PRIMARY CARDIAC TUMORS: EARLY SURGERY, COMPLETE RESECTION, CHEMOTHERAPY ENHANCES SURVIVAL.

2021 ◽  
pp. 77-79
Author(s):  
Pradeep Kumar Radhakrishnan ◽  
Gayathri Ananyajyothi Ambat ◽  
Nihas Nazer ◽  
Sushamma Murugan ◽  
Arun Vijyakaumar ◽  
...  
Keyword(s):  
Survival Rate ◽  
Adjuvant Therapy ◽  
Right Atrium ◽  
Complete Resection ◽  
Cardiac Tumors ◽  
Retrospective Evaluation ◽  
Surgical Team ◽  
Pleomorphic Sarcoma ◽  
Dismal Prognosis ◽  
Primary Cardiac Tumors

Primary cardiac tumors are rare. The incidence varies between 0.3% to 0.7% .Quarter of all primary cardiac tumors are malignant, of these 75% are sarcomas. Malignant primary cardiac sarcomas that affect right atrium are predominantly angiosarcomas while the left atrium is involved primary in pleomorphic sarcoma like malignant brous histiocytoma and leiomyosarcoma. In a young patient it usually carries a dismal prognosis if not diagnosed early and dealt with surgically followed by adjuvant therapy. Without surgical resection, the survival rate at 1yr is only 10%.Retrospective evaluation of the last 60 primary cardiac tumors done by the same surgical team over 28 years was looked into.

scholarly journals Cardiac Angiosarcoma

2011 ◽  
Vol 2011 ◽  
pp. 1-3
Author(s):  
Monique Esteves Cardoso ◽  
Leonardo Secchin Canale ◽  
Rosana Grandelle Ramos ◽  
Edson da Silva Salvador Junior ◽  
Stephan Lachtermacher
Keyword(s):  
Adjuvant Therapy ◽  
Right Atrium ◽  
Malignant Tumors ◽  
Tumor Resection ◽  
Cardiac Tumors ◽  
Primary Tumors ◽  
Cardiac Angiosarcoma ◽  
Cardiac Metastases ◽  
The Right ◽  
Primary Cardiac Tumors

Despite cardiac metastases are found in about 20% of cancer deaths, the presence of primary cardiac tumors is rare. Most primary tumors are benign, and malignant tumors comprise about 15%. We report a 21-year-old man with fever, dyspnea, and hemoptysis that was diagnosed with angiosarcoma of the right atrium and pulmonary metastasis. Patient was submitted to surgical tumor resection without adjuvant therapy and died four months after diagnosis.

scholarly journals Primary Cardiac Rhabdomyosarcoma in a child -- A case report

2020 ◽  
Author(s):  
KRISHNA PRASAD MARAM ◽  
Vikram Kudumula ◽  
Dilip Ratti
Keyword(s):  
Case Report ◽  
Left Ventricle ◽  
Right Ventricle ◽  
Malignant Tumor ◽  
Right Atrium ◽  
Malignant Tumors ◽  
Benign Tumors ◽  
Cardiac Tumors ◽  
Cardiac Rhabdomyosarcoma ◽  
Primary Cardiac Tumors

Primary cardiac tumors are rare in children, usually consist of benign tumors like rhabdomyomas and fibromas that may spontaneously regress. Primary malignant tumors are extremely rare even in adults and very few paediatric cases were reported in literature. Rhabdomyosarcoma is a rare primary malignant tumor in children and most of the reported cases occur in right ventricle, left atrium and right atrium. We report a 15 month old child with primary rhabdomyosarcoma of left ventricle presenting in cardiac tamponade and circulatory failure.

Pediatric heart transplant for unresectable primary cardiac tumor

2016 ◽  
Vol 25 (3) ◽  
pp. 207-209 ◽  
Author(s):  
Anjith Prakash Rajakumar ◽  
Sheriff Ejaz Ahmed ◽  
Roy Varghese ◽  
Sivakumar Kothandam ◽  
Udaya Charan Murmu ◽  
...  
Keyword(s):  
Heart Transplant ◽  
Complete Resection ◽  
Cardiac Tumors ◽  
Cardiac Fibroma ◽  
Term Outcome ◽  
Long Term Outcome ◽  
Primary Cardiac Tumor ◽  
Pediatric Heart Transplant ◽  
Primary Cardiac Tumors

Surgery for primary cardiac tumors in children includes complete resection, partial resection, and cardiac transplantation. A pediatric heart transplant in this setting is associated with significantly higher mortality and poorer long-term outcome, and it is reserved for unresectable tumors. We recently performed an emergency pediatric heart transplant in a 7-year-old boy with an unresectable cardiac fibroma in the left ventricle.

scholarly journals P1697 A rare case: primary cardiac sarcoma in the left and right atrium presenting with dispnea due to mitral valvular obstruction

2020 ◽  
Vol 21 (Supplement_1) ◽  
Author(s):  
S Akturk ◽  
T S Tan ◽  
M Mammadov ◽  
I Dincer ◽  
C Erol
Keyword(s):  
Computed Tomography ◽  
Left Atrium ◽  
Right Atrium ◽  
Bone Lesions ◽  
Cardiac Tumors ◽  
Iliac Wing ◽  
Left And Right ◽  
Primary Cardiac Sarcoma ◽  
The Right ◽  
Primary Cardiac Tumors

Abstract Introduction Primary cardiac tumors are extremely rare; the incidence is approximately 0.001% to 0.03%. Malignant tumors account for 25% of primary cardiac tumors, and among those, sarcomas are the most prevalent. We report a case of primary cardiac sarcoma presenting with dyspnea due to mitral valvuler obstruction. Case Report A 41-year-old woman was admitted to the hospital with dyspnea for 8 months without any obvious causes. She was healthy previous and without family history. Physical examination was normal. Thorax computed tomography (CT) scan was performed with the doubt of pulmonary disease. A 1x1 cm hypodense nodule was detected in superior segment of the right lower lobe lung. Positron emission tomography-computed tomography (PET-CT) revealed a 1*1 cm nodule in the lung. And also increased 18F-fluorodeoxyglucose uptake was observed in the left scapula, left iliac wing and right 4th rib, likely due to metastasis. Biopsy from the lesion of iliac wing was performed. Pathologic examination was primarily compatible with the malign mesenchymal tumor and sarcoma infiltration; but malignant epithelial tumor and metastasis of carcinoma could not be ruled out. Magnetic resonance imaging of the lung was performed to find the origin of the metastatic tumor. A 8,6 x 5,3 x 5,1 cm mass filling the right and left atria was detected.It was extending from the right atrium to the superior vena cava and also from the left atrium to the right inferior and superior pulmonary venules. The image of mass was compatible with sarcoma. Transthoracic echocardiography was performed. A mass in the left and right atrium was detected. It was filling the left atrium. Due to the mass, the maximum mitral gradient was 21 mm Hg and the mean mitral gradient was 10 mm Hg, as if there was mitral stenosis.Systolic pulmonary artery pressure was 40 mmHg. Mild mitral insufficiency was detected. The patient was evaluated with the department of oncology and cardiovascular surgery. It was decided that the mass was inoperable. So transesophageal echocardiography was not performed. It was thought that, the mass was primary cardiac sarcoma, pulmonary nodule and bone lesions were metastasis of this primary cardiac sarcoma. So chemotherapy protocol (ifosfamide,adriamycin,mesna) was started. Conclusion Cardiac tumors have many clinical presentations. Early stages of the disease are often asymptomatic. In advanced stages, patients present with symptoms of the classic triad (intracardiac obstruction, systemic embolization, constitutional symptoms) Symptoms are often non-spesific; so diagnostic suspicion is very important. Although cardiac sarcoma therapy includes complete surgical excision, followed by radiotherapy and chemotherapy, prognosis is still poor. Surgery can offer dramatic palliation of symptoms in cases of valvular obstruction. In conclusion, it remains clear that early diagnosis and treatment are extremely important because of their prognostic and therapeutic value. Abstract P1697 Figure.

scholarly journals Mediastinal Schwannoma Diagnosed Preoperatively as a Cyst

2014 ◽  
Vol 41 (1) ◽  
pp. 76-79 ◽  
Author(s):  
Shinichi Taguchi ◽  
Atsuo Mori ◽  
Ryo Suzuki ◽  
Ichiro Hasegawa ◽  
Hiroaki Sato ◽  
...  
Keyword(s):  
Cardiopulmonary Bypass ◽  
Large Mass ◽  
Transverse Sinus ◽  
Complete Resection ◽  
Cystic Degeneration ◽  
Cardiac Tumors ◽  
Left Main ◽  
Main Trunk ◽  
Bronchogenic Cysts ◽  
Primary Cardiac Tumors

Mediastinal schwannomas are sometimes diagnosed as pericardial or bronchogenic cysts, if cystic degeneration is extensive. When mediastinal schwannomas are not diagnosed as primary cardiac tumors, the use of cardiopulmonary bypass in their resection appears to be infrequent. We report the case of a 48-year-old woman who presented with symptoms from a suspected intrapericardial cyst. Multiple diagnostic images revealed a large mass, potentially a proteinaceous or hemorrhagic cyst, in the transverse sinus behind the ascending aorta and against the left main trunk. After complete resection with the use of cardiopulmonary bypass, the mass was identified as a benign extracardiac schwannoma. More than 3 years postoperatively, the patient had no relevant symptoms. We discuss the preoperative diagnosis, the method of resection, and our broad strategy for dealing with such a case.

A rare case of a right atrial lipoma originating from the superior vena cava: review, diagnosis and management

2021 ◽  
Author(s):  
George H Nasr ◽  
Michael Johl ◽  
Steven Sinfield ◽  
Cy Kim ◽  
Fabio Sagebin ◽  
...  
Keyword(s):  
Left Ventricle ◽  
Superior Vena Cava ◽  
Right Atrium ◽  
Rare Case ◽  
Superior Vena ◽  
Vena Cava ◽  
Right Atrial ◽  
Cardiac Tumors ◽  
The Right ◽  
Primary Cardiac Tumors

Primary cardiac tumors are usually found incidentally on imaging and are much less common than tumors that metastasize to the heart. Cardiac lipomas are benign cardiac tumors that are usually found in the right atrium or left ventricle. Primary intravascular venous lipomas of the great cardiac vessels are extremely rare and there are few reported cases of a lipoma originating from the superior vena cava causing direct compressive intracardiac effects. Here we describe a case of a symptomatic right atrial lipoma originating from the superior vena cava.

Ependymoma in childhood: prognostic factors, extent of surgery, and adjuvant therapy

2002 ◽  
Vol 97 (4) ◽  
pp. 827-835 ◽  
Author(s):  
Marie-Lise C. van Veelen-Vincent ◽  
Alain Pierre-Kahn ◽  
Chantale Kalifa ◽  
Christian Sainte-Rose ◽  
Michel Zerah ◽  
...  
Keyword(s):  
Overall Survival ◽  
Prognostic Factors ◽  
Survival Rate ◽  
Adjuvant Therapy ◽  
Complete Resection ◽  
Content Type ◽  
Chemotherapy Group ◽  
Extent Of Surgery ◽  
Fine Print

Object. The aim of this study was to investigate the effect of patient-related factors, extent of surgery, and adjuvant therapy on survival in children presenting with intracranial ependymoma. Methods. Between 1980 and 1999, 83 children (mean age 36 months) underwent surgery for intracranial ependymomas. Complete resection, verified on postoperative computerized tomography scans, was achieved in 73%. Adjuvant therapy modalities have changed over the years: before 1990 all patients received radiotherapy, whereas after 1990 the children younger than 3 years of age and later those younger than 5 years of age were treated first with chemotherapy and received radiotherapy only after their first tumor recurrence. The follow-up period averaged 70 x 49 months. Conclusions. Overall survival, intraoperative deaths excluded, was 73 ± 11% and 51 ± 14% at 5 and 10 years, respectively. The event-free survival rate at 5 and 10 years was 48 ± 12% and 46 ± 12%, respectively. Most of the events were local recurrences. Despite multiple reinterventions, the overall survival rate in this group dropped to 14%. On univariate analysis, the only significant prognostic factors were complete resection and radiotherapy. Both of these factors combined increased the 5- and 10-year survival rates to 93 and 75%, respectively. Age of the patients was not a statistically independent prognostic factor. The patients in the chemotherapy group did not fare as well as those in the radiotherapy group. A subgroup (36%) within the chemotherapy group, however, survived tumor free after a mean follow-up period of 67 months. It is not clear whether this subgroup either responded well to chemotherapy or needed no adjuvant therapy. Further research is warranted to answer this question.

scholarly journals A case report: a giant cardiac atypical lipoma associated with pericardium and right atrium

2019 ◽  
Vol 19 (1) ◽  
Author(s):  
Xin Wang ◽  
Xiaona Yu ◽  
Weidong Ren ◽  
Dongyu Li
Keyword(s):  
Case Report ◽  
Right Atrium ◽  
Rare Case ◽  
Histopathological Examination ◽  
Pathological Examination ◽  
Cardiac Tumors ◽  
Case Presentation ◽  
Atypical Lipoma ◽  
The Right ◽  
Primary Cardiac Tumors

Abstract Background Among primary cardiac tumors, atypical lipoma is very rare. In particular, cases with lipomas in both the pericardium and the atria are even rare. Case presentation We report the case of a 49-year-old male patient presented to our department because of chest pain. Echocardiography revealed two large masses in both the pericardium and the right atrium. Then the tumors were completely resected and the histopathological examination revealed atypical lipoma. The patient recovered well without any complication and discharged from hospital. Conclusions We report a very rare case of a huge atypical lipomas located on the pericardium and right atrium. These tumors were easily detected by echocardiography and final diagnosed after surgical resection and pathological examination.

scholarly journals Intracardiac EUS-B-Guided FNA for Diagnosing Cardiac Tumors

Respiration ◽  
2021 ◽  
pp. 1-5
Author(s):  
Haizea Alvarez Martinez ◽  
Jolanda C. Kuijvenhoven ◽  
Jouke T. Annema
Keyword(s):  
Left Atrium ◽  
Heart Surgery ◽  
Open Heart Surgery ◽  
Needle Aspiration ◽  
Invasive Technique ◽  
Cardiac Tumors ◽  
Surgical Interventions ◽  
Tumor Diagnostics ◽  
Specific Tumor ◽  
Primary Cardiac Tumors

Primary cardiac tumors are extremely rare. Obtaining a tissue diagnosis is difficult and commonly requires open-heart surgery with associated morbidity. Esophageal endoscopic ultrasound (EUS) and EUS with the EBUS scope (EUS-B) provide real-time sampling of centrally located lung tumors and mediastinal lymph nodes. They also provide an excellent view of the left atrium, since it is located adjacent to the esophagus. To date, left atrium tumor diagnostics by endosonography is poorly explored. We describe 2 exceptional diagnostic cases of left atrium tumors in which cardiac surgery was hazardous due to the clinical condition or previous surgical interventions. During EUS-B-guided fine-needle aspiration (FNA), the left atrial masses were successfully and safely sampled, revealing a Burkitt lymphoma and a synovial sarcoma. FNA including cell block analysis enabled specific tumor diagnosis and molecular subtyping. Our findings suggest that in selected cases, linear endosonography qualifies as a minimally invasive technique for intracardiac tumor diagnostics.

Characteristics, management, and outcomes among admissions for primary cardiac tumors: Results from the National Inpatient Sample

2021 ◽  
Author(s):  
Joseph N. Heaton ◽  
Nehal Dhaduk ◽  
Alexis K. Okoh ◽  
Khoi P. Dang‐Ho ◽  
Rajiv Tayal ◽  
...  
Keyword(s):  
Cardiac Tumors ◽  
National Inpatient Sample ◽  
Primary Cardiac Tumors
Sign in / Sign up

Export Citation Format

Share Document