scholarly journals Medical genetic study of the Republic of North Ossetia Alania. II. Nosological spectrum of hereditary pathology in three districts

2020 ◽  
pp. 10-18
Author(s):  
З.К. Гетоева ◽  
В.В. Кадышев ◽  
М.Ю. Джаджиева ◽  
В.А. Галкина ◽  
А.В. Перепелов ◽  
...  
Keyword(s):  
Russian Federation ◽  
Sensory Neuropathy ◽  
Epidemiological Studies ◽  
Hereditary Diseases ◽  
Research Centre ◽  
Federal State ◽  
Dominant Type ◽  
The Russian Federation ◽  
The Republic ◽  
North Ossetia

Представлен нозологический спектр моногенных наследственных болезней (МНБ) в трех районах Республики Северная Осетия Алания (РСОА) - Правобережном, Ардонском и Кировском, общей численностью 119 590 человек. Обследовано все население районов по протоколу генетико-эпидемиологических исследований (разработка ФГБНУ «МГНЦ»), выявлено и диагностировано 600 пациентов (из 418 семей) с различными МНБ. Всего выявлено 135 нозологических форм - 65 с аутосомно-доминантным типом наследования (АД), 57 с аутосомно-рецессивным (АР) и 14 с Х-сцепленным (Х-сц.). Определены распространенность заболеваний, частые и редкие нозологические формы. Проведено сравнение нозологического спектра и распространенности отдельных МНБ с таковыми в ранее обследованных популяциях европейской части России. Выявлены особенности разнообразия МНБ. Более высокие значения распространенности, чем в других популяциях РФ выявлены синдром Элерса-Данло, миотоническая дистрофия, несиндромальная умственная отсталость с различными типами наследования, различные формы пигментного ретинита и др. Ряд заболеваний, частых в обследованных регионах РФ, наоборот, встречались реже - вульгарный ихтиоз, нейрофиброматоз, наследственная моторно-сенсорная нейропатия и ихтиозиформная эритродеремия. In this article we present the nosological spectrum of monogenic hereditary diseases (MHD) in three districts of the Republic of North Ossetia - Alania (RNOA) - Pravoberezhny, Ardonsky and Kirovsky, with a total population of 119,590 people. The entire population of the districts was examined according to the Protocol of genetic and epidemiological studies (developed by the Federal state budgetary Research Centre for Medical Genetics), 600 patients (from 418 families) with various NBS were identified and diagnosed. We identified 136 nosological forms of MHD - 65 with autosomal dominant type of inheritance (AD), 57 with autosomal recessive (AR) and 14 with X-linked (X-lin.). We determine the prevalence of diseases, frequent and rare nosological forms. The nosological spectrum and prevalence of individual MHD were compared with previously surveyed populations in the European part of Russia: Kirov, Kostroma, Arkhangelsk, Tver, Bryansk, Rostov regions, Krasnodar territory and the Republics of Karachay-Cherkessia, Adygea, Tatarstan, Bashkortostan, Mari El, Udmurtia and Chuvashia. Features of the MHD diversity are revealed. With higher prevalence values than in other populations of the Russian Federation, Ehlers-Danlo syndrome, myotonic dystrophy, non - syndromic mental retardation with various types of inheritance and various forms of retinitis pigmentosa, etc. A number of diseases that are frequent in the Russian Federation have shown on the contrary lower prevalence values - vulgar ichthyosis, neurofibromatosis, hereditary motor-sensory neuropathy and ichthyosiform erythroderemia.

ORGANIZATION OF THE ACTIVITIES OF THE TAX CONTROL BODIES ON IDENTIFICATION AND PREVENTION OF EVASION FROM THE PAYMENT OF TAXES (ON THE EXAMPLE OF THE REPUBLIC OF NORTH OSSETIA – ALANIA)

2021 ◽  
Vol 2 (5) ◽  
pp. 62-68
Author(s):  
O. T. KOZAEVA ◽  
◽  
A. N. BOLOTAEVA ◽  
D. V. GOGICHAEVA ◽  
◽  
...  
Keyword(s):  
Russian Federation ◽  
Tax Evasion ◽  
Economic Security ◽  
Tax System ◽  
Economic Problems ◽  
Highly Efficient ◽  
Strong State ◽  
The Russian Federation ◽  
The Republic ◽  
North Ossetia

The article is devoted to the study of the features of the organization of control over tax evasion (on the example of the Republic of North Ossetia-Alania). The main dangers for the tax system of the Russian Federation are identified. It is concluded that the efficiency of the state's tax system is one of the main indicators of its economic security. A highly efficient tax system with a well-established mechanism of tax control is a mandatory component in the formation of a strong state characterized by sovereignty, independence, the ability to defend itself and the means to solve socio-economic problems.

REGIONAL CHARACTERISTICS OF PEPTIC ULCER IN THE REPUBLIC OF MORDOVIA

2019 ◽  
pp. 42-49
Author(s):  
E.I. Polozova ◽  
I.E. Trokhina ◽  
O.G. Radaykina
Keyword(s):  
Peptic Ulcer ◽  
Russian Federation ◽  
Gastroduodenal Ulcer ◽  
High Rate ◽  
Morbidity Rate ◽  
Federal State ◽  
Common Disease ◽  
Regional Characteristics ◽  
The Russian Federation ◽  
The Republic

The purpose of the work is to analyze the incidence of gastroduodenal ulcer in the Republic of Mordovia in 2008–2017, and to give regional medical and social assessment of the pathology. Materials and Methods. The authors analyzed the data of the Scientific Research Institute for Organization and Informatization of Healthcare of the Ministry of Health and Social Development of the Russian Federation and the Regional office of the Federal State Statistics Service in the Republic of Mordovia on the incidence of peptic ulcer disease in the Republic of Mordovia between 2008 and 2017. Results. The paper shows that in the Republic of Mordovia gastroduodenal ulcer is a common disease. The overall morbidity rate in the Republic of Mordovia in 2008–2017 was lower than in the Russian Federation, but it was one of the highest among the Volga region districts. The highest rates of overall morbidity rate of gastroduodenal ulcer were observed among the population of the Chamzinsky, Ichalkovsky, Torbeevsky and Tengushevsky districts. Between 2008–2017, the level of primary morbidity among the population of Mordovia as a whole was lower than the average rate in the districts. The highest rates of primary morbidity of the population were in the Ichalkovsky district of the Republic of Mordovia. Due to the current situation in the Republic of Mordovia, namely, the high rate of gastroduodenal ulcer, it is necessary to look for ways to solve the problem by means of systemic preventive measures. Such measures can influence social and psychological aspects of health of the entire population. Conclusions. Analysis of gastroduodenal ulcer rate in the Republic of Mordovia in 2008–2017 demonstrates the necessity of comprehensive target republican program on the reduction of the disease level, improvement of clinical examination as well as therapeutic and diagnostic measures aimed at increasing patients’ compliance during treatment and improving the quality of their life. Keywords: peptic ulcer, incidence, regional characteristics. Цель работы – провести анализ заболеваемости язвенной болезнью желудка и двенадцатиперстной кишки населения Республики Мордовия за 2008–2017 гг. и дать региональную медико-социальную оценку данной патологии. Материалы и методы. Проанализированы данные ФГУ «ЦНИИ организации и информатизации здравоохранения Минздравсоцразвития России» и территориального органа Федеральной службы государственной статистики по Республике Мордовия по заболеваемости язвенной болезнью в Республике Мордовия с 2008 по 2017 г. Результаты. В работе показано, что язвенная болезнь желудка и двенадцатиперстной кишки в Республике Мордовия является распространенным заболеванием. Уровень общей заболеваемости населения в Республике Мордовия в 2008–2017 гг. ниже, чем в РФ, но является одним из самых высоких среди регионов Приволжского округа. Наиболее высокие показатели общей заболеваемости язвенной болезнью желудка и двенадцатиперстной кишки всего населения отмечаются в Чамзинском, Ичалковском, Торбеевском и Теньгушевском районах. Уровень первичной заболеваемости всего населения по Мордовии в целом в течение 2008–2017 гг. был ниже, чем в среднем по районам. Наиболее высокие показатели первичной заболеваемости всего населения – в Ичалковском районе Республики Мордовия. В связи со сложившейся в Республике Мордовия ситуацией, а именно из-за высокой заболеваемости населения язвенной болезнью желудка и двенадцатиперстной кишки, необходимо искать пути решения данной проблемы на базе системных мер профилактики. Подобные меры способны оказать влияние на социальные и психологические аспекты здоровья всего проживающего населения. Выводы. Анализ заболеваемости язвенной болезнью желудка и двенадцатиперстной кишки в Республике Мордовия за 2008–2017 гг. демонстрирует целесообразность создания комплексной целевой республиканской программы по снижению уровня заболеваемости, совершенствованию организации диспансеризации, лечебных и диагностических мероприятий, направленных на увеличение комплаентности при проведении лечения и улучшение качества жизни пациентов. Ключевые слова: язвенная болезнь, заболеваемость, региональные особенности.

scholarly journals HISTORICAL NATURE OF MIGRATIONS IN THE REPUBLIC OF MORDOVIA

2020 ◽  
Vol 1 (4) ◽  
pp. 174-181
Author(s):  
Lyudmila I. Nikonova ◽  
Albina I. Minakova
Keyword(s):  
Russian Federation ◽  
Historical Analysis ◽  
Federal District ◽  
Federal State ◽  
Central State ◽  
Industrial Enterprises ◽  
The Russian Federation ◽  
The Republic ◽  
State Archives ◽  
Historical Nature

According to the Constitution of Russia, the Russian Federation is a federal state and consists of 85 equal subjects, which are characterized by a high degree of diverse conditions and the state of social and economic development. As an object of research of migration processes, the authors considered Mordovia, included in the Russian Federation on the rights of an autonomous republic in 1936. This region of the Volga Federal District is one of the important subjects of the Russian Federation, as it is endowed with extensive areas, developed industry, good ecology, hundreds of museums; it is characterized by a multi-ethnic population structure. The authors consider the main characteristics of spatial mobility of the Mordovian Territory population from the second half of the 19th century to the beginning of the 20th century. The main tendencies of migration processes development are described. Much attention is paid to the historical nature of migration, based on scientific research and state statistics. Formation of polyethnicity of the Mordovian Republic developed historically due to different factors and events. Events of the Second World War, which provoked refugee from Western countries to the regions of Russia, location of camps with war prisoners in the territory of the Republic, industrialization and development of industrial enterprises, which required an influx of foreign specialists and workers in imported equipment maintenance, job placement after graduation from higher educational institutions of the USSR fraternal countries, the change of social status: admission of international students, interethnic marriages. The factors of adaptation of displaced persons in the aspect of socio-cultural interaction with local residents in the Republic of Mordovia are of particular importance. The multifaceted study of polyethnicity in the Mordovian Republic actualizes the historical analysis, which shows the role played by the representatives of foreign peoples in forming the polyethnicity of the region, for which the authors provide statistical data of the All-Union censuses of the population of 1959, 1970 and 1979, the All-Russian census of 2002 and 2010, as well as archival materials, which are located in the Central State Archives of the Republic of Mordovia.

scholarly journals Constitutional and legal status of a federal subject in the Republic of Iraq and in the Russian Federation: a comparative legal study

2021 ◽  
Vol 118 ◽  
pp. 02020
Author(s):  
Waleed Taha Akram Toghramchy ◽  
Nahro Khasro Hussein
Keyword(s):  
Russian Federation ◽  
Legal Status ◽  
Federal State ◽  
Legal Research ◽  
Legal Norms ◽  
Division Of Powers ◽  
Study Results ◽  
The Russian Federation ◽  
The Republic ◽  
The Comparative Study

The constitutional and legal status of subjects of various federations is the issue considered by many scientists, but the area of comparative legal research remains poorly studied. The article considers the basics and features of the constitutional and legal status of the subjects of two federations that are at the stage of formation as democratic and legal states: the Russian Federation and the Federal Republic of Iraq. The purpose of the comparative study is to identify common and different elements of the constitutional and legal status of the subjects of two states and to identify on their basis a model of the constitutional and legal status of a subject of a modern, democratic, and rule-of-law state. The work is based on the comparative-legal research method. The study reveals differences in the ways of achieving the goal of building a federal state in the Russian Federation and in the Republic of Iraq. It also determines the foundations and features of the constitutional and legal status of the subjects of the two federations. The analysis of the main constitutional and legal norms establishing the procedure for the division of powers between federal and regional state authorities is carried out. The study results allow concluding that it is necessary to amend the constitutional legislation of the Republic of Iraq in order to expand the constitutional and legal status of the subjects and improve federal relations within the country.

scholarly journals SEGMENTATION OF TERRITORIES OF THE REPUBLIC OF BASHKORTOSTAN ON THE LEVEL OF MORTALITY FROM MALIGNANT NEOPLASMS

2019 ◽  
Vol 63 (1) ◽  
pp. 4-13
Author(s):  
P. A. Askarov ◽  
A. O. Karelin ◽  
I. A. Lakman ◽  
L. F. Rozanova ◽  
Zagira F. Askarova
Keyword(s):  
Cluster Analysis ◽  
Russian Federation ◽  
Malignant Tumors ◽  
Mortality Rates ◽  
Federal State ◽  
Malignant Neoplasms ◽  
Actual Problem ◽  
Republic Of Bashkortostan ◽  
The Russian Federation ◽  
The Republic

Malignant neoplasms are an actual problem due to their high prevalence, high level of disability, tendency to increase. The purpose of the study is the segmentation of the territories of the Republic of Bashkortostan (RB) by the level of mortality from malignant neoplasms (MN) as a whole by municipalities, as well as by gender and by localizations of malignant neoplasms. Material and methods. The data of official statistics of the Territorial body of the Federal State Statistics Service of the Republic of Belarus (Table C 51), Rosstat were analyzed. The study was conducted using k-means cluster analysis and rating, implemented in the Statistica system. Results. There is a significant increase in the death rate of the entire population of ZN in 41 municipalities. Analysis of standardized mortality rates shows that the mortality rate per 100 thousand of the population in the Republic of Belarus is lower than similar indicators in the Russian Federation. The exception is mortality in esophageal cancer, which is higher in both men and women than in the Russian Federation. It has been established that the regions of the fourth and fifth clusters are unfavorable in terms of mortality from MN. Discussion. Revealed a pronounced uneven distribution of the territory of the Republic of Belarus with a tendency to an increase in mortality from MN in many territories. It is possible that the main reasons for the increase in mortality rates are worsening socio-economic conditions, lower living standards, increased chemical stress in urbanized areas (air pollution), as well as insufficient promotion of healthy lifestyles among the population, preventive knowledge, and health problems. care, its poor quality. Conclusion. As a result of the analysis, it was possible to establish that cluster analysis allows us to identify areas that have similar problems related to the level and trends of mortality from malignant tumors.

scholarly journals About illegality determination of the validity of evidence through forensic examination. Information letter.

2016 ◽  
Vol 6 (3) ◽  
pp. 61-78 ◽  
Author(s):  
S.A. Smirnova ◽  
E.V. Makushkin ◽  
A.Ya. Asnis ◽  
E.V. Vaske ◽  
E.G. Dozortseva ◽  
...  
Keyword(s):  
Russian Federation ◽  
Video Recording ◽  
Associate Professor ◽  
Research Centre ◽  
Professional Activity ◽  
Federal State ◽  
Video Footage ◽  
Scientific Principles ◽  
The Russian Federation ◽  
Deputy General Director

This letter prepared in connection with a growing number of complaints of investigators and making decisions on the appointment of psychological examination of the credibility of the video recording of interrogations and dictated by the need to arrange expert practice on the study of video footage of carrying out certain investigative actions with various actors in the criminal process. The newsletter discusses the purpose of such examinations and grounds the studies, in accordance with scientific principles of professional activity of experts. The letter was prepared under the supervision of the Director of the FBI, Federal center of forensic expertise under the Ministry of justice of Russia, doctor of legal Sciences, Professor, honored lawyer of the Russian Federation, honorary worker of justice of Russia of S. A. Smirnova, Deputy General Director for science of Federal State Budgetary Institution "V. Serbsky Federal Medical Research Centre for Psychiatry and Narcology" of the Ministry of Healthcare of the Russian Federation, doctor of medical Sciences, Professor E. V., Makushkina (doctor of juridical science A. Ya. Asnis, doctor of psychological Sciences, Vaske E. V., doctor of psychological Sciences, Professor E. G. Dozortseva, doctor of psychological Sciences, Professor F. S. Safuanov, PhD, associate Professor S. N. Shishkov, PhD, Professor S. S. Shipshin, PhD, associate Professor D. S. Oshevsky, PhD V. Berdnikov, PhD, associate Professor T. N. Sekerazh, PhD A. N. Kalinin. For investigators, judges, prosecutors, heads of Federal budgetary establishments of the Ministry of justice, judicial psychologists. For investigators, judges, prosecutors, heads of Federal budgetary establishments of the Ministry of justice, judicial psychologists.

scholarly journals Forecast of the birth rate and prevalence of the population of subjects of the Russian Federation from the position of assessment of their reproductive potential

2021 ◽  
Vol 65 (6) ◽  
pp. 507-513
Author(s):  
Ravil U. Khabriev ◽  
Elmira N. Mingazova ◽  
Vasil B. Ziatdinov ◽  
Ulyana M. Lebedeva ◽  
Tatyana N. Shigabutdinova ◽  
...  
Keyword(s):  
Russian Federation ◽  
Birth Rate ◽  
Reproductive Potential ◽  
Adult Child ◽  
Morbidity Rate ◽  
Federal State ◽  
Late 20Th Century ◽  
The Russian Federation ◽  
The Republic ◽  
Predicted Values

Introduction. At present, negative trends in medical and demographic indicators continue to persist in the regions of the Russian Federation, which is seen as a consequence of a decrease in the number of young people due to the demographic “hole” of the late 20th century and an increase in the incidence of the population, especially adolescence. Therefore, to develop programs for the formation and protection of the population’s reproductive health, it is of no small importance to identify the patterns of morbidity rates in the population to determine the reproductive potential of the constituent entities of the Russian Federation. Purpose. Study the trend of population morbidity, assessment of the relationship and medium-term predicted values of the birth rate and incidence of the population of certain constituent entities of the Russian Federation to assess their reproductive potential. Material and methods: statistical materials of the Federal State Statistics Service (Rosstat) in the sections “Demography” and “Healthcare”. The analysis of the dynamics of birth rate indicators and morbidity of the population was carried out. Predictive models for fertility and morbidity of the population were built based on one-factor linear regression, where the birth rate was taken as the dependent variable, and the primary morbidity was taken as the independent variable. Results. The article presents a dynamic analysis of the birth rate, the morbidity rate of the adult, child and adolescent population in four studied territories: the Republic of Tatarstan, Sakha (Yakutia), Dagestan and the Kostroma region. It was revealed that in all regions, there is a decrease in fertility rates, starting from 2014-2015. Conclusion. Based on regression models, a forecast of the birth rate was compiled, which shows that if the existing trends continue, by 2024 relative to 2018, there will be a decrease in the birth rate in the Republic of Sakha (Yakutia) by 1.2 per 1,000 population, in the Republic of Dagestan - by 0.6 per 1,000 people, in the Kostroma region - by 0.5 per 1,000 people. However, in the Republic of Tatarstan, the indicator is forecasted to be higher than in 2018 - by 0.6 per 1,000 people.

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