scholarly journals An interesting case of Cruveilhier-Baumgarten disease: Persistent left umbilical vein in a 50 year old man

2011 ◽  
Vol 2 (1) ◽  
pp. 63-64
Author(s):  
Anubhav Thukral ◽  
Vaibhav Srivastava ◽  
Amit Nandan Dhar Dwivedi ◽  
Manish Mishra ◽  
Kamlaker Tripathi

A middle aged man of 50 years presented with features of portal hypertension without any features of liver decompensation or cirrhosis, found to have abnormal flow pattern in peri-umbilical vein, confirmed by Doppler to have a patent left umbilical vein. This represents a very treatable cause of portal hypertension as ligation of vein may result in complete reversal of disease process. The case also outlines importance of routine general examination like of seeing the direction of flow in periumbilical veins even in obvious cases of portal hypertension that helped us in detection of this case. Key Words: Portal hypertension; Periumbilical vein DOI: 10.3126/ajms.v2i1.3780 Asian Journal of Medical Sciences 2 (2011) 63-64

2019 ◽  
Vol 98 (8) ◽  
pp. 326-327 ◽  

Introduction: The umbilical vein can become recanalised due to portal hypertension in patients with liver cirrhosis but the condition is rarely clinically significant. Although bleeding from this enlarged vein is a known complication, the finding of thrombophlebitis has not been previously described. Case report: We report the case of a 62-year-old male with a history of liver cirrhosis due to alcoholic liver disease presenting to hospital with epigastric pain. A CT scan of the patient’s abdomen revealed a thrombus with surrounding inflammatory changes in a recanalised umbilical vein. The patient was managed conservatively and was discharged home the following day. Conclusion: Thrombophlebitis of a recanalised umbilical vein is a rare cause of abdominal pain in patients with liver cirrhosis.


2019 ◽  
pp. 35-40
Author(s):  
Thi Nhung Nguyen ◽  
Trung Nam Phan ◽  
Van Huy Tran

Bacground: Variceal bleeding is a severe complication of portal hypertension due to cirrhosis with high rate of motality, hence, predicting early rebleeding and mortality in cirrhotic patients with acute variceal bleeding is vital in clinical practice. Objectives: To evaluate the prognostic value of the combination of AIMS65 and MELD scores in predicting first 5 days in-hospital rebleeding and mortality in cirrhotic patients with acute variceal bleeding. Materials and Methods: 44 cirrhotic patients with acute variceal bleeding hospitalized at Hue Central Hospital. MELD and AIMS65 scores were calculated within the first 24 hours and monitoring rebleeding and mortality in the first 5 days in these patients. Results: AIMS65, MELD scores can predict first 5 days rebleeding and mortality with AUROC are 0.81, 0.69 and 0.92, 0.95, respectively. Combination of AIMS65 and MELD scores can predict first 5 days in hospital rebleeding with AUROC is 0.84, sensitivity 83.3%, specificity 81.6% (p<0.001) and mortality with AUROC is 0.96, sensitivity 100%, specificity 92.7% (p<0.001). Conclusions: The combination of AIMS65 and MELD scores increased the sensitivity, specificity and prognostic value in predicting first 5 days in-hospital rebleeding and mortality in cirrhotic patients with acute variceal bleeding in compare to each single scores. Key words: AiMS65 score, MELd, acute variceal bleeding


2021 ◽  
Vol 4 (Supplement_1) ◽  
pp. 261-263
Author(s):  
L Tsang ◽  
J Abraldes ◽  
E Wiebe ◽  
G S Sandha ◽  
S van Zanten

Abstract Results A 41-year old Asian male, who immigrated to Canada many years ago, and who had previously been successfully treated for Helicobacter pylori infection underwent gastroscopy for investigation of dyspepsia. His gastroscopy was normal except for a large subepithelial abnormality that was noted close to the gastroesophageal junction. Routine gastric biopsies from the antrum and body were normal. Subsequent endoscopic ultrasound revealed flow through the anechoic tortuous lesion and confirmed it was a very large isolated gastric varix type 1. Abdominal CT scan revealed chronic occlusion of the portal vein, splenic vein, and the portal confluence with extensive collateralization in the upper abdomen. There was complete cavernous transformation of the portal vein. Of the numerous varices in the upper abdomen, a very large varix drained into the left renal vein and indented into the posterior wall of the fundus of the stomach which accounted for the endoscopic finding. Multiple mesenteric veins were identified that connected to varices adjacent to the inferior aspect of the pancreas and duodenum. Notably, there was no evidence of cirrhosis or chronic pancreatitis. Liver enzymes, albumin, and INR were normal. Further collateral history revealed that he was hospitalized as a neonate for pneumonia with catheterization of the umbilical vein, which is known to be associated with thrombosis of the portal vein. Conclusions Detection of congenital absence of the portal vein (CAPV) is recognized more often due to advances in diagnostic imaging. Radiologically, the absence of the portal vein in CAPV is distinguished from portal vein thrombosis by the lack of venous collaterals or sequalae of portal hypertension, such as ascites or splenomegaly. A more gradual thrombosis of the portal vein may permit collaterals to develop without acute changes and is not equivalent to portal vein aplasia or agenesis as intrahepatic bile ducts are normal. The gold standard for diagnosis of CAPV is histologic absence of the portal vein in the liver on catheter angiography. CAPV is associated with abnormal embryologic development of the portal vein and frequently presents with complications of portal hypertension or portosystemic encephalopathy or the sequalae of venous shunts, hepatic or cardiac abnormalities found on imaging. Our case is an incidentally discovered absence of the portal venous system due to chronic thrombosis with extensive collateralization and an enlarged gastric varix protruding into the proximal stomach. It is well documented that canalization of the umbilical vein in infancy is associated with portal vein thrombosis, with incidences up to 68%. This case highlights the importance of eliciting a childhood hospitalization history in cases of non-cirrhotic portal hypertension. Funding Agencies None


2019 ◽  
Vol 05 (03) ◽  
pp. e82-e86 ◽  
Author(s):  
J. M. V. Amarjothi ◽  
Villalan Ramasamy ◽  
Jeyasudhahar Jesudasan ◽  
O. L. NaganathBabu

AbstractCholedochal cysts (CDC), are rare congenital dilations involving the extra hepatic biliary apparatus with or without dilation of the intrahepatic bile ducts. They are conventionally classified into five types. A new type, type VI, causing dilation of the cystic duct between the neck of the gall bladder and the common hepatic duct (CHD) has been described in medical literature which is the rarest of all these subtypes. They are commonly observed in middle aged females and are mostly symptomatic. Most of these cysts need magnetic resonance cholangiopancreatography (MRCP) for accurate diagnosis. Treatment options for these lesions are not well defined but range from simple cholecystectomy to complete excision of the entire bile duct and biliary reconstruction, as there is a concern of malignant transformation in these cysts. Hence, these rare cysts, though rare, must be borne in mind when dealing with suspicious cystic lesions in the biliary tract. Here, we present an interesting case of such a rare cyst and its management in a middle aged woman.


1970 ◽  
Vol 6 (2) ◽  
pp. 64-66 ◽  
Author(s):  
Rajat Roy ◽  
Anil Bhattarai ◽  
Prativa Shrestha ◽  
Upama Paudel ◽  
Sudip Parajuli

One 11 year old female attended dermatology OPD of College of Medical Sciences, Bharatpur. She was undergoing treatment with Dapsone for one month for Borderline lepromatous leprosy. There was history of dry scales for 3 weeks over trunk, buttock, face, back and lower extremities suggestive of Exfoliative Dermatitis. The patient was treated with Prednisolone with supportive therapy for one month. Recovery is good. Key words: Dermatology; lepromatous leprosy; exfoliative dermatitis. DOI: 10.3126/jcmsn.v6i2.3621 Journal of college of Medical Sciences-Nepal, 2010, Vol.6, No-2, 64-66


2021 ◽  
Vol 2021 ◽  
pp. 1-5
Author(s):  
Abdullah Ghali ◽  
Luis Salazar ◽  
David Momtaz ◽  
Gautham Prabhakar ◽  
Preston Richier ◽  
...  

Femoral-facial syndrome (FFS) is an exceedingly rare congenital disorder of unknown etiology related to maternal diabetes during pregnancy. It is characterized by variations of bilateral femoral hypoplasia and facial anomalies. We discuss an interesting case of a 3-year-old girl with FFS with an extensive surgical history who presented to a pediatric orthopaedic clinic with ankle pains and absent femurs. As this disease process is not frequently encountered, it is imperative for the practicing clinician to be aware of the various presentations. In this study, we discuss the different orthopaedic presentations in the literature and discuss various management recommendations.


2011 ◽  
Vol 2 (2) ◽  
pp. 110-112
Author(s):  
Anil T Kumar ◽  
Sudhir U ◽  
Bakul Gupta ◽  
Punith Kempegowda

Primary biliary cirrhosis is an autoimmune disorder affecting exclusively liver. There has been association of this autoimmune disease with various other neurological counterparts, but Opsoclonus-Myoclonus Syndrome in conjunction with primary biliary cirrhosis is unreported yet. Opsoclonus-Myoclonus Syndrome is a disorder of eye movement with an ill-defined etiology. It may be idiopathic or present as a paraneoplastic manifestation with a low response to therapeutic modalities. We present a case of primary biliary cirrhosis that developed Opsoclonus-Myoclonus Syndrome during an exaggeration of disease process which responded well to intravenous corticosteroids. Knowledge of association of Primary biliary cirrhosis with Opsoclonus-Myoclonus Syndrome and its good response to treatment in this setting will help in reducing morbidity in similar situations. Key Words: Primary biliary cirrhosis; Opsoclonus-Myoclonus Syndrome DOI: http://dx.doi.org/10.3126/ajms.v2i2.3536 Asian Journal of Medical Sciences 2 (2011) 110-112


1970 ◽  
Vol 6 (2) ◽  
pp. 18-23 ◽  
Author(s):  
S Kumar ◽  
AR Singh ◽  
R Takhelmayum ◽  
P Shrestha ◽  
JN Sinha

The prevalence of hyperuricemia has been increasing in both developed and developing countries. The purpose of present study was to know the prevalence of hyperuricemia in the population of Chitwan district as well as to compare the prevalence of hyperuricemia between Mongolian and non-Mongolian races of Chitwan district, who had attended the College of Medical Sciences and Teaching Hospital, Bharatpur, Nepal during the period of January 1999 to December 2003. In this study 3794 subjects were investigated for serum uric acid level (SUA). Hyperuricemia is defined as SUA more than 7mg/dl for males and menopausal women and 6mg/dl for pre-menopausal females. SUA was estimated by Caraway method in digital colorimeter. Overall prevalence was 21.42%; the condition was more common in men than women (26.78% vs. 16.82%; p<0.001). The prevalence was higher in Mongolian than non Mongolian both in males and females (24.50 % Vs 21.06%; p>0.05). Key words: Hyperuricemia; SUA; digital colorimeter DOI: 10.3126/jcmsn.v6i2.3612   Journal of college of Medical Sciences-Nepal, 2010, Vol.6, No-2, 18-23


1970 ◽  
Vol 6 (2) ◽  
pp. 38-41 ◽  
Author(s):  
PK Chhetri ◽  
SK Malla

Congenital ureterocele is an uncommon cause of urinary tract obstruction in the young patient. Though they may be diagnosed in utero, some however present in the first few decades of life. Most are associated with a duplex collection system with complete ureteral duplication. Here we report a case of single system ureterocele associated with only a single ureter. Key words: ureterocele; urinary tract obstruction. DOI: 10.3126/jcmsn.v6i2.3615 Journal of college of Medical Sciences-Nepal, 2010, Vol.6, No-2, 38-41


Sign in / Sign up

Export Citation Format

Share Document