Synovial sarcoma of the frontal sinus

✓ Synovial sarcoma is a soft-tissue lesion occurring predominantly in the extremities of young adults. Although the head and neck region is the second most common site of involvement, synovial sarcoma has rarely been reported in the paranasal sinus. The authors present a case of synovial sarcoma arising from the frontal sinus and review the literature of synovial sarcomas arising from the paranasal sinuses.

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Pediatric Synovial Sarcoma in the Retropharyngeal Space: A Rare and Unusual Presentation

Case Reports in Otolaryngology ◽

10.1155/2015/587386 ◽

2015 ◽

Vol 2015 ◽

pp. 1-4

Author(s):

Sanjay Vaid ◽

Neelam Vaid ◽

Sanjay Desai ◽

Varada Vaze

Keyword(s):

Head And Neck ◽

Synovial Sarcoma ◽

Pediatric Population ◽

Neck Region ◽

Retropharyngeal Space ◽

Imaging Findings ◽

Head And Neck Region ◽

English Medical Literature ◽

Synovial Sarcomas ◽

First Time

Synovial sarcomas in the head and neck are extremely rare tumors, especially in the pediatric population. 3–5% of synovial sarcomas occur in the head and neck region displaying varied imaging and histopathological features resulting in frequent misdiagnosis. These tumors have a poor prognosis; hence early diagnosis and accurate classification based on imaging, histopathology, and immunohistochemistry are critical for prompt treatment. To the best of our knowledge, imaging findings of pediatric retropharyngeal lipomatous synovial sarcoma have not been reported to date in English medical literature. We report, for the first time, a rare case of retropharyngeal lipomatous synovial sarcoma in a ten-year-old child and discuss the case-specific imaging findings in our patient using magnetic resonance imaging and computed tomography.

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Primary soft palate biphasic synovial sarcoma - case report and literature review

Romanian Journal of Rhinology ◽

10.2478/rjr-2021-0029 ◽

2021 ◽

Vol 11 (44) ◽

pp. 174-180

Author(s):

Ionut Tanase ◽

Mihaela Neagu ◽

George Dascalescu

Keyword(s):

Case Report ◽

Head And Neck ◽

Synovial Sarcoma ◽

Soft Palate ◽

Postoperative Radiotherapy ◽

Neck Region ◽

Complete Removal ◽

Head And Neck Region ◽

Pleomorphic Sarcoma ◽

Synovial Sarcomas

Abstract BACKGROUND. Synovial sarcomas of the soft tissue are a particular type of sarcomas that rarely appear in the head and neck region. CASE REPORT AND COMMENTS. We present the case of a 27-year-old patient diagnosed in 2017 with soft palate biphasic synovial sarcoma who presented with recurrent microepistaxis, nasal obstruction, left cephalalgia and aural fullness in the left ear. The clinical examination showed a tumor with approximately 4/6 cm in diameter, covered with sero-sanguinolent secretions, pulsating in nature, completely obstructing the left choana. The surgical treatment consisted of complete removal of the tumor under endoscopic guidance with electrocauterization of the insertion area, without further postoperative radiotherapy. The histopathological aspect was suggestive for pleomorphic sarcoma, poorly differentiated, confirming the local recurrence of the tumor. The patient also presented lung metastasis from undifferentiated malignant tumor. CONCLUSION. The particularity of this case is represented by the extremely rare occurrence of synovial sarcoma in the head and neck region, especially at the level of the soft palate. Complete resection of the tumor with negative margins represent the mainstay of treatment, associated with adjuvant radiotherapy, with an important role in improving disease-specific survival.

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Xanthogranuloma of the external auditory canal—an atypical anatomical manifestation

Journal of Surgical Case Reports ◽

10.1093/jscr/rjaa536 ◽

2021 ◽

Vol 2021 (3) ◽

Author(s):

James T Connell ◽

Thu Nguyen ◽

Andrew S Carney ◽

Sheldon Chong

Keyword(s):

Soft Tissue ◽

Head And Neck ◽

External Auditory Canal ◽

Neck Region ◽

Surgical Excision ◽

Paediatric Population ◽

Juvenile Xanthogranuloma ◽

Soft Tissue Lesion ◽

Cutaneous Lesions ◽

Head And Neck Region

Abstract Juvenile xanthogranuloma is a proliferative cutaneous manifestation encountered in the paediatric population. Adult cases are uncommon, but have been reported. Lesions are prevalent in the head and neck region, but rarely observed in the external auditory canal. We present the case of a 39-year-old female with a rapidly progressing obstructive soft tissue lesion of the external auditory canal. Surgical excision diagnosed the lesion as a rarely observed otological manifestation of juvenile xanthogranuloma. Surgical excision was curative with no locoregional recurrence. Otolaryngologists should consider juvenile xanthogranuloma as a differential for atypical soft tissue cutaneous lesions of the head and neck, including in divergent populations.

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Primary synovial sarcoma of the middle ear

The Journal of Laryngology & Otology ◽

10.1017/s0022215100125320 ◽

1993 ◽

Vol 107 (11) ◽

pp. 1070-1072 ◽

Cited By ~ 12

Author(s):

L. J. O'keei ◽

R. T. Ramsden ◽

A. R. Birzgalis

Keyword(s):

Young Adults ◽

Soft Tissue ◽

Head And Neck ◽

Synovial Sarcoma ◽

Synovial Tissue ◽

Middle Ear ◽

Neck Region ◽

Lower Limbs ◽

Head And Neck Region ◽

First Case

AbstractSynovial sarcoma is a soft tissue malignancy which most commonly affects the lower limbs of young adults and rarely occurs in the head and neck region. The term synovial sarcoma may be a misnomer as most of these tumours occur in tissues not known to contain synovial tissue. There has only been one previously reported case affecting the middle ear, which was metastatic, and we report the first case of primary synovial sarcoma of the middle ear.

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Synovial sarcoma of the ethmoidal sinus

The Journal of Laryngology & Otology ◽

10.1017/s0022215114002151 ◽

2014 ◽

Vol 128 (11) ◽

pp. 1022-1023 ◽

Cited By ~ 5

Author(s):

H-T Wong ◽

C-Y Ho ◽

A R Nazarina ◽

N Prepageran

Keyword(s):

Elderly Patient ◽

Case Report ◽

Soft Tissue ◽

Synovial Sarcoma ◽

Malignant Disease ◽

Neck Region ◽

High Grade ◽

Rare Entity ◽

Head And Neck Region ◽

Ethmoidal Sinus

AbstractBackground:Synovial sarcoma is a high-grade, soft tissue, malignant disease associated with poor outcome. Typically, synovial sarcoma involves the extremities, with less than 10 per cent of cases occurring in the head and neck region. Synovial sarcoma of the paranasal sinuses is a rare entity. This paper presents a case of an elderly patient with synovial sarcoma of the ethmoidal sinus.Case report:An 80-year-old woman who had right epistaxis underwent nasal endoscopy and biopsy. The pathology indicated synovial sarcoma and the patient underwent endoscopic excision of the tumour.Conclusion:Synovial sarcoma of the ethmoidal sinus is very rare. Patients should undergo excision of the tumour with post-operative radiotherapy. However, the prognosis remains poor and usually the patient succumbs to death within a year.

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The First Ever Reported Case of Primary Synovial Sarcoma of Scalp

Case Reports in Surgery ◽

10.1155/2016/5358790 ◽

2016 ◽

Vol 2016 ◽

pp. 1-6

Author(s):

Biplab Mishra ◽

Saurabh Singhal ◽

Deepak Prakash Bhirud ◽

Nitesh Kumar ◽

Saumyaranjan Mallick

Keyword(s):

Synovial Sarcoma ◽

Neck Region ◽

Young Female ◽

Rare Entity ◽

Extensive Review ◽

Diagnostic Challenge ◽

Primary Case ◽

Head Region ◽

Head And Neck Region ◽

Synovial Sarcomas

Synovial sarcomas are a rare entity with predilection for extremities and joints. The literature suggests that these tumours are rare in the head and neck region. Very few authors have reported their origin in head. Among the ones occurring in the head region, most of them are found to originate from the parotid area. According to our extensive review of available literature, there has been no reported case of the primary case of synovial sarcoma originating from the scalp convexity. We hereby report one such case in a young female which, by far to the best of our knowledge, is the first ever reported case of a synovial sarcoma occurring on the scalp. The tumour is also the largest ever reported in the literature and posed a great surgical and diagnostic challenge to our team. Through this paper, we recommend that synovial sarcoma should be included as a very rare yet possible differential diagnosis for the scalp tumours.

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Intracranial diverticulum of the frontal sinus as a complication of frontal craniotomy

Journal of Neurosurgery ◽

10.3171/jns.1979.51.6.0870 ◽

1979 ◽

Vol 51 (6) ◽

pp. 870-871 ◽

Cited By ~ 5

Author(s):

L. Anne Hayman ◽

Alfonso E. Aldama-Luebbert ◽

Robert A. Evans

Keyword(s):

Frontal Sinus ◽

Anterior Cranial Fossa ◽

Content Type ◽

Sinus Wall ◽

Cranial Fossa ◽

Sinus Mucosa ◽

Fine Print

✓ A large air-filled intracranial extradural diverticulum of the frontal sinus mucosa was removed from the anterior cranial fossa of a 47-year-old man 2 years after fracture of the posterior sinus wall during craniotomy.

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Noma and Necrotizing Fasciitis of the Face and Neck

Facial Plastic Surgery ◽

10.1055/s-0041-1722894 ◽

2021 ◽

Author(s):

Lauren E. Miller ◽

David A. Shaye

Keyword(s):

Soft Tissue ◽

Necrotizing Fasciitis ◽

Head And Neck ◽

Subcutaneous Tissue ◽

Neck Region ◽

Superficial Fascia ◽

Soft Tissue Infections ◽

Head And Neck Region ◽

Necrotizing Soft Tissue Infections ◽

The Face

AbstractNecrotizing fasciitis (NF) is part of the class of necrotizing soft tissue infections characterized by rapid fascial spread and necrosis of the skin, subcutaneous tissue, and superficial fascia. If left untreated, NF can rapidly deteriorate into multiorgan shock and systemic failure. NF most commonly infects the trunk and lower extremities, although it can sometimes present in the head and neck region. This review provides an overview of NF as it relates specifically to the head and neck region, including its associated clinical features and options for treatment. Noma, a related but relatively unknown disease, is then described along with its relationship with severe poverty.

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Synovial sarcoma: case report

RGO - Revista Gaúcha de Odontologia ◽

10.1590/1981-863720170002000123194 ◽

2017 ◽

Vol 65 (3) ◽

pp. 260-264

Author(s):

Isabella Lima Arrais RIBEIRO ◽

Larissa Cavalcanti MONTEIRO ◽

Ana Carolina Rodrigues de MELO ◽

Tácio Candeia LYRA ◽

Julio Cesar Campos FERREIRA FILHO ◽

...

Keyword(s):

Tumor Growth ◽

Synovial Sarcoma ◽

Fibrous Tissue ◽

Treatment Protocol ◽

Neck Region ◽

Cervical Region ◽

Histopathological Analysis ◽

Parotid Region ◽

Synovial Sarcomas

ABSTRACT Introduction: Synovial sarcomas are rare and aggressive neoplasms located in the head and neck region and usually occurs in young adults. Presentation of case: This report presents a case of synovial sarcoma in a 15-year-old male patient who sought medical treatment for painful symptoms and associated dysphagia. The lesion was nodular, extensive, localized in the parotid region, and extended to the left cervical region. The patient was treated in a referral hospital with a treatment protocol that initially included chemotherapy for six months and surgery to attempt to excise the lesion, but the surgery was ineffective because removal could have damaged important vital structures. The Computed Tomography scan showed a hypodense area with diffuse growth and no involvement of the facial bones and the histopathological analysis revealed pleomorphic and oval spindle cells with rounded epithelial cells that formed nests surrounded by fibrous tissue. The Immunohistochemistry analysis was conclusive for the diagnosis of a high-grade SS in the parotid and left cervical regions. The medical team opted for palliative treatment with cervical radiotherapy. The patient remained hospitalized for four months after the surgery and died after 15 months since the diagnosis for compromise of airway by fast tumor growth. Conclusion: The synovial sarcoma, when diagnosed late may reduce the survival of patients because of the complications that tumor growth can bring to the prognosis and quality of life.

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