CORRELATION BETWEEN THE INITIAL-SURGERY AGE WITH THE HIRSCHSPRUNG’S DISEASE PATIENT STOOLING PATTERNS IN ULIN HOSPITAL BANJARMASIN, SOUTH KALIMANTAN, INDONESIA  IN 2012-2015

Background: Hirschsprung's disease may lead to gastrointestinal obstruction if not appropriately treated. The initial-surgery or colostomy is intended to decompress the large bowel, prevent enterocolitis, and the stooling-patterns can be measured after definitive surgery. Objective: To determine the correlation between initial-surgery age with stooling-patterns. Materials and Methods: We performed an analytic observational study in Ulin Hospital in Banjarmasin, South Kalimantan, Indonesia, from November to December 2015 with a total sample of 31 patients. The initial-surgery age was divided into before and after 30 days, while the stooling-patterns were divided into satisfied and not satisfied. Results: There was no significant correlation between initial-surgery age with stooling patterns. Most of the patients, 18/31 (58.1%), underwent initial-surgery after 30 days, and 23/31 (74.2%) had satisfied stooling patterns after surgery. Conclusion: No significant correlation between initial-surgery age and stooling patterns among Hirschsprung's disease patients.

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Definitive surgery for Hirschsprung's disease under 4 months of age is associated with long-term complications: A cohort study

Pediatria Polska ◽

10.1016/j.pepo.2017.06.003 ◽

2017 ◽

Vol 92 (5) ◽

pp. 548-552

Author(s):

Patrycja Sosnowska ◽

Michał Błaszczyński ◽

Sebastian Moryciński ◽

Przemysław Mańkowski

Keyword(s):

Cohort Study ◽

Hirschsprung's Disease ◽

Hirschsprung’S Disease ◽

Definitive Surgery

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A prospective observational study of associated anomalies in Hirschsprung’s disease

Orphanet Journal of Rare Diseases ◽

10.1186/1750-1172-8-184 ◽

2013 ◽

Vol 8 (1) ◽

pp. 184 ◽

Cited By ~ 17

Author(s):

Alessio Pini Prato ◽

Valentina Rossi ◽

Manuela Mosconi ◽

Catarina Holm ◽

Francesca Lantieri ◽

...

Keyword(s):

Observational Study ◽

Hirschsprung's Disease ◽

Prospective Observational Study ◽

Hirschsprung’S Disease ◽

Associated Anomalies

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TREATMENT OF CONGENITAL MEGACOLON IN 50 INFANTS

PEDIATRICS ◽

10.1542/peds.38.2.185 ◽

1966 ◽

Vol 38 (2) ◽

pp. 185-193

Author(s):

Walton K. T. Shim ◽

Orvar Swenson

Keyword(s):

Hirschsprung's Disease ◽

Hirschsprung’S Disease ◽

Average Weight ◽

Older Children ◽

The Past ◽

History Of ◽

Pull Through ◽

Definitive Surgery ◽

Criteria For Selection ◽

Selection Of

Fifty infants less than 1 year old with Hirschsprung's disease were treated at Children's Memorial Hospital in the past 6 years. Thirty-two of the 35 barium enema studies yielded "diagnostic" roentgenographic studies, and 3 were "negative" for Hirschsprung's disease. Fourteen of the 50 infants had a history of diarrhea. Enterocolitis in infants may be extremely rapid in onset and progression. It should be vigorously treated with rectal irrigations and intravenous fluids. Nineteen patients (38%) had aganglionic segments extending above the rectosigmoid colon, and eight (16%) were aganglionic proximal to the splenic flexure. This includes three patients with aganglionosis of the entire colon and one that was aganglionic from the jejunum to anus. Emphasis is placed on an aggressive combined attack by pediatrician, radiologist, pathologist, and surgeon to diagnose and prepare the sick infant as early as possible for colostomy or definitive abdominal-perineal pull-through operation. Twelve infants with an average weight of 12.5 lb were operated on primarily with no deaths or complications. It is our belief that definitive surgery can be done with greater ease in an infant than in older children, but careful selection and preparation of the patient and meticulous operative technique must be exercised. The important criteria for selection of infants for immediate resection are the absence of emaciation and enterocolitis, although the infant may be small. Twenty-six infants had colostomy and resection with no deaths or complications. Our raw mortality figures show 10 deaths in 50 patients (20%). There were 7 deaths in 47 surgical patients (15%).

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Evolution in the management of Hirschsprung’s disease in the UK and Ireland: a national survey of practice revisited

Annals of The Royal College of Surgeons of England ◽

10.1308/003588410x12771863936846 ◽

2011 ◽

Vol 93 (1) ◽

pp. 34-38 ◽

Cited By ~ 27

Author(s):

TJ Bradnock ◽

GM Walker

Keyword(s):

Hirschsprung's Disease ◽

Hirschsprung’S Disease ◽

Management Strategies ◽

Operative Strategy ◽

Clinical Scenarios ◽

Regional Service ◽

Pull Through ◽

Definitive Surgery ◽

The Uk ◽

Laparoscopic Assisted

INTRODUCTION The management of Hirschsprung’s disease continues to evolve. This questionnaire survey aimed to determine current surgical management strategies for Hirschsprung’s disease in Britain. SUBJECTS AND METHODS The survey was sent electronically to all British paediatric surgeons. Initial questions explored individual experience and regional service provision. Additional questions, reserved for surgeons who perform definitive Hirschsprung’s disease surgery, addressed specific clinical scenarios. RESULTS Surveys were sent to 142 surgeons yielding 85 responses. After exclusions, 64 surveys from 21 centres were analysed. Forty-seven respondents worked in centres with designated ‘Hirschsprung’s disease surgeons’. Forty respondents perform definitive Hirschsprung’s disease surgery. In a well neonate with left-sided Hirschsprung’s disease, 34 of 40 surgeons favour primary pull-through following bowel decompression with rectal washouts; 35 of 40 surgeons aim to perform definitive surgery at less than 3 months of age, with 17 favouring laparoscopic-assisted Soave–Boley and 15 favouring an open Duhamel pull-through. Of the 40 surgeons, 36 use a staged approach to right-sided/total colonic Hirschsprung’s disease with 23 favouring a Duhamel or Long Duhamel pull-through. CONCLUSIONS The primary pull-through, using an open Duhamel or laparoscopic-assisted Soave–Boley technique, during the first 3 months of life, has become the operative strategy of choice in rectosigmoid Hirschsprung’s disease in Britain. Marked variation in practice remains for right-sided Hirschsprung’s disease.

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COMPLICATIONS AFTER TRANSABDOMINAL SOAVE’S PROCEDURE IN CHILDREN WITH HIRSCHSPRUNG’S DISEASE

ABCD Arquivos Brasileiros de Cirurgia Digestiva (São Paulo) ◽

10.1590/0102-672020180001e1421 ◽

2019 ◽

Vol 32 (1) ◽

Author(s):

Shahnam ASKARPOUR ◽

Mehran PEYVASTEH ◽

Mohammad Hossein IMANIPOUR ◽

Hazhir JAVAHERIZADEH ◽

Saeed HESAM

Keyword(s):

Large Bowel ◽

Hirschsprung's Disease ◽

Hirschsprung’S Disease ◽

Bowel Function ◽

Congenital Disorder ◽

Function Score ◽

Frequent Complication

ABSTRACT Background: Hirschsprung’s disease is a congenital disorder that causes functional obstruction of large bowel. Aim: To evaluate complication and bowel function score of children with Hirschsprung’s disease who underwent transabdominal Soave’s procedure. Methods: In this study all the children with Hirschsprung’s disease who underwent transabdominal Soave procedure were evaluated regarding bowel function and complication of trans-abdominal Soave’s procedure. Results: Were enrolled 160 children. Enterocolitis and constipation were seen in 15% of the cases. Fecal incontinency was the least frequent study which was seen in 1% of the children. Conclusion: Constipation and enterocolitis was the most frequent complication following transabdominal Soave technique.

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Assessment of lower urinary tract function in children before and after Swenson's 'pull through' for Hirschsprung's disease

Journal of Indian Association of Pediatric Surgeons ◽

10.4103/0971-9261.33225 ◽

2007 ◽

Vol 12 (2) ◽

pp. 72

Author(s):

V Bhatnagar ◽

B Jindal ◽

VP Grover

Keyword(s):

Urinary Tract ◽

Lower Urinary Tract ◽

Hirschsprung's Disease ◽

Hirschsprung’S Disease ◽

Before And After ◽

Lower Urinary Tract Function ◽

Tract Function ◽

Pull Through ◽

Lower Urinary

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Profile of Hirschsprung’s disease cases diagnosed in tertiary care teaching hospital: a retrospective observational study

International Journal of Contemporary Pediatrics ◽

10.18203/2349-3291.ijcp20200678 ◽

2020 ◽

Vol 7 (3) ◽

pp. 551

Author(s):

S. Prabakaran ◽

K. Kasthuri Thilagam

Keyword(s):

Observational Study ◽

Hirschsprung's Disease ◽

Hirschsprung’S Disease ◽

Tertiary Care ◽

Disease Diagnosis ◽

Retrospective Observational Study ◽

Histopathological Study ◽

Full Thickness ◽

Colostomy Site ◽

Surgery Department

Background: To date, there are very few studies of Hirschsprung’s disease. Hence, the study was conducted to profile Hirschsprung’s disease in a tertiary care setting.Methods: This is a retrospective observational study that evaluated the admitted patients with Hirschsprung’s disease in the pediatric surgery department. Biopsy was taken from the patient in the form of the full thickness of intestine, seromuscular biopsy, resection from the colostomy site when doing closure and or appendix was taken and subjected to histopathological study with routine eosin and haematoxylin stain.Results: Among the study population, 21(28.8%) children were aged less than one month, and only 10(13.7%) were aged 11 years and above. There were 45(61.6%) participants were male and 28(38.4%) female. Most common biopsy site was appendix in 33(46.2%), followed by Ileum full-thickness biopsy in 6(8.2%) , Ileum Seromuscular biopsy in 5(6.8%%) ,Colon full-thickness biopsy in 4(5.6%) subjects. Among the 73 participants, 46(63%) were clinically suspected cases, and the remaining 27(36.9%) were clinically established cases. Among clinically suspected, the majority (50.7%) had ganglionic cells only in proximal segments.Conclusions: the Hirschsprung's disease diagnosis was established mostly in younger males.

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Validity of Barium Enema as Hirschsprung’s Disease Diagnostic Tools for Infant in Sanglah Hospital Denpasar

JBN (Jurnal Bedah Nasional) ◽

10.24843/jbn.2021.v05.i01.p03 ◽

2021 ◽

Vol 5 (1) ◽

pp. 16

Author(s):

I Made Darmajaya ◽

I Ketut Subhawa

Keyword(s):

Negative Predictive Value ◽

Barium Enema ◽

Diagnostic Tool ◽

Predictive Value ◽

Hirschsprung's Disease ◽

Hirschsprung’S Disease ◽

Total Sample ◽

Diagnostic Tools ◽

Cross Tabulation ◽

Sensitivity Specificity

Aim: To determine the validity (sensitivity, specificity, likelihood ratio) of barium enema as Hirschsprung's disease diagnostic tool in infants. Methods: This study was a diagnostic test of barium enema compared with postoperative histopathology examinations as the gold standard. The population were all patients with indigestion symptom be discovered at the pediatric surgical clinic of Sanglah Hospital Denpasar. The sampling method was consecutive sampling, satisfy inclusion criteria (< 12 months old, indicate classic symptoms of Hirschsprung’s disease). The total sample of the study was 52 patients. Sensitivity, specificity, positive and negative predictive value were analysed using cross-tabulation test of barium enema and postoperative histopathology. Results: A total of 52 patients were evaluated during the study period, mean of age was 3.31 months old, and boys:girls (75%:25%). Based on symptoms, 98.08% of patients were delayed release of meconium more than 24-48 hours and abdominal distention. Among all the patients reviewed, sensitivity, specificity, positive and negative predictive value of barium enema for diagnostic of Hirschsprung’s disease was 95.5%, 87.5%, 97.7%, and 77.8%. Conclusion: Barium enema can be used as an early diagnostic tool for infants suspected of Hirschsprung’s disease.

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