scholarly journals The First Ever Reported Case of Primary Synovial Sarcoma of Scalp

2016 ◽  
Vol 2016 ◽  
pp. 1-6
Author(s):  
Biplab Mishra ◽  
Saurabh Singhal ◽  
Deepak Prakash Bhirud ◽  
Nitesh Kumar ◽  
Saumyaranjan Mallick

Synovial sarcomas are a rare entity with predilection for extremities and joints. The literature suggests that these tumours are rare in the head and neck region. Very few authors have reported their origin in head. Among the ones occurring in the head region, most of them are found to originate from the parotid area. According to our extensive review of available literature, there has been no reported case of the primary case of synovial sarcoma originating from the scalp convexity. We hereby report one such case in a young female which, by far to the best of our knowledge, is the first ever reported case of a synovial sarcoma occurring on the scalp. The tumour is also the largest ever reported in the literature and posed a great surgical and diagnostic challenge to our team. Through this paper, we recommend that synovial sarcoma should be included as a very rare yet possible differential diagnosis for the scalp tumours.

2015 ◽  
Vol 2015 ◽  
pp. 1-4
Author(s):  
Sanjay Vaid ◽  
Neelam Vaid ◽  
Sanjay Desai ◽  
Varada Vaze

Synovial sarcomas in the head and neck are extremely rare tumors, especially in the pediatric population. 3–5% of synovial sarcomas occur in the head and neck region displaying varied imaging and histopathological features resulting in frequent misdiagnosis. These tumors have a poor prognosis; hence early diagnosis and accurate classification based on imaging, histopathology, and immunohistochemistry are critical for prompt treatment. To the best of our knowledge, imaging findings of pediatric retropharyngeal lipomatous synovial sarcoma have not been reported to date in English medical literature. We report, for the first time, a rare case of retropharyngeal lipomatous synovial sarcoma in a ten-year-old child and discuss the case-specific imaging findings in our patient using magnetic resonance imaging and computed tomography.


2005 ◽  
Vol 103 (6) ◽  
pp. 1077-1080 ◽  
Author(s):  
Gary L. Gallia ◽  
Daniel M. Sciubba ◽  
Christine L. Hann ◽  
Siva P. Raman ◽  
William H. Westra ◽  
...  

✓ Synovial sarcoma is a soft-tissue lesion occurring predominantly in the extremities of young adults. Although the head and neck region is the second most common site of involvement, synovial sarcoma has rarely been reported in the paranasal sinus. The authors present a case of synovial sarcoma arising from the frontal sinus and review the literature of synovial sarcomas arising from the paranasal sinuses.


2021 ◽  
Vol 11 (44) ◽  
pp. 174-180
Author(s):  
Ionut Tanase ◽  
Mihaela Neagu ◽  
George Dascalescu

Abstract BACKGROUND. Synovial sarcomas of the soft tissue are a particular type of sarcomas that rarely appear in the head and neck region. CASE REPORT AND COMMENTS. We present the case of a 27-year-old patient diagnosed in 2017 with soft palate biphasic synovial sarcoma who presented with recurrent microepistaxis, nasal obstruction, left cephalalgia and aural fullness in the left ear. The clinical examination showed a tumor with approximately 4/6 cm in diameter, covered with sero-sanguinolent secretions, pulsating in nature, completely obstructing the left choana. The surgical treatment consisted of complete removal of the tumor under endoscopic guidance with electrocauterization of the insertion area, without further postoperative radiotherapy. The histopathological aspect was suggestive for pleomorphic sarcoma, poorly differentiated, confirming the local recurrence of the tumor. The patient also presented lung metastasis from undifferentiated malignant tumor. CONCLUSION. The particularity of this case is represented by the extremely rare occurrence of synovial sarcoma in the head and neck region, especially at the level of the soft palate. Complete resection of the tumor with negative margins represent the mainstay of treatment, associated with adjuvant radiotherapy, with an important role in improving disease-specific survival.


2014 ◽  
Vol 128 (11) ◽  
pp. 1022-1023 ◽  
Author(s):  
H-T Wong ◽  
C-Y Ho ◽  
A R Nazarina ◽  
N Prepageran

AbstractBackground:Synovial sarcoma is a high-grade, soft tissue, malignant disease associated with poor outcome. Typically, synovial sarcoma involves the extremities, with less than 10 per cent of cases occurring in the head and neck region. Synovial sarcoma of the paranasal sinuses is a rare entity. This paper presents a case of an elderly patient with synovial sarcoma of the ethmoidal sinus.Case report:An 80-year-old woman who had right epistaxis underwent nasal endoscopy and biopsy. The pathology indicated synovial sarcoma and the patient underwent endoscopic excision of the tumour.Conclusion:Synovial sarcoma of the ethmoidal sinus is very rare. Patients should undergo excision of the tumour with post-operative radiotherapy. However, the prognosis remains poor and usually the patient succumbs to death within a year.


2017 ◽  
Vol 65 (3) ◽  
pp. 260-264
Author(s):  
Isabella Lima Arrais RIBEIRO ◽  
Larissa Cavalcanti MONTEIRO ◽  
Ana Carolina Rodrigues de MELO ◽  
Tácio Candeia LYRA ◽  
Julio Cesar Campos FERREIRA FILHO ◽  
...  

ABSTRACT Introduction: Synovial sarcomas are rare and aggressive neoplasms located in the head and neck region and usually occurs in young adults. Presentation of case: This report presents a case of synovial sarcoma in a 15-year-old male patient who sought medical treatment for painful symptoms and associated dysphagia. The lesion was nodular, extensive, localized in the parotid region, and extended to the left cervical region. The patient was treated in a referral hospital with a treatment protocol that initially included chemotherapy for six months and surgery to attempt to excise the lesion, but the surgery was ineffective because removal could have damaged important vital structures. The Computed Tomography scan showed a hypodense area with diffuse growth and no involvement of the facial bones and the histopathological analysis revealed pleomorphic and oval spindle cells with rounded epithelial cells that formed nests surrounded by fibrous tissue. The Immunohistochemistry analysis was conclusive for the diagnosis of a high-grade SS in the parotid and left cervical regions. The medical team opted for palliative treatment with cervical radiotherapy. The patient remained hospitalized for four months after the surgery and died after 15 months since the diagnosis for compromise of airway by fast tumor growth. Conclusion: The synovial sarcoma, when diagnosed late may reduce the survival of patients because of the complications that tumor growth can bring to the prognosis and quality of life.


Author(s):  
Ashiya Goel ◽  
Aman . ◽  
Vinny Raheja ◽  
Manisha Kumari

<p class="abstract"><span lang="EN-US">Chondroid syringomas are uncommon cutaneous neoplasms of sweat gland origin which are slow-growing, nontender, subcutaneous or intracutaneous in location and often occurring in the head and neck region. Chondroid syringoma should be considered in the differential diagnosis of any subcutaneous nodule over the face. The clinician may miss the diagnosis of this lesion and if it is suspected, tumour should be excised with a margin of normal tissue and regular follow up should be done.</span></p>


2020 ◽  
Vol 12 (1) ◽  
pp. 19-21
Author(s):  
Raghavendra Rao ◽  
Srilatha Parampalli Srinivas ◽  
Varsha M. Shetty

AbstractPerifollicular fibroma (PFF) is a rare proliferative lesion originating from the perifollicular connective tissue sheath. It may be congenital or acquired manifesting as skin colored to pink, asymptomatic papules of 1-5 mm in size. They are commonly distributed in the head and neck region. Multiple PFFs may be associated with internal malignancy or as a part of Birt-Hogg-Dube syndrome. Histopathology serves as an essential tool in clinching the diagnosis. Herein we report a case of giant congenital PFF.


Author(s):  
Chandre Gowda Bendiganahalli Venkate Gowda ◽  
Rakshita R. Kamath

<p class="abstract">Independently arising acrochordon of the external auditory canal is a rare entity with only one reported case in literature. We present here the second such case. A 54-yr old lady presented to our outpatient department with complains of aural fullness and reduced hearing in right ear for 2 weeks. Clinical examination showed a pedunculated polypoidal growth in the external auditory canal. Excisional biopsy and histopathology revealed an acrochordon. Following the procedure, patient was free of symptoms and all structures of the right ear were normal. In the head and neck region, acrochordons have only but once been reported in the external auditory canal and hence should be considered as a differential diagnosis in the masses of this region. Resection must be done for confirmation of diagnosis, differentiation from neoplasia and alleviation of symptoms when associated.  </p>


2013 ◽  
Vol 4 (2) ◽  
pp. 86-88 ◽  
Author(s):  
Raza Hussain ◽  
Asif Loya ◽  
Arif Jamshed ◽  
Adeel Haider Tirmazi

ABSTRACT Synovial sarcomas of head and neck are very rare and account for only 3% of all sarcomas. Approximately 5% of synovial sarcomas arise in the head and neck region and hypopharynx and larynx are the most and least often affected anatomic sites respectively. We describe a rare case of primary hypopharyngeal synovial sarcoma in a young adult. How to cite this article Jamshed A, Loya A, Tirmazi AH, Hussain R. Synovial Cell Sarcoma of the Hypopharynx. Int J Head Neck Surg 2013;4(2):86-88.


2021 ◽  
Vol 6 (4) ◽  
pp. 288-290
Author(s):  
Punam Prasad Bhadani ◽  
Sneha Aditi ◽  
Avinash Singh

Epidermal inclusion cysts (EIC) are benign lesions that can be encountered throughout the body, but with a low incidence in the head and neck region. (1.6 to 7%) The various locations in this region where the cyst can arise are sublingual, submental, submandibular and buccal mucosa. EIC present in the tonsils are extremely rare and reported less than 0.01% in published English literature. We report a rare and incidental finding of epidermal inclusion cyst with actinomycetes in tonsil in a 57 year old male who presented with sore throat and difficulty in swallowing.


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