scholarly journals MR and CT imaging in the Dyke-Davidoff-Masson syndrome: report of three cases and contribution to pathogenesis and differential diagnosis

1998 ◽  
Vol 56 (4) ◽  
pp. 803-807 ◽  
Author(s):  
PAULO HENRIQUE AGUIAR ◽  
WEI LIU CHING ◽  
HELIO LEITÃO ◽  
F. ISSA ◽  
GUILHERME LEPSKI ◽  
...  
Keyword(s):  
Differential Diagnosis ◽  
Mental Retardation ◽  
Brain Injury ◽  
Paranasal Sinuses ◽  
Facial Asymmetry ◽  
Cerebral Injury ◽  
Radiological Features ◽  
Cerebral Hemiatrophy ◽  
The Brain ◽  
Syndrome Report

Cerebral hemiatrophy or Dyke-Davidoff-Masson syndrome is a condition characterized by seizures, facial asymmetry, contralateral hemiplegia or hemiparesis, and mental retardation. These findings are due to cerebral injury that may occur early in life or in utero. The radiological features are unilateral loss of cerebral volume and associated compensatory bone alterations in the calvarium, like thickening, hyperpneumatization of the paranasal sinuses and mastoid cells and elevation of the petrous ridge. The authors describe three cases. Classical findings of the syndrome are present in variable degrees according to the extent of the brain injury. Pathogenesis is commented.

scholarly journals Dyke Davidoff Masson Syndrome with Abdominal Epilepsy-Rare Presentation

2013 ◽  
Vol 3 (2) ◽  
pp. 25-28
Author(s):  
Shitanshu Srivastava ◽  
Rajat Pratap Singh ◽  
KL Srivastava
Keyword(s):  
Mental Retardation ◽  
Abdominal Pain ◽  
Facial Asymmetry ◽  
Severe Abdominal Pain ◽  
Medical Sciences ◽  
Rare Presentation ◽  
Radiological Features ◽  
Cerebral Hemiatrophy ◽  
Right Cerebral Hemisphere ◽  
Ct And Mri

Dyke Davidoff Masson Syndrome (DDMS) with abdominal epilepsy, is a rare clinical condition. It is characterized by severe abdominal pain with seizures, facial asymmetry, contralateral hemiparesis, and mental retardation. Diagnosis is made clinically coupled with radiological features which include cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses along with abnormal EEG and response to antiepileptic drugs. Here we report a case of DDMS with abdominal epilepsy in a 10 year old male child who presented with recurrent episodes of severe abdominal pain followed by seizures, hemiparesis and mental retardation. CT and MRI showed hemiatrophy of right cerebral hemisphere. DOI: http://dx.doi.org/10.3126/ajms.v3i2.6172 Asian Journal of Medical Sciences 3(2012) 25-28

scholarly journals Dyke–Davidoff–Masson syndrome with crossed cerebellar atrophy

2017 ◽  
Vol 21 (1) ◽  
Author(s):  
Sanjay M. Khaladkar ◽  
Shishir Chauhan ◽  
Abhijit M. Patil ◽  
Siddappa G. Gandage ◽  
Surbhi Chauhan Kalra
Keyword(s):  
Mental Retardation ◽  
Middle Cerebral Artery ◽  
Cerebellar Atrophy ◽  
Facial Asymmetry ◽  
Rare Condition ◽  
Female Child ◽  
Left Middle Cerebral Artery ◽  
Cerebral Hemiatrophy ◽  
Radiological Changes ◽  
Left Middle

Dyke–Davidoff–Masson syndrome is a rare condition with classical, clinical and radiological changes – mental retardation, hemiparesis, facial asymmetry, seizures and cerebral hemiatrophy with calvarial changes. Contralateral cerebellar atrophy is rare and occurs if insult occurs after 1 month of age. We report a case of a 6-year-old female child presenting with right-sided hemiparesis, convulsions and left cerebral hemiatrophy with an old infarct in left middle cerebral artery (MCA) territory, ipsilateral calvarial thickening and right (crossed) cerebellar atrophy.

scholarly journals PRIMARY EWING'S SARCOMA OF THE NASAL CAVITY IN PEDIATRIC PRACTICE

2021 ◽  
Vol 06 (01) ◽  
pp. 102-103
Author(s):  
Bekisheva Aigul Bekisheva Aigul ◽  
Makhneva Anna Makhneva Anna ◽  
Bulegenova Minira Bulegenova Minira ◽  
Abyov Galyjan Abyov Galyjan ◽  
Remkulova Mahabbat Remkulova Mahabbat
Keyword(s):  
Differential Diagnosis ◽  
Nasal Cavity ◽  
Tumor Cells ◽  
Paranasal Sinuses ◽  
Ewing’S Sarcoma ◽  
Ewing's Sarcoma ◽  
Diagnostic Methods ◽  
Pelvic Bone ◽  
Radiological Features ◽  
The Right

Introduction: Ewing's sarcoma (ES) is an aggressive tumor occuring more frequently in childhood and adolescence, mainly observed during the first three decades of life. Microscopically consists of small round cells, with a high nuclear cytoplasmic index, originating from primitive neuroectodermal cells. Most often such tumor occurs in early childhood or adolescence. [1] Ewing's sarcoma refers to tumors of the bone tissue : the limbs, ribs, and pelvic bone, but also it may occur in soft tissues, which means any localization in the human body. Among extra-skeletal localities, ES rarely occurs in the head and neck (2-3% of all ES) and extremely rare in the nasal cavity or paranasal sinuses [1,2,3]. Diagnosis the primary of ES nasal localization is complex and mainly depends on histopathological research, as visual diagnostic methods (x-ray, CT, MRI) do not identify the type of tumor. MRI examination of tumors of such localization may suggest a malignant nature, so further differential diagnosis should exclude the following: malignant lymphoma, rhabdomyosarcoma, moderately differentiated carcinomas, and ES. These tumors have common radiological features, so they require additional research [4,5]. From abovementioned, the following clinical case of primary Ewing's sarcoma in the nasal cavity in a 14-year-old girl seemed to be interesting . The patient complained on the difficulty of breathing, swelling in the right half of the nose wing. MRI showed a large neopasm of the facial skull on the right (pterygoid and subterranean fossa, right half of the nose, nasopharynx, latticed bone and paranasal sinuses). Histological examination of the samples revealed a solid neoplastic tissue consisting of monomorphic small circular or oval cells with a high nuclear-cytoplasmic index. Some exapnsion of the tumor cells around the vessels was observed, while part of epithelial lining and glandular structures were preserved in the same places. Foci of necrosis and extensive hemorrhages were visualized. The immunohistochemical study with the CD99 antibody showed a total positive membrane reaction with the closure of the stained membranes ( with the presence of membranes ring staining ). The reaction with anti Fli1 revealed total nuclear staining of tumor cells, except for the stromal cells. Thus: as primary Ewing's sarcoma affects the sinus tract very rarely, diagnosis of the tumor in this location is difficult. MRI and other visual methods in these cases are not informative, because a number of tumors have common radiological features, that make the differential diagnosis very difficult. In this regard, the pathomorphological study including immunohistochemical research is the main method of diagnosing ES.

scholarly journals Dyke-Davidoff-Masson Syndrome

2012 ◽  
Vol 1 (2) ◽  
pp. 84-86 ◽  
Author(s):  
Naba Raj Koirala ◽  
Roshana Khadka ◽  
Manoj Bhattarai ◽  
Dibya Tulachan ◽  
Ajay Kumar Das ◽  
...  
Keyword(s):  
Mental Retardation ◽  
Upper Limb ◽  
Facial Asymmetry ◽  
Young Girl ◽  
Severe Mental Retardation ◽  
Medical College ◽  
Cerebral Hemiatrophy ◽  
Ct Brain ◽  
Radiologic Features

Dyke-Davidoff-Masson Syndrome (DDMS) is characterized by seizures, facial asymmetry, contralateral hemiplegia and mental retardation. The characteristic radiologic features are cerebral hemiatrophy with homolateral hypertrophy of the skull and sinuses. Here we report a case of a 16 years young girl who presented with seizures severe mental retardation and weakness of left upper-limb and on CT brain was diagnosed to have DDMS.DOI: http://dx.doi.org/10.3126/jonmc.v1i2.7306 Journal of Nobel Medical College (2012), Vol.1 No.2 p.84-86

scholarly journals Distant Organ Damage in Acute Brain Injury

2020 ◽  
Vol 10 (12) ◽  
pp. 1019
Author(s):  
Natalia Rachfalska ◽  
Zbigniew Putowski ◽  
Łukasz J. Krzych
Keyword(s):  
Brain Injury ◽  
Brain Injuries ◽  
Organ Damage ◽  
Acute Brain Injury ◽  
The Body ◽  
Cerebral Injury ◽  
Systemic Diseases ◽  
Comprehensive Review ◽  
Distant Organ ◽  
The Brain

Acute brain injuries pose a great threat to global health, having significant impact on mortality and disability. Patients with acute brain injury may develop distant organ failure, even if no systemic diseases or infection is present. The severity of non-neurologic organs’ dysfunction depends on the extremity of the insult to the brain. In this comprehensive review we sought to describe the organ-related consequences of acute brain injuries. The clinician should always be aware of the interplay between central nervous system and non-neurological organs, that is constantly present. Cerebral injury is not only a brain disease, but also affects the body as whole, and thus requires holistic therapeutical approach.

scholarly journals Adult Presentation of Dyke-Davidoff-Masson Syndrome: A Case Report

2016 ◽  
Vol 8 (1) ◽  
pp. 20-26 ◽  
Author(s):  
Ujjawal Roy ◽  
Ajay Panwar ◽  
Adreesh Mukherjee ◽  
Debsadhan Biswas
Keyword(s):  
Mental Retardation ◽  
Rare Disease ◽  
Medical Literature ◽  
Facial Asymmetry ◽  
Rare Entity ◽  
Radiological Findings ◽  
Cerebral Hemiatrophy ◽  
Long Duration ◽  
Frontal Sinuses ◽  
Adult Presentation

Dyke-Davidoff-Masson syndrome (DDMS) is a rare disease which is clinically characterized by hemiparesis, seizures, facial asymmetry, and mental retardation. The classical radiological findings are cerebral hemiatrophy, calvarial thickening, and hyperpneumatization of the frontal sinuses. This disease is a rare entity, and it mainly presents in childhood. Adult presentation of DDMS is unusual and has been rarely reported in the medical literature. Key Messages: DDMS is a rare disease of childhood. However, it should be kept in mind as a diagnostic possibility in an adult who presents with a long duration of progressive hemiparesis with seizures and mental retardation. Cerebral hemiatrophy, calvarial thickening, and hyperpneumatization of the frontal sinuses are diagnostic for this illness on brain imaging.

scholarly journals Clinical Features of Traumatic Brain Injury in Various Kinds of Brain Damage

2019 ◽  
Vol 8 (3) ◽  
pp. 295-301
Author(s):  
Y. B. Vasilyeva ◽  
A. E. Talypov ◽  
S. S. Petrikov
Keyword(s):  
Traumatic Brain Injury ◽  
Differential Diagnosis ◽  
Brain Injury ◽  
Brain Damage ◽  
Pupil Size ◽  
Muscle Tone ◽  
Neurological Status ◽  
Neurologic Examination ◽  
Different Types ◽  
The Brain

Various circumstances of the injury lead to various types of brain damage. The main types of destructive effects are countracoup effect and acceleration/deceleration. The high intensity injuring force creates conditions for occurrence of combinations of different types of damage leading to aggravation of pathological processes caused by trauma, complication of clinical picture, difficulties of diagnosis and treatment, prolongation of hospital stay, and requires an additional methods of research and treating the injured. Finding the genesis of symptoms observed upon neurologic examination, and especially the differential diagnosis between primary and secondary lesions of the brain stem are nessesary to choose the emergency care for victims with severe traumatic brain injury, as well as to forecast the outcomes of treatment. The dynamics of neurological symptoms (level of wakefulness, pupil size, eyeball mobility, muscle tone and limb movement disorders, pathological plantar reflexes) have significant differences in patients with various types of brain damage, which makes a regular assessment of neurological status extremely important in these patients.

Confronting the grey zone after severe brain injury

2019 ◽  
Vol 3 (6) ◽  
pp. 707-711 ◽  
Author(s):  
Andrew Peterson ◽  
Adrian M. Owen
Keyword(s):  
Brain Injury ◽  
Ethical Issues ◽  
Vegetative State ◽  
Clinical Care ◽  
Grey Zone ◽  
Severe Brain Injury ◽  
New Methods ◽  
Legal Decision Making ◽  
Technological Developments ◽  
The Brain

In recent years, rapid technological developments in the field of neuroimaging have provided several new methods for revealing thoughts, actions and intentions based solely on the pattern of activity that is observed in the brain. In specialized centres, these methods are now being employed routinely to assess residual cognition, detect consciousness and even communicate with some behaviorally non-responsive patients who clinically appear to be comatose or in a vegetative state. In this article, we consider some of the ethical issues raised by these developments and the profound implications they have for clinical care, diagnosis, prognosis and medical-legal decision-making after severe brain injury.

Lessons Learned From Coaching Postsecondary Students With Traumatic Brain Injury

2020 ◽  
Vol 5 (1) ◽  
pp. 88-96
Author(s):  
Mary R. T. Kennedy
Keyword(s):  
College Students ◽  
Traumatic Brain Injury ◽  
Brain Injury ◽  
Sense Of Self ◽  
Scientific Evidence ◽  
Sudden Onset ◽  
Lessons Learned ◽  
Speech Language Pathologists ◽  
The Brain ◽  
Exhaustive List

Purpose The purpose of this clinical focus article is to provide speech-language pathologists with a brief update of the evidence that provides possible explanations for our experiences while coaching college students with traumatic brain injury (TBI). Method The narrative text provides readers with lessons we learned as speech-language pathologists functioning as cognitive coaches to college students with TBI. This is not meant to be an exhaustive list, but rather to consider the recent scientific evidence that will help our understanding of how best to coach these college students. Conclusion Four lessons are described. Lesson 1 focuses on the value of self-reported responses to surveys, questionnaires, and interviews. Lesson 2 addresses the use of immediate/proximal goals as leverage for students to update their sense of self and how their abilities and disabilities may alter their more distal goals. Lesson 3 reminds us that teamwork is necessary to address the complex issues facing these students, which include their developmental stage, the sudden onset of trauma to the brain, and having to navigate going to college with a TBI. Lesson 4 focuses on the need for college students with TBI to learn how to self-advocate with instructors, family, and peers.

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