scholarly journals A case of Fabry disease followed up for a long time from a neuro-otological point of view

2021 ◽  
Vol 80 (4) ◽  
pp. 277-284
Author(s):  
Tomoe Yoshida ◽  
Masahiko Yamamoto ◽  
Mitsuya Suzuki

2014 ◽  
Vol 29 (2) ◽  
pp. 271-279 ◽  
Author(s):  
Mikko Tuominen ◽  
Hannu Teisala ◽  
Janne Haapanen ◽  
Mikko Aromaa ◽  
Jyrki M. Mäkelä ◽  
...  

Abstract Superhydrophobic nanoparticle coating was created on the surface of board using liquid flame spray (LFS). The LFS coating was carried out continuously in ambient conditions without any additional hydrophobization steps. The contact angle of water (CAW) of ZrO2, Al2O3 and TiO2 coating was adjusted reversibly from >150° down to ~10−20° using different stimulation methods. From industrial point of view, the controlled surface wetting has been in focus for a long time because it defines the liquid-solid contact area, and furthermore can enhance the mechanical and chemical bonding on the interface between the liquid and the solid. The used stimulation methods included batch-type methods: artificial daylight illumination and heat treatment and roll-to-roll methods: corona, argon plasma, IR (infra red)- and UV (ultra violet)-treatments. On the contrary to batch-type methods, the adjustment and switching of wetting was done only in seconds or fraction of seconds using roll-to-roll stimulation methods. This is significant in the converting processes of board since they are usually continuous, high volume operations. In addition, the creation of microfluidic patterns on the surface of TiO2 coated board using simple photomasking and surface stimulation was demonstrated. This provides new advantages and possibilities, especially in the field of intelligent printing. Limited durability and poor repellency against low surface tension liquids are presently the main limitations of LFS coatings.



Acta Juridica ◽  
2021 ◽  
Vol 2021 ◽  
pp. 85-106
Author(s):  
J Barnard-Naudé

This paper is a response to Dale Hutchison’s recent arguments about the role of fairness in contract law after the Constitution. From the point of view of transformative constitutionalism, the paper argues that the fairness ‘debate’ in the South African law of contract should be approached as what it so patently is, namely, as evidence of a deep ideological conflict that has existed in our law of contract for a very long time, and that this debate now exists within the context of a larger debate about the appropriate transformative reach of the Constitution. The argument takes the form of two ‘dangerous supplements’ to Hutchison’s discourse. The first of these supplements contends that indeterminacy is a symptom of the common law itself, rather than a result of contract law’s contact with the Constitution. The second dangerous supplement suggests a responsible judicial engagement with bona fides and ubuntu, one that can exploit the strengths of both the common law and the Constitution and that understands good faith and ubuntu to be ‘inter-linking’ constitutional values that should be enlisted in unison or at least in resonance when it comes to the question of fairness in our contemporary law of contract. In conclusion, I offer a reading of Hutchison’s own politics of contract law and contend that his is an altruistic politics committed to the standard form. I contend that this politics of contract law is consistent with a transformative understanding of the post-apartheid legal order. ‘Law, like every other cultural institution, is a place where we tell one another stories about our relationships with ourselves, one another, and authority. In this, law is no different from the Boston Globe, the CBS evening news, Mother Jones, or a law school faculty meeting. When we tell one another stories, we use languages and themes that different pieces of the culture make available to us, and that limit the stories we can tell. Since our stories influence how we imagine, as well as how we describe, our relationships, our stories also limit who we can be’.



2016 ◽  
Vol 1 (1) ◽  
pp. 109-126
Author(s):  
Drance Elias da Silva

This Article may be situated within the rapport field between Philosophy and Social Sciences, at the search regarding to the concept concerning the Representation. Regarding to Philosophy, under a general view, the concept, concerning Representation, has been, since a long time, understood as a trail which one would get througl reaching to the real and true ones. Representation, as the thought contents expression form had not been known departing from Philosophy as a barrier against the objectivity concerning the knowledge. Representation, in its source, has been constituting itself a cognictive, inmanent reflection, related to the conscience inner subjectivity. But departing from the episthemological point of view, it has been not so easy for the campus concerning the Culture Sciences as a totality. In the theory regarding to knowledge, the Social Sciences campus and, more specifically, in the human life Symbolic dimension constitutive aspects, it has been, often, accepted negatively as an entry door for the histotical social reality. Nowadays, one may conclude that the contents concerning the Culture are deeply rooted within the histotical reality, which may present new dimension the reading regarding to the Symbolical side concerning the human life, under the view regarding to the unseen aspect, such as the intellectualistic Western dominant Culture allows understanding the way which could be in.



2020 ◽  
Vol 16 (2) ◽  
pp. 47-56
Author(s):  
F. A. Asadullin

The problem of disintegration of the Islamic Ummah a long time ago became the one of the most important for the Islamic world and worldview. The wave of violence in the Near and Middle East sharpened some regional conflicts, which have already taken place before. The paper deals with the roots of this conflict atmosphere in the Early Islamic period. As the tradition affirms, the Prophet Muhammad predicted the Ummah to split in 73 sects. Today there exist in any case not less than 73 different Islamic schools, movements and organizations, which mutually and constantly contest their doctrinal authenticity. Moreover, the activity of quasi- Islamic extremist organisations like the ISIS, which is forbidden inside as well as outside the Russian Federation, is quite remarkable. All these factors demonstrate, that from the academic point of view it is actual to critically research the nature of fragmentation and disintegration of Islamic communities through the prism of prophetic legends. This paper is to consider as an attempt to resolve this multidimensional problem.



2013 ◽  
Vol 30 ◽  
pp. 89-101 ◽  
Author(s):  
Ferdy Hubers ◽  
Helen de Hoop

Dutch prescriptive grammar rules dictate that the complementizer dan ‘than’ should be used in comparative constructions of inequality. This has been an issue for grammarians from the sixteenth century onwards when als ‘as’ started to be used as an alternative form in this type of context. In order to find out why and when people choose one comparative marker over the other, we examined the use of these markers in the Spoken Dutch Corpus (CGN). We found that the use of dan is overall more common than als in comparative constructions of inequality, even though from a linguistic point of view als might be favoured. The choice between als and dan turns out to be strongly correlated with the level of education. Although this factor has been assumed to be of influence for a long time, as far as we know it has never been quantitatively tested before. We conclude that the effect of the level of education we found reflects the strong influence of the prescriptive rule taught in schools, repressing the use of als in comparatives of inequality.



2019 ◽  
Vol 2 (8(38)) ◽  
pp. 28-30
Author(s):  
Ната Бердзули

The narrative dates from a long time ago and the subject of its research was to study fundamental principles of narration.It is so old that the ideas of its structure have been developed in the ancient times. The etymology of the term "narrative", is derived from the Latin and its meaning is narration. This term was emerged in the literary studies as a result of novelist works by Roland Bart, Claude Bremann, Cvetan Todorov and others. In the twentieth century, many theories were created about the narrative, and in the same century, the main analytical components of narrative - story, sound, time, point of view, character, role were established.Narrative can be considered as a feature of postmodernism, because narrative sources take special significance in postmodernism.While researching modern literature a significant function is given to the variety of narrative usages. The aim of the theme is to research the narrative function on the basis of comparative analysis of Aka Morchiladze's creative works.Aka Morchiladze's novels are filled with familiar literary or historical motives, acting people, stories, but itcreates a different reality through narrative or literary plays.The author creates a narrative text based on literary texts and "historical information". Historical information that is used in the text does not correspond to reality, and we, the readers, think that we are about to learn “historical novel” and the narrator is a historian,-not a novelist. Finally, we realize that we deal with the "fake history", allusion of writer's fantasy and literary and historical facts. Therefore, with regards of the presented issues, it is necessary to take into consideration the specificity of postmodern literature and peculiarities of realization of this specificity in Georgian reality. Narrative sources are of particular importance in postmodernism, which is one of the most important elements of the study of the text to be analyzed.



Learning takes place if there is a repeat of stimuli, or otherwise, extinction occurs, which is forgetting. To make the consumers learn the product and not lose sight for a long time is a primary focus for marketers. It means that marketers are more concerned about individuals' information storage and retrieval process. This chapter discusses the information-processing system, parts of this system, and forgetting as well as memorizing. At the end of the chapter, memory is evaluated from the point of view of marketing.



Author(s):  
Torbjörn Tännsjö

The maximin/leximin theory is applied in real medical life. The general result, in relation to any welfare state assuming its global obligations, is that more resources ought to be directed to the care and cure of people suffering from mental illness; less should be spent on marginal life extension (especially among elderly patients).The urgency of mental health, when the matter is assessed from the point of view of the maximin/leximin theory, has to do with the fact that people often suffer for very long time from mental disease rendering it plausible to assume that many people in this category garner throughout their lives a net deficit in terms of happiness. Hence they are the patients who are worst off. The problem with marginal life extension among elderly patients has to do with the fact that many among them have throughout their long lives already garnered a lot of happiness. Now these people have to stand back when there is fierce competition for available medical resources.



2019 ◽  
Vol 105 ◽  
pp. 04035
Author(s):  
Oleg Mazavin ◽  
Mikhail Kaz ◽  
Irina Roshchina

The article presents the results of the analysis of the practice of implementation the concept of universal basic income. It is shown that in estimating the results of a series of experiments in this field, conducted in a number of countries, it is recommended to abandon the approach based on the positivist point of view. For a long time, it dominated science in general and economic research in particular, but it continues to influence many researchers today. This conclusion should be taken into account in the formation of the structure and composition of regions’ welfare indices. The research materials are placed in a broad historical context. On the one hand, this made it possible to more vividly present the prerequisites, characteristics and consequences of repeated attempts to introduce universal basic income into the practice of social insurance, undertaken in different countries of the world (Finland, Canada, Kenya, Iran, India, USA). On the other hand, to reveal the possibilities and problems of using universal basic income as a tool to help overcome the dysfunctional development of certain territories, including mining regions.



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