Tailgut Cyst (Retrorectal Hamartoma): Report of a Pediatric Case

2007 ◽  
Vol 10 (4) ◽  
pp. 325-327 ◽  
Author(s):  
M. Laura Galluzzo ◽  
Marcela Bailez ◽  
Aixa Reusmann ◽  
Roberto Gonzalez ◽  
M.T.G. de Dávila
Keyword(s):  
Fibrous Tissue ◽  
Surgical Excision ◽  
Lumbar Pain ◽  
Presacral Space ◽  
Tailgut Cyst ◽  
Concomitant Disease ◽  
Complete Excision ◽  
Retrorectal Space ◽  
Congenital Lesion ◽  
Complete Surgical Excision

Tailgut cyst (TGC) is an uncommon congenital lesion, located in the retrorectal/presacral space. We report a 12-year-old girl with lumbar pain and a retrorectal mass. She had mental retardation, hypothyroidism, didelphus uterus, sacrum vertebrae, and coccyx agenesis, without chromosomic anomalies. Three surgeries were performed for the complete excision of the tumor. Microscopically, the mass consisted of cystic spaces lined by a wide variety of epithelia and a stroma composed of fibrous tissue containing bundles of smooth muscle fibers. According to these findings, the diagnosis was TGC. This is a rare congenital lesion that usually presents as a multiloculated cyst in the retrorectal space of young women; TGC requires complete surgical excision to prevent recurrences, infections, and malignant transformation. This case was unique because of the association of TGC with other malformative features and concomitant disease in a pediatric patient.

A rare presentation of abdominal pain as cloacal cyst: A case report

2021 ◽  
Vol 2 (2) ◽  
Author(s):  
Fakhr-o-sadat Anaraki ◽  
◽  
Mehdi Tavallaei ◽  
Hasti Zarfeshani ◽  
◽  
...  
Keyword(s):  
Computed Tomography ◽  
Abdominal Pain ◽  
Surgical Excision ◽  
Tailgut Cyst ◽  
Congenital Disease ◽  
Rare Presentation ◽  
Complete Excision ◽  
Retrorectal Space ◽  
Midline Laparotomy ◽  
Complete Surgical Excision

Retrorectal hamartoma or tailgut cyst is an uncommon congenital disease of presacral and retrorectal space and is embryologically part of some forms of enteric cysts. The rarity of this disease leads to difficulty in diagnosis and surgical management. Complete surgical excision is the treatment of choice for tailgut cysts. We present a case of a 40-year-old man, who presented to us with abdominal pain for four months, which had become more prominent while defecation and after eating. Abdominal computed tomography demonstrated a cyst in the lower interperitoneal cavity. Surgical complete excision of the mass was done with midline laparotomy. Histopathology confirmed cloacal cyst.

scholarly journals Malignancy within a Tail Gut Cyst: A Case of Retrorectal Carcinoid Tumour

2014 ◽  
Vol 2014 ◽  
pp. 1-4 ◽  
Author(s):  
A. A. Abukar ◽  
B. J. Parcell ◽  
C. B. Lim ◽  
P. V. Patil ◽  
A. Ramsanahie ◽  
...  
Keyword(s):  
Differential Diagnosis ◽  
Neuroendocrine Tumour ◽  
Carcinoid Tumour ◽  
Surgical Excision ◽  
Presacral Space ◽  
Tailgut Cyst ◽  
Diagnostic Strategy ◽  
Rectal Pain ◽  
Ct Guided ◽  
Complete Surgical Excision

Purpose.Tailgut cysts with malignant transformation are rare entities. We discuss the diagnostic strategy and treatment of a malignancy within a tailgut cyst.Methods.In this study we report on the case of a 61-year-old man with a malignant neuroendocrine tumour arising within a tailgut cyst and an overview of the literature emphasising the histopathological characteristics and differential diagnosis.Results.Our patient presented with lower back pain, rectal pain, and increased urgency of defecation. MRI scan and CT-guided biopsy on histological analysis revealed a diagnosis of carcinoid tumour of the presacral space. The patient subsequently underwent an abdominoperineal excision of the rectum.Conclusions.This case highlights the importance of tailgut cysts as a differential diagnosis of presacral masses. It is a rare congenital lesion developing from remnants of the embryonic postanal gut and is predominantly benign in nature. Approximately half of cases remain asymptomatic; therefore, diagnosis is often delayed. Magnetic resonance imaging is the investigation of choice and an awareness of the possibility of malignant potential is critical to avoiding missed diagnosis and subsequent morbidity. Complete surgical excision allows accurate diagnosis, confirmation of oncological clearance, and prevention of mortality.

scholarly journals Juvenile Nasopharyngeal Angiofibroma - Excision Through Lateral Rhinotomy and Sublabial Approach - A Case Report

1970 ◽  
Vol 20 (1) ◽  
pp. 78-81
Author(s):  
NK Sinha ◽  
MH Rashid ◽  
MM Shaheen ◽  
DC Talukder ◽  
MAY Fakir ◽  
...  
Keyword(s):  
Surgical Excision ◽  
Complete Removal ◽  
Definitive Treatment ◽  
Surgical Approaches ◽  
Complete Excision ◽  
Nasopharyngeal Angiofibroma ◽  
Male Adolescents ◽  
Large Size ◽  
Complete Surgical Excision ◽  
Sublabial Approach

Juvenile angiofibroma is a rare hypervascular, locally aggressive benign tumour which is exclusively found in the nose and paranasal sinuses of male adolescents. The definitive treatment for this tumour is complete surgical excision. Different surgical approaches are used for complete excision. Most recent development is excision of the tumour using endoscopes. But in certain cases with large size and different extensions, open transfacial approaches are the choice for complete removal and for less operative bleeding, which are the main challenges for surgical excision of this tumour. DOI: http://dx.doi.org/10.3329/jdmc.v20i1.8587 J Dhaka Med Coll. 2011; 20(1) :78-81

scholarly journals Orbital Schwannoma

2020 ◽  
Vol 81 (04) ◽  
pp. 376-380
Author(s):  
Mark B. Chaskes ◽  
Mindy R. Rabinowitz
Keyword(s):  
Surgical Excision ◽  
Treatment Goals ◽  
Resonance Imaging ◽  
Recurrence Rates ◽  
Complete Excision ◽  
Representative Case ◽  
Presenting Symptoms ◽  
Complete Surgical Excision ◽  
Imaging Characteristics ◽  
Magnetic Resonance Imaging Mri

AbstractOrbital schwannomas are rare neoplasms of the orbit. The presenting symptoms are often nonspecific. Classic imaging characteristics seen on magnetic resonance imaging (MRI) and orbital ultrasound can be useful to help aid in the diagnosis of orbital schwannoma. When diagnosed, the goal of treatment is complete surgical excision. The location of the tumor within the orbit dictates which surgical approach would provide the best exposure. When complete excision is achieved, recurrence rates are very low.This article addresses the etiology, patient population, presentation, natural history, and differential diagnosis of orbital schwannomas. Imaging characteristics and histopathologic subtypes are reviewed. Treatment goals, approaches, and specialties involved in the management of these patients is discussed. Finally, a representative case is presented.

A MODIFIED PERIUNGUAL APPROACH FOR TREATMENT OF SUBUNGUAL GLOMUS TUMOUR

Hand Surgery ◽  
2007 ◽  
Vol 12 (03) ◽  
pp. 217-221 ◽  
Author(s):  
S. T. Fong ◽  
Y. L. Lam ◽  
Y. C. So
Keyword(s):  
Surgical Excision ◽  
Glomus Tumour ◽  
Complete Excision ◽  
Nail Bed ◽  
Peripheral Lesion ◽  
Nail Deformity ◽  
Complete Surgical Excision ◽  
Central Lesions

Subungal glomus tumours are uncommon; the only treatment is complete surgical excision. Transungual approach is often preferred; however, secondary nail deformity may occur. Lateral periungual approach is used to avoid this complication, but this approach provides limited exposure and is used for peripheral lesion only. We describe a modified periungual approach which can be applied to central lesions. This approach can provide adequate exposure for complete excision of the subungual tumour while avoiding incision of the nail bed.

Gliomas of the optic nerve or chiasm

1988 ◽  
Vol 68 (1) ◽  
pp. 85-98 ◽  
Author(s):  
Ellsworth C. Alvord ◽  
Steven Lofton
Keyword(s):  
Optic Nerve ◽  
Growth Rates ◽  
Surgical Excision ◽  
Sufficient Information ◽  
Low Grade ◽  
Complete Excision ◽  
Content Type ◽  
Complete Surgical Excision ◽  
Table Analysis ◽  
Fine Print

✓ A review of the literature revealed 623 cases of optic gliomas with sufficient information to permit actuarial (life-table) analysis concerning the prognosis of this disease by the patients' age, tumor site, treatment, and presence of concomitant neurofibromatosis or extension into the hypothalamus or ventricle. All of these factors are important. The development of mathematical models led to the conclusion that these tumors, generally regarded histologically as low-grade astrocytomas, actually have a very wide but continuous range of growth rates. Some grow rapidly enough to be explained by simple exponential doubling at a constant rate, but most behave as though their growth decelerates. Decelerating growth rates make comparisons of various groups of patients difficult. No support is found for the classical hypothesis that some may be hamartomas. Inadequately treated gliomas of the optic nerve or chiasm bear about the same poor prognosis. However, tumors of the optic nerve (intracranial as well as intraorbital) have an excellent prognosis following complete surgical excision and only a slightly poorer prognosis following irradiation. About 5% of optic nerve gliomas recur in the chiasm following “complete” intraorbital excision. Patients with neurofibromatosis have about twice the recurrence rate following complete excision of an intraorbital glioma. Optic chiasmal gliomas appear to respond to irradiation with doses above 4500 rads. Patients with neurofibromatosis have about the same prognosis as patients without neurofibromatosis following irradiation of a chiasmal glioma.

scholarly journals Duodenal Duplication Cyst in Close Proximity of Ampulla of Vater: A Surgical Challenge

2018 ◽  
Vol 7 (3) ◽  
pp. 39
Author(s):  
Nahla Kechiche ◽  
Rabeb Farhani ◽  
Rachida Lamiri ◽  
Abdelatif Nouri
Keyword(s):  
Surgical Excision ◽  
Ampulla Of Vater ◽  
Duplication Cyst ◽  
Complete Excision ◽  
Duodenal Duplication ◽  
Complete Surgical Excision ◽  
Close Proximity ◽  
Duodenal Duplication Cyst ◽  
Upper Gastrointestinal ◽  
The Ideal

Prompt preoperative diagnosis of duodenal duplication cyst is uncommon owing to its extreme rarity. The ideal treatment of intestinal duplication cyst is complete surgical excision, though in few cases, due to the proximity to the bilio-pancreatic duct, the complete excision is not possible. We herein present an infant presenting with bilious vomiting starting few days after birth. Ultrasonography and CT scan provided the diagnosis of the duplication cyst in relation to duodenum. A successful surgical management by a subtotal excision was done. Although duodenal duplication is seldom seen, it should be considered in differential diagnoses of upper gastrointestinal tract (GIT) occlusion.

scholarly journals Radio-pathological correlation of a retroperitoneal teratoma in a 2-year-old girl: a case report

2021 ◽  
Vol 7 (2) ◽  
pp. 28-31
Author(s):  
Deki Choden ◽  
Kinley Sangay Dorji ◽  
Sonam Choden
Keyword(s):  
Case Report ◽  
Surgical Excision ◽  
Abdominal Distension ◽  
Imaging Findings ◽  
Complete Excision ◽  
Palpable Mass ◽  
Retroperitoneal Teratoma ◽  
Retroperitoneal Neoplasm ◽  
Complete Surgical Excision ◽  
Retroperitoneal Tumors

ABSTRACTRetroperitoneal teratoma is a extragonadal germ cell tumor comprising 5% of all teratomas in children, and the third most common retroperitoneal neoplasm in children. This is a case report of a 2 years old girl who presented with abdominal distension and palpable mass. The imaging findings of the mass was characteristic of retroperitoneal teratoma which was confirmed by histopathology report following complete excision. Retroperitoneal tumor is an uncommon tumor in children with characteristic imaging findings. Computed tomography is mainly used to evaluate the extent of the disease. Most of the retroperitoneal tumors are benign and curable with complete surgical excision.

scholarly journals Management mature sacrococcygeal teratoma: a case report

2019 ◽  
Vol 7 (10) ◽  
pp. 3891
Author(s):  
Budiman Ritonga ◽  
Kadek Deddy Ariyanta ◽  
I. Made Darmajaya
Keyword(s):  
Surgical Excision ◽  
Sacrococcygeal Teratoma ◽  
Posterior Aspect ◽  
Complete Excision ◽  
Primary Wound Closure ◽  
Complete Surgical Excision ◽  
Pelvic Tumors ◽  
Multiple Classification ◽  
Sacrococcygeal Region ◽  
Pregnancy And Delivery

Mature sacrococcygeal teratoma (SCT) are uncommon neoplasm comprised of mixed elements derived from three germ layers. They attract attention because of their gross appearance and bizarre histology. Tumor of the sacrococcygeal region, referred to as sacrococcygeal teratomas (SCTs) in most reports, generally present in two distinct fashions: neonates with large predominately external lesions, which are detected in utero or at birth and are rarely malignant; and older infants and children who present with primarily hidden pelvic tumors with a much higher rate of malignancy. Sacrococcygeal teratomas are the most common extragonadal tumor in neonates, accounting for up to 70% of all teratomas in childhood. A 3 to 4:1 female to male ratio is generally reported. Surgical resection remains the mainstay of therapy and recurrence is rare following complete excision. A 14 years old girl was presented to us by her parents with a mass at the buttock since birth. She was delivered at home by traditional midwife after a term, unsupervised pregnancy to a 35 years old woman. Both pregnancy and delivery were uneventful. Direct rectal examination revealed a mass has displaced the recto-sigmoid anteriorly. The CT scan revealed a heterogenous mass with a solid, cystic, and multiple classification density at the anterior of coccygeus bone, and push the coccygeus to the posterior. The mass infiltrated the subcutis, and attached to the posterior aspect of rectum. A 14 years old girl presented by mature SCT since newborn comprising ectoderm, mesoderm, and endoderm tissue. She had a complete surgical excision (including coccygectomy) with primary wound closure. A complete surgical excision remains the mainstay of therapy of mature SCT.

scholarly journals A Rare Cause of Low Back Pain: Report of a Tailgut Cyst

2012 ◽  
Vol 2012 ◽  
pp. 1-4 ◽  
Author(s):  
E. A. Joyce ◽  
D. O. Kavanagh ◽  
D. C. Winter
Keyword(s):  
Low Back Pain ◽  
Back Pain ◽  
Surgical Excision ◽  
Fistula Formation ◽  
Tailgut Cyst ◽  
Low Back ◽  
Mri Imaging ◽  
Retrorectal Space ◽  
Developmental Abnormalities ◽  
History Of

Tailgut cysts, also known as retrorectal cystic hamartomas, are rare developmental abnormalities that typically occur in the retrorectal space. They are believed to arise from remnants of the embryonic hindgut (Hjermstad and Helwig, 1988). They can present as incidental findings during routine examination but over half of patients are thought to present with symptoms. MRI has become the modality of choice to image these frequently misdiagnosed cysts. Biopsy is not recommended. Complete intact surgical excision is advised to avoid the potential complications of these cysts which include infection, fistula formation, and the possibility of malignant transformation (Hjermstad and Helwig (1988), Mathis et al. (2010)). We describe the case of a 46-year-old female who presented with a 6-month history of low back pain. CT and MRI imaging demonstrated a complex retrorectal lesion with supralevator and infralevator components. This was removed using a combined transperineal and transabdominal approach. Histology confirmed a tailgut cyst.

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