index (CIFI) test to analyze the physical, psychological and social state of our cochlear implant patients. Method: Between 01. 11. 2016 and 31. 05. 2018, 30 patients filled the questionnaire before and 6 and 12 months after the implantation. Results and conclusion: Results showed a remarkable improvement in the quality of life in several patients even after 6 months. Further improvements could be measured after 12 months. Orv Hetil. 2019; 160(33): 1296–1303.

scholarly journals Multicentre cohort study of cochlear implantation outcomes in Thailand

BMJ Open ◽  
2021 ◽  
Vol 11 (11) ◽  
pp. e054041
Author(s):  
Patorn Piromchai ◽  
Napas Tanamai ◽  
Sivaporn Kiatthanabumrung ◽  
Suwicha Kaewsiri ◽  
Kanthong Thongyai ◽  
...  
Keyword(s):  
Quality Of Life ◽  
Cohort Study ◽  
Cochlear Implant ◽  
Cochlear Implantation ◽  
Secondary Outcome ◽  
University Hospitals ◽  
Implant Surgery ◽  
Cochlear Implant Surgery ◽  
The Mean

ObjectivesTo report the status and outcomes of cochlear implantation in Thailand.DesignCohort study.SettingTertiary care and university hospitals.ParticipantsPatients who underwent cochlear implant surgery in Thailand.InterventionsThis project collected data from all government and university hospitals in Thailand where cochlear implant surgery was performed between 2016 and 2020.Primary and secondary outcome measuresBaseline characteristics, operation data, complications, audiological outcomes and quality of life were reported.ResultsThis study included 458 patients, and nearly half of the patients were children and adolescents (46.94%). The mean age of the patients was 2.96±5.83 years. At 1 year postoperatively, the mean pure tone average of the hearing threshold in the implanted ear significantly improved from unaided preoperative baseline (mean difference (MD) 64.23 dB HL; 95% CI 59.81 to 68.65; p<0.001). The mean speech recognition threshold also improved (MD 55.96 dB HL; 95% CI 49.50 to 62.42, p<0.001). The quality-of-life scores of the EQ-5D-5L, PedsQL and HUI3 questionnaires at 1 year showed improved mobility (range, 0–5; MD 0.65; 95% CI 0.05 to 1.25; p=0.037), hearing (range, 0–6; MD 0.96; 95% CI 0.30 to 1.61; p=0.006) and speech (range, 0–5; MD 0.44; 95% CI 0.04 to 0.84; p=0.031). Common complications included electrode dislodgement (2.18%), vertigo (1.23%) and meningitis (1.93%).ConclusionsExcellent audiological outcomes and improvement in the quality of life in the mobility, hearing and speech domains were observed in patients who underwent cochlear implantation in Thailand.

Quality of Life after Sequential Bilateral Cochlear Implantation: An Updated Comprehensive Cochlear Implant Questionnaire

2016 ◽  
Vol 156 (2) ◽  
pp. 334-340 ◽  
Author(s):  
Edmund A. Nahm ◽  
Penny Liberatos ◽  
Qiuhu Shi ◽  
Erica Lai ◽  
Ana H. Kim
Keyword(s):  
Quality Of Life ◽  
Cochlear Implant ◽  
Cochlear Implantation

Delayed cochlear implantation after surgical labyrinthectomy

2011 ◽  
Vol 126 (1) ◽  
pp. 63-65 ◽  
Author(s):  
H A Osborn ◽  
R Yeung ◽  
V Y W Lin
Keyword(s):  
Quality Of Life ◽  
Case Report ◽  
Time Delay ◽  
Treatment Option ◽  
Cochlear Implantation ◽  
Significant Delay ◽  
Cochlear Ossification ◽  
Viable Treatment

AbstractBackground:Cochlear implantation has been used to rehabilitate profoundly deafened adults for more than 25 years. However, surgical labyrinthectomy is often considered a contraindication to cochlear implantation, especially if there is a significant delay between the two procedures. As the role of cochlear implantation continues to expand, this idea requires reconsideration.Case report:A 59-year-old woman presented to our clinic after undergoing bilateral surgical labyrinthectomies for intractable Ménière's disease 21 years prior. Despite the significant time delay, she underwent cochlear implantation with a good audiological outcome and improved quality of life.Conclusion:Changes to the cochlea and vestibule following surgical labyrinthectomy include cochlear ossification and obliteration of the vestibule. These issues have been thought to limit the potential for cochlear implantation, especially when there is a significant delay between the two procedures. However, delayed cochlear implantation, even decades after labyrinthectomy, remains a viable treatment option which can benefit selected patients.

Self-Determination Calibration for Cochlear Implant Rehabilitation

2019 ◽  
pp. 121-154
Author(s):  
Dionysios Politis ◽  
Sophia Aidona ◽  
Petros Stagiopoulos ◽  
Georgios Kyriafinis ◽  
Jannis Constantinidis
Keyword(s):  
Quality Of Life ◽  
Cochlear Implant ◽  
Cochlear Implantation ◽  
Cognitive Skills ◽  
Therapeutic Approach ◽  
Medical Intervention ◽  
Hearing Impaired ◽  
Self Determination

Cochlear implantation is a well-established therapeutic approach for deaf or hearing-impaired patients. After the medical intervention, which aims to restore hearing, subjects undergo rehabilitation procedures in order to cure instructional disadvantages, problematic schooling circumstances, or deficits in their sociability. Essential physical, mental, social, and cognitive skills are taken into perspective, as the prerequisite of a notable aptitude determines the suitability of a subject to get professional and communal roles. Quality of life, as an indicator, provides the metrics that demonstrate the level of adoption with established norms.

Postlingually Deaf Adults of All Ages Derive Equal Benefits from Unilateral Multichannel Cochlear Implant

2011 ◽  
Vol 22 (10) ◽  
pp. 637-643 ◽  
Author(s):  
Edward Park ◽  
David B. Shipp ◽  
Joseph M. Chen ◽  
Julian M. Nedzelski ◽  
Vincent Y.W. Lin
Keyword(s):  
Quality Of Life ◽  
Speech Recognition ◽  
Cochlear Implant ◽  
Hearing Aids ◽  
Cochlear Implantation ◽  
Hearing Aid ◽  
Age Groups ◽  
Perceived Quality Of Life ◽  
Deaf Adults

Background: Controversy still exists regarding the impact of age on speech recognition following cochlear implant in postlingually deaf adults. In some studies elderly recipients did not perform as well as younger patients on standard speech recognition tests. Furthermore, previous studies have shown that cochlear implantation improves quality of life, as measured by self-administered questionnaires, but the sample sizes of these studies have been relatively small, thus making age stratification a challenge. Purpose: The primary objective was to assess whether the age at which a patient receives a unilateral cochlear implant affects improvements in speech recognition scores and perceived quality of life. A secondary objective was to determine whether preoperative use of hearing aids correlates with improvement in speech recognition and perceived quality of life after cochlear implantation. Research Design: A retrospective study in a tertiary referral center. Patients: A total of 161 postlingually deaf adults, who were divided based on age (<50, 50–65, >65) and on prior hearing aid(s) use. Intervention: All patients received a unilateral multichannel cochlear implant. Data Collection and Analysis: Speech recognition was quantified by percent correct scores on the Hearing in Noise Test sentences delivered in a quiet setting only (HINT%), and quality of life was quantified by the Hearing Handicap Inventory (HHI) before and 1 yr after cochlear implantation. Results: Speech recognition, as measured by HINT%, improved significantly and to similar extents in all three age groups following cochlear implantation. Similarly, quality of life as quantified by HHI improved markedly and to similar extents in all age groups. Whether hearing aids were used pre-implant, or whether the cochlear implant (CI) was implanted on the same side or contralateral to the hearing aid side, had no substantial effect on the patients’ performances on either speech recognition or quality of life. Moreover, there were no statistically significant correlations between pre-implant speech recognition scores and pre-implant quality of life scores or between postimplant speech recognition scores and postimplant quality of life scores. Conclusion: The findings of the present study demonstrate that cochlear implantation improves HINT% and HHI scores to similar extents across all age groups. This finding suggests that elderly patients may derive speech recognition and quality of life benefits similar to those of younger patients and that age should not be an essential factor in the determination of CI candidacy. Furthermore, prior use of a hearing aid, and its location in relation to the cochlear implant, does not influence the extent of improvement in speech recognition or quality of life measurements following cochlear implantation.

Remission of Refractory Benign Familial Chronic Pemphigus (Hailey-Hailey Disease) with the Addition of Systemic Cyclosporine

2015 ◽  
Vol 19 (2) ◽  
pp. 163-166 ◽  
Author(s):  
Sowmya Varada ◽  
Marigdalia K. Ramirez-Fort ◽  
Yahya Argobi ◽  
A. David Simkin
Keyword(s):  
Quality Of Life ◽  
Case Report ◽  
Mechanism Of Action ◽  
Autosomal Dominant ◽  
Skin Lesions ◽  
Mechanisms Of Action ◽  
The Body ◽  
Lateral Neck ◽  
First Line

Background Benign chronic familial pemphigus (BFCP) is an autosomal dominant dermatosis characterized by flares of painful and often debilitating blistering lesions in high friction areas of the body such as the groin, axillae, lateral neck, and intergluteal cleft. Limited knowledge of its pathophysiology has made treatment of BFCP a considerable challenge and efficacy with current first line therapies, topical corticosteroids and antibiotics, is variable. Case Report We present a case of this disease in a 52 year old woman that has responded dramatically to the addition of oral cyclosporine to her existing regimen of oral acitretin, with significant improvement of skin lesions, mobility, and quality of life. Cyclosporine's mechanism of action in BFCP is poorly understood, although it possibly acts through inhibition of proinflammatory cytokines in keratinocytes or modulation of intracellular calcium. BFCP, the use of cyclosporine for its treatment, and possible mechanisms of action of cyclosporine are reviewed.

scholarly journals Prospective study on health-related quality of life in patients before and after cochlear implantation

2021 ◽  
Author(s):  
Michaela Plath ◽  
Theresa Marienfeld ◽  
Matthias Sand ◽  
Philipp S. van de Weyer ◽  
Mark Praetorius ◽  
...  
Keyword(s):  
Quality Of Life ◽  
Cochlear Implant ◽  
Cochlear Implantation ◽  
Hearing Impaired ◽  
Health Related Quality ◽  
Before And After ◽  
Related Quality ◽  
Health Related ◽  
Over Time

Abstract Purpose Assessing cochlear implant (CI)-associated patient outcomes is a focus of implant research. Most studies have analyzed outcomes retrospectively with low patient numbers and few measurement time points. In addition, standardized CI-specific health-related quality of life (HRQoL) instruments have not been used. To address this, we prospectively assessed HRQoL in patients before and after implantation. Methods We assessed HRQoL using the Nijmegen Cochlear Implant Questionnaire (NCIQ), Abbreviated Profile of Hearing Aid Benefit (APHAB), Hearing Participation Scale (HPS), and the Visual Analogue Scale (VAS) in 100 deaf or severely hearing-impaired patients (57 unilaterally deaf and 43 bilaterally deaf) before and 3, 6, and 12 months after cochlear implantation. We compared the results of unilaterally and bilaterally hearing-impaired patients and patients with or without a hearing aid. Principal component (PCA) and exploratory factor analyses (EFA) were also conducted. Results The NCIQ measured improvements in all 6 domains after CI and correlated well with other QoL instruments. The PCA revealed that the NCIQ can be better explained by physical, physical advanced, and socio-psychological components. The APHAB score ameliorated over time, except for the background noise domain. The overall HPS score improved over time, but the hearing handicap subscore significantly decreased. Sociodemographic influences on the questionnaire scores were relatively weak. Conclusion Assessing HRQoL is essential for quantifying the patient outcome after CI. NCIQ scores in our patient cohort showed improved HRQoL in all domains and we recommend that the NCIQ be used as a first-line questionnaire for assessing QoL in hearing-impaired patients after CI.

scholarly journals Sense of taste in patients after cochlear implantation-preliminary study

2021 ◽  
Vol 21 (4) ◽  
pp. 1801-7
Author(s):  
Piotr H Skarzynski ◽  
Marcin Wojciechowski ◽  
Magdalena B Skarzynska ◽  
Piotr Fronczak
Keyword(s):  
Quality Of Life ◽  
Cochlear Implant ◽  
Cochlear Implantation ◽  
Well Being ◽  
Weak Correlation ◽  
Entire Study ◽  
Cochlear Implant Surgery ◽  
Taste Disorders ◽  
Preliminary Study

Background: Taste is the leading sense in how we determine the quality of consumed food. Proper gustatory sensation largely determines the well-being and health of an organism, and this affects their quality of life.Objectives: The aim of the present study was to estimate the risk of early taste disorders following implantation surgery. Methods: Twenty patients underwent a taste test before, 1 day after, and 1 month after cochlear implantation. The taste sensations of sweet, sour, salty, and bitter were determined. Results: Statistical analysis showed no significant differences (p > 0.05) between individual tests among the entire study group. After dividing the respondents into smoking (n=6) and non-smoking (n=14) groups, only a weak correlation (p =0.043) was found between the results of the first and second examination in the smoker group. However, a statistically significant decrease in the number of saline-sensitive (p<0.001) and acid-sensitive (p = 0.042) subjects was observed. Conclusion: These findings suggest that people after a cochlear implant may have transient taste disorders. Taste disorder called dysgeusia may be an early complication after the implantation procedure contributing to deterioration of patients quality of life. Keywords: Sense of taste; taste disorders; cochlear implant surgery; quality of life, partial deafness treatment.

scholarly journals Qualidade de vida de pacientes deficientes auditivos adultos pré e pós-linguais usuários de implante coclear / Quality of life for adult patients of pre-lingual and post-lingual deafness cochlear implantation users

2020 ◽  
Vol 65 (1) ◽  
pp. 1
Author(s):  
Thais Rodrigues Talarico ◽  
Cilmara Cristina Alves Costa Levy ◽  
Carmen Lucia Penteado Lancellotti
Keyword(s):  
Quality Of Life ◽  
Hearing Loss ◽  
Cochlear Implant ◽  
Cochlear Implants ◽  
Cochlear Implantation ◽  
Sickness Impact Profile ◽  
Patient Records ◽  
Hearing Impairments ◽  
Assess Quality

Objetivo: Avaliar a qualidade de vida (QV) de pacientes adultos com deficiência auditiva pré e pós-lingual usuários de implante coclear (IC). Método: Os pacientes entrevistados foram adultos implantados de 2004 a 2011 no Departamento de Otorrinolaringologia. Eles responderam ao questionário WHOQoL–BREF e, pela analise dos prontuários, foram identificados como pré ou pós-linguais. Desses pacientes, 17 eram pós-linguais e 8 pré-linguais. Resultados: Verificou-se que, no questionário geral, os participantes pré-linguais apresentaram resultado (escore = 77,4) e os pós-linguais, (escore = 76,3). Os melhores resultados foram os dos domínios físico e psicológico, tanto entre os pacientes pré quanto entre os pós-linguais. Conclusões: Podemos constatar que os pacientes pré-linguais apresentam um resultado pouco melhor que os pós-linguais na pontuação total do questionário, mas a análise dos benefícios do IC nos demais domínios mostrou resultados similares nos dois grupos pesquisados.Palavras chave: Implante coclear, Qualidade de vida, Perfil de impacto da doença, Adulto, Pessoas com deficiência auditivaABSTRACTPurpose: Assess quality of life of adult pre and postlingual hearing impaired patients users of cochlear implants. Method: The interviewed patients were adults who had received their implants between 2004 and 2011 at the Department of Otolaryngology. The questionnaire WHOQoL–BREF was applied and patient records were used to check whether the patient had pre or post-lingual hearing loss. Out of the total, there were 17 post-lingual and 8 pre-lingual patients. Results: We have noticed that pre-lingual patients had the score in the general questionnaire of 77.4, whereas post-lingual subjects reached the score 76.3 in the general questionnaire. The domains that showed good results for pre-lingual subjects were physical (score= 82.4) and psychological (score 78.1), and for post-lingual subjects the score for physical and psychological domains were 82.3 and 77.4, respectively. Conclusion: We have observed that pre-lingual patients presented somewhat worse results than post-lingual subjects in the general score, but when the benefits of cochlear implant are taken into account, this difference between the groups practically disappears.Keywords: Cochlear implantation, Quality of life, Sickness impact profile, Adult, Persons with hearing impairments

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