scholarly journals A Report of Incontinentia Pigmenti in an 11-year-old Girl

2021 ◽  
Vol In Press (In Press) ◽  
Author(s):  
Zahra Azarbayjani ◽  
Zahra Enshaei ◽  
Alireza Eshghi

Introduction: Incontinentia pigmenti (IP) is a rarely diagnosed x-linked dominant disease affecting tissues of ectodermal and mesodermal origin such as cutaneous tissues, teeth, eyes, hair, and the central nervous system. Dermatologic manifestations are often the first signs observed in patients diagnosed with IP and are present in nearly all the subjects, but they are less harmful and do not require treatment. Oral manifestations in patients diagnosed with IP might affect both the deciduous and permanent teeth, with tooth shape anomalies and hypodontia, delayed tooth eruption, cleft palate, and high arched palate. These oral abnormalities influence feeding, quality of life (QoL), and self-esteem of the patient but can be successfully corrected by oral rehabilitation. Case Presentation: Here, we report the case of a female patient, aged 11 years, presenting with dental manifestations such as hypodontia, conical teeth, delayed tooth eruption, narrow and atrophic dental ridge, and also some non-dental findings of IP. Her dental ‎management included oral hygiene instructions, extraction of all unrestorable primary molars, and composite filling of all primary canines. Conclusions: A removable space maintainer was constructed for the patient, which resulted in favorable esthetic outcomes, proper re-establishment of mastication, and improved self-esteem.

2020 ◽  
pp. 1-2
Author(s):  
Naseem. P ◽  
Firoz. A ◽  
Parvathy Suresh

Oligodontia is the congenital absence of six or more than six teeth in either permanent or primary dentition. Because of the missing teeth in these patient’s esthetic, functional and psychological problems may arise. Oral rehabilitation is recommended for the positive development of self-esteem as well as for improved speech, masticatory function and facial esthetics. Congenital absence of incisors may jeopardize the esthetic appearance of a child, especially during years of transition into adolescence. In such situations, interim restorations can be provided before any definitive treatment. This paper deals with the full mouth oral rehabilitation of an 11-year old child using a multidisciplinary approach involving acrylic crowns, 2*4 appliance, anterior functional space maintainer and direct composite restoration.


2020 ◽  
Vol 5 (1) ◽  
pp. 1-12
Author(s):  
Rey Bintang Pamungkas ◽  
Jeffrey .

Abstract. Introduction: The deciduous tooth period is an important period in child development. Premature loss of deciduous teeth is defined as the loss of deciduous teeth before they approach the eruption of permanent teeth. The prevalance of premature loss offered in several studies obtained was between 4.3% and 42.6%. Method: An 10 years-old-boy accompanied by her mother came to RSGMP Unjani, complaints of lower right nack teeth missing because they have to extracted since 3 mouth ago. Tooth have been extracted because of caries. Result: Result of clinical examination was found premature loss teeth 75, 74, and 85. The space in Moyers analysis was +0.2 mm in region 3 and +0.1 mm in region 4. Patient was treated with a fungsional removable-space-maintainer on teeth 75, 74, and 85. Conclusion: The results of premature loss is excess space in the arch, so to prevent further occlusion abnormalities in child’s growth and development process, we need a special appliance that is used to protect the space due to premature loss of deciduous teeth. Keywords: Premature loss, space maintainer, deciduous teeth


2019 ◽  
Vol 10 (2) ◽  
pp. 91-96
Author(s):  
Silvane Silva Evangelista ◽  
Juliana Arid ◽  
Katia Regina Felizardo Vasconcelos ◽  
Giuseppe Valduga Cruz ◽  
André Luiz Tannus Dutra ◽  
...  

Background and Aims: Animal models have been demonstrating that MMPs have an important function in the tooth eruption process. The aim of this study was to evaluate the association between genetic polymorphisms in MMP8 and MMP13 and delayed tooth eruption of permanent teeth. Materials and Methods: This cross-sectional study selected 216 children, 9- to 12-year-old, from public schools at Manaus, Amazonas, Brazil. During oral clinical examination, each permanent tooth emerged in the oral cavity was evaluated. Children were considered with delayed tooth eruption when at least one permanent tooth was delayed and were classified in 2 groups: children “with delayed tooth emergency” and “without delayed tooth emergency.” Saliva samples were collected from DNA extraction. The genetic polymorphisms rs17099443 and rs3765620 in MMP8, and rs478927 and rs2252070 in MMP13 were genotyped. Statistical Analysis: PLINK V1.07 ( http://pngu.mgh.harvard.edu/purcell/plink/ ) and GraphPad Prism 5.0 (San Diego, CA, USA) were used. The c2 or Fisher exact test was used to calculate genotypes and alleles distributions. To compare the mean number of delayed teeth according to genotypes, the Kruskal-Wallis test with multiple comparison Dunn test was used. The established alpha for all comparisons was .05. Results: The polymorphism rs17099443 in MMP8 was associated with delayed tooth eruption in the genotype distribution ( P = .05). In the allele distribution, the C allele was underrepresented in children with delayed tooth eruption ( P = .01; OR = 0.61, 95% confidence interval, 0.41–0.9). Conclusion: The genetic polymorphism rs17099443 in MMP8 is associated with delayed tooth eruption.


2004 ◽  
Vol 27 (2) ◽  
pp. 133-136 ◽  
Author(s):  
Angela Scarparo Caldo-Teixeira ◽  
Regina Maria Puppin-Rontani

Hypodontia is characterized by partial or total congenital missing of one or more teeth, on one or both dentitions. Heredity is the main etiological factor and the principal clinical features are reduction on number, size and form of teeth, and late eruption. Removable partial prosthesis, fixed prosthesis, overdentures and adhesive prosthesis are alternative treatments, and the indication is type dependent. The aim of this study was to describe the clinical case of an eleven-year-old child with eight missing permanent teeth of idiopathic etiology.The patient had facial and skeletal symmetry, normal development and was not related to any syndrome. Clinical characteristics: permanent teeth with good periodontal conditions (16, 12, 11, 21, 22, 26, 36, 31, 42, 46), primary teeth (53, 63, 64, 73, 83); overbite and microdontia on teeth 12 and 22. The treatment plan was done initially by documenting of the case for teeth analysis (study casting models, periapicals and panoramic x-rays, and photographs), and followed by the exodontics of teeth 73 and 83.A removable appliance in autocured acrylic resin, using teeth in acrylic for maintenance of functional space and occlusion was planned and carried out.An anterior track for vertical dimension gain was used because of his accentuated overbite. The patient will be monitored until the end of the craniofacial growth, when it will be again evaluated and forwarded for the final oral rehabilitation. Hypodontia diagnosis and management should be performed as early as possible not to interfere with the craniofacial development of the child.


2013 ◽  
Vol 9 (1) ◽  
Author(s):  
Parampreet Pannu ◽  
Virat Galhotra ◽  
Pooja Ahluwalia ◽  
Ramandeep Singh Gambhir

Objective: Tooth agenesis is one of the most common congenital anomalies seen in humans. Although ab¬sence of one or more teeth is common, absence of multiple teeth is rare. Oligodontia is a rare developmental anomaly, involving agenesis of six or more permanent teeth, excluding the third molars. The reported preva¬lence of oligodontia in permanent dentition is 0.14%. Oligodontia can be presented as an isolated condition or as a part of a syndrome. Discussion: The present case report highlights a unique case of non-syndromic oligodontia, with agenesis of four permanent incisors, left permanent canine and right second premolar in the mandibular arch and its management with a novel fixed functional prosthetic appliance. Conclusion: Prosthetic rehabilitation is an urgent need for these kind of patients so that they do not suffer from mastica¬tory and esthetic problems which can eventually lower the self esteem of individuals.


1973 ◽  
Vol 52 (6) ◽  
pp. 1202-1208 ◽  
Author(s):  
Gerald Orner

Eruption constants for the permanent dentition were determined in 212 mongoloid children and 124 of their unaffected sibs. Eruption of the permanent teeth in sibs was like that of other normal children. Mongoloid children resembled their sibs in general characteristics of tooth eruption, but showed a consistent tendency toward later mean ages of eruption for each tooth type.


2013 ◽  
Vol 37 (4) ◽  
pp. 411-413
Author(s):  
M Nishiguchi ◽  
K Satoh ◽  
Y Kamasaki ◽  
T Hoshino ◽  
T Fujiwara

The dental management of an 8-year-old girl with osteopathia striata with cranial sclerosis (OS-CS) is described. The girl presented with various oral abnormalities. The aim of this case report was to describe in detail the dental findings in a patient with OC-CS and the precautions to be taken when planning treatment. In the present case, many dental anomalies, such as delayed eruption of the permanent teeth, obliteration of the dental pulp, short roots, fused roots and taurodontism, were detected. In patients with OS-CS, routine dental care from an early stage is recommended to manage this anomaly properly.


2013 ◽  
Vol 2013 ◽  
pp. 1-4 ◽  
Author(s):  
Sophie Ronceray ◽  
Juliette Miquel ◽  
Antoine Lucas ◽  
Gérald E. Piérard ◽  
Trinh Hermanns-Lê ◽  
...  

Ehlers-Danlos syndrome type VIII (EDS-VIII) is a very rare autosomal dominant disease characterized by early-onset periodontitis associated with features of Ehlers-Danlos syndrome. We report a 32-year-old man whose chronic leg ulcer led to the diagnosis of EDS-VIII. He had severe periodontitis with complete loss of permanent teeth and skin fragility with thin skin, atrophic scars, and brownish atrophic pretibial plaques. Leg ulcer is not a prominent feature of EDS-VIII. We suggest adding EDS-VIII to the list of rare diseases accounting for chronic leg ulcers, if this case report prompts others to report leg ulcers associated with EDS-VIII.


Sign in / Sign up

Export Citation Format

Share Document