scholarly journals Sirenomelia: A Case Report

2018 ◽  
Vol 56 (214) ◽  
pp. 974-976
Author(s):  
Pramod Kattel

Sirenomelia is primarily a congenital anomaly where a normally paired lower limb is replaced by a single midline limb and is characterized by single umbilical artery. Such cases though considered rare do occur at our set-up and to make health workers aware regarding the condition, so that they can be managed well when encountered, lays the importance of reporting such case. A referred case of Sirenomelia from Dhading district hospital was presented to Emergency department of Paropakar Maternity and Women’s Hospital on 6th March 2016 of 18 year “Young Primigravida at 34 week and 5 days of gestation in second stage of labor” following ultrasonography diagnosis for better management. After confirming the diagnosis, preterm vaginal delivery was performed with a live baby of 1250 gm consisting of multiple congenital anomalies and poor Apgar score. Such cases do occur at our set-up so that if anomaly scanning is done routinely, 

2018 ◽  
Vol 08 (04) ◽  
pp. e328-e331 ◽  
Author(s):  
Nadereh Taee ◽  
Fariba Tarhani ◽  
Mojgan Goodarzi ◽  
Mohammad Safdari ◽  
Amir Bajelan

AbstractThe mermaid syndrome (sirenomelia) is an extremely rare anomaly, an incidence of 1 in 100,000 births, in which a newborn born with legs joined together featuring a mermaid-like appearance (head and trunk like humans and tail like fish), and in most cases die shortly after birth. Gastrointestinal and urogenital anomalies and single umbilical artery are clinical outcome of this syndrome. There are two important hypotheses for pathogenesis of mermaid syndrome: vitelline artery steal hypothesis and defective blastogenesis hypothesis. The cause of the mermaid syndrome is unknown, but there are some possible factors such as age younger than 20 years and older than 40 years in mother and exposure of fetus to teratogenics. Here, we introduced 19-year-old mother's first neonate with mermaid syndrome. The mother had gestational diabetes mellitus and neonate was born with single lower limb, ambiguous genitalia, and thumb anomalies, and 4 days after birth, the neonate died due to multiple anomalies and imperforated anus.


1970 ◽  
Vol 2 (2) ◽  
pp. 78-80
Author(s):  
Ashma Rana ◽  
Geeta Gurung ◽  
Jitendra Pariyar ◽  
Sunil Pokharel ◽  
Shilu Adhikari

A woman with a history of laparotomy and corrective abdominal surgery for acute puerperal uterine inversion reverted by division of the inversion ring anteriorly "Dobbins's operation" subsequently was successful to undergo assisted vaginal breech delivery arriving at second stage of labor warranting, manual removal of placenta which was complied with the management of PPH. This case is reported because of the rarity of uterine inversion itself in the first place. Next because of the conception taking place spontaneously after morbid puerperal period and then the pregnancy advancing to term: all the management beginning from correction of uterine inversion to retained placenta being handled in the same facility a rare event too in our set up. Key words: Uterine inversion and subsequent birth, manual removal of the placenta.      doi:10.3126/njog.v2i2.1462 N. J. Obstet. Gynaecol 2007 Nov-Dec; 2 (2): 78 - 80


2017 ◽  
Vol 34 (2) ◽  
pp. 138-145
Author(s):  
Amy Bildner ◽  
Daniel Jackson

This case study describes an obstetrical patient who presented for a routine second-trimester morphology sonogram in which the fetus was found to have arthrogryposis multiplex congenita. Other abnormalities visualized included a single umbilical artery, hypoplastic nasal bone, polyhydramnios, and poorly visualized lateral ventricles. Amniocentesis demonstrated a normal microarray with a negative result for cytomegalovirus and toxoplasmosis. This case study highlights the utility of prenatal sonography to identify functional abnormalities of the fetal musculoskeletal system.


2021 ◽  
Vol 4 (1) ◽  
pp. 32-36
Author(s):  
Sari Pratiwi Apidianti

Childbirth is a very stressful process because it involves two lives that must be saved, namely the mother and the child in the womb, so that this birthing mother needs a lot of preparation in the labor process starting from physical, mental and preparations that will be brought during childbirth. Based on a preliminary study in January, it was found that 80% of mothers gave birth who did not know the stage II labor process. The purpose of this study was to describe the knowledge of mothers giving birth about the stage II labor process at the Grujugan Polindes, Larangan District, Pamekasan Regency. This type of research is descriptive. The population was all pregnant women trimeser III (> 36 weeks) in March-May 2013 at the Grujugan Polindes, Larangan District, Pamekasan Regency, as many as 30 respondents by means of non probability sampling, namely total sampling. The variable of this study is the knowledge of the mother about the second stage of labor. Based on the research results, it is known that almost half of the 30 respondents (47%), namely 14 respondents have sufficient knowledge. Efforts can be made to overcome these problems. So health workers must always improve counseling and always provide information both verbally and from print and video media, as well as teach maternity and pregnant women about the process and procedures for childbirth so that mothers can apply it. .


Author(s):  
Reetika Joshi ◽  
Veino Kuveio Duomai ◽  
Bianchi Sangma

Sirenomelia sequence or mermaid syndrome is a rare congenital structural anomaly characterized by different degrees of fusion of lower limbs, thoracolumbar spinal anomalies, sacrococcygeal agenesis, genitourinary and anorectal atresia. The incidence of sirenomelia is 0.8-1 cases/ 105 births with male to female ratio being 3:1. A malformations patient with 40 weeks of gestation admitted with complaints of decreased fetal movements for one week. An emergency C-section was done in view of term pregnancy with severe oligohydramnios and intrauterine growth restriction with poor bishop’s score. A 1.9 kg live baby with fused lower limbs was delivered. The new born baby had narrow chest, fused both lower limbs and feet with 11 toes, small rudimentary external genitalia, imperforate anus and single umbilical artery. The baby also had features of potter’s facies including low set large ears, receding chin and prominent infraorbital folds. Sirenomelia is a rare fatal congenital anomaly. Early detection by prenatal ultrasound will help in timely termination of pregnancy.


2020 ◽  
Vol 7 (1) ◽  
pp. 21-26
Author(s):  
Isofi Laspiriyanti ◽  
Lina Puspitasari

Background: Stiff perineum is caused by the nerves of the perineal muscle contain pyruvic acidwhich enters the mitochondria which are converted into lactic acid. Lactic acid causes metabolicproblems and shrinks between the perineal muscle cells, so the perineum becomes stiff. Theimpact of a stiff perineum can inhibit the second stage of labor which increases the risk of death tothe fetus and causes damage to the birth canal or laceration. Research Objectives: to accelerate thesecond stage of labor. Research Method: The design of this study uses the case study method. Thesampling method used was non probability sampling through a purposive sampling approach of 3patients. Patients used as participants were maternity patients in Cilacap District Hospital. Datawas collected from January 2 to January 25, 2019. After tabulation with data that has beenanalyzed using analysis of explanation and time series. Results: The study showed there was agreat impact of the Perineum Massage Midwifery Care for the Acceleration of Second Stage ofLabor in Maternity Women. With the results of the first participant the process of acceleratinglabor took place within 15 minutes. In the second participant, the process of labor accelerationtook place within 10 minutes. And in the third participant the process of accelerating labor tookplace within 20 minutes. Conclusion: Thus, that Perineum Massage Care for the Acceleration ofSecond Stage of Labor is really effective.


2015 ◽  
Vol 43 (2) ◽  
Author(s):  
Marcos Javier Cuerva ◽  
Pablo Tobias ◽  
Jose Angel Espinosa ◽  
Jose Luis Bartha

AbstractTo evaluate the accuracy of criteria followed by obstetricians when performing a Kristeller maneuver in cases of prolonged second stage of labor.In this prospective observational study, the station of the fetal head was measured using the angle of progression (intrapartum ultrasound) just prior to the intervention of the managing obstetrician in 52 women with prolonged second stage of labor. The managing obstetricians were blinded to the sonographic results. The decision of performing a Kristeller maneuver was taken by the obstetricians based on digital palpation and their experience. Delivery mode, Apgar score, umbilical artery pH value, episiotomy, perineal tears, bleeding, and time to delivery were recorded.Kristeller maneuver was performed in 36/52 (69.2%) cases. There were no significant differences between the Kristeller and the non-Kristeller group regarding the angle of progression. There were no significant differences between both groups with respect to delivery mode, perineal tears, episiotomy, bleeding, Apgar score, and umbilical artery pH value.Our study failed to define any criteria followed by obstetricians when performing a Kristeller maneuver in cases of prolonged second stage of labor. There was no relation between the angle of progression and the decision to perform a Kristeller maneuver.


1998 ◽  
Vol 5 (1) ◽  
pp. 171A-171A
Author(s):  
E XENAKIS ◽  
J PIPER ◽  
M MCFARLAND ◽  
C SUITER ◽  
O LANGER

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